Case ReportAortic pseudoaneurysm after endarterectomy for small aorta syndrome

- Small Aorta Syndrome is a rare pathology that affects almost exclusively young and middle aged women.
- In the past thromboendarterectomy with patch graft was one of the preferred treatment options.
- Aortoiliac PA has been rarely observed after endarterectomy.
- Endovascular treatment should be preferred considering morbidity and mortality of open surgery.
- Open surgery was preferred because of small iliac diameters unsuitable for endovascular treatment.

IntroductionSmall Aorta Syndrome (SAS) or hypoplastic aorto-iliac syndrome is a rare pathology of the aorta that affects almost exclusively young or middle-aged women and is characterized by smaller dimension of the aorta and iliac axes. Etiopathogenesis is unclear and many factors have been invoked. The smaller caliber of the aorta and iliac arteries may predispose to aorto-iliac occlusive disease development.In the past aorto-iliac endarterectomy (AE) with patch closure was utilized as an alternative to surgical bypass in order to correct steno-obstructive syndromes affecting carriers of SAS. Little is known about long term outcomes of this type of surgery.Presentation of the caseDuring investigations for acute colecystitis, an aortic pseudoaneurysm (PA) was diagnosed by ultrasound in a 73 old year woman. She was submitted twenty-two years ago for SAS with disabling claudication to aortic endarterectomy (AE) with patch graft insertion. Considering all the vascular options available she was submitted to open surgery with replacement of the aortic bifurcation.DiscussionAortic PA is a relatively common complication after bypass surgery but is rarely observed after AE. It requires prompt intervention to prevent subsequent complications such as rupture, thrombosis, distal embolism or aorto-enteric fistula.ConclusionEndovascular treatment for aortic PA should be always considered the treatment of choice but the open surgical option was preferred in this particular case because of the small diameters of the iliac accesses, making them unsuitable for an endovascular approach.