کد مقاله کد نشریه سال انتشار مقاله انگلیسی نسخه تمام متن
4128359 1270921 2011 4 صفحه PDF دانلود رایگان
عنوان انگلیسی مقاله ISI
Un sarcome cutané congénital rare : la tumeur fibrohistiocytaire plexiforme
موضوعات مرتبط
علوم پزشکی و سلامت پزشکی و دندانپزشکی آسیب‌شناسی و فناوری پزشکی
پیش نمایش صفحه اول مقاله
Un sarcome cutané congénital rare : la tumeur fibrohistiocytaire plexiforme
چکیده انگلیسی
We report the unusual case of a three-year-old girl which presented since birth a pigmented tumor of the left side 0.5 cm in diameter. Surgical removal was decided given the hypothesis of a congenital naevo-cellular naevus. The histological study ended with the diagnosis of plexiform fibrohistiocytic tumor (PFHT). Two other congenital PFHT have been reported until now. PFHT is a rare mesenchymal neoplasm of intermediate malignancy, first reported by Enzinger and Zhang in 1988 which may be difficult to diagnose, because of its low frequency, particulary in congenital cases. It is important to distinguish it from others childhood cutaneous tumors (particulary plexiform neurofibroma, cellular neurothekeoma, infantile myofibromatosis, and fibrous hamartoma). The tumor has a high local recurrence rate and complete surgical resection of the tumor, with wider margins, is required.
ناشر
Database: Elsevier - ScienceDirect (ساینس دایرکت)
Journal: Annales de Pathologie - Volume 31, Issue 3, June 2011, Pages 222-225
نویسندگان
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