
Repetitive nerve stimulation transiently opens the mitochondrial permeability transition pore in motor nerve terminals of symptomatic mutant SOD1 mice
Keywords: انتقال نفوذی میتوکندری منفی است; CsA; cyclosporin A; DAP; diaminopyridine; ETC; electron transport chain; fALS; familial amyotrophic lateral sclerosis; LAL; levator auris longus muscle; mPTP; mitochondrial permeability transition pore; Rh-123; rhodamine 123; SOD1; Cu/Zn superoxide dismut