MANEJO ACTUAL DE LA FIBROSIS QUÍSTICA

The median survival and the quality of life of Cystic Fibrosis patients has increased remarkably in the last decades, changing from a lethal disease to a chronic disease, with a majority of patients in adult age, due to better knowledge of the pathology, precocious diagnosis, and preventive and aggressive management of the respiratory and nutritional complications, realised in specialized and multidisciplinary centers. This article describes the present management of the disease and its complications.