دانلود مقالات ISI درباره Ncl + ترجمه فارسی

Compartmentalized zinc deficiency and toxicities caused by ZnT and Zip gene over expression result in specific phenotypes in Drosophila

Keywords: ER; endoplasmic reticulum; (e)GFP; (enhanced) green fluorescent protein; RFP; red fluorescent protein; Ztox; zinc toxicity; NCL; neuronal ceroid lipofuscinosis; Drosophila; Zinc homeostasis; Zip; ZnT; Ion transport;

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2015 سفارش ترجمه

Mechanistic studies of anticancer aptamer AS1411 reveal a novel role for nucleolin in regulating Rac1 activation

Keywords: AS1411; Aptamer; Nucleolin; Rac1; Methuosis; Macropinocytosis; CRO; cytosine-rich oligonucleotide (an inactive control sequence); G-LISA; GTPase-linked immunosorbent assay; G-rich; guanosine-rich; MP; macropinocytosis; NCL; nucleolin; NIH; National Instit

دانلود رایگان متن کامل مقاله ISI 14 صفحه سال انتشار : 2015 سفارش ترجمه

Numerical modeling of supercritical CO2 natural circulation loop

Keywords: 1D; one dimensional; 2D; two dimensional; BARC; Bhabha Atomic Research Centre; CFD; computational fluid dynamics; CHF; critical heat flux; HHHC; horizontal heater horizontal cooler; HHVC; horizontal heater vertical cooler; NCL; natural circulation loop; N

دانلود رایگان متن کامل مقاله ISI 16 صفحه سال انتشار : 2015 سفارش ترجمه

A rewriting logic semantics for NCL

Keywords: Multimedia document validation; Multimedia authoring; Rewriting theory; Maude; NCL

دانلود رایگان متن کامل مقاله ISI 29 صفحه سال انتشار : 2015 سفارش ترجمه

Clinical, Electrophysiological, Imaging, and Ultrastructural Description in 68 Patients With Neuronal Ceroid Lipofuscinoses and Its Subtypes

Keywords: histopathology; MRI; neuronal ceroid lipofuscinoses; NCL; skin; ultrastructure;

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2014 سفارش ترجمه

Gene disruption of Mfsd8 in mice provides the first animal model for CLN7 disease

Keywords: β-gal; β-galactosidase; CtsD; cathepsin D; CD68; cluster of differentiation 68; GFAP; glial fibrillary acidic protein; Lamp1; lysosome-associated membrane protein 1; Lamp2; lysosome-associated membrane protein 2; MFSD8; major facilitator superfamily dom

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2014 سفارش ترجمه

Case studyCLN6 disease caused by the same mutation originating in Pakistan has varying pathology

Keywords: Batten; Neuronal ceroid lipofuscinosis; NCL; CLN6; Pathology; Prenatal;

دانلود رایگان متن کامل مقاله ISI 4 صفحه سال انتشار : 2013 سفارش ترجمه

Amlodipine prevents apoptotic cell death by correction of elevated intracellular calcium in a primary neuronal model of Batten disease (CLN3 disease)

Keywords: CLN; ceroid-lipofuscinosis neuronal (gene symbol); NCL; neuronal ceroid-lipofuscinoses; GFP; green fluorescent protein; siRNA; small inhibiting RNA; Primary neurons; Batten disease; Apoptosis; L-type calcium channel antagonists; Calcium signaling;

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2013 سفارش ترجمه

Proteomic profiling of a mouse model of acute intestinal Apc deletion leads to identification of potential novel biomarkers of human colorectal cancer (CRC)

Keywords: AhCre+Apcfl/fl; acute conditional transgenic deletion of the Apc gene in the murine intestinal epithelium; AhCre+Apc+/+; wild type control for acute conditional transgenic deletion of the Apc gene in the murine intestinal epithelium; Apc; adenomatous poly

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2013 سفارش ترجمه

Design, synthesis and evaluation of antimicrobial activity of N-terminal modified Leucocin A analogues

Keywords: AMP; antimicrobial peptide; CD; circular dichroism; DIC; 1,3-diisopropylcarbodiimide; Fmoc; 9-fluorenylmethyloxycarbonyl; HOBt; N-hydroxybenzotriazole; RP-HPLC; reversed phase high performance liquid chromatography; LAB; lactic acid bacteria; LeuA; Leucoc

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2013 سفارش ترجمه

Research Report17β-Hydroxysteroid dehydrogenase Type IV, a Z-linked gene, is higher in females than in males in visual and auditory regions of developing zebra finches

Keywords: E2; estradiol; HSD17B4; 17β-hydroxysteroid dehydrogenase type IV; Hp; hippocampus; HA; hyperpallium apicale; NCM; caudomedial nidopallium; NCL; caudolateral nidopallium; LMAN; lateral magnocellular nucleus of the anterior nidopallium; RA; robust nucleus

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2013 سفارش ترجمه

Genetic basis and phenotypic correlations of the neuronal ceroid lipofusinoses

Keywords: NCL, Neuronal ceroid lipofuscinosis; EPMR, progressive epilepsy with mental retardationBatten; CLN; Neuronal ceroid lipofuscinosis; NCL

دانلود رایگان متن کامل مقاله ISI 4 صفحه سال انتشار : 2013 سفارش ترجمه

Electrical transport behaviour of bio-polymer electrolyte system: Potato starch + ammonium iodide

Keywords: Biodegradable; Ambient immune; Electrolyte; NCL; Dielectric

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2012 سفارش ترجمه

Intravenous high-dose enzyme replacement therapy with recombinant palmitoyl-protein thioesterase reduces visceral lysosomal storage and modestly prolongs survival in a preclinical mouse model of infantile neuronal ceroid lipofuscinosis

Keywords: NCL; neuronal ceroid lipofuscinosis; PPT1; palmitoyl-protein thioesterase-1; CLN1; ceroid lipofuscinosis, neuronal-1; GROD; granular osmiophilic deposits; FBS; fetal bovine serum; MU-6S-Palm-βGlc; 4-methylumbelliferyl-6-thiopalmitoyl-β-D-glucoside; PBS;

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2012 سفارش ترجمه

Cln5-deficiency in mice leads to microglial activation, defective myelination and changes in lipid metabolism

Keywords: Neuronal ceroid lipofuscinoses; NCL; erCln5; Microglia; Lipid metabolism; Myelin; Oligodendrocytes

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2012 سفارش ترجمه

Proteolytic cleavage of the disease-related lysosomal membrane glycoprotein CLN7

Keywords: BFA; brefeldin A; CHX; cycloheximide; Ctsb; cathepsin B; Ctsl; cathepsin L; DMEM; Dulbecco's minimal essential medium; endo H; endoglycosidase H; ER; endoplasmic reticulum; GFP; green fluorescent protein; HEK293; human embryonic kidney 293; HGSNAT; hepari

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2012 سفارش ترجمه

Mouse models of neuronal ceroid lipofuscinoses: Useful pre-clinical tools to delineate disease pathophysiology and validate therapeutics

Keywords: NCL; Lysosome; Autophagy; Cathepsin D; Apoptosis; Therapeutic

دانلود رایگان متن کامل مقاله ISI 15 صفحه سال انتشار : 2012 سفارش ترجمه

Septal area lesions impair spatial working memory in homing pigeons (Columba livia)

Keywords: DBB; diagonal band of Broca; FIRST4; first four choices; HF; hippocampal formation; SL; lateral septum; SM; medial septum; NCL; nidopallium caudolaterale; PE; proactive errors; PFC; prefrontal cortex; RE; retroactive errors; SpWM; spatial working memory;

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2011 سفارش ترجمه

Protein quality control mechanisms and neurodegenerative disorders: Checks, balances and deadlocks

Keywords: UPP; ubiquitin-proteasome pathway; ALP; autophagy-lysosomal pathway; NLD; neurodegenerative lysosomal disorders; NCL; neuronal ceroid lipofuscinoses; Neurodegeneration; Ubiquitin-proteasome; Autophagosome-lysosome; Protein aggregation; Neuronal incl

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2010 سفارش ترجمه

Chloride channelopathies

Keywords: Bartter syndrome; CFTR; Dent's disease; Gnathodiaphyseal dysplasia; Macular dystrophy; Neuronal ceroid lipofuscinosis; NCL; Thomsen's disease

دانلود رایگان متن کامل مقاله ISI 17 صفحه سال انتشار : 2009 سفارش ترجمه

A new large animal model of CLN5 neuronal ceroid lipofuscinosis in Borderdale sheep is caused by a nucleotide substitution at a consensus splice site (c.571 + 1G >>> A) leading to excision of exon 3

Keywords: CLN5; NCL; Batten disease; mRNA splicing; Animal model; Borderdale sheep; Lysosomal storage disease

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2008 سفارش ترجمه

Is a bird in the hand worth two in the future? The neuroeconomics of intertemporal decision-making

Keywords: ACC; anterior cingulate cortex; BLA; basolateral amygdala; BOLD; blood-oxygen-level dependent; cAMP; cyclic adenosine monophosphate; CS; conditioned stimulus; DLPFC; dorsolateral prefrontal cortex; EUT; expected utility theory; HSAT; Hebbian synapses with

دانلود رایگان متن کامل مقاله ISI 32 صفحه سال انتشار : 2008 سفارش ترجمه

Neuronal ceroid lipofuscinosis in Devon cattle is caused by a single base duplication (c.662dupG) in the bovine CLN5 gene

Keywords: NCL; Batten disease; CLN5; Cattle; Lysosomal storage disease; Animal model

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2006 سفارش ترجمه

Diagnosis of the neuronal ceroid lipofuscinoses: An update

Keywords: NCL; Diagnosis; Phenotype

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2006 سفارش ترجمه

Molecular genetics of the NCLs — status and perspectives

Keywords: Batten; CLN; Gene; Mutation; NCL; Neuronal ceroid lipofuscinosis

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2006 سفارش ترجمه

Functional biology of the neuronal ceroid lipofuscinoses (NCL) proteins

Keywords: Batten disease; Lysosomal degradation; NCL; Neurodegeneration; Storage disease

دانلود رایگان متن کامل مقاله ISI 14 صفحه سال انتشار : 2006 سفارش ترجمه

Characterizing pathogenic processes in Batten disease: Use of small eukaryotic model systems

Keywords: Batten disease; Model system; NCL

دانلود رایگان متن کامل مقاله ISI 14 صفحه سال انتشار : 2006 سفارش ترجمه

GABAB receptor-mediated modulation of cutaneous input at the cuneate nucleus in anesthetized cats

Keywords: GABAB-mediated inhibition; somatosensory system; cutaneous transmission; dorsal column nuclei; iontophoresis; cat; BiCu; bicuculline; CL; cuneolemniscal neuron; CN; cuneate nucleus; DCN; dorsal column nuclei (cuneate and gracilis); ML; medial lemniscus; n

دانلود رایگان متن کامل مقاله ISI 16 صفحه سال انتشار : 2006 سفارش ترجمه

The common organization of the amygdaloid complex in tetrapods: New concepts based on developmental, hodological and neurochemical data in anuran amphibians

Keywords: A; anterior nucleus of the dorsal thalamus; AA; anterior amygdala; ac; anterior commissure; Acc; nucleus accumbens; Ad; anterodorsal tegmental nucleus; Av; anteroventral tegmental nucleus; AOB; accesory olfactory bulb; Apl; amygdala pars lateralis; Apm; a

دانلود رایگان متن کامل مقاله ISI 30 صفحه سال انتشار : 2006 سفارش ترجمه

Comparison of dynamic performance for direct and fluid coupled indirect heat exchange systems

Keywords: Direct heat exchanger; Fluid coupled indirect heat exchanger; FCL; NCL; Dynamic performance; FEM;

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2005 سفارش ترجمه

Influence of the physicochemical properties of liposomes on the accelerated blood clearance phenomenon in rats

Keywords: ABC; accelerated blood clearance; CHOL; cholesterol; 3H-CHE; 3H-cholesterylhexadecyl ether; CL; conventional liposomes; CLh; hepatic clearance; DCP; dicetylphosphate; DPPC; dipalmitoyl phsophatidylcholine; DPPG; dipalmitoyl phsophatidylglycerol; HEPC; hyd

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2005 سفارش ترجمه

Glial activation spreads from specific cerebral foci and precedes neurodegeneration in presymptomatic ovine neuronal ceroid lipofuscinosis (CLN6)

Keywords: Astrocytosis; Batten disease; Brain macrophages; Fluorescent; Lysosomal storage disease; Microglia; NCL; Neuropathology; Storage body accumulation; Subunit c;

دانلود رایگان متن کامل مقاله ISI 15 صفحه سال انتشار : 2005 سفارش ترجمه