
Novel pathogenic mechanism and therapeutic approaches to angioedema associated with C1 inhibitor deficiency
Keywords: Angioedema; C1 inhibitor; complement; endothelial cells; vascular leakage; B1R; B2R; gC1QR; bradykinin; leakage assay; AAE; Acquired angioedema; ADMEC; Human adult dermal microvascular endothelial cell; APL; Attack phase plasma; B1R; Type 1 bradykinin rec