Application of 2D surface ERT to on-site wastewater treatment survey
Keywords: هستند; On-site wastewater treatment; ERT; Sensitivity analysis; Outline detection
مقالات ISI هستند (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Anti-α-galactosidase A antibody response to agalsidase beta treatment: Data from the Fabry Registry
Keywords: هستند; CI; confidence interval; ERT; enzyme replacement therapy; αGAL; α-galactosidase A; GPS&RM; Genzyme Global Patient Safety & Risk Management; IAR; infusion-associated reaction; Fabry disease; Lysosomal storage diseases; Alpha-galactosidase; Enzyme replace
Severely impaired health status at diagnosis of Pompe disease: A cross-sectional analysis to explore the potential utility of neonatal screening
Keywords: هستند; IPA; International Pompe Association; ERT; enzyme replacement therapy; GAA; acid alpha-glucosidase; LVMI; left ventricular mass index; HHD; hand-held dynamometry; FVC; forced vital capacity; BERA; brainstemâevoked response audiometry; AIMS; Alberta Infa
Long-term efficacy of hematopoietic stem cell transplantation on brain involvement in patients with mucopolysaccharidosis type II: A nationwide survey in Japan
Keywords: هستند; ADL; activities of daily living; DQ; development quotient; ERT; enzyme replacement therapy; FIM; functional independence measure; GAG; glycosaminoglycan; HSCT; hematopoietic stem cell transplantation; IQ; intelligence quotient; JSPH; Japanese Society for
Biomarkers for the mucopolysaccharidoses: Discovery and clinical utility
Keywords: هستند; 6MWT; six-minute walk test; BMP; bis(monoacylglycero)phosphate; CLN; ceroid lipofuscinosis; CSF; cerebral spinal fluid; DPP-IV; dipeptidyl peptidase IV; ESI-MS/MS; electrospray ionization-tandem mass spectrometry; ERT; enzyme replacement therapy; GAG; gly
Developing treatment options for metachromatic leukodystrophy
Keywords: هستند; ARSA; arylsulfatase A; LSD; lysosomal storage disease; MLD; metachromatic leukodystrophy; HSCT; hematopoietic stem cell transplantation; UCBT; umbilical cord blood transplantation; MSCT; mesenchymal stem cell transplantation; ERT; enzyme replacement thera
Current diagnosis and management of mucopolysaccharidosis VI in the Asia-Pacific region
Keywords: هستند; ARSB; arylsulfatase B gene; ASB; arylsulfatase B; BMT; bone marrow transplantation; DBS; dry blood spot; dx; diagnosis; ERT; enzyme replacement therapy; GAG; glycosaminoglycan; HSCT; hematopoietic stem cell transplantation; LSDP; Life Saving Drugs Program
Enzyme replacement therapy in patients with Fabry disease: State of the art and review of the literature
Keywords: هستند; MRI; Fabry disease; ERT;
Constraining 3-D electrical resistance tomography with GPR reflection data for improved aquifer characterization
Keywords: هستند; GPR; ERT; Aquifer characterization; Constrained inversion
A multinational, multidisciplinary consensus for the diagnosis and management of spinal cord compression among patients with mucopolysaccharidosis VI
Keywords: هستند; ARSB; Arylsulfatase B gene; ARSB; Arylsulfatase B protein (also known as N-acetylgalactosamine 4-sulfatase); CCC; Cervical cord compression; CPAP; Continuous positive airway pressure; C1 or C2; Cervical vertebra 1 or cervical vertebra 2, atlantoaxial join
Effects of ginsenoside Rg1 or 17β-estradiol on a cognitively impaired, ovariectomized rat model of Alzheimer's disease
Keywords: هستند; ANOVA; analysis of variances; AD; Alzheimer's disease; ADAM 10; a disintegrin and metallopeptidase domain 10; Aβ; amyloid β-proteins; APP; amyloid precursor protein; BACE 1; β-site APP-cleaving enzyme 1; d-gal; d-galactose; E2; 17β-estradiol; ER; es
Estrogen mediation of hormone responses to exercise
Keywords: هستند; E2; 17-β estradiol; E1; estrone; E1S; estrone sulfate; β-EN; beta-endorphin; ACTH; adrenocorticotropic hormone; DHEA; dehydroepiandrosterone; CEE; conjugated equine estrogens; ERT; estrogen replacement therapy; HRT; hormone replacement therapy; NHRT; no
Interactions between age, sex, and hormones in experimental ischemic stroke
Keywords: هستند; AChE; acetylcholinesterase; AIF; apoptosis inducing factor; AMP; adenosine monophosphate; ATP; adenosine-5â²-triphosphate; AVPV; anteroventral periventricular nucleus; BDNF; brain-derived neurotrophic factor; bFGF; basic fibroblast growth factor; BTK; Br
Aerobic training as an adjunctive therapy to enzyme replacement in Pompe disease
Keywords: هستند; GAA; acid α-glucosidase; rhGAA; recombinant human alglucosidase alfa; ERT; enzyme replacement therapy; GSDII; glycogen storage disease type II; CI-MPR; cation-independent mannose-6-phosphate receptor; PGC-1α; peroxisome proliferator-activated receptor g
The implementation of multi-task geophysical survey to locate Cleopatra Tomb at Tap-Osiris Magna, Borg El-Arab, Alexandria, Egypt “Phase II”
Keywords: هستند; Archaeology; Tap-Osiris Magna; Cleopatra Tomb; VLF-EM; ERT;
A saline tracer test monitored via both surface and cross-borehole electrical resistivity tomography: Comparison of time-lapse results
Keywords: هستند; ERT; Electrical resistivity tomography; Tracer test; Hydrogeology; Cross-hole methods
Analysis of rainfall distribution on spatial and temporal patterns of wheat yield in Mediterranean environment
Keywords: هستند; Yield spatial variability; Rainfall distribution; Fallow; Growing season; Wheat; ERT; NDVI
Geophysical investigations of geology and structure at the Martis Creek Dam, Truckee, California
Keywords: هستند; Earthen dams; Martis Creek; Truckee Basin; ERT; Magnetotellurics; Seismic methods
2-D joint structural inversion of cross-hole electrical resistance and ground penetrating radar data
Keywords: هستند; ERT; RTT; Joint structural inversion; Wavelet thresholding
Effect of aerobic and resistance exercise training on late-onset Pompe disease patients receiving enzyme replacement therapy
Keywords: هستند; GAA; acid α-glucosidase; ERT; enzyme replacement therapy; 6MWT; 6-min shuttle walk test; LBM; lean body mass; BMD; bone mineral density; DXA; dual X-ray absorbtiometry; Pompe disease; Aerobic training; Resistance exercise;
Diagnostic dilemma: A young woman with Fabry disease symptoms, no family history, and a “sequencing cryptic” α-galactosidase a large deletion
Keywords: هستند; α-Gal A; α-galactosidase A; GL-3 or Gb3; globotriaosylceramide; ERT; enzyme replacement therapy; MLPA; Multiplex Ligation-dependent Probe Amplification; PCR; polymerase chain reaction; Fabry disease; Lysosomal storage disease; α-galactosidase A; Gene r
The effects of Labisia pumila var. alata on bone markers and bone calcium in a rat model of post-menopausal osteoporosis
Keywords: هستند; LPva; Labisia pumila var. arata; ERT; Estrogen Replacement Therapy; CTx; Serum terminal C-telopeptide type 1 collagen; ELISA; Enzyme-linked immunosorbent assay; AAS; Atomic Absorption Spectrophotometer; Labisia pumila var. arata; Osteoporosis; Ovariectomy
Carotid intima-media thickness is increased in patients with mucopolysaccharidoses
Keywords: هستند; C-IMT; carotid intima-media thickness; MPS; mucopolysaccharidosis; GAG; glycosaminoglycan; ERT; enzyme replacement therapy; HSCT; hematopoietic stem cell transplant; CHOC; Children's Hospital of Orange County; IVSd; end-diastolic intraventricular septal t
Improving the accuracy of MRI spleen and liver volume measurements: A phase III Gaucher disease clinical trial setting as a model
Keywords: هستند; Gaucher disease; MRI; ERT; Spleen volume; Liver volume
Later-Onset Pompe Disease: Early Detection and Early Treatment Initiation Enabled by Newborn Screening
Keywords: هستند; CK; Creatine kinase; ERT; Enzyme replacement therapy; GMQ; Gross motor quotient; GAA; Acid α-glucosidase; NBS; Newborn screening; PDMS-II; Peabody Developmental Motor Scale, Second Edition;
Higher apoptotic state in Fabry disease peripheral blood mononuclear cells.
Keywords: هستند; Gb3; globotriaosylceramide; LSD; lysosomal storage disorder; ER; endoplasmic reticulum; MPS; mucopolysaccharidosis; PBMC; peripheral blood mononuclear cells; MFI; mean fluorescence intensity; ERT; enzyme replacement therapy; GLA; α-galactosidase A; DGJ;
Generation of induced pluripotent stem (iPS) cells derived from a murine model of Pompe disease and differentiation of Pompe-iPS cells into skeletal muscle cells
Keywords: هستند; GAA; Acid α-glucosidase; ERT; Enzyme replacement therapy; iPS; Induced pluripotent stem; Wt-iPS; Wild type-iPS; EB; Embryoid body; Pompe disease; Acid α-glucosidase; Induced pluripotent stem (iPS); Skeletal muscle; Reprogramming factor;
A novel mucopolysaccharidosis type I associated splice site mutation and IDUA splice variants
Keywords: هستند; Cq; quantification cycles; DS; dermatan sulfate; ERT; enzyme replacement therapy; GAGs; glycosaminoglycans; HSCT; hematopoietic stem cell transplantation; HS; heparan sulfate; IDUA; α-l-iduronidase; MPS I; mucopolysaccharidosis type I; PTC; premature ter
Prevalence and Characterization of Cardiac Involvement in Hunter Syndrome
Keywords: هستند; ECG; Electrocardiographic; ECHO; Echocardiographic; ERT; Enzyme replacement therapy; HOS; Hunter Outcome Survey; I2S; Iduronate-2-sulfatase; LVH; Left ventricular hypertrophy; LVM; Left ventricular mass; LVMh; Left ventricular mass indexed to height;
Neuroprotective effects of puerarin against beta-amyloid-induced neurotoxicity in PC12 cells via a PI3K-dependent signaling pathway
Keywords: هستند; AD; Alzheimer's disease; ERT; estrogen replacement therapy; SERMs; selective estrogen receptor modulators; MTT; 3-(4,5-dimethylthiazol-2-yl)-2,5-diphenyltetraz-olium bromide; LDH; Lactate dehydrogenase; FACS; Fluorescence activated cell sorting; PBS; phos
Murine β-galactosidase stability is not dependent on temperature or protective protein/cathepsin A
Keywords: هستند; A; alanine; ERT; enzyme replacement therapy; GLB1; β-galactosidase; GS; galactosialidosis; hGLB1; human GLB1; I; isoleucine; LSD; lysosomal storage disorder; M; methionine; mGLB1; mouse GLB1; NB-DGJ; N-butyldeoxygalactonojirimycin; PCR; polymerase chain
Newborn Bloodspot Screening for Lysosomal Storage Disorders
Keywords: هستند; ACMG; American College of Medical Genetics; DBS; Dried blood spot; ERT; Enzyme replacement therapy; HSCT; Hematopoietic stem cell transplantation; LSD; Lysosomal storage disorders; MPS; Mucopolysaccharidosis; MS/MS; Tandem mass spectrometry; NBS; Newborn
Impact of high-dose, chemically modified sulfamidase on pathology in a murine model of MPS IIIA
Keywords: هستند; MPS IIIA; Mucopolysaccharidosis IIIA; CNS; central nervous system; LSD; lysosomal storage disorder; SGSH; N-sulfoglucosamine sulfohydrolase; HS; heparan sulfate; ERT; enzyme replacement therapy; M6P; mannose-6-phosphate; M6PR; mannose-6-phosphate receptor
Early Clinical Markers of Central Nervous System Involvement in Mucopolysaccharidosis Type II
Keywords: هستند; CNS; Central nervous system; ERT; Enzyme replacement therapy; GAG; Glycosaminoglycan; IT; Intrathecal; MPS II; Mucopolysaccharidosis type II; NP; Neural parenchyma;
Assessment of integrated electrical resistivity data on complex aquifer structures in NE Nuba Mountains – Sudan
Keywords: هستند; 3D; VES; ERT; Nuba Mountains; Sudan
4D active time constrained resistivity inversion
Keywords: هستند; 4D; Time lapse; Inversion; ERT; Resistivity; Geophysical monitoring;
Research reportNeuroprotective action of proline-rich polypeptide-1 in β-amyloid induced neurodegeneration in rats
Keywords: هستند; Neurodegeneration; β-Amyloid; PRP-1; Neuroprotection; ANOVA; analysis of variance; Aβ; beta-amyloid; AD; Alzheimer disease; β-ARs; β-adrenoreceptors; EEC; European Communities Council; EC; entorhinal cortex; ERT; estrogen replacement therapy; FDA; Fed
Geophysical exploration for lithological control of arsenic contamination in groundwater in Middle Ganga Plains, India
Keywords: هستند; Groundwater; Arsenic contamination; Claybarrier; Geophysical surveys; ERT; TEM
Assessing the contribution of electrical resistivity tomography (ERT) and self-potential (SP) methods for a water well drilling program in fractured/karstified limestones
Keywords: هستند; ERT; SP; Fractures; Limestone; Coupling coefficient; Boreholes;
Structural study of the Ballandaz landslide (French Alps) using geophysical imagery
Keywords: هستند; Seismics; ERT; Landslide; French Alps
Pathogenesis of aortic dilatation in mucopolysaccharidosis VII mice may involve complement activation
Keywords: هستند; MPS; mucopolysaccharidosis; Cts; cathepsin; MMP; matrix metalloproteinase; GUSB; β-glucuronidase; GAGs; glycosaminoglycans; TLR4; toll-like receptor 4; TNFα; tumor necrosis factor alpha; IL-6; interleukin 6; M6P; mannose 6-phosphate; ERT; enzyme replace
Digital photogrammetric analysis and electrical resistivity tomography for investigating the Picerno landslide (Basilicata region, southern Italy)
Keywords: هستند; Roto-translational slide; Aerial photos; Analytical and digital photogrammetry; ERT; DEM difference
Mapping of contaminant plumes with geoelectrical methods. A case study in urban context
Keywords: هستند; Urban contaminated sites; Geoelectrical; IP; Organic phase; Biodegradation; ERT
Prognostic factors for the late onset Pompe disease with enzyme replacement therapy: From our experience of 4 cases including an autopsy case
Keywords: هستند; Pompe disease; Late onset; GAA; ERT; PVOD;
Home treatment with intravenous enzyme replacement therapy with idursulfase for mucopolysaccharidosis type II - data from the Hunter Outcome Survey
Keywords: هستند; BiPAP; bi-level positive airway pressure; CPAP; continuous positive airway pressure; ERT; enzyme replacement therapy; GAG; glycosaminoglycan; HOS; Hunter Outcome Survey; I2S; iduronate-2-sulfatase; IRR; infusion-related reaction; MPS II; mucopolysaccharid
Detection of soil moisture and vegetation water abstraction in a Mediterranean natural area using electrical resistivity tomography
Keywords: هستند; Electrical resistivity tomography; ERT; Water availability; Rooting depth; Rocky soils; Mediterranean
The breast cancer “plunge” after initial publication of the WHI results: An alternative explanation
Keywords: هستند; Breast cancer; Hormone therapy; Estrogen–progestin therapy; Estrogen-only therapy; HRT; HT; ERT; ET; WHI study; SEER 9 database
CFD and ERT investigations on two-phase flow regimes in vertical and horizontal tubes
Keywords: هستند; Two-phase flow; ERT; Modeling; VOF; CFD
Analysis of partial suspension in stirred mixing cells using both MRI and ERT
Keywords: هستند; Tomography; MRI; ERT; Mixing; Partial suspension; Velocity field
An electrical resistance tomography method for determining mixing in batch addition with a level change
Keywords: هستند; Tomography; Mixing; Batch production; Level change; ERT