Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; IgA deficiency; Diagnostic delay; Primary antibody deficiency; Hypogammaglobulinemia;
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Keywords: نقص ایمنی متغیر شایع; common variable immunodeficiency; immunoglobulins; lymphocyte subsets; primary immunodeficiency; severe combined immunodeficiency;
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; Lung Disease; Interstitial; Complications;
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; somatic hypermutation; class-switch recombination; hypermutation; pediatric; switch; AICDA; Activation-induced cytidine deaminase; Bcl-6; B-cell lymphoma 6; CSR; Class-switch recombination; CT; Circle transcript; CVID; Co
Keywords: نقص ایمنی متغیر شایع; T-cell deficiency; combined immunodeficiency; hematopoietic stem cell transplantation; natural history; CID; Combined immunodeficiency; CVID; Common variable immunodeficiency; HSCT; Hematopoietic stem cell transplantation; IL2Rg; IL-2 receptor gamma chain
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; Complement deficiency; Group A Streptococcus; Haemophilus influenzae; Immunoglobulin deficiency; Neisseria gonorrhoeae; Neisseria meningitidis; Primary immunodeficiency; Streptococcus pneumoniae;
Keywords: نقص ایمنی متغیر شایع; ADCC; antibody-dependent cell-mediated cytotoxicity; AP3; adaptor protein 3; CHS; Chediak-Higashi syndrome; CMV; cytomegalovirus; CNKD; classical natural killer cell deficiency; CrkL; chicken tumor virus number 10 regulator of kinase-like; CTL; cytotoxi
Keywords: نقص ایمنی متغیر شایع; Primary immunodeficiency disease; whole-exome sequencing; copy number variants; AD; Autosomal dominant; ALPS; Autoimmune lymphoproliferative syndrome; AR; Autosomal recessive; BCM; Baylor College of Medicine; BHCMG; Baylor-Hopkins Center for Mendelian Gen
Keywords: نقص ایمنی متغیر شایع; Hiperplasia nodular regenerativa; Inmunodeficiencia común variable; Hipertensión portalNodular regenerative hyperplasia; Common variable immunodeficiency; Portal hypertension
Keywords: نقص ایمنی متغیر شایع; Nodular regenerative hyperplasia; Common variable immunodeficiency; Portal hypertensionHiperplasia nodular regenerativa; Inmunodeficiencia común variable; Hipertensión portal
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; Adult; Infection
Keywords: نقص ایمنی متغیر شایع; Bronchiectasis; Lung transplantation; Survival; Bronchiolitis obliterans syndrome; Pseudomonas aeruginosa; Chronic airway infection; ABPA; Allergic bronchopulmonary aspergillosis; AMR; Antibody-mediated rejection; BAL; Bronchoalveolar lavage; BMI; Body ma
Keywords: نقص ایمنی متغیر شایع; BAFF-R; B-cell activating factor receptor; CMV; Cytomegalovirus; CVID; common variable immunodeficiency; ESID; European Society for Immunodefiencies; GS; Good syndrome; G-CSF; Granulocyt e-Colony Stimulating Factor; TACI; Transmembrane activator and CAML
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; Diagnosis; Respiratory management
Keywords: نقص ایمنی متغیر شایع; Immunology; primary immunodeficiency; whole-exome sequencing; hematopoietic stem cell transplantation; common variable immunodeficiency; severe combined immunodeficiency; hyper-IgE syndrome; AD; Autosomal dominant; AR; Autosomal recessive; BCL10; B-cell l
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; CVID; Granulomatous interstitial lung disease; Interstitial lung disease; Bronchiectasis; Primary antibody deficiency; AR; Autosomal recessive; CT; Computed tomography; CTLA-4; Cytotoxic T lymphocyte-associated protein
Keywords: نقص ایمنی متغیر شایع; Autoimmunity; primary immunodeficiency diseases; BÂ cells; T cells; AID; Activation-induced cytidine deaminase; AIHA; Autoimmune hemolytic anemia; AIRE; Autoimmune regulator; ALPS; Autoimmune lymphoproliferative disease; ANA; Anti-nuclear autoantibody; AP
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; inflammatory complications; mucosal disease; innate lymphoid cells; CVID; Common variable immunodeficiency; CVIDc; CVID with inflammatory disease; CyTOF; Mass cytometry; Id-2; Inhibitor of DNA binding 2; ILC; Innate lymph
Keywords: نقص ایمنی متغیر شایع; CVID; Common variable immunodeficiency; ICOS; inducible T-cell costimulator; TACI; transmembrane activator and calcium mobilizing ligand interactor; ESID; European society of immune deficiencies; TNF; tumor necrosis factor; IFN-γ; interferon gamma; IL- 6
Keywords: نقص ایمنی متغیر شایع; Primary immunodeficiency; Common variable immunodeficiency; Bronchial asthma; Wheezes; Airway infection; Hypogammaglobulinemia
Keywords: نقص ایمنی متغیر شایع; Pneumonia; Bronchiectasis; Common variable immunodeficiency; Hypogammaglobulinemia
Keywords: نقص ایمنی متغیر شایع; Granuloma; Lymphoid interstitial lung disease; Organizing pneumonia; Common variable immunodeficiency; Immunohistochemistry
Keywords: نقص ایمنی متغیر شایع; Immunology; primary immunodeficiency; dedicator of cytokinesis 8; HIV1; recombination-activating gene 1; intravenous immunoglobulin; common variable immunodeficiency; severe combined immunodeficiency; newborn screening; ADA; Adenosine deaminase; ApoE; Apo
Keywords: نقص ایمنی متغیر شایع; Primary immunodeficiency; Autoimmunity; Tolerance; Regulatory T cell; Apoptosis; Common variable immunodeficiency;
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; CVID; Antibody deficiency; Primary immune deficiency; Immune activation; Autoimmunity; Lymphoproliferation;
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; Granulomas; Sarcoidosis; Granulomatous disease; Imunodeficiência comum variável; Granulomas; Sarcoidose; Doença granulomatosa;
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; Granulomas; Sarcoidosis; Granulomatous diseaseImunodeficiência comum variável; Granulomas; Sarcoidose; Doença granulomatosa
Keywords: نقص ایمنی متغیر شایع; Live viral and bacterial vaccines; primary immunodeficiency disease; severe combined immunodeficiency disease; cellular immune reconstitution; CVID; Common variable immunodeficiency; HCT; Hematopoietic stem cell transplantation; Hib; Haemophilus influenza
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; Primary immunodeficiency; Primary antibody deficiency; Humoral deficiency;
Keywords: نقص ایمنی متغیر شایع; AIHA; autoimmune hemolytic anemia; ASH; American Society of Hematology; CLL; chronic lymphocytic leukemia; CMV; cytomegalovirus; CVID; common variable immunodeficiency; GPRD; General Practice Research Database; DIC; disseminated intravascular coagulation;
Keywords: نقص ایمنی متغیر شایع; Adaptive immunity; allergic rhinitis; asthma; atopic dermatitis; epidemiology; immune dysfunction; immune incompetence; infection; innate immunity; phenotype; risk; susceptibility; ACIP; Advisory Committee on Immunization Practices; BSI; Bloodstream infec
Keywords: نقص ایمنی متغیر شایع; Immunity; immunodeficiency; gut microbiota; intestinal lipid metabolism; CD; Crohn disease; CVID; Common variable immunodeficiency; IBD; Inflammatory bowel disease; SCFA; Short-chain fatty acid; TLR; Toll-like receptor;
Keywords: نقص ایمنی متغیر شایع; Autoantibodies; Autoimmune disorders; Autoimmune enteropathy; Common variable immunodeficiency; Olmesartan; Seronegative celiac disease; Villous atrophy
Keywords: نقص ایمنی متغیر شایع; Antitumor immunity; Common variable immunodeficiency; B lymphomas; Non-Hodgkin's lymphoma; Epstein-Barr virusInmunidad antitumoral; Inmunodeficiencia variable común; Linfomas B; Linfoma no Hodgkin; Virus Epstein-Barr
A novel mutation in TAP1 gene leading to MHC class I deficiency: Report of two cases and review of the literature
Keywords: نقص ایمنی متغیر شایع; Anti-HBc IgG; antibody against Hepatitis B core antigen; CVID; common variable immunodeficiency; ER; endoplasmic reticulum; HBeAg; Hepatitis B envelope antigen; HBsAg; Hepatitis B surface antigen; HBV; Hepatitis B virus; HLA; human leukocyte antigen; Ig;
Patterns of constitutively phosphorylated kinases in B cells are associated with disease severity in common variable immunodeficiency
Keywords: نقص ایمنی متغیر شایع; BCR; B-cell receptor; Btk; Bruton's tyrosine kinase; CD40L; CD40 ligand; CVID; Common variable immunodeficiency; Erk; extracellular signal-related kinase; IκBα; NFκB inhibitor α; Ig; immunoglobulin; IVIG; intravenous immunoglobulin; PCA; principle com
Review articleAbnormality of regulatory T cells in common variable immunodeficiency
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; T cell; Regulatory T cells;
NFKB1 regulates human NK cell maturation and effector functions
Keywords: نقص ایمنی متغیر شایع; NFKB1; Nuclear Factor kappa-B, subunit 1; CVID; Common Variable Immunodeficiency; NFKB2; Nuclear Factor kappa-B, subunit 2; NK cells; natural killer cells; IFN-γ; Interferon-gamma; MFI; mean fluorescence intensity; IL-2; Interleukin-2; IL-12; Interleukin
Immune defects caused by mutations in the ubiquitin system
Keywords: نقص ایمنی متغیر شایع; Ubiquitin; nuclear factor κB; immunodeficiency; CVID; Common variable immunodeficiency; DUB; Deubiquitinating enzyme; EDA-ID; Ectodermal dysplasia with immunodeficiency; HECT; Homologous to EGAP C-terminus; HOIL-1; Heme-oxidase iron responsive element bi
Increase of circulating α4β7+ conventional memory CD4 and regulatory T cells in patients with common variable immunodeficiency (CVID)
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; Enteropathy; T cell; Homing; α4β7; Diagnostics;
Physical health conditions and quality of life in adults with primary immunodeficiency diagnosed during childhood: AÂ French Reference Center for PIDs (CEREDIH) study
Keywords: نقص ایمنی متغیر شایع; Primary immunodeficiency; childhood; young adults; health status; quality of life; CEREDIH; French Reference Center for PIDs; CTCAE; Common Terminology Criteria for Adverse Events; CVID; Common variable immunodeficiency; ENT; Ear, nose, and throat; F-CILC
Rapid CommunicationCorrelation of bone marrow abnormalities, peripheral lymphocyte subsets and clinical features in uncomplicated common variable immunodeficiency (CVID) patients
Keywords: نقص ایمنی متغیر شایع; CVID; common variable immunodeficiency; RTE; recent thymic emigrants; CVID; B cells; Bone marrow;
Infectious Chronic Rhinosinusitis
Keywords: نقص ایمنی متغیر شایع; Bacterial; Exacerbation; Immunodeficiency; Infectious; Microbiome; Pathogenesis; Rhinosinusitis; Sinonasal; CF; Cystic fibrosis; CFTR; Cystic fibrosis transmembrane conductance regulator; CRS; Chronic rhinosinusitis; CRSsNP; Chronic rhinosinusitis without
Autoimmunity and infection in common variable immunodeficiency (CVID)
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; CD21low B cells; Autoimmunity; Chronic inflammatory diseases; Recurrent infections
Chemokine, cytokine and type I interferon production induced by Toll-like receptor activation in common variable immune deficiency
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; Toll-like receptor agonists; Chemokines; Cytokines;
The extended phenotype of LPS-responsive beige-like anchor protein (LRBA) deficiency
Keywords: نقص ایمنی متغیر شایع; LPS-responsive beige-like anchor protein; primary immunodeficiency; common variable Immunodeficiency; autoimmunity; hypogammaglobulinemia; enteropathy; lymphoproliferation; ALPS; Autoimmune lymphoproliferative syndrome; ALPS-Ph; Autoimmune lymphoprolifera
Impaired selective cytokine production by CD4+ T cells in Common Variable Immunodeficiency associated with the absence of memory B cells
Keywords: نقص ایمنی متغیر شایع; CVID; Common Variable Immunodeficiency; PBMCs; Peripheral blood mononuclear cells; PMA; Phorbol 12-myristrate 13-acetate; SEB; Staphylococcal enterotoxin B; MFI; mean fluorescence intensity; ICOS; Inducible coestimulator; BAFFR; B cell activating factor r
Role of apoptosis in common variable immunodeficiency and selective immunoglobulin A deficiency
Keywords: نقص ایمنی متغیر شایع; Common variable immunodeficiency; IgA deficiency; Apoptosis
Altered fraction of regulatory B and T cells is correlated with autoimmune phenomena and splenomegaly in patients with CVID
Keywords: نقص ایمنی متغیر شایع; AHA; autoimmune hemolytic anemia; AI; autoimmune; aTreg; activated regulatory T cell; CVID; common variable immunodeficiency; ESID; European Society for immunodeficiencies; Foxp3; Forkhead box protein 3; IL-10; interleukin-10; ITP; immune thrombocytopenia
A comparison of B cell subsets in primary immune deficiencies that progress with antibody deficiency and age-matched healthy children
Keywords: نقص ایمنی متغیر شایع; Antibody deficiency; B cells; Common variable immunodeficiency; Hypogammaglobulinaemia; Immunoglobulins; Lymphocytes; Memory B cell; Primary immunodeficiency; Transient hypogammaglobulinaemia