Keywords: کلاژن VI; Odontogenesis; Dentin; Collagen VI; Bone marrow stromal cells; PNIPAAm; Tissue engineering;
مقالات ISI کلاژن VI (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Distrofias musculares congénitas
Keywords: کلاژن VI; Distrofia muscular; merosina; colágeno VI; SEPN1; LMNA; distroglicano; algoritmo diagnóstico; Muscular dystrophy; merosin; collagen VI; SEPN1; Lamin A/C; Dystroglycan; diagnostic guideline.;
Collagen VI disorders: Insights on form and function in the extracellular matrix and beyond
Keywords: کلاژن VI; Collagen VI; Ullrich congenital muscular dystrophy; Bethlem myopathy; Muscle; Cancer; Diabetes;
Case reportClinical and neuroimaging findings in two brothers with limb girdle muscular dystrophy due to LAMA2 mutations
Keywords: کلاژن VI; Limb girdle muscular dystrophy; Laminin α2; Collagen VI; Muscle MRI;
ReviewMuscle redox disturbances and oxidative stress as pathomechanisms and therapeutic targets in early-onset myopathies
Keywords: کلاژن VI; AP-1; activator protein 1; ARE; antioxidant response element; CMs; congenital myopaties; CMDs; congenital muscular dystrophies; ColVI; collagen VI; CPK; creatine phosphokinase; DMD; duchenne muscular dystrophy; ER; endoplasmic reticulum; GPx; glutathione
Full length articleDefining the hierarchical organisation of collagen VI microfibrils at nanometre to micrometre length scales
Keywords: کلاژن VI; Collagen VI; Articular cartilage; Pericellular matrix; SBF-SEM; Tomography;
Collagen VI-NG2 axis in human tendon fibroblasts under conditions mimicking injury response
Keywords: کلاژن VI; TGFβ1; transforming growth factor β1; PCM; pericellular matrix; Tendon repair; Collagen VI; NG2 proteoglycan; Transforming growth factor β1; Cell migration;
Paternal germline mosaicism in collagen VI related myopathies
Keywords: کلاژن VI; UCMD; Collagen VI; Germline mosaicism
Monoamine oxidase inhibition prevents mitochondrial dysfunction and apoptosis in myoblasts from patients with collagen VI myopathies
Keywords: کلاژن VI; BM; Bethlem myopathy; ColVI; collagen VI; CsA; cyclosporine A; Ct; cycle threshold; Ctrl; controls; ÎΨm; mitochondrial membrane potential; FCCP; carbonyl cyanide p-trifluoromethoxyphenylhydrazone; GAPDH; glyceraldehyde-3-phosphate dehydrogenase; H2O2; h
Diagnostic approach to the congenital muscular dystrophies
Keywords: کلاژن VI; Congenital muscular dystrophy; Collagen VI; Laminin alpha2; Alpha-dystroglycan; SEPN1; Lamin A/C; RYR1; Diagnostic guideline;
Poor survival with wild-type TP53 ovarian cancer?
Keywords: کلاژن VI; Ovarian cancer; p53 mutation; Wild-type p53; EDA2R; Survival statistics; Collagen VI;
Collagen VI in cancer and its biological mechanisms
Keywords: کلاژن VI; collagen VI; cancer; angiogenesis; inflammation; chemotherapy resistance; therapeutic target
Expression of collagen VI α5 and α6 chains in human muscle and in Duchenne muscular dystrophy-related muscle fibrosis
Keywords: کلاژن VI; Collagen VI; Skeletal muscle; Myotendinous junctions; Fibrosis; Duchenne muscular dystrophy
Flow cytometry analysis: A quantitative method for collagen VI deficiency screening
Keywords: کلاژن VI; Ullrich congenital muscular dystrophy (UCMD); Bethlem myopathy (BM); Collagen VI; Diagnosis; Flow cytometry;
Dysfunctional tendon collagen fibrillogenesis in collagen VI null mice
Keywords: کلاژن VI; Collagen VI; Tendon; Development; Fibrillogenesis; Tendon biomechanics; Collagen VI-null mouse;
Differential and restricted expression of novel collagen VI chains in mouse
Keywords: کلاژن VI; Collagen VI; VWA; UCMD; Bethlem myopathy;
Collagen VI protects against neuronal apoptosis elicited by ultraviolet irradiation via an Akt/Phosphatidylinositol 3-kinase signaling pathway
Keywords: کلاژن VI; collagen VI; neuroprotection; UV; Akt/PI3K; NeurotoxQ; DAPI; 4â²-6-diamidino-2-phenylindole; ECM; extracellular matrix; GAPDH; glyceraldehyde 3-phosphate dehydrogenase; GFAP; glial fibrillary acidic protein; JNK; jun N-terminal kinase; MAP-2; microtubule
The knee osteoarthritis susceptibility locus DVWA on chromosome 3p24.3 is the 5′ part of the split COL6A4 gene
Keywords: کلاژن VI; DVWA; COL6A4; Collagen VI; VWA; Osteoarthritis
Autosomal recessive inheritance of classic Bethlem myopathy
Keywords: کلاژن VI; Bethlem myopathy; Collagen VI; COL6A2; Autosomal recessive inheritance
Lentiviral-mediated RNAi in vivo silencing of Col6a1, a gene with complex tissue specific expression pattern
Keywords: کلاژن VI; RNA interference; Lentiviral vectors; Transgenic mice; Collagen VI
Altered threshold of the mitochondrial permeability transition pore in Ullrich congenital muscular dystrophy
Keywords: کلاژن VI; BAPTA-AM; 1,2-bis(o-aminophenoxy)-ethane-N,N,Nâ²,Nâ²-tetraacetc acid tetraacetoxymethyl ester; Cs; Cyclosporin; EGTA; ethylene glycol-bis(2-aminoethyl)-N,N,Nâ²,Nâ²-tetraacetic acid; FCCP; carbonylcyanide-p-trifluoromethoxyphenyl hydrazone; PTP; permea
Exclusion of biglycan mutations in a cohort of patients with neuromuscular disorders
Keywords: کلاژن VI; Congenital muscular dystrophy; Biglycan; α-Dystroglycan; Collagen VI
Therapy of Collagen VI-Related Myopathies (Bethlem and Ullrich)
Keywords: کلاژن VI; Bethlem myopathy; Ullrich congenital muscular dystrophy; collagen VI; outcome measures; therapy;
An enhancer required for transcription of the Col6a1 gene in muscle connective tissue is induced by signals released from muscle cells
Keywords: کلاژن VI; Collagen VI; Muscle; Mesenchymal cells; Transcriptional enhancer
Use of SILAC for exploring sheddase and matrix degradation of fibroblasts in culture by the PIII SVMP atrolysin A: Identification of two novel substrates with functional relevance
Keywords: کلاژن VI; Snake venom metalloproteinases; SILAC; Sheddase; Annexin V; Collagen VI; Extracellular matrix;
Variable penetrance of COL6A1 null mutations: Implications for prenatal diagnosis and genetic counselling in Ullrich congenital muscular dystrophy families
Keywords: کلاژن VI; Collagen VI; Ullrich congenital muscular dystrophy; Bethlem myopathy; Prenatal diagnosis
Congenital Muscular Dystrophies and the Extracellular Matrix
Keywords: کلاژن VI; muscular dystrophy; congenital; extracellular matrix; dystroglycan; collagen VI