Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal Nocturnal Hemoglobinuria; Eculizumab; Thrombosis; Aplastic anemia;
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Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Complement; Paroxysmal Nocturnal Hemoglobinuria; Atypical Hemolytic Uremic Syndrome;
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Aplastic anemia; Autoimmune myelofibrosis; Bone marrow failure; Paroxysmal nocturnal hemoglobinuria; Systemic lupus erythematosus;
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal nocturnal hemoglobinuria; thrombosis; neutrophilic infiltrate;
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal nocturnal hemoglobinuria; Eculizumab; Hematopoietic stem cell transplantation;
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Extracellular vesicles; Paroxysmal nocturnal hemoglobinuria; Eculizumab; Thrombosis; PNH; paroxysmal nocturnal hemoglobinuria; EV; extracellular vesicle; PFP; platelet-free plasma; TGA; thrombin generation assay; GPI; glycosylphosphatidylinositol; PS; pho
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Alternative pathway of complement; Paroxysmal nocturnal hemoglobinuria; Atypical hemolytic uremic syndrome; HELLP syndrome; Cold agglutinin disease; Complementopathy;
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Thalassemia; Aplastic anemia; Paroxysmal nocturnal hemoglobinuria; Spur cell anemia; Burns; Drug induced;
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal nocturnal hemoglobinuria; Pediatric, adolescent; Intravascular hemolysis;
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal nocturnal hemoglobinuria; Lactate dehydrogenase; Hemolysis; Thrombosis; Symptoms;
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; RBC; red blood cell; NGS; next-generation sequencing; HS; hereditary spherocytosis; SNV; single nucleotide variants; HE; hereditary elliptocytosis; ANK1; ankyrin 1; SPTB; spectrin, beta, erythrocytic; SPTA1; spectrin alpha, erythrocytic 1; SLC4A1; solute
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal nocturnal hemoglobinuria; Eculizumab; Thromboelastography; Thrombin generation test; Thrombodynamics; Global haemostatic tests
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; aHUS; hemolytic uremic syndrome; CP; classical pathway; LP; lectin pathway; AP; alternative pathway; FDA; Food and Drug Administration; EMA; European Medicines Agency; PNH; paroxysmal nocturnal hemoglobinuria; C5D; C5 deficient; NHS; normal human serum; E
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal Nocturnal Hemoglobinuria; Thrombosis; Eculizumab; Complement C5; Hemostasis;
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Autologous stem cell transplantation; Multiple myeloma; Paroxysmal nocturnal hemoglobinuria; PIG-A gene
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal nocturnal hemoglobinuria; Hemolytic anemia; Alternative pathway of complement; Humanized anti-C5 monoclonal antibody; Eculizumab; C3 blockade; C1 inhibition; Bone marrow failure;
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; AET; 2-aminoethylisothiouronium bromide; AIHA; autoimmune hemolytic anemia; Câ²; complement; CR1; complement receptor 1; FPP; fermented papaya preparation; GPI; glycosylphosphatidylinositol; Hb; hemoglobin; MAC; membrane attack complex; NAC; N-acetylcyst
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Complement; Therapy; Placenta; Eculizumab; Paroxysmal nocturnal hemoglobinuria;
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal nocturnal hemoglobinuria; Reduced-intensity; Hematopoietic cell transplantation; Survival; Fludarabine
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; CVF; cobra venom factor; rCVF; recombinant CVF; hCVF; humanized CVF; MAC; membrane attack complex; PNH; paroxysmal nocturnal hemoglobinuria; MI/RI; myocardial ischemia reperfusion injury; GI/RI; gastrointestinal ischemia reperfusion injury; AMD; age-relat
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; AMD; age-related macular degeneration; C3; complement component 3; DPBS; Dulbecco's phosphate-buffered saline; HDMS; high definition mass spectrometry; NHP; non-human primate; NMR; nuclear magnetic resonance; PNH; paroxysmal nocturnal hemoglobinuria; Sar;
Pharmacokinetics of human recombinant C1-esterase inhibitor and development of anti-drug antibodies in healthy dogs
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; AUC; area under the curve; AUClast; area under the plasma concentration-time curve from the time of dosing to the last measurable (positive) concentration; AUC-INFobs; area under the plasma concentration-time curve from the time of dosing extrapolated to
Properdin: A multifaceted molecule involved in inflammation and diseases
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; aHUS; atypical hemolytic uremic syndrome; AAA; abdominal aortic aneurysm; AAV; ANCA-associated vasculitis; AMD; age-related macular degeneration; AMR; antibody-mediated rejection; ANCA; anti-neutrophil cytoplasmic antibody; AP; alternative pathway; APC; a
C3-mediated extravascular hemolysis in PNH on eculizumab: Mechanism and clinical implications
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal nocturnal hemoglobinuria; complement inhibition; intravascular hemolysis; extravascular hemolysis; C3; C5;
CR1 gene polymorphisms in Chinese patients with paroxysmal nocturnal hemoglobinuria
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; PNH; paroxysmal nocturnal hemoglobinuria; MAF; minor allele frequency; GPI; glycosylphosphatidylinositol; LDH; lactate dehydrogenase; AA; aplastic anemia; CR; complement receptor; PIGA; phosphatidylinositol glycan class A; FLAER; fluorescent aerolysin; HW
Multiple Lacunar Infarcts in Paroxysmal Nocturnal Hemoglobinuria
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Stroke; paroxysmal nocturnal hemoglobinuria; magnetic resonance; cerebrovascular disease; hematopoietic disorder;
Controlling the anaphylatoxin C5a in diseases requires a specifically targeted inhibition
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Complement activation; C5a blockade; Trypsin; Thrombin; Eculizumab; aHUS; atypical hemolytic uremic syndrome; APH50; 50% haemolytic complement activity of alternative pathway; C3N; C3 glomerulonephritis; CH50; 50% haemolytic complement activity of classic
Compstatin Cp40 blocks hematin-mediated deposition of C3b fragments on erythrocytes: Implications for treatment of malarial anemia
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; APC; alternative pathway of complement; Cp40; second generation Compstatin analogue; DV; digestive vacuole; MESF; molecules of equivalent soluble fluorochrome; NHS; normal human serum; PNH; paroxysmal nocturnal hemoglobinuria; RBC; red blood cell; Malaria
Comparative proteomic analysis of CD34+ cells in bone marrow between severe aplastic anemia and normal control
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; SAA; severe aplastic anemia; DAD1; dolichyl-diphosphooligosaccharide-protein glycosyltransferase subunit; IF1; ATPase inhibitor, mitochondrial isoform 1 precursor; TNF-α; tumour necrosis factor-alpha; IFN-γ; interferon-gamma; CTL; cytotoxicity T cells
Selectivity of C3-opsonin targeted complement inhibitors: A distinct advantage in the protection of erythrocytes from paroxysmal nocturnal hemoglobinuria patients
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Complement targeted inhibition; Paroxysmal nocturnal hemoglobinuria; Alternative pathway; miniFH;
Anemia aplásica. Hemoglobinuria paroxÃstica nocturna
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Anemia aplásica; Fracaso medular; Hemoglobinuria paroxÃstica nocturna; Hemólisis; Aplastic anemia; Bone-marrow failure; Paroxysmal nocturnal hemoglobinuria; Hemolysis;
Acquired somatic mutations of isocitrate dehydrogenases 1 and 2 (IDH1 and IDH2) in preleukemic disorders
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; IDH mutations; Preleukemia disorders; Aplastic anemia; Paroxysmal nocturnal hemoglobinuria; Myeloproliferative neoplasms; Myelodysplastic syndrome
Congenital CD59 Deficiency
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; CD59 deficiency; Glycosylphosphatidylinositol anchor; Paroxysmal nocturnal hemoglobinuria; Terminal complement system; Membrane attack complex inhibitory factor; Homologous restriction factor; Membrane inhibitor of reactive lysis;
Aplastic Anemia & MDS International Foundation (AA&MDSIF): Bone marrow failure disease scientific symposium 2012
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Myelodysplastic syndromes; Aplastic anemia; Paroxysmal nocturnal hemoglobinuria; Bone marrow failure; Epigenetic therapy; Immunosuppressive therapy; Stem cell transplantation; Complement
Seroreactivity to LGL leukemia-specific epitopes in aplastic anemia, myelodysplastic syndrome and paroxysmal nocturnal hemoglobinuria: Results of a bone marrow failure consortium study
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; LGL leukemia; Aplastic anemia; Myelodysplastic syndrome; Paroxysmal nocturnal hemoglobinuria; HTLV antibody;
Recurrent venous thromboembolism while on anticoagulant therapy
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Anticoagulation; Heparin; Malignancy; Paroxysmal nocturnal hemoglobinuria; Thrombosis; Vasculitis; Warfarin
Paroxysmal nocturnal hemoglobinuria and other complement-mediated hematological disorders
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal nocturnal hemoglobinuria; Complement alternative pathway; Complement component 3; Complement component 5; Eculizumab; TT30; C3-targeted therapy
Nocna napadowa hemoglobinuria - wieloletnie obserwacje. Charakterystyka kliniczna i analiza wielkoÅci klonu z defektem kotwicy glikozylofosfatydyloinozytolowej (GPI)
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; nocna napadowa hemoglobinuria; objawy kliniczne; rozpoznanie NNH; niewydolnoÅÄ szpiku; Paroxysmal Nocturnal Hemoglobinuria; clinical symptoms; PNH diagnosis; bone marrow failure;
GPI-anchor remodeling: Potential functions of GPI-anchors in intracellular trafficking and membrane dynamics
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; ACE; angiotensin-converting enzyme; CLIC; clathrin-independent carrier; COPII; coat protein complex II; DRM; detergent-resistant membrane; ER; endoplasmic reticulum; ERES; ER-exit sites; EtNP; ethanolamine-phosphate; GalNAc; N-acetylgalactosamine; GEEC; G
Selective inhibition of the membrane attack complex of complement by low molecular weight components of the aurin tricarboxylic acid synthetic complex
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; C5b-9; Complement C9 protein; Alzheimer's disease; Macular degeneration; Paroxysmal nocturnal hemoglobinuria;
What are RBC-transfusion-dependence and -independence?
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Anemia; RBC-transfusions; Myelodysplastic syndrome; Myeloproliferative neoplasm; Aplastic anemia; Paroxysmal nocturnal hemoglobinuria; Anemia therapy
Aplastic Anemia & MDS International Foundation (AA&MDSIF): Bone Marrow Failure Disease Scientific Symposium 2010
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Myelodysplastic syndromes; Aplastic anemia; Paroxysmal nocturnal hemoglobinuria; Bone marrow failure; Epigenetic therapy; Immunosuppressive therapy; Stem cell transplantation; Complement
Fanconi Syndrome and CKD in a Patient With Paroxysmal Nocturnal Hemoglobinuria and Hemosiderosis
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Fanconi syndrome; chronic kidney disease; hemosiderosis; hypokalemia; paroxysmal nocturnal hemoglobinuria;
A closer look at paroxysmal nocturnal hemoglobinuria
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal nocturnal hemoglobinuria; Hemolysis; Thrombosis; Aplastic anemia; Bone marrow failure
Current Status of Allogeneic Hematopoietic Stem Cell Transplantation for Paroxysmal Nocturnal Hemoglobinuria
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal nocturnal hemoglobinuria; Allogeneic hematopoietic stem cell transplantation
Impact of transfusion dependency on survival in patients with early myelodysplastic syndrome without excess of blasts
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; AML; acute myeloid leukemia; EF; ejection fraction; FAB; French-American-British; IM; intermediate; IPSS; International Prognostic Scoring System; ISCN; International System for Cytogenetics Nomenclature; LFS; leukemia free survival; LV; left ventricu
Chasing Clot: Thrombophilic States and the Interventionalist
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; APC; activated protein C; aPL; antiphospholipid; APS; antiphospholipid syndrome; AT; antithrombin; DVT; deep vein thrombosis; ET; essential thrombocythemia; HIT; heparin-induced thrombocytopenia; LMWH; low molecular weight heparin; MTHFR; methylenetetrahy
Advances in the diagnosis and therapy of paroxysmal nocturnal hemoglobinuria
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Paroxysmal nocturnal hemoglobinuria; PIG-A; Nitric oxide; Eculizumab; FLAER; Proaerolysin; Complement; Glycosylphosphatidylinositol anchored protein
Hemoglobinuria paroxÃstica nocturna
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Hemoglobinuria paroxÃstica nocturna; PIG-A; Glucosilfosfatidilinositol; CitometrÃa de flujo; Paroxysmal nocturnal hemoglobinuria; PIG-A gene; Glycosylphosphatidiylinositol; Flow cytometry;
Infarctus cérébral complication de l'hémoglobinurie paroxystique nocturne
Keywords: هموگلوبینوری شب ادراری پراکسیاسمی; Hémoglobinurie paroxystique nocturne; Infarctus cérébral; Paroxysmal nocturnal hemoglobinuria; Cerebral infarction;