Congenital nasal pyriform aperture stenosis: The report of four rare cases

Congenital nasal pyriform aperture stenosis (CNPAS) is an unusual cause of upper airway obstruction that may happen because of respiratory distress, cyclic cyanosis or feeding problems. Bony overgrowth of maxillary nasal process sounds responsible for this deformity. Diagnosis is based on clinical evidence and radiologic findings. Failure to conservative management, respiratory distress and feeding problems are all indications of surgical treatments. In our experience, the sublabial approach is known as the most effective to these patients at any age. Otolaryngologists and pediatricians should therefore consider CNPAS as a rare but treatable cause in the patients with upper respiratory problems.