Lipomatosis arborescente. Presentación de un caso pediátrico

Synovial lipomatosis, described by Albert Hoffa in 1904, is a rare and benign entity of the synovial membrane. The knee joint is the most frequent site, although it can occur in other joints. Middle-aged men are most often affected; it is rarely found in children. It is normally monoarticular, although in some cases it appears in more than one joint. Of unknown etiology, it is thought to be a reactive, rather than a neoplastic, process. The pathology shows characteristic arborescent radiological, macroscopic and microscopic morphology due to adipose infiltration of sub-synovial tissue, which is essential for diagnosis. We report a case of synovial lipomatosis in a 12 year old girl and discuss the radiological and pathological findings, differential diagnosis and treatment.