دانلود مقالات ISI درباره هستند + ترجمه فارسی

Regolith properties under trees and the biomechanical effects caused by tree root systems as recognized by electrical resistivity tomography (ERT)

Keywords: هستند; Biomechanical weathering; Tree roots; Soil; Regolith; Electrical resistivity tomography; ERT; Hillslope; Beskidy;

دانلود رایگان متن کامل مقاله ISI 29 صفحه سال انتشار : 2018 سفارش ترجمه

Novel 3-D homogeneity metrics of multiple components in gas-stirred liquid systems

Keywords: هستند; 2-D; two-dimensional; 3-D; three-dimensional; Adj.; adjusted; CD; centered L2-star discrepancy; DCI; digital color imaging; ERT; electrical resistance tomography; H1 ~ H2; human estimation set; M1 ~ M9; experimental cases; PDF; probability distribution fu

دانلود رایگان متن کامل مقاله ISI 32 صفحه سال انتشار : 2018 سفارش ترجمه

A pilot study to test the reliability of the ERT method in the identification of mixed sulphides bearing dykes: The example of Sidi Flah mine (Anti-Atlas, Morocco)

Keywords: هستند; ERT; Structural investigation; Mixed sulphides; Petrographical analyses; Anti-Atlas; Morocco;

دانلود رایگان متن کامل مقاله ISI 34 صفحه سال انتشار : 2018 سفارش ترجمه

Millettia macrophylla (Fabaceae) phenolic fraction prevents differentiation of 3T3-L1 adipocytes and the increased risks of cardiovascular diseases in ovariectomized rats

Keywords: هستند; CS; calf serum; DCM; dichloromethane; DMEM; Dulbecco's Modified Eagle Medium; DMSO; dimethylsulfoxide; DEX; dexamethasone; E2V; Estradiol valerate; ER; estrogen receptor; ERT; estrogen replacement therapy; IBMX; 3-isobutyl-1-methylxanthine; PF; phenolic f

دانلود رایگان متن کامل مقاله ISI 46 صفحه سال انتشار : 2018 سفارش ترجمه

Combined application of GPR and ERT for the assessment of a wall structure at the Heptapyrgion fortress (Thessaloniki, Greece)

Keywords: هستند; GPR; ERT; Combined GPR and ERT; Non-destructive testing; GPR numerical modelling; Wall assessment;

دانلود رایگان متن کامل مقاله ISI 47 صفحه سال انتشار : 2018 سفارش ترجمه

Molecular genetics and metabolism, special edition: Diagnosis, diagnosis and prognosis of Mucopolysaccharidosis IVA

Keywords: هستند; Mucopolysaccharidosis IVA; N-acetylgalactosamine-6-sulfate; Keratan sulfate; Chondroitin-6-sulfate; Spondyloepiphyseal dysplasia; 3-MSCT; 3-Minute Stair Climb Test; 4MU-Gal6S; 4-methylumbelliferyl-β-D-galactopyranoside-6-sulfate; 6-MWT; 6-Minute Walk Tes

دانلود رایگان متن کامل مقاله ISI 95 صفحه سال انتشار : 2018 سفارش ترجمه

Electrical resistivity tomography data across the Hockai Fault Zone (Ardenne, Belgium)

Keywords: هستند; ERT; Fault zone; Resistivity; 3D;

دانلود رایگان متن کامل مقاله ISI 4 صفحه سال انتشار : 2017 سفارش ترجمه

Origin of α-mannosidase activity in CSF

Keywords: هستند; AD; Alzheimer's disease; BBB; blood-brain barrier; CSF; cerebrospinal fluid; DLB; dementia with Lewy bodies; ERT; enzyme replacement therapy; EV; extracellular vesicles; FTD; Fronto-Temporal Dementia; LP; lumbar puncture; MAN2B1; lysosomal α-mannosidas

دانلود رایگان متن کامل مقاله ISI 4 صفحه سال انتشار : 2017 سفارش ترجمه

A pilot study on using rapamycin-carrying synthetic vaccine particles (SVP) in conjunction with enzyme replacement therapy to induce immune tolerance in Pompe disease

Keywords: هستند; ERT; enzyme replacement therapy; rhGAA; recombinant human acid-α-glucosidase; CRIM; cross-reactive immunologic material; HSAT; high and sustained antibody titer; MTX; methotrexate; SVP-Rapa; synthetic vaccine particles carrying rapamycin; NP; empty nanop

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2017 سفارش ترجمه

Albuterol as an adjunctive treatment to enzyme replacement therapy in infantile-onset Pompe disease

Keywords: هستند; 6MWT; 6-minute walk test; AE; adverse event; CI-MPR; cation-independent mannose-6-phosphate receptor; CK; creatine kinase; CRIM; cross-reactive immunologic material; ERT; enzyme replacement therapy; GAA; acid alpha-glucosidase; Glc4; glucose tetrasacchari

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2017 سفارش ترجمه

Effect of enzyme replacement therapy with alglucosidase alfa (Myozyme®) in 12 patients with advanced late-onset Pompe disease

Keywords: هستند; GAA; acid alpha-glycosidase; ERT; enzyme replacement therapy; FVC; forced vital capacity; MIP; maximum inspiratory pressure; MEP; maximum expiratory pressure; MFM; Motor Measure Function scale; Pompe disease; Advanced; Respiratory failure; Enzyme replacem

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2017 سفارش ترجمه

The effect of galsulfase enzyme replacement therapy on the growth of patients with mucopolysaccharidosis VI (Maroteaux-Lamy syndrome)

Keywords: هستند; ASB; Arylsulfatase B; CDC; Centers for Disease Control and Prevention; ERT; Enzyme replacement therapy; GAG; Glycosaminoglycans; MPS VI; Mucopolysaccharidosis VI; uGAG; Urinary glycosaminoglycans; Mucopolysaccharidosis; Mucopolysaccharidosis VI; Maroteaux

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2017 سفارش ترجمه

Amelioration of serum 8-OHdG level by enzyme replacement therapy in patients with Fabry cardiomyopathy

Keywords: هستند; Fabry disease; ERT; Oxidative stress; Cardiomyopathy;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2017 سفارش ترجمه

Combined application of vertical electrical sounding and 2D electrical resistivity imaging for geothermal groundwater characterization: Hammam Sayala hot spring case study (NW Tunisia)

Keywords: هستند; ERT; IP; VES; Geothermal; Hot spring; Hammam Sayala (NW Tunisia);

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2017 سفارش ترجمه

Enzyme replacement therapy attenuates disease progression in two Japanese siblings with mucopolysaccharidosis type VI: 10-Year follow up

Keywords: هستند; Case report; Deficient N-acetylgalactosamine 4-sulfatase; Enzyme replacement therapy; Galsulfase; Glycosaminoglycan; Mucopolysaccharidosis type VI; ASB; N-acetylgalactosamine 4-sulfatase; ECHO; echocardiography; ERT; enzyme replacement therapy; fT4; free

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2017 سفارش ترجمه

Combined GPR and ERT exploratory geophysical survey of the Medieval Village of Pancorbo Castle (Burgos, Spain)

Keywords: هستند; GPR; ERT; Attribute analysis; Archaeology; Archaeometry;

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2017 سفارش ترجمه

Oxidative profile exhibited by Mucopolysaccharidosis type IVA patients at diagnosis: Increased keratan urinary levels

Keywords: هستند; 8-OHdG; 8-hydroxy-2′-deoxyguanosine; Cr; creatinine; DI; damage index; DTNB; 5,5′-dithiobis(2-nitrobenzoic acid); Endo III; endonuclease III; ELISA; enzyme-linked immunoassay; ERT; enzyme replacement therapy; FU; fluorescence units; GAGs; glycosaminog

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2017 سفارش ترجمه

Use of electric resistivity tomography (ERT) for detecting underground voids on highly anthropized urban construction sites

Keywords: هستند; ERT; geophysics; underground voids;

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2017 سفارش ترجمه

Mucopolysaccharidosis Type I Newborn Screening: Best Practices for Diagnosis and Management

Keywords: هستند; CNS; Central nervous system; DBS; Dried blood spot; ERT; Enzyme replacement therapy; GAG; Glycosaminoglycan; HSCT; Hematopoietic stem cell transplantation; IDUA; α-L-iduronidase; MPS; Mucopolysaccharidoses; MPS I; Mucopolysaccharidosis type I; MRI; Magne

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2017 سفارش ترجمه

Reductions in glucosylsphingosine (lyso-Gb1) in treatment-naïve and previously treated patients receiving velaglucerase alfa for type 1 Gaucher disease: Data from phase 3 clinical trials

Keywords: هستند; β-GC; β-glucocerebrosidase; CCL18; chemokine (C-C motif) ligand 18; ERT; enzyme replacement therapy; GD; Gaucher disease; lyso-Gb1; glucosylsphingosine; MN; multiples of normal; Gaucher disease; Glucosylsphingosine; Lyso-Gb1; Velaglucerase alfa; Enzyme

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2017 سفارش ترجمه

Insight into the phenotype of infants with Pompe disease identified by newborn screening with the common c.-32-13T > G “late-onset” GAA variant

Keywords: هستند; NBS; Newborn screening; IOPD; Infantile onset Pompe disease; LOPD; Late onset Pompe disease; GAA; Acid α-glucosidase; ERT; Enzyme replacement therapy; RUSP; Recommended uniform screening panel; CK; Creatine kinase; Glc4; Urinary glucose tetrasaccharide;

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2017 سفارش ترجمه

Original articleLongitudinal follow-up to evaluate speech disorders in early-treated patients with infantile-onset Pompe disease

Keywords: هستند; Infantile-onset Pompe disease; Speech disorder; Articulation disorder; Hypernasality; Speech intelligibility; Enzyme replacement therapy; AROM; active range of motion; CRIM; cross-reactive immunologic material; ERT; enzyme replacement therapy; FEES; fiber

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2017 سفارش ترجمه

Application of ERT and GPR geophysical testing to the subsoil characterization of cultural heritage sites in Napoli (Italy)

Keywords: هستند; Geophysical testing; ERT; GPR; Cultural heritage;

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2017 سفارش ترجمه

A long term follow-up study of the development of hip disease in Mucopolysaccharidosis type VI

Keywords: هستند; MPS; mucopolysaccharidosis; MPS VI; mucopolysaccharidosis type VI; GAG; glycosaminoglycan; AP; anteroposterior; Lau; Lauenstein; ERT; enzyme replacement therapy; HSCT; hematopoietic stem-cell transplantation; AI; acetabular index; NSA; neck shaft angle; S

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2017 سفارش ترجمه

Efficacy of laronidase therapy in patients with mucopolysaccharidosis type I who initiated enzyme replacement therapy in adult age. A systematic review and meta-analysis

Keywords: هستند; ERT; enzyme replacement therapy; MPS-I; Muchopolysaccharidosis Type I; GAG; glycosaminoglycan; uGAGs; urine glycosaminoglycans; 6MWT; 6-min walking test; HSCT; hematopoietic stem cell transplantation; FVC; forced vital capacity; VA; visual acuity; NHA; no

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2017 سفارش ترجمه

Monitoring the evolution and migration of a methane gas plume in an unconfined sandy aquifer using time-lapse GPR and ERT

Keywords: هستند; Stray gas; Fugitive methane; GPR; ERT; Groundwater contamination; Borden aquifer;

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2017 سفارش ترجمه

Using interpolation techniques to determine the optimal profile interval in ground-penetrating radar applications

Keywords: هستند; GPR; Ground Penetrating Radar; ERT; Electrical Resistivity Tomography; FDEM; Frequency-Domain Electromagnetics; 2D/3D; Two/Three Dimensions; RMSE; Root Mean Square Error; PI; Profile Interval; TI; Trace Interval; GPR synthetic data; Profile interval; Trac

دانلود رایگان متن کامل مقاله ISI 14 صفحه سال انتشار : 2017 سفارش ترجمه

Improved characterisation and modelling of measurement errors in electrical resistivity tomography (ERT) surveys

Keywords: هستند; ERT; Resistivity; Measurement errors; Uncertainty; Linear mixed effects; Inversion;

دانلود رایگان متن کامل مقاله ISI 17 صفحه سال انتشار : 2017 سفارش ترجمه

Macro-mixing characterisation of a stirred model fermenter of non-Newtonian liquid by flow following sensor particles and ERT

Keywords: هستند; Macro mixing; Biogas fermenter; Flow follower; Sensor particle; ERT; CFD;

دانلود رایگان متن کامل مقاله ISI 18 صفحه سال انتشار : 2017 سفارش ترجمه

Four novel mutations in the N-acetylgalactosamine-6-sulfate sulfatase gene among Egyptian patients with Morquio A disease

Keywords: هستند; MPS IVA; Mucopolysaccharidosis type 4 -A; GALNS; N-acetylgalactosamine-6-sulfatase; GAGs; Glycosaminoglycans; NRC; National Research Centre; MPSs; Mucopolysaccharidoses; GLB1; β-Galactosidase; KS; Keratan Sulfate; C6S; Chondroitin-6-Sulfate; kDa; Kilo

دانلود رایگان متن کامل مقاله ISI 21 صفحه سال انتشار : 2017 سفارش ترجمه

Measuring inline velocity profile of shampoo by electrical resistance tomography (ERT)

Keywords: هستند; ERT; Local velocity; Micro-structure; Shampoo;

دانلود رایگان متن کامل مقاله ISI 21 صفحه سال انتشار : 2017 سفارش ترجمه

Structurally coupled inversion of ERT and refraction seismic data combined with cluster-based model integration

Keywords: هستند; ERT; Refraction seismics; Structurally coupled inversion; Joint inversion; Cluster analysis;

دانلود رایگان متن کامل مقاله ISI 28 صفحه سال انتشار : 2017 سفارش ترجمه

Simulations of Cytochrome P450 3A4-Mediated Drug-Drug Interactions by Simple Two-Compartment Model-Assisted Static Method

Keywords: هستند; bioavailability; cytochrome P450; drug interaction; dynamic simulation; first pass metabolism; hepatic clearance; intestinal metabolism; pharmacokinetics; simulations; parallel tube model; Ae (Ae,oral); dose fractions of urinary excreted unchanged drug af

دانلود رایگان متن کامل مقاله ISI 39 صفحه سال انتشار : 2017 سفارش ترجمه

Geophysical approach to the study of a periglacial blockfield in a mountain area (Ztracené kameny, Eastern Sudetes, Czech Republic)

Keywords: هستند; Blockfield; Permafrost; Periglacial; ERT; SRT; Eastern Sudetes;

دانلود رایگان متن کامل مقاله ISI 41 صفحه سال انتشار : 2017 سفارش ترجمه

Episodic activity of a dormant fault in tectonically stable Europe: The Rauw fault (NE Belgium)

Keywords: هستند; RVG; Roer Valley Graben; LRG; Lower Rhine Graben; SCR; stable continental region; LGM; Late Glacial Maximum; ESR; electron spin resonance; OSL; optically stimulated luminescence; EMR; electromagnetic resistivity; ERT; electrical resistivity tomography; GP

دانلود رایگان متن کامل مقاله ISI 45 صفحه سال انتشار : 2017 سفارش ترجمه

Using computational fluid dynamics to analyze the performance of the Maxblend impeller in solid-liquid mixing operations

Keywords: هستند; Solid-liquid mixing; Computational fluid dynamics (CFD); Maxblend impeller; Homogeneity; Solid suspension; Mixing index; CFD; computational fluid dynamics; ERT; electrical resistance tomography; PBT; pitched blade turbine; RSD; relative standard deviation

دانلود رایگان متن کامل مقاله ISI 52 صفحه سال انتشار : 2017 سفارش ترجمه

Clinical evaluation of chitotriosidase enzyme activity in Gaucher and Niemann Pick A/B diseases: A retrospective study from India

Keywords: هستند; LSDs; Lysosomal Storage Disorders; CT; Chitotriosidase; GD; Gaucher disease; NPD A/B; Niemann Pick disease A/B; ERT; Enzyme Replacement Therapy; Chitotriosidase; Gaucher; Niemann Pick A/B; Lysosomal Storage Disorders;

دانلود رایگان متن کامل مقاله ISI 4 صفحه سال انتشار : 2016 سفارش ترجمه

Selenoureido-iminosugars: A new family of multitarget drugs

Keywords: هستند; Glycosidase inhibition; Iminosugars; Selenoureas; AChE inhibition; Antioxidant; GPx mimic; AChE; acetylcholinesterase; CCT; chemical chaperone therapy; DNJ; 1-deoxynojirimycin; ERT; enzyme replacement therapy; GBA1; β-glucosidase acid 1; GI50; growth inh

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2016 سفارش ترجمه

Reliability of the functional measures of the corticospinal pathways to dorsiflexor muscles during maximal voluntary contractions

Keywords: هستند; CSP; cortical silent period; CSP50; cortical silent period during a 50% MVC submaximal contraction; CSP75; cortical silent period during a 75% MVC submaximal contraction; CSPMVC; cortical silent period during a MVC; CV; coefficient of variation; EMG; elec

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2016 سفارش ترجمه

Nine-year experience in Gaucher disease diagnosis at the Spanish reference center Fundación Jiménez Díaz

Keywords: هستند; FJD; Fundación Jiménez Díaz; GD; Gaucher disease; GBA; acid β-glucosidase; ERT; enzyme replacement therapy; Spanish Gaucher disease; Gaucher disease; GBA gene; Chitotriosidase;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2016 سفارش ترجمه

Very Early Treatment for Infantile-Onset Pompe Disease Contributes to Better Outcomes

Keywords: هستند; AST; Aspartate aminotransferase; Bayley-III; Bayley Scale of Infant and Toddler Development, Third Edition; CK; Creatine kinase; CRIM; Cross-reactive immunologic; ERT; Enzyme-replacement therapy; GAA; Acid α-glucosidase; IOPD; Infantile-onset Pompe disea

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2016 سفارش ترجمه

Tandem mass spectrometry multiplex analysis of methylated and non-methylated urinary Gb3 isoforms in Fabry disease patients

Keywords: هستند; OMIM; Online Mendelian Inheritance in Man; α-GAL A; α-galactosidase A; ERT; enzyme replacement therapy; CFDI; Canadian Fabry Disease Initiative; Gb3 or GL-3; globotriaosylceramide; CTH; ceramide trihexoside; Ga2; galabiosylceramide; CDH; ceramide dihexo

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2016 سفارش ترجمه

Sinkhole risk assessment by ERT: The case study of Sirino Lake (Basilicata, Italy)

Keywords: هستند; Piping; Sinkhole; Hydrogeology; ERT;

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2016 سفارش ترجمه

Original ArticlesOutcomes of Long-Term Treatment with Laronidase in Patients with Mucopolysaccharidosis Type I

Keywords: هستند; MPS I; mucopolysaccharidosis type I; enzyme replacement therapy; laronidase; 6MWT; 6-minute walk test; ERT; Enzyme replacement therapy; FVC; Forced vital capacity; GAG; Glycosaminoglycan; MPS I; Mucopolysaccharidosis type I; uGAG; Urinary glycosaminoglyca

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2016 سفارش ترجمه

Prospective exploratory muscle biopsy, imaging, and functional assessment in patients with late-onset Pompe disease treated with alglucosidase alfa: The EMBASSY Study

Keywords: هستند; 6MWT; 6-Minute Walk Test; AE; adverse event; BMI; body mass index; CI; confidence interval; ERT; enzyme replacement therapy; FVC; forced vital capacity; GAA; α-glucosidase; HRLM; high-resolution light microscopy; PFT; pulmonary function testing; GMFCS-E&

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2016 سفارش ترجمه

Risk factors for severe clinical events in male and female patients with Fabry disease treated with agalsidase beta enzyme replacement therapy: Data from the Fabry Registry

Keywords: هستند; eGFR; estimated glomerular filtration rate; ERT; enzyme replacement therapy; ESRD; end-stage renal disease; GL-3; globotriaosylceramide; IEC; independent ethics committee; IRB; institutional review board; LVH; left ventricular hypertrophy; UP/Cr; urinary

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2016 سفارش ترجمه

Short-term effects of impurities in the CO2 stream injected into fractured carbonates

Keywords: هستند; BHP; bottom-hole pressure; BOP; balance of plant; CCS; carbon capture and storage; CIUDEN; Fundation Ciudad de la Energía; DOT; pressure vessel used to store fluids at above atmospheric pressure, the acronym is department of transport; DTS; distributed t

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2016 سفارش ترجمه

Implementation of ground penetrating radar and electrical resistivity tomography for inspecting the Greco-Roman Necropolis at Kilo 6 of the Golden Mummies Valley, Bahariya Oasis, Egypt

Keywords: هستند; Archeology; Bahariya Oasis; GPR; ERT; Golden Mummies

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2016 سفارش ترجمه

Detection of illegal mine voids using electrical resistivity tomography: The case-study of Raniganj coalfield (India)

Keywords: هستند; ERT; Joint inversion; Mine voids; Illegal mining; Raniganj coalfield; India

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2016 سفارش ترجمه

Inside the polygonal walls of Amelia (Central Italy): A multidisciplinary data integration, encompassing geodetic monitoring and geophysical prospections

Keywords: هستند; GPR; ERT; Geomatic techniques; 3D imaging; Amelia; Cultural heritage

دانلود رایگان متن کامل مقاله ISI 14 صفحه سال انتشار : 2016 سفارش ترجمه