Treatment of severe Parkes Weber syndrome with flexion contracture of the lower limb

SummaryVascular malformations are difficult to treat, especially in cases with fast-flow arteriovenous fistulae. We herein present a case of severe Parkes Weber syndrome of the right lower limb, complicated by progressive heart failure and limb ischemia, eventually necessitating hip disarticulation. Vascular control was achieved with suture ligation of the right common iliac artery at its bifurcation, and ligation of the femoral artery from the inguinal site, but the patient still required massive transfusion due to a large amount of blood loss. Unfortunately, because of pulmonary edema, she died on the 5th postoperative day.