کد مقاله کد نشریه سال انتشار مقاله انگلیسی نسخه تمام متن
1998287 1065778 2015 4 صفحه PDF دانلود رایگان
عنوان انگلیسی مقاله ISI
How strict is galactose restriction in adults with galactosaemia? International practice
ترجمه فارسی عنوان
محدودیت گالاکتوز در بالغین با گالاکتوزمی چقدر سخت است؟ تمرین بین المللی
کلمات کلیدی
موضوعات مرتبط
علوم زیستی و بیوفناوری بیوشیمی، ژنتیک و زیست شناسی مولکولی زیست شیمی
چکیده انگلیسی


• All centres treating adults with galactosaemia restrict lactose
• Some centres still restrict galactose in fruit, vegetables, lentils & offal in adults.
• Patient led modest lactose relaxation (trace amounts) occurs in some centres.
• 32% of adult patients were lost to dietetic follow-up.

Dietary management of 418 adult patients with galactosaemia (from 39 centres/12 countries) was compared. All centres advised lactose restriction, 6 restricted galactose from galactosides ± fruits and vegetables and 12 offal. 38% (n = 15) relaxed diet by: 1) allowing traces of lactose in manufactured foods (n = 13) or 2) giving fruits, vegetables and galactosides (n = 2). Only 15% (n = 6) calculated dietary galactose. 32% of patients were lost to dietetic follow-up. In adult galactosaemia, there is limited diet relaxation.

ناشر
Database: Elsevier - ScienceDirect (ساینس دایرکت)
Journal: Molecular Genetics and Metabolism - Volume 115, Issue 1, May 2015, Pages 23–26
نویسندگان
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