Keywords: فومارات هیدراتاز; Galectin-3; Fumarate hydratase; Fibroblasts; Aortic stenosis;
مقالات ISI فومارات هیدراتاز (ترجمه نشده)
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Keywords: فومارات هیدراتاز; AML; Acute myeloid leukemia; BBB; blood-brain barrier; BCAAs; branched-chain amino acids; ecDNA; extrachromosomal DNA; FH; fumarate hydratase; GBM; glioblastoma multiforme; HIF1/2; hypoxia-inducible factor 1/2; IDH1/2; isocitrate dehydrogenases 1/2; LXR;
Keywords: فومارات هیدراتاز; HNE; 4-hydroxynonenal; NMR; nuclear magnetic resonance; MS; mass spectrometry; LC-MS; liquid chromatography-mass spectrometry; GC-MS; gas chromatography-mass spectrometry; CE-MS; capillary electrophoresis-mass spectrometry; MALDI-IMS; matrix-assisted lase
Keywords: فومارات هیدراتاز; ETC; electron transport complexes; ROS/RNS; reactive oxygen or nitrogen spices; âÏm; mitochondrial inner membrane potential; TCA; TriCarboxylic acid cycle; MPTP; mitochondrial permeability transition pore; mtDNA; mitochondrial DNA; ND5; NADH dehydrogen
Keywords: فومارات هیدراتاز; 2-DG; 2-deoxyglucose; 2-HG; 2-hydroxyglutarate; 5mC; 5-methlycystosine; ACACA; acetyl-CoA carboxylase; AML; acute myeloid leukemia; AMPK; adenosine monophosphate-activated protein kinase; ATP; adenosine triphosphate; ALDH; aldehyde dehydrogenase; ADCs; an
Keywords: فومارات هیدراتاز; Hereditary leiomyomatosis and renal cell cancer; fumarate hydratase; atypical leiomyoma; myomectomy;
Keywords: فومارات هیدراتاز; Non-small cell lung cancer; Tricarboxylic acid cycle; Succinate dehydrogenase; Fumarate hydratase; Isocitrate dehydrogenase; Single nucleotide polymorphisms; Prognosis;
Keywords: فومارات هیدراتاز; AMDIS; automated mass spectral deconvolution and identification system; ANOVA; analysis of variance; EI; electron ionization; ER; estrogen receptor; FH; fumarate hydratase; GC; gas chromatography; HER2; human epidermal growth factor receptor 2; HIF; hypox
Keywords: فومارات هیدراتاز; ACSS; acetyl-CoA synthetase; ADI; arginine deiminase; AML; acute myeloid leukaemia; AMPK; AMP-activated protein kinase; ALL; acute lymphoblastic leukaemia; ASS; argininosuccinate synthase; BCAAs; branched-chain amino acids; BPTES; bis-2-(5-phenylacetamido
Keywords: فومارات هیدراتاز; α-KG; alpha-ketoglutarate; 2-HG; 2-hydroxyglutarate; 5hmC; 5-hydroxymethylcytosine; 5mC; 5-methylcytosine; AML; acute myeloid leukemia; ASXL1; additional sex combs-like 1; AZA; azacytidine; CMML; chronic myelomonocytic leukemia; DAC; decitabine; DNMT3A;
Keywords: فومارات هیدراتاز; ACLY; ATP-citrate lyase; ATM; ataxia telangiectasia mutated; BCL-2; B-cell leukemia-2; Chk2; checkpoint homolog kinase 2; CiC; citrate carrier; DIC; dicarboxylate carrier; DNMT; DNA methyltransferase; FH; fumarate hydratase; H3K27; histone 3 lysine 27; HA
Keywords: فومارات هیدراتاز; Coupled assay; Fumarate hydratase; Oxaloacetate decarboxylating malic enzyme; Succinate:ubiquinone oxidoreductase;
Case ReportAn atypical case of Hereditary Leiomyomatosis and Renal Cell Cancer (HLRCC)-associated renal cell carcinoma identified by next-generation sequencing
Keywords: فومارات هیدراتاز; Renal cell carcinoma; HLRCC; Fumarate hydratase; Next-generation sequencing;
SWI/SNF protein expression status in fumarate hydratase-deficient renal cell carcinoma: immunohistochemical analysis of 32 tumors from 28 patients
Keywords: فومارات هیدراتاز; SWI/SNF complex; HLRCC; Fumarate hydratase; Renal cell carcinoma; SMARCB1; INI1; ARID1A;
Fumarate hydratase-specific T cell response in Chinese patients with autoimmune hepatitis
Keywords: فومارات هیدراتاز; Autoimmune hepatitis; Fumarate hydratase; T cell response; Cytokines;
Next generation immunohistochemistry: Emerging substitutes to genetic testing?
Keywords: فومارات هیدراتاز; PRKAR1A; β-catenin; SDHB; Fumarate hydratase; 2SC; HRASQ61R; BAP1; Parafibromin; Glucagon; Carney complex; FAP-associated cribriform-morular variant of papillary thyroid carcinoma; Familial succinate dehydrogenase-related pheochromocytoma/paraganglioma;
Current PerspectiveHIF-2alpha: Achilles' heel of pseudohypoxic subtype paraganglioma and other related conditions
Keywords: فومارات هیدراتاز; Hypoxia-inducible factor; Paraganglioma; Renal cell carcinoma; von Hippel-Lindau; Krebs cycle; SDHx; Succinate dehydrogenase complex; FH; Fumarate hydratase; MDH2; Malate dehydrogenase 2; VHL; Von Hippel-Lindau; HIF2A; Hypoxia-inducible factor 2 alpha; PH
Molecular Dissection of Complete Response to Receptor Tyrosine Kinase Inhibition in Type II Papillary Renal Cell Carcinoma
Keywords: فومارات هیدراتاز; DNA damage repair; Fumarate hydratase; Hereditary leiomyomatosis and renal cell cancer; Pazopanib; Sunitinib;
Subcellular localization of glycolytic enzymes and characterization of intermediary metabolism of Trypanosoma rangeli
Keywords: فومارات هیدراتاز; ALD; aldolase; ENO; enolase; FH; fumarate hydratase; FRD; fumarate reductase; GALK; galactokinase; GAPDH; glyceraldehyde-3-phosphate dehydrogenase; GlcK; glucokinase; GlDH; glutamate dehydrogenase; GPDH; glycerol-3-phosphate dehydrogenase; G6PDH; glucose-
Dual loss of succinate dehydrogenase (SDH) and complex I activity is necessary to recapitulate the metabolic phenotype of SDH mutant tumors
Keywords: فومارات هیدراتاز; 3-NPA; 3-nitropropionic acid; Co; complex; FH; fumarate hydratase; PC; pyruvate carboxylase; TCA cycle; tricarboxylic acid cycle; SDH; succinate dehydrogenase; 3-nitropropionic acid (PubChem CID: 1678); Atpenin A5 (PubChem CID: 54676868); rotenone (PubChe
Transcriptomic and proteomic analyses of leaves from Clematis terniflora DC. under high level of ultraviolet-B irradiation followed by dark treatment
Keywords: فومارات هیدراتاز; ACL; ATP-citrate lyase; AH; aconitate hydratase; CCD; carotenoid cleavage dioxygenase; CCR; cinnamoyl-CoA reductase; CHS; chalcone synthase; COMT; caffeic acid 3-O-methyltransferase; CS; citrate synthase; CMS; chorismate synthase; C4H; trans-cinnamate 4-m
The Crabtree and Warburg effects: Do metabolite-induced regulations participate in their induction?
Keywords: فومارات هیدراتاز; 2HG; 2-hydroxyglutarate; 6PGD; 6-phosphogluconate dehydrogenase; ACC; acetyl-CoA carboxylase; ANT; adenine nucleotide translocase; ADP; adenosine diphosphate; AMP; adenosine monophosphate; AMPK; AMPKinase; ATP; adenosine triphosphate; Fru6P; fructose 6 ph
Mitochondrial dysfunctions in cancer: Genetic defects and oncogenic signaling impinging on TCA cycle activity
Keywords: فومارات هیدراتاز; Isocitrate dehydrogenase; Fumarate hydratase; Succinate dehydrogenase; HIF; p53; Aconitase;
A novel effect of DMOG on cell metabolism: direct inhibition of mitochondrial function precedes HIF target gene expression
Keywords: فومارات هیدراتاز; α-KG; α-ketoglutarate; AMPK; AMP-activated protein kinase; DMSO; dimethyl sulfoxide; EGFP; enhanced green fluorescence protein; EPAS1; endothelial PAS domain-containing protein 1 (known as HIF-2α); EPO; erythropoietin; esiRNA; endoribonuclease-prepared
Redox proteomic identification of HNE-bound mitochondrial proteins in cardiac tissues reveals a systemic effect on energy metabolism after doxorubicin treatment
Keywords: فومارات هیدراتاز; DOX; doxorubicin; ATP5B; ATP synthase subunit β; DLD; dihydrolipoyl dehydrogenase; SDHA; succinate dehydrogenase [ubiquinone] flavoprotein subunit; NDUFS2; NADH dehydrogenase [ubiquinone] iron-sulfur protein 2; ROS; reactive oxygen species; HNE; 4-hydr
Quantitative proteomic analysis of the inhibitory effects of CIL-102 on viability and invasiveness in human glioma cells
Keywords: فومارات هیدراتاز; CIL-102; Fumarate hydratase; ROS; JNK1/2; p70S6K;
Adrenal Nodular Hyperplasia in Hereditary Leiomyomatosis and Renal Cell Cancer
Keywords: فومارات هیدراتاز; kidney; leiomyomatosis and renal cell cancer, hereditary; adrenal gland diseases; fumarate hydratase; diagnostic imagingACTH, adrenocorticotropic hormone; CT, computerized tomography; FDG, fludeoxyglucose; FH, fumarate hydratase; HLRCC, hereditary leiomyo
Fumarate hydratase isoforms of Leishmania major: Subcellular localization, structural and kinetic properties
Keywords: فومارات هیدراتاز; FH; fumarate hydratase; LmFH; fumarate hydratase from Leishmania major; LmFH-1; fumarate hydratase from L. major encoded by LmjF24.0320 gene; LmFH-2; fumarate hydratase from L. major encoded by LmjF29.1960 gene; Fumarate hydratase; Leishmania major; cell
Metabolic reprogramming in cancer: Unraveling the role of glutamine in tumorigenesis
Keywords: فومارات هیدراتاز; Gls; glutaminase; GDH; glutamate dehydrogenase; PC; pyruvate carboxylase; GFAT; fructose-6-phosphate amido-transferase; GSH; glutathione; GlcNAc; N-acetyl-d-glucosamine; PRPP; 5-phospho-α-d-ribosyl 1-pyrophosphate; AOA; aminooxyacetate; EAA; essential am
A two-dimensional screen for AMPK substrates identifies tumor suppressor fumarate hydratase as a preferential AMPKα2 substrate
Keywords: فومارات هیدراتاز; AMP-activated protein kinase; cell signaling; fumarate hydratase; protein kinase substrates; protein phosphorylation; surface plasmon resonance
Cellular prion protein overexpression disturbs cellular homeostasis in SH-SY5Y neuroblastoma cells but does not alter p53 expression: a proteomic study
Keywords: فومارات هیدراتاز; prion protein; signal transduction; cytoskeleton; protein folding; annexin V; transgelin 2; ADHX; alcohol dehydrogenase class III; ANXA5; annexin V; CV028; UPF0027 protein; DMEM; Dulbecco's modified Eagle medium; FCS; fetal calf serum; FKBP4; FK506-bindin
New genes and/or molecular pathways associated with adrenal hyperplasias and related adrenocortical tumors
Keywords: فومارات هیدراتاز; Phosphodiesterases; Multiple endocrine neoplasia; Carney triad; Carney-Stratakis syndrome; Fumarate hydratase;
Hereditary multiple cutaneous leiomyoma resulting from novel mutations in the fumarate hydratase gene
Keywords: فومارات هیدراتاز; Leiomyoma; Fumarate hydratase; Hereditary multiple leiomyoma of the skin; Multiple cutaneous and uterine leiomyoma;
Differential metabolic consequences of fumarate hydratase and respiratory chain defects
Keywords: فومارات هیدراتاز; Mitochondria; Fumarate hydratase; Redox state; Respiratory chain defect
Conventional renal cancer in a patient with fumarate hydratase mutation
Keywords: فومارات هیدراتاز; HLRCC; Bilateral renal cell cancer; Clear cell; fumarate hydratase; FH
Compensatory alterations in energy homeostasis characterized in uterine tumors from hereditary leiomyomatosis and renal cell cancer
Keywords: فومارات هیدراتاز; Hereditary leiomyomatosis and renal cell cancer; fumarate hydratase; leiomyoma; glycolysis; enolase; aldolase; pyruvate kinase; Krebs cycle;
No evidence for epigenetic inactivation of fumarate hydratase in leiomyomas and leiomyosarcomas
Keywords: فومارات هیدراتاز; Fumarate hydratase; Leiomyoma; Leiomyosarcoma; Western blotting
Mitochondrial disorders in renal tumors
Keywords: فومارات هیدراتاز; Hypoxia-inducible factor; Mitochondria; Kidney cancer; Oncocytoma; Clear cell renal carcinoma; Reactive oxygen species; Succinate dehydrogenase; Fumarate hydratase