Le syndrome de Mounier-Kuhn ou trachéobronchomégalie

Tracheobronchomegaly is a very rare disease which may be congenital or acquired. It is characterised by marked tracheobronchial dilatation and recurrent lower respiratory tract infections. Clinical presentation is not specific. Radiological diagnosis is often easy, based on chest radiograph and CT findings mainly relying on an assessment of the diameter or cross-sectional area of the trachea and main bronchi. Impact on the parenchyma must be evaluated.