Keywords: آرژینینوسوکتینات سنتتاز; AIF; apoptosis-inducing factor; ASL; argininosuccinate lyase; ASS; argininosuccinate synthetase; AST; aspartate aminotransferase; BER; base excision repair; cGC; cyclic guanylyl cyclase; CNS; central nervous system; DRP-1; dynamin-related protein 1; EAE;
مقالات ISI آرژینینوسوکتینات سنتتاز (ترجمه نشده)
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Keywords: آرژینینوسوکتینات سنتتاز; Urea cycle disorders; Glycerol phenylbutyrate; Children; Infants; Ammonia; Glutamine; ARG1; arginase 1; ASL; argininosuccinate lyase; ASS; argininosuccinate synthetase; BMI; body mass index; BSA; body surface area; CDC; Centers for Disease Control and Pre
Keywords: آرژینینوسوکتینات سنتتاز; ACL; ATP citrate lyase; Akt; Protein kinase B; ASCT2; Alanine, serine, cysteine-preferring transporter 2; ASS; Argininosuccinate synthetase; BMI; Body mass index; CAF; Cancer-associated fibroblasts; ER; Estrogen receptor; FASN; Fatty acid synthase; GPC; G
Keywords: آرژینینوسوکتینات سنتتاز; Urea cycle disorder; Citrullinemia; Argininosuccinate synthetase; Prenatal diagnosis; Amniotic fluid; Chorionic villus sampling;
Keywords: آرژینینوسوکتینات سنتتاز; ADC; arginine decarboxylase; ASL; argininosuccinate lyase; ASS; argininosuccinate synthetase; DG; dentate gyrus; GABA; γ-aminobutyric acid; MIA; maternal immune activation; NO; nitric oxide; NOS; nitric oxide synthase; PFC; prefrontal cortex; poly I:C; p
Modelling urea-cycle disorder citrullinemia type 1 with disease-specific iPSCs
Keywords: آرژینینوسوکتینات سنتتاز; Argininosuccinate synthetase; Citrullinemia type 1; iPSC; Hepatocyte; l-arginine; Urea cycle disorder;
CommunicationPRMT7 Interacts with ASS1 and Citrullinemia Mutations Disrupt the Interaction
Keywords: آرژینینوسوکتینات سنتتاز; PRMT; protein arginine methyltransferase; Y2H; yeast two-hybrid; ASS1; argininosuccinate synthetase; co-IP; co-immunoprecipitation; GST; glutathione S-transferase; GFP; green fluorescent protein; CD; circular dichroism; BSA; bovine serum albumin; protein
Profiles of amino acids and biogenic amines in the plasma of Cri-du-Chat patients
Keywords: آرژینینوسوکتینات سنتتاز; 5-HT; serotonin; 5p; chromosome 5; AcOrn; acetyl ornitine; ADMA; dimethylarginine asymmetric; ADP; adenosine diphosphate; AGAT; glycine amidinotransferase; Ala; alanine; Alpha AAA; alpha-aminoadipic acid; Arg; arginine; ASL; argininosuccinate lyase; Asn;
Purification of a dimeric arginine deiminase from Enterococcus faecium GR7 and study of its anti-cancerous activity
Keywords: آرژینینوسوکتینات سنتتاز; ADI; arginine deiminase; ASS; argininosuccinate synthetase; CK; carbamate kinase; CF; cytoplasmic fractions; DMSO; dimethylsulfoxide; GRAS; generally recognized as safe; HKC; heat-killed cells; Hep-G2; Human hepatocellular carcinoma cell line; IC50; half-
Prenatal diagnosis of citrullinemia type 1: A Chinese family with a novel mutation of the ASS1 gene
Keywords: آرژینینوسوکتینات سنتتاز; Prenatal diagnosis; Citrullinemia type 1; Argininosuccinate synthetase; ASS1 gene
Reduced protein oxidation in Wistar rats supplemented with marine Ï3 PUFAs
Keywords: آرژینینوسوکتینات سنتتاز; 1/2-DE; one/two-dimensional gel electrophoresis; AKR; 3-α-hydroxysteroid dehydrogenase; ALA; α-linolenic acid; ARA; arachidonic acid; ASS; argininosuccinate synthetase; AST; aspartate aminotransferase; DHA; docosahexaenoic acid; DNPH; 2,4-dinitrophenylh
Ammonia Control in Children Ages 2 Months through 5 Years with Urea Cycle Disorders: Comparison of Sodium Phenylbutyrate and Glycerol Phenylbutyrate
Keywords: آرژینینوسوکتینات سنتتاز; ASA; Argininosuccinic acid; ASL; Argininosuccinate lyase; ASS; Argininosuccinate synthetase; AUC0-24; 24-hour area under the curve; DSMB; Data and safety monitoring board; G tube; Gastrostomy tube; GPB; Glycerol phenylbutyrate; NaPBA; Sodium phenylbutyrat
Proline rich-oligopeptides: Diverse mechanisms for antihypertensive action
Keywords: آرژینینوسوکتینات سنتتاز; ACE; angiotensin I-converting enzyme; ASS; argininosuccinate synthetase; Bj; Bothrops jararaca; BK; bradykinin; PRO; proline-rich oligopeptide; ([Ca2+]i); intracellular calcium concentration; CNP; C-type natriuretic peptide; CNS; central nervous system; H
Regional variations and age-related changes in arginine metabolism in the rat brain stem and spinal cord
Keywords: آرژینینوسوکتینات سنتتاز; ADC; arginine decarboxylase; ANOVA; analysis of variance; ASL; argininosuccinate lyase; ASS; argininosuccinate synthetase; eNOS; endothelial nitric oxide synthase; HPLC; high-performance liquid chromatography; iNOS; inducible nitric oxide synthase; LC/MS;
Targeting autophagy as a potential therapeutic approach for melanoma therapy
Keywords: آرژینینوسوکتینات سنتتاز; 5-ALA; 5-aminolevulinic acid; AMBRA1; autophagy/Beclin 1 regulator 1; APC; antigen-presenting cell; ASS; argininosuccinate synthetase; ATG; autophagy-related; ATM; Ataxia telangiectasia mutated; BafA1; bafilomycin A1; Bif-1; endophilin B1; BN; benign nevi
Amino acid disorders detected by quantitative amino acid HPLC analysis in Thailand: An eight-year experience
Keywords: آرژینینوسوکتینات سنتتاز; ASL; argininosuccinate lyase; ASS; argininosuccinate synthetase; CPS1; carbamoylphosphate synthetase I; HCY; homocystinuria; HPA; hyperphenylalaninemia; HPLC; high-performance liquid chromatography; IEM; inborn error of metabolism; MSUD; maple syrup urine
Effects of supplementation on food intake, body weight and hepatic metabolites in the citrin/mitochondrial glycerol-3-phosphate dehydrogenase double-knockout mouse model of human citrin deficiency
Keywords: آرژینینوسوکتینات سنتتاز; AGC; aspartate-glutamate carrier; ASS; argininosuccinate synthetase; CTLN2; adult-onset type II citrullinemia; Ctrn-KO; Slc25a13 (citrin) knockout; KO; knockout; MCT; medium-chain triglycerides; mGPD; mitochondrial glycerol-3-phosphate dehydrogenase; NI
Polyethyleneimine-Based Core-Shell Nanogels: A Promising siRNA Carrier for Argininosuccinate Synthetase mRNA Knockdown in HeLa Cells
Keywords: آرژینینوسوکتینات سنتتاز; Polyethyleneimine; Gelatin; siRNA delivery; Argininosuccinate Synthetase; Core-shell nanogel
Bradykinin-potentiating peptides: Beyond captopril
Keywords: آرژینینوسوکتینات سنتتاز; Bradykinin; Snake venom; Bradykinin-potentiating peptide; Angiotensin-converting enzyme; Captopril; Argininosuccinate synthetase
Metabolomic analysis reveals hepatic metabolite perturbations in citrin/mitochondrial glycerol-3-phosphate dehydrogenase double-knockout mice, a model of human citrin deficiency
Keywords: آرژینینوسوکتینات سنتتاز; AASS; α-aminoadipate δ-semialdehyde synthase; AGC; aspartate-glutamate carrier; αKG; α-ketoglutarate; ANOVA; analysis of variance; Ala; alanine; Arg; arginine; ASA; argininosuccinate; Asp; aspartate; ASS; argininosuccinate synthetase; CE/MS; capilla
Growth hormone and growth hormone secretagogue effects on nitrogen balance and urea synthesis in steroid treated rats
Keywords: آرژینینوسوکتینات سنتتاز; BW; body weight; CUNS; capacity of urea-N synthesis; GH; growth hormone; IGF-1; insulin-like growth factor I; CPS; carbamoyl phosphate synthetase; OTC; ornithine transcarboxylase; ASS; argininosuccinate synthetase; ASL; argininosuccinate lyase; ARG; argin
Identification of a liver-specific cAMP response element in the human argininosuccinate synthetase gene
Keywords: آرژینینوسوکتینات سنتتاز; Argininosuccinate synthetase; Urea cycle; DNase 1 hypersensitive site mapping; cAMP response element (CRE); cAMP response element-binding protein (CREB); cAMP-dependent protein kinase A; Tissue-specific extinguisher 1 (TSE1)
Polyaspartoyl·l-arginine inhibits platelet aggregation through stimulation of NO release from endothelial cells
Keywords: آرژینینوسوکتینات سنتتاز; Polyaspartoyl·l-arginine; Platelet aggregation; Rat aortic endothelial cell; Nitric oxide; l-arginine; Argininosuccinate synthetase; Citrulline–NO cycle
Contrasting features of urea cycle disorders in human patients and knockout mouse models
Keywords: آرژینینوسوکتینات سنتتاز; Urea; Hyperammonemia; Knockout; N-Acetylglutamate synthase; Carbamyl phosphate synthetase I; Ornithine transcarbamylase; Argininosuccinate synthetase; Argininosuccinate lyase; Arginase
Citrin deficiency as a cause of chronic liver disorder mimicking non-alcoholic fatty liver disease
Keywords: آرژینینوسوکتینات سنتتاز; AGC; aspartate-glutamate carrier; NADH; nicotinamide adenine dinucleotide; ATP; adenosine triphosphate; ASS; argininosuccinate synthetase; NICCD; neonatal intrahepatic cholestasis caused by citrin deficiency; CTLN2; adult-onset type II citrullinemia; NA
Tuning adenosine A1 and A2A receptors activation mediates l-citrulline-induced inhibition of [3H]-acetylcholine release depending on nerve stimulation pattern
Keywords: آرژینینوسوکتینات سنتتاز; ACh; acetylcholine; ADA; adenosine deaminase; ADO; adenosine; AF-DX 116; 11-[2-1[(diethylamino)methyl-1-piperidinyl]-acetyl]-5,11-dihydro-6H-pyrido[2,3-b][1,4]benzodiazepine-6-one; ASL; argininosuccinate lyase; ASS; argininosuccinate synthetase; BAY 41-22
Arginine, citrulline and nitrate concentrations in the cerebrospinal fluid from patients with acute hydrocephalus
Keywords: آرژینینوسوکتینات سنتتاز; Sample pretreatment; Inflammation; Cerebrospinal fluid drainage; Argininosuccinate synthetase
Biphasic effect of IL-1β on the activity of argininosuccinate synthetase in Caco-2 cells. Involvement of nitric oxide production
Keywords: آرژینینوسوکتینات سنتتاز; Interleukin-1β; Nitric oxide; Argininosuccinate synthetase; Caco-2 cellsASS, argininosuccinate synthetase; DMEM, Dulbecco's modified Eagles's medium; IL-1β, interleukin-1 beta; INF-γ, interferon gamma; l-NMMA, NG-methyl-l-arginine; NOS, nitric oxide synth
Pyruvate ameliorates the defect in ureogenesis from ammonia in citrin-deficient mice
Keywords: آرژینینوسوکتینات سنتتاز; Adult-onset type II citrullinemia; Hyperammonemia; Argininosuccinate synthetase; Citrin deficiency; Pyruvate; Redox state; UreogenesisAGC, aspartate-glutamate carrier; Ala, alanine; Arg, arginine; Asn, asparagine; Asp, aspartate; ASS, argininosuccinate sy
Modulation of intestinal urea cycle by dietary spermine in suckling rat
Keywords: آرژینینوسوکتینات سنتتاز; Argininosuccinate synthetase; Nutrient; Polyamine; Intestine; Urea cycle; Weaning;
Arginine deprivation and metabolomics: Important aspects of intermediary metabolism in relation to the differential sensitivity of normal and tumour cells
Keywords: آرژینینوسوکتینات سنتتاز; Cancer; Arginine; Arginase; Citrulline; Ornithine; Deprivation; Catabolism; Cell proliferation; Cell death; Channelling; Urea cycle intermediates; Argininosuccinate synthetase; Argininosuccinate lyase;
Toxicity and adaptive immune response to intracellular transgenes delivered by helper-dependent vs. first generation adenoviral vectors
Keywords: آرژینینوسوکتینات سنتتاز; Argininosuccinate synthetase; Intracellular transgene; Adaptive immunity; First generation adenovirus; Helper-dependent adenovirus; Urea cycle; β-Galactosidase;