دانلود مقالات ISI درباره Cftr + ترجمه فارسی

Implementation of the first worldwide quality assurance program for cystic fibrosis multiple mutation detection in population-based screening

Keywords: ACMG; American College of Medical Genetics; CFF; Cystic Fibrosis Foundation; CFTR; Cystic Fibrosis Transmembrance Conductance Regulator gene; DBS; dried-blood spot; IRT; Immunoreactive trypsinogen; NBS; Newborn screening; NSQAP; Newborn Screening Quality

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2011 سفارش ترجمه

SNARE protein regulation of cardiac potassium channels and atrial natriuretic factor secretion

Keywords: ABC; ATP-binding cassette; AK; adenylate kinase; ANF; atrial natriuretic factor; BNP; brain natriuretic peptide; CFTR; cystic fibrosis transmembrane regulator; Cav; voltage-gated calcium; CK; creatine kinase; CNP; c-type natriuretic peptide; DPP; dipeptid

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

Assessment of CFTR function in homozygous R117H-7T subjects

Keywords: Cystic fibrosis; R117H; NPD; ICM; CFTR

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

Measurement of cystic fibrosis transmembrane conductance regulator activity using fluorescence spectrophotometry

Keywords: CFTR; Cystic fibrosis; Chloride channel; SPQ; Chloride fluorescence spectrophotometry;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

Isolation of mouse pancreatic alpha, beta, duct and acinar populations with cell surface markers

Keywords: CK19; cytokeratin 19; CFTR; cystic fibrosis transmembrane receptor; MafA; musculoaponeurotic fibrosarcoma oncogene homolog A; GP2; glycoprotein 2; Pdx1; pancreatic and duodenal homeobox factor 1; HNF4α; hepatocyte nuclear factor 4 alpha; TTR; transthyret

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

Concentration of the antibacterial precursor thiocyanate in cystic fibrosis airway secretions

Keywords: ASL; airway surface liquid; CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; CFU; colony-forming unit; Duox; dual oxidase; FEV1; forced expiratory volume in 1 s; H2O2; hyrogen peroxide; LPO; lactoperoxidase; MPO; myeloperox

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

Targeting maladaptive glutathione responses in lung disease

Keywords: BSO; l-buthionine sulfoximine; γ-GCL; γ-glutamylcysteine ligase; GSH; glutathione; MRP; multi-drug resistant protein; ELF; epithelial lining fluid; BALF; bronchoalveolar lavage fluid; SOD; superoxide dismutase; IPF; idiopathic pulmonary fibrosis; ARDS;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

Characterization of the L683P mutation of SLC26A9 in Xenopus oocytes

Keywords: Cl− channel; Xenopus oocytes; SLC26A9-L683P; CFTR;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

β-Adrenoceptor/PKA-stimulation, Na+-Ca2+ exchange and PKA-activated Cl− currents in rabbit cardiomyocytes: A conundrum

Keywords: Cardiac myocyte; CFTR; NCX; Rabbit atrial myocyte; Rabbit ventricular myocyte; Whole-cell patch-clamp recording;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

An expeditious access to 5-pyrimidinol derivatives from cyclic methylglyoxal diadducts, formation of argpyrimidines under physiological conditions and discovery of new CFTR inhibitors

Keywords: Methylglyoxal; 2-Oxoaldehydes; Argpyrimidine; Arginine; Antioxidants; 5-Pyrimidinols; CFTR

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2011 سفارش ترجمه

Curcumin is a lipid dependent inhibitor of the Na,K-ATPase that likely interacts at the protein-lipid interface

Keywords: BS3; Bis-(sulfosuccinimidyl)suberate; CFTR; cystic fibrosis transmembrane conductance regulator; DMSO; dimethyl sulfoxide; ECL; enhanced chemiluminescence; EC50; ligand concentration producing half-maximum effect; Na,K-ATPase; sodium and potassium activat

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2011 سفارش ترجمه

A novel highly charged exopolysaccharide produced by two strains of Stenotrophomonas maltophilia recovered from patients with cystic fibrosis

Keywords: Ac; acetyl; CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; deAc-SMA-EPS; S. maltophilia de-O-acetylated EPS; EPS; exopolysaccharide; ESI-MS; electrospray ionization mass spectrometry; FR-I; fraction I; FR-II; fraction II;

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2011 سفارش ترجمه

Fluid transport and cystogenesis in autosomal dominant polycystic kidney disease

Keywords: Chloride; CFTR; NKCC1; Aquaporins; Vasopressin; Osmoregulation; Epithelial cell; Polycystins; Na+-K+-ATPase

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2011 سفارش ترجمه

Genistein stimulates duodenal HCO3− secretion through PI3K pathway in mice

Keywords: Genistein; CFTR; Phosphatidylinositol 3-kinase; Duodenum; Bicarbonate secretion;

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2011 سفارش ترجمه

Cognitive, Behavioral, and Systems NeuroscienceResearch PaperThe possible additional role of the cystic fibrosis transmembrane regulator to motoneuron inhibition produced by glycine effects

Keywords: glycine; chloride channels; postsynaptic currents; atonia; REM sleep; ACSF; artificial cerebrospinal fluid; AHP; afterhyperpolarization potential; BSA; bovine serum albumin; CFTR; cystic fibrosis transmembrane regulator; ChAT; choline acetyl transferase;

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2011 سفارش ترجمه

Curcumin and genistein additively potentiate G551D-CFTR

Keywords: Cystic fibrosis; CFTR; G551D mutation; Genistein; Curcumin; Additive effect

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2011 سفارش ترجمه

Cordyceps militaris extract stimulates Cl− secretion across human bronchial epithelia by both Ca2+- and cAMP-dependent pathways

Keywords: AC; adenylate cyclase; AM; acetoxymethylester; BAPTA; 1,2-bis(2-aminophenoxy)ethane-N,N,N′,N′-tetraacetic acid; CaCC; calcium-activated Cl− channel; cAMP; cyclic adenosine monophosphate; CFTR; cystic fibrosis transmembrane conductance regulator; CFT

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2011 سفارش ترجمه

Regulatory mechanism of duodenal bicarbonate secretion

Keywords: AC; adenylate cyclase; cNOS; constitutive nitric oxide synthase; cAMP; 3′,5′-cyclic adenosine monophosphate; cGMP; 3′,5′-cyclic guanosine monophosphate; COX; cyclooxygenase; CFTR; cystic fibrosis transmembrane conductance regulator; dbcAMP; dibuty

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2011 سفارش ترجمه

A mechanistic approach for islet amyloid polypeptide aggregation to develop anti-amyloidogenic agents for type-2 diabetes

Keywords: Amylin; Amyloidogenesis; Diabetes mellitus type-2; Intrinsically disordered polypeptide; π-π stacking; AFM; atomic force microscopy; CFTR; cystic fibrosis transmembrane conductance regulator; CGRP; calcitonin gene related peptide; DM-2; type-2 diabete

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2011 سفارش ترجمه

Gene and cell therapy for cystic fibrosis: From bench to bedside

Keywords: Cystic fibrosis; CFTR; Human artificial chromosome; Animal model; Vector development; Gene delivery; In utero gene therapy; Stem cells

دانلود رایگان متن کامل مقاله ISI 15 صفحه سال انتشار : 2011 سفارش ترجمه

Lineage Tracing Evidence for Transdifferentiation of Acinar to Duct Cells and Plasticity of Human Pancreas

Keywords: Metaplasia; Reprogramming; Exocrine Pancreas; Tissue Engineering; BrdU; 5′-bromodeoxyuridine; CAII; carbonic anhydrase II; CFTR; cystic fibrosis transmembrane conductance regulator; CK19; cytokeratin 19; CMV; cytomegalovirus promoter; DAPI; 4′,6-diami

دانلود رایگان متن کامل مقاله ISI 15 صفحه سال انتشار : 2011 سفارش ترجمه

Recruitment of the oncoprotein v-ErbA to aggresomes

Keywords: TRα1; thyroid hormone receptor α1; T3; thyroid hormone; AEV; avian erythroblastosis virus; TGF-β; transforming growth factor-β; LMB; leptomycin B; MTOC; microtubule organizing center; HDAC6; histone deacetylase 6; CFTR; cystic fibrosis transmembrane c

دانلود رایگان متن کامل مقاله ISI 17 صفحه سال انتشار : 2011 سفارش ترجمه

Trypsin Reduces Pancreatic Ductal Bicarbonate Secretion by Inhibiting CFTR Cl− Channels and Luminal Anion Exchangers

Keywords: Acinar Cells; Ductal Epithelium; Animal Model; Pancreatic Enzymes; BAPTA-AM; 1,2-bis(o-aminophenoxy)ethane-N,N,N′,N′-tetraacetic acid; CFTR; cystic fibrosis transmembrane conductance regulator Cl− channel; CFTRinh-172; CFTR inhibitor-172; [Ca2+]i; i

دانلود رایگان متن کامل مقاله ISI 18 صفحه سال انتشار : 2011 سفارش ترجمه

Hypochloremia and hyponatremia as the initial presentation of cystic fibrosis in three adults

Keywords: Mucoviscidose; CFTR; Hyponatrémie; Hypochlorémie; Alcalose métaboliqueCystic fibrosis; CFTR; Hyponatremia; Hypochloremia; Metabolic alkalosis

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2010 سفارش ترجمه

Mutational spectrum of cystic fibrosis in the Lebanese population

Keywords: Cystic fibrosis; Lebanon; CFTR

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2010 سفارش ترجمه

IL-17 primes airway epithelial cells lacking functional Cystic Fibrosis Transmembrane conductance Regulator (CFTR) to increase NOD1 responses

Keywords: Interleukin; Bacteria; Lung; Inflammation; Signal transduction; Receptors; AECs; airway epithelial cells; CF; cystic fibrosis; CFTR; CF transmembrane conductance regulator; CIKS; Connection to IκB Kinase and Stress-activated protein kinase; CXCL8; Cyst-X

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2010 سفارش ترجمه

Hepatobiliary disease in cystic fibrosis

Keywords: bile acids; biliary cirrhosis; CFTR; children; Cystic Fibrosis; liver; modifier genes

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2010 سفارش ترجمه

Association of cystic fibrosis genetic modifiers with congenital bilateral absence of the vas deferens

Keywords: Congenital bilateral absence of the vas deferens; CBAVD; CFTR; cystic fibrosis; CF; modifier gene; TGF-β; EDNRA

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2010 سفارش ترجمه

The 50 year evolution of in vitro systems to reveal salt transport functions of teleost fish gills

Keywords: Mitochondrion-rich cell; Chloride cell; Pavement cell; Gill bar; Opercular epithelium; Primary cell culture; CFTR; NKCC; V-type H+-ATPase

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2010 سفارش ترجمه

CFTR-dependent susceptibility of the cystic fibrosis-host to Pseudomonas aeruginosa

Keywords: Cftr; Ceramide; Cystic fibrosis; P. aeruginosa

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2010 سفارش ترجمه

Osteopenia in Cftr-deltaF508 mice

Keywords: Bone disease; Genetically modified mouse; Cftr; deltaF508; Femur

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2010 سفارش ترجمه

Differential regulation of CFTRΔF508 degradation by ubiquitin ligases gp78 and Hrd1

Keywords: ER; endoplasmic reticulum; ERAD; ER-associated degradation; CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; CUE; coupling of ubiquitin to ER degradation; GFP; green fluorescent protein; RNAi; RNA interference; E2; ubiquitin

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2010 سفارش ترجمه

Model of the cAMP activation of chloride transport by CFTR channel and the mechanism of potentiators

Keywords: CFTR; Cystic fibrosis; Potentiators

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2010 سفارش ترجمه

A 10-year large-scale cystic fibrosis carrier screening in the Italian population

Keywords: Cystic fibrosis; Screening; CF carrier; CFTR; Reverse dot-blot

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2010 سفارش ترجمه

Molecular dynamics analysis of the wild type and dF508 mutant structures of the human CFTR–nucleotide binding domain 1

Keywords: Cystic fibrosis; Nuclear binding domain; dF508; CFTR

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2010 سفارش ترجمه

Psychological Effects of False-Positive Results in Cystic Fibrosis Newborn Screening: A Two-Year Follow-Up

Keywords: CF; Cystic fibrosis; CFTR; Cystic fibrosis transmembrane conductance regulator; CRCM; Specialized cystic fibrosis centers; HZ; Heterozygous; IRT; Immunoreactive trypsin; NBS; Newborn screening; PHT; Persistent hypertrypsinemia; PPCV; Parental Perception o

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2010 سفارش ترجمه

Sputum Induction in Routine Clinical Care of Children with Cystic Fibrosis

Keywords: BMI; Body mass index; CF; Cystic fibrosis; CFTR; Cystic fibrosis transmembrane conductance regulator; ES; Spontaneously expectorated sputum; FEV1; Forced expiratory volume in 1 second; HS; Hypertonic saline; IS; Induced sputum; SI; Sputum induction; TS; T

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2010 سفارش ترجمه

Entry of Burkholderia organisms into respiratory epithelium: CFTR, microfilament and microtubule dependence

Keywords: Burkholderia cenocepacia; Burkholderia dolosa; Invasion; Respiratory epithelium; LC3; LCFSN; CFTR; Microfilaments; Microtubules

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2010 سفارش ترجمه

Tobacco carcinogen NNK transporter MRP2 regulates CFTR function in lung epithelia: Implications for lung cancer

Keywords: Lung cancer; Tobacco-specific carcinogen; NNK; MRP2; CFTR; Protein interaction

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2010 سفارش ترجمه

A novel donor splice site characterized by CFTR mRNA analysis induces a new pseudo-exon in CF patients

Keywords: Splicing; CFTR; mRNA; Cystic fibrosis; Pseudo-exon

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2010 سفارش ترجمه

Quantification of the Relative Contribution of Environmental and Genetic Factors to Variation in Cystic Fibrosis Lung Function

Keywords: ANOVA; Analysis of variance; CF; Cystic fibrosis; CFTR; Cystic fibrosis transmembrane conductance regulator gene; FEV1; Forced expiratory volume in 1 second;

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2010 سفارش ترجمه

The cystic fibrosis transmembrane conductance regulator (CFTR) is expressed in maturation stage ameloblasts, odontoblasts and bone cells

Keywords: CFTR; Immunostaining; Ameloblasts; Osteoblasts; Osteoclasts; Cftr-knockout;

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2010 سفارش ترجمه

Rescue of F508del-CFTR by RXR motif inactivation triggers proteome modulation associated with the unfolded protein response

Keywords: Cystic fibrosis; CFTR; Unfolded protein response; Protein trafficking; RXR motif; Therapeutic target

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2010 سفارش ترجمه

ΔF508 CFTR processing correction and activity in polarized airway and non-airway cell monolayers

Keywords: Cystic fibrosis; CFTR; Ion transportBHK, baby hamster kidney cells; CF, cystic fibrosis; CFBE41o−, cystic fibrosis bronchial epithelial cells; CFTR, cystic fibrosis transmembrane conductance regulator; ERAD, endoplasmic reticulum associated degradation; F

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2010 سفارش ترجمه

Cystic fibrosis: Exploiting its genetic basis in the hunt for new therapies

Keywords: Cystic fibrosis; CFTR; Gene therapy; Corrector; Potentiator; Transcriptional read-through

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2010 سفارش ترجمه

An Update on Cystic Fibrosis Screening

Keywords: Cystic fibrosis; Prenatal diagnosis; Carrier screening; CFTR; Pregnancy;

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2010 سفارش ترجمه

Dynamic Regulation of CFTR Bicarbonate Permeability by [Cl−]i and Its Role in Pancreatic Bicarbonate Secretion

Keywords: CFTR; Bicarbonate; Pancreatic Secretion; WNK1/OSR1/SPAK Kinases; CFTR; cystic fibrosis transmembrane conductance regulator; [Cl−]i; intracellular Cl− concentration; Erev; reversal potential; [HCO3−]i; intracellular bicarbonate concentration; IBMX; 3

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2010 سفارش ترجمه

Carrier Screening for Cystic Fibrosis

Keywords: Cystic fibrosis; Carrier testing; CFTR; Mutation panel;

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2010 سفارش ترجمه

Cystic fibrosis across Europe: EuroCareCF analysis of demographic data from 35 countries

Keywords: Database; Rare disease; Geography; Chronic disease; Genetics; p.Phe508del; CFTR

دانلود رایگان متن کامل مقاله ISI 17 صفحه سال انتشار : 2010 سفارش ترجمه

Genetic factors in chronic pancreatitis; implications for diagnosis, management and prognosis

Keywords: Chronic pancreatitis; Genes; Mutations; Trypsin; PRSS1; PRSS2; SPINK1; CTRC; CFTR

دانلود رایگان متن کامل مقاله ISI 20 صفحه سال انتشار : 2010 سفارش ترجمه