
Nesprin-1 and actin contribute to nuclear and cytoskeletal defects in lamin A/C-deficient cardiomyopathy
Keywords: نوع وحشی; α-SMA; α-Smooth muscle actin; DCM; Dilated cardiomyopathy; INM; Inner nuclear membrane; KASH; Klarsicht-ANC-Syne-homology domain; LINC; Linker-of-nucleoskeleton-and-cytoskeleton complex; ONM; Outer nuclear membrane; TGFβ1; Transforming growth facto