دانلود مقالات ISI درباره Adpkd + ترجمه فارسی

Fatty Acid Oxidation is Impaired in An Orthologous Mouse Model of Autosomal Dominant Polycystic Kidney Disease

Keywords: Polycystic kidney disease; Autosomal Dominant Polycystic Kidney Disease; Pkd1; ADPKD; Mouse model; Systems biology; Metabolism; Fatty acid oxidation; Fatty acid oxidation defect; Lipid metabolism; Diet

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2016 سفارش ترجمه

Cardiac dysfunction in Pkd1-deficient mice with phenotype rescue by galectin-3 knockout

Keywords: ADPKD; apoptosis; cardiac dysfunction; cardiomyopathy; galectin-3; Pkd1-deficiency;

دانلود رایگان متن کامل مقاله ISI 18 صفحه سال انتشار : 2016 سفارش ترجمه

Repulsive guidance molecule b inhibits renal cyst development through the bone morphogenetic protein signaling pathway

Keywords: ADPKD; autosomal dominant polycystic kidney disease; BMP; bone morphogenetic protein; DBA; Dolichos biflorus agglutinin; ESRF; end-stage renal failure; HGF; hepatocyte growth factor; MDCK; Madin-Darby canine kidney; RGMb; repulsive guidance molecule b; ST

دانلود رایگان متن کامل مقاله ISI 43 صفحه سال انتشار : 2016 سفارش ترجمه

Bardet-Biedl syndrome: A model for translational research in rare diseases

Keywords: AAV; adeno-associated vector; ADPKD; autosomal dominant polycystic kidney disease; BBS; Bardet-Biedl Syndrome; CDE; common data element; CRIBBS; Clinical Registry Investigating Bardet-Biedl Syndrome; DDAVP; desmopressin acetate; GRDR®; Global Rare Di

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2015 سفارش ترجمه

The Cholangiopathies

Keywords: ADPLD; autosomal dominant polycystic liver disease; ADPKD; autosomal dominant polycystic kidney disease; AIDS; acquired immunodeficiency syndrome; ARPKD; autosomal recessive polycystic kidney disease; cAMP; cyclic adenosine monophosphate; CF; cystic fibro

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2015 سفارش ترجمه

Embryonal Fyn-associated substrate (EFS) and CASS4: The lesser-known CAS protein family members

Keywords: 5-HT; 5-hydroxytryptamine, serotonin; A549; non-small cell lung cancer cell line; AD; Alzheimer's disease; ADPKD; autosomal dominant polycystic kidney disease; Aire; autoimmune regulator; AP-1; activator protein 1; APP; amyloid precursor protein; AREB6; Z

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2015 سفارش ترجمه

Autosomal-dominant polycystic kidney disease (ADPKD): executive summary from a Kidney Disease: Improving Global Outcomes (KDIGO) Controversies Conference

Keywords: ADPKD; diagnosis; end-stage renal disease; management; patient support; polycystic kidney disease;

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2015 سفارش ترجمه

Endothelin and Tubulointerstitial Renal Disease

Keywords: Endothelin; acute kidney injury; polycystic kidney disease; ADPKD; ET-1; ETA; ETB;

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2015 سفارش ترجمه

Glycogen synthase kinase-3β promotes cyst expansion in polycystic kidney disease

Keywords: Keywords; ADPKD; vasopressin; chronic kidney disease; cell signaling;

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2015 سفارش ترجمه

The SAM domain of ANKS6 has different interacting partners and mutations can induce different cystic phenotypes

Keywords: ADPKD; genetic kidney disease; renal pathology;

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2015 سفارش ترجمه

Management of urinary tract infection in solid organ transplant recipients: Consensus statement of the Group for the Study of Infection in Transplant Recipients (GESITRA) of the Spanish Society of Infectious Diseases and Clinical Microbiology (SEIMC) and

Keywords: AB; asymptomatic bacteriuria; ADPKD; autosomal dominant polycystic kidney disease; AMB; amphotericin B; CFU; colony forming units; CPE; carbapenemase-producing Enterobacteriaceae; ESBL; extended-spectrum beta-lactamase; ESBLE; extended-spectrum beta-lacta

دانلود رایگان متن کامل مقاله ISI 21 صفحه سال انتشار : 2015 سفارش ترجمه

Consensus Expert Recommendations for the Diagnosis and Management of Autosomal Recessive Polycystic Kidney Disease: Report of an International Conference

Keywords: ADPKD; Autosomal-dominant polycystic kidney disease; ARPKD; Autosomal-recessive polycystic kidney disease; CHF; Congenital hepatic fibrosis; CKD; Chronic kidney disease; CMV; Cytomegalovirus; GA; Gestational age; HNF1B; Hepatocyte nuclear factor-1beta; HT

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2014 سفارش ترجمه

Defective pre-mRNA splicing in PKD1 due to presumed missense and synonymous mutations causing autosomal dominant polycystic disease

Keywords: ADPKD; autosomal dominant polycystic kidney disease; bp; base pairs; cDNA; DNA complementary to RNA; DMEM; Dulbecco's Modified Eagle's Medium; dNTP; deoxyribonucleoside triphosphate; ESE; exonic splicing enhancers; ESS; exonic splicing silencers; ISE; int

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2014 سفارش ترجمه

Identification of novel mutations of PKD1 gene in Chinese patients with autosomal dominant polycystic kidney disease by targeted next-generation sequencing

Keywords: ADPKD; Mutation; PKD1; Targeted next-generation sequencing;

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2014 سفارش ترجمه

Dietary n-3 polyunsaturated fatty acids or soy protein isolate did not attenuate disease progression in a female rat model of autosomal recessive polycystic kidney disease

Keywords: Rat; Polycystic kidney disease; n-3 PUFAs; Soy protein; Diet therapy; AA; arachidonic acid; ADPKD; autosomal dominant polycystic kidney disease; ALA; α-linolenic acid; ARPKD; autosomal recessive polycystic kidney disease; BUN; blood urea nitrogen; CO; co

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2014 سفارش ترجمه

Analysis of data from the ERA-EDTA Registry indicates that conventional treatments for chronic kidney disease do not reduce the need for renal replacement therapy in autosomal dominant polycystic kidney disease

Keywords: ADPKD; epidemiology; renoprotective therapy;

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2014 سفارش ترجمه

Evidence of a third ADPKD locus is not supported by re-analysis of designated PKD3 families

Keywords: ADPKD; molecular genetics; polycystic kidney disease;

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2014 سفارش ترجمه

Nephrectomy for Non-neoplastic Kidney Diseases

Keywords: Chronic pyelonephritis; Dysplasia; ADPKD; ARPKD; Xanthogranulomatous pyelonephritis; Reflux nephropathy; Obstructive nephropathy;

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2014 سفارش ترجمه

Renal cyst growth is the main determinant for hypertension and concentrating deficit in Pkd1-deficient mice

Keywords: ADPKD; cystic kidney; hypertension; nitric oxide; renin-angiotensin system;

دانلود رایگان متن کامل مقاله ISI 14 صفحه سال انتشار : 2014 سفارش ترجمه

Research ArticleEverolimus does not further reduce polycystic liver volume when added to long acting octreotide: Results from a randomized controlled trial

Keywords: PLD; polycystic liver disease; ADPKD; autosomal dominant polycystic kidney disease; PCLD; isolated polycystic liver disease; mTOR; mammalian target of rapamycin; CT; computerized tomography; PCK; polycystic kidney; Polycystic liver disease; PCLD; ADPKD; O

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2013 سفارش ترجمه

Short-term renal hemodynamic effects of tolvaptan in subjects with autosomal dominant polycystic kidney disease at various stages of chronic kidney disease

Keywords: ADPKD; clinical trial; glomerular filtration rate; renal hemodynamics; tolerance; vasopressin;

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2013 سفارش ترجمه

Polycystin-2 mutations lead to impaired calcium cycling in the heart and predispose to dilated cardiomyopathy

Keywords: ADPKD; autosomal dominant polycystic kidney disease; APD; action potential duration; AV; atrioventricular; bpm; beats per minute; dpf; days post fertilization; CICR; calcium-induced calcium release; ER; endoplasmic reticulum; hpf; hours post fertilization

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2013 سفارش ترجمه

Original ResearchFull Report: Clinical-LiverYoung Women With Polycystic Liver Disease Respond Best to Somatostatin Analogues: A Pooled Analysis of Individual Patient Data

Keywords: Liver Cysts; PCLD; ADPKD; Drug Therapy; ADPKD; autosomal dominant polycystic kidney disease; CI; confidence interval; CT; computed tomography; IPD; individual patient data; PCLD; autosomal dominant polycystic liver disease; PLD; polycystic liver disease;

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2013 سفارش ترجمه

Pregnancy in Chronic Kidney Disease

Keywords: Pregnancy in kidney disease; Preeclampsia; Lupus nephritis; ADPKD; Diabetic nephropathy; Reflux nephropathy;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2013 سفارش ترجمه

Low birth weight is associated with earlier onset of end-stage renal disease in Danish patients with autosomal dominant polycystic kidney disease

Keywords: ADPKD; clinical epidemiology; ESRD; intrauterine growth; risk factors;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2012 سفارش ترجمه

Long-Term Impact of Laparoscopic Cyst Decortication on Renal Function, Hypertension and Pain Control in Patients with Autosomal Dominant Polycystic Kidney Disease

Keywords: polycystic kidney, autosomal dominant; laparoscopy; ADPKD; adult dominant polycystic kidney disease; ATI; antihypertensive therapeutic index; BP; blood pressure; CKD; chronic kidney disease; CrCl; creatinine clearance; eGFR; estimated glomerular filtratio

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2012 سفارش ترجمه

A missense mutation in PKD1 attenuates the severity of renal disease

Keywords: ADPKD; functional assay; hypomorphic allele; missense variant; mutation analysis

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2012 سفارش ترجمه

Polycystin-1 and polycystin-2 are both required to amplify inositol-trisphosphate-induced Ca2+ release

Keywords: Polycystin; ADPKD; Inositol 1,4,5-trisphosphate receptor; Endoplasmic reticulum; Ca2+ release

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2012 سفارش ترجمه

Analysis of baseline parameters in the HALT polycystic kidney disease trials

Keywords: ADPKD; chronic renal disease; kidney volume; polycystic kidney disease; renal function

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2012 سفارش ترجمه

Crystal structure and characterization of coiled-coil domain of the transient receptor potential channel PKD2L1

Keywords: CRD; cytoplasmic regulatory domain; PKD2L1; polycystic kidney disease 2-like 1; PKD1; polycystic kidney disease 1; PKD1L3; polycystic kidney disease 1-like 3; ER; endoplasmic reticulum; HEK; human embryonic kidney; ADPKD; autosomal dominant polycystic kid

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2012 سفارش ترجمه

Inhibition of histone deacetylases targets the transcription regulator Id2 to attenuate cystic epithelial cell proliferation

Keywords: ADPKD; gene expression; gene transcription; proliferation; renal epithelial cell

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2012 سفارش ترجمه

Inhibition of Cdc25A Suppresses Hepato-renal Cystogenesis in Rodent Models of Polycystic Kidney and Liver Disease

Keywords: Animal Model; Phosphatase; Therapeutic Strategy; Cell Division; ADPKD; autosomal-dominant polycystic kidney disease; ARPKD; autosomal-recessive polycystic kidney disease; Cdc25; cell division cycle 25; Cdk; cyclin-dependent kinase; PCK; polycystic kidney;

دانلود رایگان متن کامل مقاله ISI 16 صفحه سال انتشار : 2012 سفارش ترجمه

Polycystic Liver Diseases: Congenital Disorders of Cholangiocyte Signaling

Keywords: AC; adenyl cyclase; AC6; adenylyl-cyclases-6; ADPKD; autosomal-dominant polycystic kidney disease; AKT; v-akt murine thymoma viral oncogene homolog 1; ARPKD; autosomal-recessive polycystic kidney disease; cAMP; cycle adenosine monophosphate; CD; Caroli di

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2011 سفارش ترجمه

Polycystic kidney disease: The complexity of planar cell polarity and signaling during tissue regeneration and cyst formation

Keywords: ADPKD; Polycystic kidney disease; Renal development; Renal epithelial regeneration; Planar cell polarity; Hippo signaling

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

Short-term effects of tolvaptan on renal function and volume in patients with autosomal dominant polycystic kidney disease

Keywords: ADPKD; kidney volume; polycystic kidney disease; renal function; vasopressin

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

Angiogenic growth factors correlate with disease severity in young patients with autosomal dominant polycystic kidney disease

Keywords: ADPKD; cardiovascular disease; children; kidney volume; VEGF

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

What’s new in… Ciliopathies

Keywords: ADPKD; ARPKD; Bardet-Biedl syndrome; centrosomes; cilia; ciliopathies; cysts; Meckel-Gruber syndrome; nephronopthisis; polycystic kidney disease

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

Secondary, Somatic Mutations Might Promote Cyst Formation in Patients With Autosomal Dominant Polycystic Liver Disease

Keywords: Cholangiocytes; Genetic Analysis; Pathogenesis; Liver Disease; ADPKD; autosomal dominant polycystic kidney disease; ER; endoplasmic reticulum; LOH; loss of heterozygosity; PCLD; polycystic liver disease; SNP; single nucleotide polymorphism;

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2011 سفارش ترجمه

Autosomal dominant polycystic kidney disease: Genetics, mutations and microRNAs

Keywords: ADPKD; PKD gene; Mutation; Gene variation; Polycystic kidney disease; Variants of uncertain significance

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2011 سفارش ترجمه

Biologic and Clinical Features of Benign Solid and Cystic Lesions of the Liver

Keywords: Adenoma; Hepatocellular; Hyperplasia; Hemangioma; Polycystic Liver Disease; Cystadenoma; AAS; anabolic androgenic steroids; ADPKD; autosomal dominant polycystic kidney disease; AP; alkaline phosphatase; BMI; body mass index; CA19-9; carbohydrate antigen 1

دانلود رایگان متن کامل مقاله ISI 20 صفحه سال انتشار : 2011 سفارش ترجمه

ReviewCongenital disorders of glycosylation in hepatology: The example of polycystic liver disease

Keywords: CDG; congenital disorders of glycosylation; PCLD; polycystic liver disease; SEC63; SEC63 homolog (S. cerevisiae); PRKCSH; protein kinase C substrate 80K-H (80 kDa protein, Heavy chain); ADPKD; autosomal dominant polycystic kidney disease; ER; endoplasmic

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2010 سفارش ترجمه

Diagnosis of Autosomal-Dominant Polycystic Kidney Disease: An Integrated Approach

Keywords: Diagnosis; screening; ADPKD

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2010 سفارش ترجمه

Clinical utility of calcimimetics targeting the extracellular calcium-sensing receptor (CaSR)

Keywords: CaSR; calcium-sensing receptor; Cao2+; extracellular calcium concentration; PTH; parathyroid hormone; NKF; National Kidney Foundation; FDA; US Food and Drug Administration; CKD; chronic kidney disease; MGluR; metabotropic glutamate receptor; GABA; gamma a

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2010 سفارش ترجمه

Activation of Trpv4 Reduces the Hyperproliferative Phenotype of Cystic Cholangiocytes From an Animal Model of ARPKD

Keywords: Calcium; PKD; Cholangiocytes; Trpv4; AA; arachidonic acid; ARPKD; autosomal-recessive polycystic kidney disease; ADPKD; autosomal-dominant polycystic kidney disease; CCL; cholangiocyte cell line; EET; epoxyecosatrienoic acid; EGFP; Enhanced Green Fluoresc

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2010 سفارش ترجمه

Treatment Strategies and Clinical Trial Design in ADPKD

Keywords: Polycystic kidney disease; ADPKD; Cyclic AMP; Vasopressin V2 receptor antagonist; Mammalian target of rapamycin; Somatostatin analogs; Consortium for radiologic imaging study of PKD;

دانلود رایگان متن کامل مقاله ISI 15 صفحه سال انتشار : 2010 سفارش ترجمه

Intracellular Ca2+ storage in health and disease: A dynamic equilibrium

Keywords: Aβ; amyloid-β; AD; Alzheimer's disease; ADPKD; autosomal dominant polycystic kidney disease; APP; amyloid precursor protein; Bax; Bcl-2-associated Xprotein; BI-1; Bax Inhibitor-1; [Ca2+]cyt; cytosolic Ca2+ concentration; [Ca2+]ER; endoplasmic-reticulum

دانلود رایگان متن کامل مقاله ISI 18 صفحه سال انتشار : 2010 سفارش ترجمه

ERK1/2-Dependent Vascular Endothelial Growth Factor Signaling Sustains Cyst Growth in Polycystin-2 Defective Mice

Keywords: ADPKD; autosomal dominant polycystic kidney disease; CC3; cleaved caspase-3; DMOG; 2-oxoglutarate analogues dimethyloxaloylglycine; ERK; extracellular signal-regulated kinase; HIF; hypoxia-inducible factor; MEK; mitogen signal-regulated kinase; PC1; pol

دانلود رایگان متن کامل مقاله ISI 19 صفحه سال انتشار : 2010 سفارش ترجمه

Incompletely penetrant PKD1 alleles suggest a role for gene dosage in cyst initiation in polycystic kidney disease

Keywords: ADPKD; mutation; hypomorphic allele; childhood; PKD1

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2009 سفارش ترجمه

Lanreotide Reduces the Volume of Polycystic Liver: A Randomized, Double-Blind, Placebo-Controlled Trial

Keywords: ADPKD; autosomal dominant polycystic kidney disease; cAMP; cyclic adenosine monophosphate; CT; computerized tomography; GGT; γ-glutamyl transferase; HRQoL; health-related quality of life; PCK; polycystic kidney; PCLD; polycystic liver disease; PKD; polyc

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2009 سفارش ترجمه

Deficiency of polycystic kidney disease-1 gene (PKD1) expression increases A3 adenosine receptors in human renal cells: Implications for cAMP-dependent signalling and proliferation of PKD1-mutated cystic cells

Keywords: ADPKD; Polycystin-1; Adenosine receptor; cAMP-dependent signalling; NFkB activation; Renal cell

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2009 سفارش ترجمه