IgG4-related disease underlying the pathogenesis of coronary artery disease

► IgG4-related disease is a newly emerging clinicopathological entity. ► IgG4-related disease may involve wide variety of organs, including aorta. ► It may also involve coronary artery. ► IgG4-related coronary periarteritis may be manifested as aneurysm and pseudotumor. ► Optimal diagnostic and therapeutic strategies should be investigated further.