Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; Morbidity; Mortality; Ethnicity; Prevalence; HCUP; Health Care Cost and Utilization Project; ICD-9; International Classification of Diseases, Ninth Revision; IDF; Immune Deficiency Foundation; KID; Kids' Inpatient Databa
مقالات ISI بیماری های اولیه کمبود ایمنی (ترجمه نشده)
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در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: بیماری های اولیه کمبود ایمنی; Flow cytometry; Intracellular protein; Monoclonal antibody; Primary immunodeficiency disease; Surface protein; ADA; adenosine deaminase; ALPS; autoimmune lymphoproliferative syndrome; APECED; autoimmune polyendocrinopathy-candidiasis-ectodermal dystrop
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency; Hematologic malignancy; Lymphoma; Leukemia; Hodgkin; AD; Autosomal dominant; ADA; Adenosine deaminase; AML; Acute myeloid leukemia; AR; Autosomal recessive; CID; combined immunodeficiency; HL; Hodgkin lymphoma; HLH; Hemophagocyti
Keywords: بیماری های اولیه کمبود ایمنی; Plasma cell; primary immunodeficiency diseases; common variable immunodeficiency;
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; Hypogammaglobulinaemia; Phagocyte defects; Combined immunodeficiencies; Frequency;
Keywords: بیماری های اولیه کمبود ایمنی; Adverse events following immunization; Primary immunodeficiency diseases; Live vaccines; Non-live vaccines;
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; Respiratory syncytial virus; Rotavirus; Varicella-zoster virus; Influenza virus; Cellular immunodeficiency
Keywords: بیماری های اولیه کمبود ایمنی; Autoimmunity; primary immunodeficiency diseases; BÂ cells; T cells; AID; Activation-induced cytidine deaminase; AIHA; Autoimmune hemolytic anemia; AIRE; Autoimmune regulator; ALPS; Autoimmune lymphoproliferative disease; ANA; Anti-nuclear autoantibody; AP
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; Subcutaneous immunoglobulin; Systematic review
High frequencies of asymptomatic Epstein-Barr virus viremia in affected and unaffected individuals with CTLA4 mutations
Keywords: بیماری های اولیه کمبود ایمنی; ALPS; autoimmune lymphoproliferative syndrome; APDS; activated phosphoinositide 3-kinese δ syndrome; BENTA; B-cell expansion with nuclear factor-κB and T-cell anergy; EBV; Epstein-Barr virus; ITP; immune thrombocytopenic purpura; LCLs; lymphoblastoid ce
Primary immunodeficiencies associated with EBV-Induced lymphoproliferative disorders
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; Epstein-Barr virus; Lymphoproliferative disorders;
CD18 deficiency evolving to megakaryocytic (M7) acute myeloid leukemia: Case report
Keywords: بیماری های اولیه کمبود ایمنی; CD18; Beta-2 integrins; Primary immunodeficiency diseases; Leukocyte adhesion deficiency type 1; Megakaryocytic (M7) acute myeloid leukemia;
A first pilot study on the neonatal screening of primary immunodeficiencies in Spain: TRECS and KRECS identify severe T- and B-cell lymphopaenia
Keywords: بیماری های اولیه کمبود ایمنی; Newborn screening; Primary immunodeficiency diseases; Severe combined immunodeficiency; X-linked agammaglobulinaemia; LymphopaeniaCribado neonatal; Inmunodeficiencias primarias; Inmunodeficiencia combinada grave; Agammaglobulinemia ligada al cromosoma C;
Primer estudio piloto en España sobre el cribado neonatal de las inmunodeficiencias primarias: TRECS y KRECS identifican linfopenias T y B graves
Keywords: بیماری های اولیه کمبود ایمنی; Cribado neonatal; Inmunodeficiencias primarias; Inmunodeficiencia combinada grave; Agammaglobulinemia ligada al cromosoma C; Linfopenia; Newborn screening; Primary immunodeficiency diseases; Severe combined immunodeficiency; X-linked agammaglobulinaemia;
The CARD11-BCL10-MALT1 (CBM) signalosome complex: Stepping into the limelight of human primary immunodeficiency
Keywords: بیماری های اولیه کمبود ایمنی; CARD11-BCL10-MALT1 signalosome complex; primary immunodeficiency diseases; combined immunodeficiency; congenital B-cell lymphocytosis; paracaspase; next-generation sequencing; nuclear factor κB; CARMA1
The T-cell-dependent antibody response assay in nonclinical studies of pharmaceuticals and chemicals: Study design, data analysis, interpretation
Keywords: بیماری های اولیه کمبود ایمنی; APC; antigen presenting cells; AUC; area under the curve; CP; cut point; ECL; electrochemiluminescence; ELISA; enzyme-linked immunosorbent assay; EPA; Environmental Protection Agency; GLP; good laboratory practice; HMW; high molecular weight; HBsAg; Hepat
Reviews and feature articleMolecular mechanisms of mucocutaneous immunity against Candida and Staphylococcus species
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; signal transducer and activator of transcription; signal transducer and activator of transcription 1 and 3; IL-17; Candida species; Staphylococcus species; AD-HIES; Autosomal dominant hyper-IgE syndrome; AIRE; Autoimmune
Bacillus Calmette-Guérin (BCG) complications associated with primary immunodeficiency diseases
Keywords: بیماری های اولیه کمبود ایمنی; BCG vaccination; Complications; Primary immunodeficiency diseases; Severe combined immunodeficiency; Mendelian susceptibility to mycobacterial diseases
Primary immunodeficiency diseases in Latin America: Proceedings of the Second Latin American Society for Immunodeficiencies (LASID) Advisory Board
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; Latin America; Diagnosis; Treatment; Education; Registry;
Critical issues and needs in management of primary immunodeficiency diseases in Latin America
Keywords: بیماری های اولیه کمبود ایمنی; Diagnosis; Education; Latin America; Primary immunodeficiency diseases; Registry; Treatment
Potential therapeutic applications of antisense morpholino oligonucleotides in modulation of splicing in primary immunodeficiency diseases
Keywords: بیماری های اولیه کمبود ایمنی; Pre-mRNA splicing; Antisense morpholino oligonucleotides; Genetic disorders; Primary immunodeficiency diseases;
Diagnosis and treatment of primary immunodeficiency disease in patients with gastrointestinal symptoms
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; Gastrointestinal infections; Chronic and acute diarrhea; Malabsorption; Inflammatory bowel diseases; Immunoglobulin replacement therapy
A History of Bone Marrow Transplantation
Keywords: بیماری های اولیه کمبود ایمنی; Bone marrow transplantation; History; Primary immunodeficiency diseases;
Primary immunodeficiencies may reveal potential infectious diseases associated with immune-targeting mAb treatments
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; monoclonal antibody therapy; infectionsAPS-1, Autoimmune polyendocrine syndrome type 1; BAFF, B-cell–activating factor; BAFF-R, B-cell–activating factor receptor; HIES, Hyper-IgE syndrome; HSE, Herpes simplex virus encep
The French national registry of primary immunodeficiency diseases
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; Registry; Epidemiology; Prevalence; Expertise
A History of Bone Marrow Transplantation
Keywords: بیماری های اولیه کمبود ایمنی; Bone marrow transplantation; History; Primary immunodeficiency diseases;
Bone Marrow Transplantation for Primary Immunodeficiency Diseases
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; Hematopoietic stem cell transplantation; Bone marrow transplantation; Reduced intensity conditioning;
Immunoglobulin Replacement Therapy in Children
Keywords: بیماری های اولیه کمبود ایمنی; Intravenous immunoglobulin therapy; Subcutaneous immunoglobulin therapy; Primary immunodeficiency diseases
Primary immunodeficiency diseases: An update from the International Union of Immunological Societies Primary Immunodeficiency Diseases Classification Committee
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; T cells; B cells; phagocytes; complement; immune dysregulation syndromes; innate immunityNK, Natural killer; PID, Primary immunodeficiency disease; STAT, Signal transducer and activator of transcription; TRAPS, TNF recep
Primary immunodeficiency diseases: An update from the International Union of Immunological Societies Primary Immunodeficiency Diseases Classification Committee Meeting in Budapest, 2005
Keywords: بیماری های اولیه کمبود ایمنی; Primary immunodeficiency diseases; T cells; B cells; phagocytes; complement; immune dysregulation syndromes; innate immunityHIGM, Hyper-IgM; IUIS, International Union of Immunological Societies; PID, Primary immunodeficiency disease; RAG, Recombination ac