Precursor B-cell lymphoblastic lymphoma presenting as a malignant ear tumour in a five-month-old child

SummaryEar manifestation of malignant lymphoma is very rare in childhood. The authors present a two-month-old girl with precursor B-cell lymphoblastic lymphoma/leukaemia appearing as a rapid growing malignant right ear tumour. This is the second reported case of childhood lymphoma occurring as an external ear swelling, similar to that which had previously been presented in a two-year-old boy.The authors comment on the diagnostic and therapeutic problems connected to the uncommon auricular mass. The characteristics of childhood malignant tumours and their therapy are discussed. Needle aspiration is not diagnostic in the case of non-Hodgkin lymphoma (NHL). A surgical sample was taken and histological and immunohistological examinations were made in order to establish a correct diagnosis. The baby received chemotherapy by Interfant-2006 ALL protocol. Two months later the ear tumour had totally disappeared. Authors call the attention of paediatricians and otolaryngologists to the fact that atypical lesions of the head and neck regions may represent a potential for NHL in children.The importance of team work among the pediatric ORL specialists and pediatric oncologic centres for improving curability rate is emphasized.