
Marfan syndrome; A connective tissue disease at the crossroads of mechanotransduction, TGFβ signaling and cell stemness
Keywords: Cardiomyopathy; Fibrillin; Marfan syndrome; Mechanotransduction; Osteopenia; Stem cell niche; TGFβ; Thoracic aortic aneurysm; AngII; Angiotensin II; AT1r; AngII type I receptor; BMD; Bone mineral density; DCM; Dilated cardiomyopathy; ECM; Extracellular m