Keywords: اسیدهای چرب زنجیر بسیار طولانی; Peroxisome; Lysosome; Storage disorder; Very long chain fatty acids;
مقالات ISI اسیدهای چرب زنجیر بسیار طولانی (ترجمه نشده)
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در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: اسیدهای چرب زنجیر بسیار طولانی; DAG; diacylglycerol; DAS; days after sowing; DGDG; digalactosyldiacylglycerol; DW; dry weight; MGDG; monogalactosyldiacylglycerol; PC; phosphatidylcholine; SDP1; Sugar-dependent lipase1; TAG; triacylglycerol; VLCFA; very long chain fatty acids; Triacylgly
Keywords: اسیدهای چرب زنجیر بسیار طولانی; Peroxisomal biogenesis disorder; Zellweger spectrum disorder; PEX6; Polimicrogyria; VLCFA; PBD; peroxisomal biogenesis disorder; VLCFA; very long chain fatty acids; CGH Array; comparative genomic hybridization array; DHAPAT; dihydroxyacetonephosphate acyl
Keywords: اسیدهای چرب زنجیر بسیار طولانی; CHO; Chinese hamster ovary; DLP1; dynamin-like protein 1; ER; endoplasmic reticulum; FIS1; fission 1; H. polymorpha; Hansenula polymorpha; MFF; mitochondrial fission factor; MAPL; mitochondria-anchored protein ligase; MDV; mitochondria-derived vesicle; mP
Keywords: اسیدهای چرب زنجیر بسیار طولانی; BHT; butylhydroxytoluene; DRM; detergent-resistant membranes; FA; fatty acid; FB1; fumonisin B1; LCB; long chain base; LCFA; long chain fatty acids; OPA; o-phthaldialdehyde; PEG; polyethylene glycol; PM; plasma membrane; SAT; sphinganine-N-acyltransferase
Keywords: اسیدهای چرب زنجیر بسیار طولانی; ACS; acyl-CoA synthetase; ACSVL; very-long-chain acyl-CoA synthetase; AP; alkaline phosphatase; AST; aspartate aminotransferase; ATF-2; activating transcription factor-2; Bax; Bcl-2 associated X protein; CE; cholesterol ester; Cer; ceramides; CerS; cerami
Enantiomeric separation of triacylglycerols containing very long chain fatty acids
Keywords: اسیدهای چرب زنجیر بسیار طولانی; Triacylglycerols; Very long chain fatty acids; Very long-chain polyunsaturated fatty acids; Enantiomeric separation; Non-aqueous reversed-phase-HPLC;
Application of a diagnostic methodology by quantification of 26:0 lysophosphatidylcholine in dried blood spots for Japanese newborn screening of X-linked adrenoleukodystrophy
Keywords: اسیدهای چرب زنجیر بسیار طولانی; X-ALD; X-linked adrenoleukodystrophy; VLCFA; very long chain fatty acids; CALD; cerebral X-ALD; AMN; adrenomyeloneuropathy; CCALD; childhood cerebral X-ALD; HSCT; hematopoietic stem cell transplantation; DBS; dried blood spots; NDBS; newborn dried blood s
Original articleLong-term outcome of patients with X-linked adrenoleukodystrophy: A retrospective cohort study
Keywords: اسیدهای چرب زنجیر بسیار طولانی; X-linked adrenoleukodystrophy; Addison's disease; Very long chain fatty acids; Leukodystrophy; AI; adrenal insufficiency; ACTH; adrenocorticotropin; CCALD; childhood cerebral X-ALD; FSIQ; full scale intelligence quotient (IQ) score; HSCT; hematopoietic st
7-Ketocholesterol is increased in the plasma of X-ALD patients and induces peroxisomal modifications in microglial cells: Potential roles of 7-ketocholesterol in the pathophysiology of X-ALD
Keywords: اسیدهای چرب زنجیر بسیار طولانی; 7KC; 7-ketocholesterol; X-ALD; X-linked adrenoleukodystrophy; HODE; hydroxyoctadecadienoic acid; CCALD; childhood cerebral ALD; ACALD; adolescent cerebral ALD; AMN; adrenomyeloneuropathy; VLCFA; very long chain fatty acids; Microglial BV-2 cells; 7-Ketoch
ReviewVersatility of peroxisomes: An evolving concept
Keywords: اسیدهای چرب زنجیر بسیار طولانی; VLCFA; very long chain fatty acids; ROS; reactive oxygen species; GOX; glycolate oxidase; CAT; catalase; PMP; peroxisomal membrane protein; RNS; reactive nitrogen species; GSNOR; S-nitrosoglutathione reductase; ACOX; acyl-CoA oxidase; IPN; isopenicillin N
Astrocytes and mitochondria from adrenoleukodystrophy protein (ABCD1)-deficient mice reveal that the adrenoleukodystrophy-associated very long-chain fatty acids target several cellular energy-dependent functions
Keywords: اسیدهای چرب زنجیر بسیار طولانی; ABCD1; peroxisomal ATP-binding cassette transporter 1; ALDP; adrenoleukodystrophy protein; AMN; adrenomyeloneuropathy; cALD; cerebral ALD; CPA; cyclopiazonic acid; CRC; Ca2Â + retention capacity; DHE; dihydroethidium; DMEM; Dulbecco's modified Eagle's med
Acyl-CoA binding protein and epidermal barrier function
Keywords: اسیدهای چرب زنجیر بسیار طولانی; Acyl-CoA binding protein; Epidermal barrier; Stratum corneum; Very long chain fatty acids; Monoalkyl–diacyl-glycerol; Ceramide
Long-term biopermanence of ceramides, cholesteryl esters, and ether-linked triglycerides with very-long-chain PUFA in the cadmium-damaged testis
Keywords: اسیدهای چرب زنجیر بسیار طولانی; Germ cells; Sertoli cells; Macrophages; Sphingomyelins; Triacylglycerols; Very long chain fatty acids;
Site-directed mutagenesis of a fatty acid elongase ELO-like condensing enzyme
Keywords: اسیدهای چرب زنجیر بسیار طولانی; VLCFA; very long chain fatty acids; CoA; coenzyme A; KCS; 3-ketoacylCoA synthase; GC/MS; gas chromatography/mass spectrometry; ER; endoplasmic reticulum; Fatty acid elongation; Condensing enzyme; ELO;
Direct imaging of plant metabolites in leaves and petals by desorption electrospray ionization mass spectrometry
Keywords: اسیدهای چرب زنجیر بسیار طولانی; Desorption electrospray ionization; Mass spectrometry imaging; Hypericum perforatum; Very long chain fatty acids; Plant metabolites
Peroxisomal ABC transporters: Structure, function and role in disease
Keywords: اسیدهای چرب زنجیر بسیار طولانی; ABCD; ATP-binding cassette protein subfamily D; AMN; adrenomyeloneuropathy; CCALD; child cerebral ALD; CNS; central nervous system; DHCA; dihydroxycholestanoic acid; DHA; docosahexaenoic acid; GFP; green fluorescent protein; iPS; induced pluripotent stem;
Incidence of Abcd1 level on the induction of cell death and organelle dysfunctions triggered by very long chain fatty acids and TNF-α on oligodendrocytes and astrocytes
Keywords: اسیدهای چرب زنجیر بسیار طولانی; Very long chain fatty acids; C24:0; C26:0; TNF-α; Cell death; Mitochondria; Lysosome; Peroxisome; Primary culture of glial cells; 158N oligodendrocytes; C6 glioma cells
Combined deficiency of peroxisomal β-oxidation and ether lipid synthesis in mice causes only minor cortical neuronal migration defects but severe hypotonia
Keywords: اسیدهای چرب زنجیر بسیار طولانی; Peroxisome biogenesis disorders; Neuronal migration; Mouse model; Plasmalogens; Very long chain fatty acids; Hypotonia;
Role of very-long-chain fatty acids in plant development, when chain length does matter
Keywords: اسیدهای چرب زنجیر بسیار طولانی; Very long chain fatty acids; Waxes; Sphingolipids; Phospholipids; Membranes; Postgenital fusionAcides gras à très longues chaînes; Cires; Sphingolipides; Phospholipides; Fusions postgénitales; Composants structuraux
Composition of the epicuticular and intracuticular wax layers on Kalanchoe daigremontiana (Hamet et Perr. de la Bathie) leaves
Keywords: اسیدهای چرب زنجیر بسیار طولانی; Kalanchoe daigremontiana; Crassulaceae; Chain length; Friedelin; Glutinol; Leaf surface; Triterpenoids; Very long chain fatty acids;
Evaluation of five methods for derivatization and GC determination of a mixture of very long chain fatty acids (C24:0–C36:0)
Keywords: اسیدهای چرب زنجیر بسیار طولانی; D003; Very long chain fatty acids; Derivatization methods; Capillary gas chromatography; Validation
Diagnosis of X-linked adrenoleukodystrophy in blood leukocytes
Keywords: اسیدهای چرب زنجیر بسیار طولانی; X-linked adrenoleukodystrophy; X-ALD; Gas chromatography-mass spectrometry; GC–MS; Very long chain fatty acids; Immunofluorescence; ALDP; Adrenoleukodystrophy protein
Identification of very long chain fatty acids from sugar cane wax by atmospheric pressure chemical ionization liquid chromatography-mass spectroscopy
Keywords: اسیدهای چرب زنجیر بسیار طولانی; Sugar cane wax; Very long chain fatty acids; Liquid chromatography-mass spectrometry - atmospheric pressure chemical ionization;
Therapy of X-Linked Adrenoleukodystrophy
Keywords: اسیدهای چرب زنجیر بسیار طولانی; Adrenoleukodystrophy; adrenomyeloneuropathy; adrenal insufficiency; bone marrow transplant; very long chain fatty acids; peroxisomal disorders; neonatal screening;
2004 Pathogenesis of Rare Neuroimmunologic Disorders, Hyatt Regency Inner Harbor, Baltimore, MD, August 19th 2004-August 20th 2004
Keywords: اسیدهای چرب زنجیر بسیار طولانی; ADEM; Acute disseminated encephalomyelitis; AchR; Acetylcholine receptor; ALD; Adrenoleukodystrophy; ALDP; Protein encoded by X-ALD gene ABCD1; AMAN; Acute motor axonal neuropathy; APC; Antigen presenting cell; APL; Altered peptide ligand; C. jejuni; Camp
Temporal gene expression of 3-ketoacyl-CoA reductase is different in high and in low erucic acid Brassica napus cultivars during seed development
Keywords: اسیدهای چرب زنجیر بسیار طولانی; HEAR; high erucic acid rapeseed; LEAR; low erucic acid rapeseed; VLCFA; very long chain fatty acids; LPAAT; lysophosphatidic acid acyltransferase; TAG; triacylglycerols; WAP; week after pollination; HPTLC; high-performance thin layer chromatography; Brass
Nonmyeloablative stem cell transplantation and cell therapy for malignant and non-malignant diseases
Keywords: اسیدهای چرب زنجیر بسیار طولانی; ALL; acute lymphoblastic leukemia; AML; acute myeloid leukemia; ATG; anti-thymocyte globulin; BMT; bone marrow transplantation; CGD; chronic granulomatous disease; CML; chronic myeloid leukemia; CTL; cytotoxic T lymphocytes; CSA; cyclosporine A; DLI; dono