Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; ADAMTS13; disintegrin and metalloproteinase with a thrombospondin type 1 motif, member 13; aHUS; atypical hemolytic uremic syndrome; BU; Bethesda units; CF; complement factor; CFHR; complement factor H-related; HUS; hemolytic uremic syndrome; iTTP; auto
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Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic thrombocytopenic purpura; Best practice; Plasma exchange; Adverse events; Patient care;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Autopsy; Extranodal marginal zone lymphoma; MALT lymphoma; Thrombotic thrombocytopenic purpura; ADAMTS13;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; IFN; interferon; TMA; thrombotic microangiopathy; HUVECs; human umbilical vein endothelial cells; IFNAR; IFN-α/β receptor; JAKs; Janus kinases; STAT; signal transducer and activator of transcription; mAb; monoclonal antibody; VEGF; vascular endothelial
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; aHUS; atypical hemolytic uremic syndrome; AP; alternative pathway; C3; complement component 3; C5; complement component 5; C3G; C3 glomerulopathy; CFB; complement factor B; CFH; complement factor H; CFI; complement factor I; COMS; complement serology pane
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; PSS; pediatric severe sepsis; MODS; multiple organ dysfunction syndrome; PE; plasma exchange; TAMOF; thrombocytopenia associated multiple organ failure; TTP; thrombotic thrombocytopenic purpura; CHA; Children's Hospital Association; PHIS; Pediatric Health
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Atypical hemolytic uremic syndrome; Complement; Eculizumab; Terminal complement inhibitor; Thrombotic microangiopathy; AH50; Alternative pathway function; TMA; Thrombotic microangiopathy; HUS; Hemolytic uremic syndrome; aHUS; Atypical HUS; LDH; Lactate de
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic thrombocytopenic purpura; Refractory disease; ADAMTS13; Rituximab; Immunotherapy;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Immune thrombocytopenia; Autoimmune hemolytic anemia; Thrombotic thrombocytopenic purpura; Splenectomy; Second-line treatment;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; acute kidney injury; chronic kidney disease; estimated glomerular filtration rate; KDIGO criteria; thrombotic thrombocytopenic purpura;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; atypical hemolytic uremic syndrome; blood outgrowth endothelial cells; complement; thrombotic microangiopathy; thrombotic thrombocytopenic purpura; von Willebrand factor;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Plasma exchange; Plasmapheresis; Thrombotic microangiopathy; Thrombotic thrombocytopenic purpura; Hemolytic uremic syndrome; Apheresis;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; atypical haemolytic—uraemic syndrome; complement system; pHUS; Shiga toxin-mediated haemolytic—uraemic syndrome; thrombotic microangiopathy; thrombotic thrombocytopenic purpura; von Willebrand factor
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic thrombocytopenic purpura; Hemolytic uremic syndrome; ADAMTS13; Complement activation; Plasma therapy; Eculizumab;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic thrombocytopenic purpura; Plasmapheresis; Rituximab; Diagnosis; Treatment; Classification;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic thrombocytopenic purpura; ADAMTS13; Rituximab; Immunotherapy
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; AFE; amniotic fluid embolism; DIC; disseminated intravascular coagulation; HELLP; hemolysis, elevated liver enzymes, and low platelets; HUS; hemolytic uremic syndrome; LDH; lactate dehydrogenase; MMR; maternal mortality rate; OHSS; ovarian hyperstimulatio
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic microangiopathy; Thrombotic thrombocytopenic purpura; Hemolytic uraemic syndrome; Apheresis; Plasma exchange; MicroangiopatÃa trombótica; Púrpura trombocitopénica trombótica; SÃndrome urémico hemolÃtico; Aféresis; Recambios plasmático
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic microangiopathy; Atypical hemolytic uremic syndrome; Hemolytic uremic syndrome; Thrombotic thrombocytopenic purpura;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Absolute immature platelet count; %-IPF; Thrombotic microangiopathy; Thrombotic thrombocytopenic purpura; Hypertension; Therapeutic plasma exchange
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic thrombocytopenic purpura; Pathologic fracture; Convulsion
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Multiple sclerosis; Thrombotic microangiopathy; Interferon Beta; Disease modifying treatment; Thrombotic thrombocytopenic purpura; Malignant hypertension;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Polymorphonuclear leukocyte; neutrophil granulocyte; elastase; thrombotic thrombocytopenic purpura; disease activity; complement activation;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; AIHA; autoimmune hemolytic anemia; ASH; American Society of Hematology; CLL; chronic lymphocytic leukemia; CMV; cytomegalovirus; CVID; common variable immunodeficiency; GPRD; General Practice Research Database; DIC; disseminated intravascular coagulation;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic thrombocytopenic purpura; Atypical hemolytic uremic syndrome; ADAMTS13; Complement activation; Diagnosis
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; TTP; Thrombotic Thrombocytopenic Purpura; HIV; Human Immunodeficiency Virus; SLE; Systemic Lupus Erythematosus; MAHA; microangiopathic haemolytic anaemia; TMA; thrombotic microangiopathy; PE; plasma exchange; APS; antiphospholipid syndrome; LDH; lactate d
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic microangiopathy; Thrombotic thrombocytopenic purpura; Hemolytic uremic syndrome; Shiga toxin; Complement dysregulation; Eculizumab
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Atypical hemolytic uremic syndrome; Complement system; Microangiopathic hemolytic anemia; Thrombotic microangiopathy; Thrombotic thrombocytopenic purpura
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; anetoderma; antiphospholipid antibody syndrome; chronic venous ulcer; hemostasis; hypercoagulable states; livedo reticularis; livedo vasculopathy; purpura; superficial venous thrombosis; thrombosis; APC; activated protein C; APLA; antiphospholipid antibod
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic thrombocytopenic purpura; ADAMTS13; Plasma exchange; Rituximab; Immunotherapy; Purpura thrombotique thrombocytopénique; ADAMTS13; Ãchanges plasmatiques; Rituximab; Immunothérapie;
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic thrombocytopenic purpura; ADAMTS13; Clopidogrel; Hemolytic uremic syndrome; Rituximab
A multicenter experience of thrombotic microangiopathies in Turkey: The Turkish Hematology Research and Education Group (ThREG)-TMA01 study
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic microangiopathy; Thrombotic thrombocytopenic purpura; Hemolytic-uremic syndrome; TTP; HUS;
Validation of the PLASMIC score, a clinical prediction tool for thrombotic thrombocytopenic purpura diagnosis, in Chinese patients
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic thrombocytopenic purpura; Validation studies; ADAMTS 13 protein;
Cobalamin deficiency presenting with thrombotic microangiopathy (TMA) features: A systematic review
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Cobalamin; Hemolytic anemia; Pseudo-thrombotic microangiopathy; Vitamin B12; Thrombotic thrombocytopenic purpura;
Thrombotic and hemorrhagic complications in children and young adult recipients of Hematopoietic Stem Cell Transplant (HSCT)
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; HSCT; Hematopoietic Stem Cell Transplant; HE; hemorrhagic events; TE; thrombotic events; Cy; cyclophosphamide; Bu; busulfan; VTE; Venous Thromboembolism; ACE; Advanced Cohort Explorer; PE; pulmonary embolism; DVT; Deep Vein Thrombosis; SOS; sinusoidal obs
Differential sensitivity of von Willebrand factor activity assays to reduced VWF molecular weight forms: A large international cross-laboratory study
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; ELISA; enzyme linked immunosorbent assay; GPIb; glycoprotein Ib; HMW; high molecular weight (VWF); NAC; Nâacetycysteine; TTP; thrombotic thrombocytopenic purpura; VWF; von Willebrand factor; VWF:Ab; VWF activity assays based on the binding of a monoclon
Identification of serotypes and virulence markers (stx) of Escherichia coli isolated from patients with diarrhea in Shiraz, Iran
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Stx; shiga toxin like gene; EHEC; enterohemorrhagic Escherichia coli; ETEC; enterotoxigenic E. coli; EPEC; enteropathogenic E. coli; EIEC; enteroinvasive E. coli; EAEC; enteroaggregative E. coli; STEC; and Shiga toxin-producing E. coli; EHEC; referred to
Thrombocytopenia associated with TAVI-The summary of possible causes
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; AS; aortic valve stenosis; BCMD; blood contacting medical devices; DAPT; dual antiplatelet therapy; DIC; disseminated intravascular coagulation; ES; Edwards Sapien; FS; Freedom Solo; F1+2; prothrombin fragments 1+2; GP; platelet glycoprotein; HIT; heparin
Article originalLe purpura thrombotique thrombocytopénique à la Martinique : étude rétrospective entre 2008 et 2015Thrombotic thrombocytopenia purpura in Martinique: Retrospective study between 2008 and 2015
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Purpura thrombotique trombocytopénique; ADAMTS-13; Ãchanges plasmatiques; Microangiopathie thrombotique; Afro-caribbéens; Thrombotic thrombocytopenic purpura; ADAMTS-13; Plasmatic exchange; Thrombotic microangiopathy; Afro-Caribbean;
ADAMTS13-specific circulating immune complexes as potential predictors of relapse in patients with acquired thrombotic thrombocytopenic purpura
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; ADAMTS13 protein; Immune complexes; Relapse; Risk factors; Thrombotic thrombocytopenic purpura;
Full Length ArticlePost-traumatic stress disorder and depression in survivors of thrombotic thrombocytopenic purpura
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; TTP; thrombotic thrombocytopenic purpura; PTSD; post-traumatic stress disorder; DSM-5; diagnostic and statistical manual of mental disorders; PCL-5; post-traumatic stress disorder checklist for DSM-5; BDI-II; Beck Depression Inventory II; OR; odds ratio;
Exploration d'ADAMTS13 dans le purpura thrombotique thrombocytopénique
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; ADAMTS13; auto-anticorps anti-ADAMTS13; facteur Willebrand; microangiopathie thrombotique; plasmathérapie; purpura thrombotique thrombocytopénique; syndrome d'Upshaw-Schulman; ADAMTS13; anti-ADAMTS13 autoantibodies; Willebrand factor; thrombotic micro
Review Articlevon Willebrand factor and its cleaving protease ADAMTS13 balance in coronary artery vessels: Lessons learned from thrombotic thrombocytopenic purpura. A narrative review
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Acute coronary syndrome; Thrombotic thrombocytopenic purpura; ADAMTS13;
The role of human leukocyte antigen DRB1-DQB1 haplotypes in the susceptibility to acquired idiopathic thrombotic thrombocytopenic purpura
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Thrombotic thrombocytopenic purpura; HLA-DRB1-DQB1 haplotypes; PTPN22 c.1858C>T polymorphism; Gender;
Towards developing criteria for scleroderma renal crisis: A scoping review
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; ANCA; anti-neutrophil cytoplasmic antibody; HUS; hemolytic uremic syndrome; MAHA; microangiopathic hemolytic anemia; SRC; scleroderma renal crisis; SSc; systemic sclerosis; TTP; thrombotic thrombocytopenic purpura; Scleroderma (or systemic sclerosis); Ren
Potential influences of complement factor H in autoimmune inflammatory and thrombotic disorders
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; aHUS; atypical haemolytic uremic syndrome; AMD; age-related macular degeneration; aPL; anti-phospholipid antibodies; C3-NeF; C3- nephritic factor; CCP; complement control protein; CEP; Carboxyethylpyrrole; CL; Cardiolipin; CNV; copy number variation; CR;
Pseudo-maladie de Still, anasarque, microangiopathie thrombotique et dysautonomie : présentation atypique d'une maladie de Castleman multicentrique. Discussion du syndrome TAFRO
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Maladie de Castleman multicentrique; Syndrome TAFRO; Maladie de Still de l'adulte; Microangiopathie thrombotique; Dysautonomie; Multicentric Castleman's disease; TAFRO syndrome; Adult-onset Still's disease; Thrombotic thrombocytopenic purpura; Dysautono
Prise en charge du purpura thrombotique thrombopénique dans deux centres français : à partir de 27 patients
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; Purpura thrombotique thrombocytopénique; ADAMTS13; Ãchanges plasmatiques; Rituximab; Microangiopathie thrombotique; Thrombotic thrombocytopenic purpura; ADAMTS13; Plasmatic exchange; Rituximab; Thrombotic microangiopathy;
Genetyczne i autoimmunologiczne mikroangiopatie zakrzepowe u dzieci - wspóÅczesna strategia diagnostyki i leczenia
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; atypowy zespól hemolityczno-mocznicowy; plamica maÅopÅytkowa; leki biologiczne; aHUS-TTP; Thrombotic thrombocytopenic purpura; Biologic drugs;
Degradation of two novel congenital TTP ADAMTS13 mutants by the cell proteasome prevents ADAMTS13 secretion
Keywords: ترومبوتیک ترومبوسیتوپنیک پورپورا; ADAMTS13; Von Willebrand factor-cleaving protease; Thrombotic thrombocytopenic purpura; Mutation; Congenital; Proteasome;