Keywords: هیپوگاماگلوبولینمی; Intravenous immunoglobulin; Subcutaneous immunoglobulin; Hypogammaglobulinemia; Chronic lymphocytic leukemia; Lymphoma; Myeloma; Hematopoietic cell transplantation; Anaphylaxis; CAR-T therapy; B-cell signaling and survival pathways.;
مقالات ISI هیپوگاماگلوبولینمی (ترجمه نشده)
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Keywords: هیپوگاماگلوبولینمی; lung transplantation; infection; hypogammaglobulinemia; BAFF; risk factors;
Keywords: هیپوگاماگلوبولینمی; Hypogammaglobulinemia; Infections; Multiple myeloma; Quality of life; Subcutaneous immunoglobulin;
Keywords: هیپوگاماگلوبولینمی; Hashimoto encephalopathy; corticosteroid treatment; anti-B-cell therapy; rituximab; hypogammaglobulinemia;
Keywords: هیپوگاماگلوبولینمی; Common variable immunodeficiency; IgA deficiency; Diagnostic delay; Primary antibody deficiency; Hypogammaglobulinemia;
Keywords: هیپوگاماگلوبولینمی; Chronic lymphocytic leukaemia; Infections; Secondary cancers; Autoimmune diseases; Hypogammaglobulinemia;
Keywords: هیپوگاماگلوبولینمی; complement; heart transplantation; hypogammaglobulinemia; infection; risk factors;
Keywords: هیپوگاماگلوبولینمی; Single ventricle; Fontan; Protein-losing enteropathy (PLE); T-cell lymphopenia; Hypogammaglobulinemia; Secondary immunodeficiency; Warts; ALC; absolute lymphocyte count; NK; natural killer; PLE; protein-losing enteropathy; SVSP; Single Ventricle Survivors
Keywords: هیپوگاماگلوبولینمی; Primary immunodeficiency; Common variable immunodeficiency; Bronchial asthma; Wheezes; Airway infection; Hypogammaglobulinemia
Keywords: هیپوگاماگلوبولینمی; Pneumonia; Bronchiectasis; Common variable immunodeficiency; Hypogammaglobulinemia
Keywords: هیپوگاماگلوبولینمی; Hypogammaglobulinemia; Serum protein electrophoresis; Immunofixation electrophoresis; Monoclonal protein;
Keywords: هیپوگاماگلوبولینمی; Rituximab; ANCA; Vasculitis; Autoimmune; Hypogammaglobulinemia; Infection;
Keywords: هیپوگاماگلوبولینمی; Non-Hodgkin lymphoma; Rituximab; Fludarabine; Hypogammaglobulinemia
Keywords: هیپوگاماگلوبولینمی; Common variable immunodeficiency; hypogammaglobulinemia; hematopoietic stem cell transplantation; immunologic reconstitution; immunoglobulin substitution/replacement; outcome; mortality; survival; aGvHD; Acute graft-versus-host disease; BM; Bone marrow; c
Keywords: هیپوگاماگلوبولینمی; Hypogammaglobulinemia; Etiology; Infection; Vaccination
Keywords: هیپوگاماگلوبولینمی; Rituximab; Immunodeficiency; Hypogammaglobulinemia; Immunoglobulin replacement therapy; IGRT; B-cell phenotype; Persistent immunodeficiency after treatment with immunomodulatory drug; PITID; AIHA; Autoimmune hemolytic anemia; CLL; Chronic lymphocytic leuk
The Brain-Lung-Thyroid syndrome (BLTS): A novel deletion in chromosome 14q13.2-q21.1 expands the phenotype to humoral immunodeficiency
Keywords: هیپوگاماگلوبولینمی; NKX2-1; Brain-lung-thyroid syndrome; NFKBIA; Hypogammaglobulinemia; Joint hyperlaxity;
Combined immunodeficiency and atopy caused by a dominant negative mutation in caspase activation and recruitment domain family member 11 (CARD11)
Keywords: هیپوگاماگلوبولینمی; Caspase activation and recruitment domain family member 11; combined immunodeficiency; hypogammaglobulinemia; nuclear factor κB; cytokine secretion; T-cell repertoire; T-cell mitogen and antigen responses; autoimmunity; asthma; eczema and food allergies;
Good syndrome associated with pure red cell aplasia in a patient with a history of thymoma: A case report and literature review
Keywords: هیپوگاماگلوبولینمی; Good syndrome; Pure red cell aplasia; Thymoma; Hypogammaglobulinemia;
Clinical relevance of hypogammaglobulinemia, clinical and biologic variables on the infection risk and outcome of patients with stage A chronic lymphocytic leukemia
Keywords: هیپوگاماگلوبولینمی; Chronic lymphocytic leukemia; Immunoglobulins; Hypogammaglobulinemia; Infections; A stage;
Defective IL-4 signaling in T cells defines severe common variable immunodeficiency
Keywords: هیپوگاماگلوبولینمی; Autoimmunity; CVID; IL-4Rα; Th1; T cell; Phospho-flow cytometry; IL-4 signaling; Hypogammaglobulinemia;
Damaging heterozygous mutations in NFKB1 lead to diverse immunologic phenotypes
Keywords: هیپوگاماگلوبولینمی; Nuclear factor κ light-chain enhancer of activated B cells; hypogammaglobulinemia; autoinflammation; Behçet disease; NFKB1; p50; p105; B cell; IκBα; NF-κB inhibitor α; IKK; Inhibitor of κB kinase; NEMO; NF-κB essential modulator; NF-κB; Nuclear f
Amylose pulmonaire AL révélée par une toux : à propos d'une observation
Keywords: هیپوگاماگلوبولینمی; Amylose; Myélome; Pneumopathie interstitielle; Hypogammaglobulinémie; Amyloidosis; Multiple myeloma; Interstitial pneumonia; Hypogammaglobulinemia;
The extended phenotype of LPS-responsive beige-like anchor protein (LRBA) deficiency
Keywords: هیپوگاماگلوبولینمی; LPS-responsive beige-like anchor protein; primary immunodeficiency; common variable Immunodeficiency; autoimmunity; hypogammaglobulinemia; enteropathy; lymphoproliferation; ALPS; Autoimmune lymphoproliferative syndrome; ALPS-Ph; Autoimmune lymphoprolifera
Exclusion of Patients with a Severe T-Cell Defect Improves the Definition of Common Variable Immunodeficiency
Keywords: هیپوگاماگلوبولینمی; CVID; Definition; Hypogammaglobulinemia; Immunodeficiency; Late onset combined immunodeficiency; Prognosis; CID; Combined immunodeficiency; CVID; Common variable immunodeficiency; ESID; European Society for Immune Deficiency; HGUS; Hypogammaglobulinemia o
Immune deficiencies, infection, and systemic immune disordersDefects of B-cell terminal differentiation in patients with type-1 Kabuki syndrome
Keywords: هیپوگاماگلوبولینمی; Kabuki syndrome; KMT2D; KDM6A; hypogammaglobulinemia; memory B cells; CD21lo B cells; class-switch recombination; somatic hypermutation; PTIP; AICDA; AID; polymerase eta; AICDA; Activation-induced cytidine deaminase; cKS; Clinical Kabuki syndrome (no iden
Immunoglobulin G replacement for the treatment of infective complications of rituximab-associated hypogammaglobulinemia in autoimmune disease: A case series
Keywords: هیپوگاماگلوبولینمی; Rituximab; Vasculitis; Autoimmune; Hypogammaglobulinemia; Infection; Replacement therapy;
CD21 and CD19 deficiency: Two defects in the same complex leading to different disease modalities
Keywords: هیپوگاماگلوبولینمی; CD21; CD19; CD81; Hypogammaglobulinemia; Primary antibody deficiency;
Substytucja immunoglobulin u chorych na przewlekłą białaczkę limfocytową i szpiczaka plazmocytowego
Keywords: هیپوگاماگلوبولینمی; przewlekła białaczka limfocytowa; szpiczak plazmocytowy; immunoglobuliny; powikłania infekcyjne; hypogammaglobulinemiaChronic lymphocytic leukemia; Plasma cell myeloma; Immunoglobulin; Infectious complications; Hypogammaglobulinemia
Preliminary reportSubcutaneous IgG replacement therapy is safe and well tolerated in lung transplant recipients
Keywords: هیپوگاماگلوبولینمی; Lung transplant; Hypogammaglobulinemia; Subcutaneous IgG;
Granulomatoses au cours des déficits immunitaires primitifs de l’adulte
Keywords: هیپوگاماگلوبولینمی; Déficit immun commun variable; Hypogammaglobulinémie; Granulomatose; SarcoïdoseCommon variable immunodeficiency; Hypogammaglobulinemia; Granulomatosis; Sarcoidosis
Association Between Low Serum Zinc Concentration and Hypogammaglobulinemia in Foals of Different Age Categories
Keywords: هیپوگاماگلوبولینمی; Zinc; Hypogammaglobulinemia; Foals; Trace elements; Serum proteins;
Incidence of Hypogammaglobulinemia in Patients Receiving Rituximab and the Use of Intravenous Immunoglobulin for Recurrent Infections
Keywords: هیپوگاماگلوبولینمی; Gamma globulin; Hypogammaglobulinemia; Infections; Lymphoma; Rituximab
Bronchiolitis obliterans syndrome, hypogammaglobulinemia, and infectious complications of lung transplantation
Keywords: هیپوگاماگلوبولینمی; bronchiolitis obliterans syndrome; hypogammaglobulinemia; fungal infection; community-acquired respiratory viral infection; lung transplantation;
TACI mutations and impaired B-cell function in subjects with CVID and healthy heterozygotes
Keywords: هیپوگاماگلوبولینمی; CVID; TACI; hypogammaglobulinemia; activation-induced cytidine deaminase; Toll-like receptor 9AID, Activation induced cytidine deaminase; APRIL, A proliferation-inducing ligand; BAFF, B-cell activating factor; BCMA, B-cell maturation antigen; CpG, Cytosin
Deficiency of caspase recruitment domain family, member 11 (CARD11), causes profound combined immunodeficiency in human subjects
Keywords: هیپوگاماگلوبولینمی; CARD11; human; combined immunodeficiency; hypogammaglobulinemia; profound combined immunodeficiency disorder; transitional B cell; nuclear factor κB; B cell-activating factor receptor; inducible T-cell costimulator; germinal center; APC; Allophycocyanin;
Diagnosis and Treatment of Gastrointestinal Disorders in Patients With Primary Immunodeficiency
Keywords: هیپوگاماگلوبولینمی; Immune System; Hypogammaglobulinemia; IBD; Inflammatory Intestinal Disease; 6-MP; mercaptopurine; AZA; azathioprine; CGD; chronic granulomatous disease; CVID; common variable immunodeficiency; FOXP3; forkhead box P3; GI; gastrointestinal; GVHD; graft-vers
Antibody deficiency in patients with ataxia telangiectasia is caused by disturbed B- and T-cell homeostasis and reduced immune repertoire diversity
Keywords: هیپوگاماگلوبولینمی; Ataxia telangiectasia; class switch recombination; somatic hypermutation; κ-deleting recombination excision circle; hypogammaglobulinemia; B-cell subsets; T-cell subsets; AT; Ataxia telangiectasia; ATM; Ataxia telangiectasia mutated; DSB; Double-strand b
Une maladie systémique génétique : description clinique chez l’adulte de la dystrophie myotonique de type 1
Keywords: هیپوگاماگلوبولینمی; Dystrophie myotonique; Cardiopathie; Insuffisance respiratoire; Cataracte; Hypogammaglobulinémie; Troubles du sommeil; Troubles métaboliques; Troubles endocriniensMyotonic dystrophy; Cardiopathy; Restrictive lung disease; Cataract; Hypogammaglobulinemia;
Serum killing of Ureaplasma parvum shows serovar-determined susceptibility for normal individuals and common variable immuno-deficiency patients
Keywords: هیپوگاماگلوبولینمی; SV; serovar; U; Ureaplasma; CVID; common variable immunodeficiency; MAC; membrane attack complex; HPA; health protection agency; USM; Ureaplasma specific growth medium; CFB; complement fixation buffer; VBS; veronal buffered saline; HI-NHS; heat inactivate
Adult Primary Immune Deficiency: What Are We Missing?
Keywords: هیپوگاماگلوبولینمی; Adult; Clinical; Common variable immune deficiency; Good's syndrome; Hypogammaglobulinemia; Immune deficiency; Primary immune deficiency; T-cell immune deficiency
CD27 deficiency is associated with combined immunodeficiency and persistent symptomatic EBV viremia
Keywords: هیپوگاماگلوبولینمی; EBV; viremia; hypogammaglobulinemia; CD27; immunodeficiency; T cell; B cell; natural killer cell; phenotype; CTL; Cytotoxic T lymphocyte; CVID; Common variable immunodeficiency; FACS; Fluorescence-activated cell sorting; GC; Germinal center; NK; Natural k
Clinical, molecular, and cellular immunologic findings in patients with SP110-associated veno-occlusive disease with immunodeficiency syndrome
Keywords: هیپوگاماگلوبولینمی; Veno-occlusive disease with immunodeficiency; hypogammaglobulinemia; SP110; B-cell development; BMT; Bone marrow transplantation; CD40L; CD40 ligand; CMV; Cytomegalovirus; DAVID; Database for Annotation, Visualization and Integrated Discovery; hVOD; Hepat
Genetic CD21 deficiency is associated with hypogammaglobulinemia
Keywords: هیپوگاماگلوبولینمی; CD21; complement receptor; hypogammaglobulinemia; common variable immunodeficiency; B lymphocyte; α-kLC; Goat F(abâ²)2 anti-human κ light chain antibodies; BCR; B-cell receptor; CR; Complement receptor; CVID; Common variable immunodeficiency; PnPS14; P
Diagnostic strategy for patients with hypogammaglobulinemia in rheumatology
Keywords: هیپوگاماگلوبولینمی; Hypogammaglobulinemia; Chronic inflammatory rheumatism; Primary immunodeficiency; Diagnosis; Etiologies
Bone marrow failure due to T-cell large granular lymphocytic leukemia in a patient with essential thrombocythemia
Keywords: هیپوگاماگلوبولینمی; Cyclosporine; Hydroxyurea; Hypogammaglobulinemia; T-LGLL; Thrombocytosis;
The C76R transmembrane activator and calcium modulator cyclophilin ligand interactor mutation disrupts antibody production and B-cell homeostasis in heterozygous and homozygous mice
Keywords: هیپوگاماگلوبولینمی; Hypogammaglobulinemia; B cell; common variable immunodeficiency; primary immunodeficiency; transmembrane activator and calcium modulator cyclophilin ligand; a proliferation-inducing ligand; lymphoproliferation; APRIL; A proliferation-inducing ligand; BAFF
Progressive multifocal leukoencephalopathy in a patient with Good's syndrome
Keywords: هیپوگاماگلوبولینمی; Thymoma; Hypogammaglobulinemia; JC virus; Progressive multifocal leukoencephalopathy; Good's syndrome
Fatal adult-onset antibody deficiency syndrome in a patient with cartilage hair hypoplasia
Keywords: هیپوگاماگلوبولینمی; Cartilage hair hypoplasia; Primary immunodeficiency; Hypogammaglobulinemia
Lichen plan buccal érosif associé à un syndrome de Good
Keywords: هیپوگاماگلوبولینمی; Syndrome de Good; Lichen plan buccal érosif; Hypogammaglobulinémie; ThymomeGood syndrome; Oral erosive lichen planus; Hypogammaglobulinemia; Thymoma