دانلود مقالات ISI درباره Cftr + ترجمه فارسی

Structural insights into PDZ-mediated interaction of NHERF2 and LPA2, a cellular event implicated in CFTR channel regulation

Keywords: NHERF2; LPA2; X-ray crystallography; CFTR; Scaffold protein; Cystic fibrosis;

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2014 سفارش ترجمه

Increased frequency of CFTR gene mutations identified in Indian infertile men with non-CBAVD obstructive azoospermia and spermatogenic failure

Keywords: CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane regulator gene; CBAVD; congenital bilateral absence of the vas deferens; SSCP; single strand conformational polymorphism; ARMS; amplification refractory mutation system; Male infertility; Cystic fib

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2014 سفارش ترجمه

S-nitrosothiols increases cystic fibrosis transmembrane regulator expression and maturation in the cell surface

Keywords: Cystic fibrosis; CFTR; S-nitrosothiol; S-nitrosylation; Chaperones; Molecular therapy;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2014 سفارش ترجمه

Chemical rescue of ΔF508-CFTR in C127 epithelial cells reverses aberrant extracellular pH acidification to wild-type alkalization as monitored by microphysiometry

Keywords: Cystic fibrosis; pH; Bicarbonate; CFTR; Glycerol; Corrector;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2014 سفارش ترجمه

Effects of dietary stevioside/rebaudioside A on the growth performance and diarrhea incidence of weaned piglets

Keywords: ADFI; average daily feed intake; ADG; average daily gain; F:G; feed:gain ratio; BW; body weight; CFTR; cystic fibrosis transmembrane conductance regulator; Diarrhea incidence; Growth performance; Rebaudioside A; Stevioside; Weaned piglets;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2014 سفارش ترجمه

Airway hyperresponsiveness in FVB/N delta F508 cystic fibrosis transmembrane conductance regulator mice

Keywords: Lung; Airway hyperresponsiveness; Cftr; Murine models;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2014 سفارش ترجمه

TPL2 signalling: From Toll-like receptors-mediated ERK1/ERK2 activation to Cystic Fibrosis lung disease

Keywords: ABIN-2; A20-binding inhibitor of NF-κB 2; CF; Cystic Fibrosis; CFTR; Cystic Fibrosis transmembrane conductance regulator; EGFR; epidermal growth factor receptor; ERK; extracellular signal-regulated kinase; GSH; glutathione; IFN; Interferon; IKK; I-kappa-

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2014 سفارش ترجمه

Bronchorelaxation of the human bronchi by CFTR activators

Keywords: Human airway; Smooth muscle; CFTR; Relaxation; Pharmacology;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2014 سفارش ترجمه

An image analysis method to quantify CFTR subcellular localization

Keywords: CFTR; Apical; Image analysis; Deconvolution

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2014 سفارش ترجمه

Neonatal screening for cystic fibrosis: Comparing the performances of IRT/DNA and IRT/PAP

Keywords: CF-NBS; cystic fibrosis newborn screening; IRT; immunoreactive trypsinogen; PAP; pancreatitis-associated protein; Neonatal screening; Cystic fibrosis; PAP; IRT; CFTR; Non-inferiority;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2014 سفارش ترجمه

Cystic fibrosis transmembrane regulator (CFTR) in human trophoblast BeWo cells and its relation to cell migration

Keywords: CFTR; BeWo cells; Ion currents; Wound healing; Forskolin; CFTRinh-172;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2014 سفارش ترجمه

The relative frequency of CFTR mutation classes in European patients with cystic fibrosis

Keywords: CF; Cystic Fibrosis; CFTR; Cystic Fibrosis Transmembrane Conductance Regulator; ECFSPR; European Cystic Fibrosis Society Patient Registry; PTC; premature termination codon; CFTR mutations; Cystic fibrosis; Genotype; Prevalence; CFTR mutation classes; Alle

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2014 سفارش ترجمه

Actin directly interacts with different membrane channel proteins and influences channel activities: AQP2 as a model

Keywords: Actin; Cytoskeleton; Channel; AQP2; CFTR; ENaC;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2014 سفارش ترجمه

Research ArticleFunctional crosstalk between the adenosine transporter CNT3 and purinergic receptors in the biliary epithelia

Keywords: AE2; anion exchanger 2; AQP1; aquaporin 1; NT; nucleoside transporter; CNT; concentrative nucleoside transporter; ENT; equilibrative nucleoside transporter; CFTR; cystic fibrosis transmembrane conductance regulator; GUSB; beta-D-glucuronidase; NRC; normal

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2014 سفارش ترجمه

Campylobacter jejuni infection suppressed Cl− secretion induced by CFTR activation in T-84 cells

Keywords: Campylobacter jejuni; CFTR; Diarrhea; Short-circuit current; Efflux assay;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2014 سفارش ترجمه

On the structural organization of the intracellular domains of CFTR

Keywords: CFTR; NBD; Regulatory domain; Cystic fibrosis; Structure;

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2014 سفارش ترجمه

Osmoregulation and branchial plasticity after acute freshwater transfer in red drum, Sciaenops ocellatus

Keywords: Euryhaline; Ionocyte; Ionoregulation; NHE; NKCC; CFTR; Sodium; Chloride; Salinity transfer

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2014 سفارش ترجمه

Effect of ivacaftor on CFTR forms with missense mutations associated with defects in protein processing or function

Keywords: CFTR; Ivacaftor; Potentiator; VX-770;

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2014 سفارش ترجمه

A comprehensive analysis of aquaporin and secretory related gene expression in neonate and adult cholangiocytes

Keywords: AE2; anion exchange protein 2; AQP; aquaporin; CFTR; cystic fibrosis transmembrane conductance regulator; D; day of life; mRNA; messenger RNA; SR; secretin receptor; Cholestasis; Liver; Water transport;

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2014 سفارش ترجمه

CFTR genotype and clinical outcomes of adult patients carried as cystic fibrosis disease

Keywords: BMI; Body Mass Index; CF; Cystic Fibrosis; CFTR; Cystic Fibrosis Transmembrane Regulator; CI; Confidential Interval; DM; Diabetes mellitus; FEF25-75%; Forced Expiratory Flow 25-75%; FEV1%; Forced Expiratory Volume In 1 Second; FVC; Forced Vital Capaci

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2014 سفارش ترجمه

Genotype-specific alterations in vascular smooth muscle cell function in cystic fibrosis piglets

Keywords: CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; dF; CFTR-F508del; ER; endoplasmic reticulum; IP3; inositol triphosphate; PSS; physiologic saline solution; VSMC; vascular smooth muscle cell; WT; wild-type.; Cystic fibrosis t

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2014 سفارش ترجمه

Genetics of cystic fibrosis: CFTR mutation classifications toward genotype-based CF therapies

Keywords: CBAVD; congenital bilateral absence of the vas deferens; CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; CFTR-RD; CFTR related disease; COPD; chronic obstructive pulmonary disease; EJC; exon junction complex; NBD; nucleotid

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2014 سفارش ترجمه

Neutral endopeptidase (CD10) is abundantly expressed in the epididymis and localized to a distinct population of epithelial cells - Its relevance for CNP degradation

Keywords: ANP; atrial natriuretic peptide; CNP; C-type natriuretic peptide; cGMP; cyclic guanosine monophosphate; CFTR; cystic fibrosis transmembrane conductance regulator; GC-B; guanylyl cyclase type B; neutral endopeptidase; NEP; SMA; smooth muscle actin; Neutral

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2014 سفارش ترجمه

Steviol retards renal cyst growth through reduction of CFTR expression and inhibition of epithelial cell proliferation in a mouse model of polycystic kidney disease

Keywords: Steviol; CFTR; AMPK; Renal cystogenesis; mTOR;

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2014 سفارش ترجمه

Functional interaction of the cystic fibrosis transmembrane conductance regulator with members of the SLC26 family of anion transporters (SLC26A8 and SLC26A9): Physiological and pathophysiological relevance

Keywords: cAMP; cyclic adenosine monophosphate; CF; cystic fibrosis; CFBE4Io-; cystic fibrosis bronchial epithelial cell line; CFTR; cystic fibrosis transmembrane conductance regulator; CHO-K1; Chinese hamster ovary-K1; DHPLC; denaturing high performance liquid chr

دانلود رایگان متن کامل مقاله ISI 10 صفحه سال انتشار : 2014 سفارش ترجمه

Redox balance in Cystic Fibrosis

Keywords: Oxidative stress; CFTR; Nrf2 dysfunction; Antioxidants; GSH; glutathione; GSSG; glutathione disulfide; Cys; cysteine; Cys-Cys; cystine; CFTR; Cystic fibrosis transmembrane conductance regulator; Nrf2; nuclear factor erythroid 2 - related factor 2; Trx; Th

دانلود رایگان متن کامل مقاله ISI 11 صفحه سال انتشار : 2014 سفارش ترجمه

Emerging Role of MicroRNAs and Long Noncoding RNAs in Respiratory Disease

Keywords: CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; HASM; human airway smooth muscle; IPF; idiopathic pulmonary fibrosis; lncRNA; long noncoding RNA; MALAT1; metastasis associated in lung adenocarcinoma transcript 1; MEG3; mate

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2014 سفارش ترجمه

The cystic fibrosis V232D mutation inhibits CFTR maturation by disrupting a hydrophobic pocket rather than formation of aberrant interhelical hydrogen bonds

Keywords: CFTR; V232D processing mutation; Cystic fibrosis; Processing mutations; Packing of TM segments; Correctors;

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2014 سفارش ترجمه

Testosterone decreases fluid and chloride secretions in the uterus of adult female rats via down-regulating cystic fibrosis transmembrane regulator (CFTR) expression and functional activity

Keywords: Testosterone; Uterus; Fluid; Cl−; CFTR;

دانلود رایگان متن کامل مقاله ISI 12 صفحه سال انتشار : 2014 سفارش ترجمه

A survey of detergents for the purification of stable, active human cystic fibrosis transmembrane conductance regulator (CFTR)

Keywords: CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; CMC; critical micelle concentration; DTT; dithiothreitol; EM; electron microscopy; GFP; green fluorescent protein; HEK; human embryonic kidney cells; Inh172; CFTR Inhibitor 17

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2014 سفارش ترجمه

Cold acclimation of NaCl secretion in a eurythermic teleost: Mitochondrial function and gill remodeling

Keywords: Opercular epithelium; CFTR; NKCC; Anaerobiosis; Eurythermic; Euryhaline; Fatty acid; Lipid

دانلود رایگان متن کامل مقاله ISI 13 صفحه سال انتشار : 2014 سفارش ترجمه

ReviewCharacterization of animal models for primary sclerosing cholangitis (PSC)

Keywords: ANA; anti-nuclear antibody; ANCA; anti-neutrophil cytoplasmic antibody; ANIT; alpha-naphthylisothiocyanate; BA; bile acids; BDL; bile duct ligation; BEC; biliary epithelial cell; CCC; cholangiocellular carcinoma; Cftr; cystic fibrosis transmembrane conduc

دانلود رایگان متن کامل مقاله ISI 14 صفحه سال انتشار : 2014 سفارش ترجمه

Aquaporin-4 as a molecular partner of cystic fibrosis transmembrane conductance regulator in rat Sertoli cells

Keywords: CFTR; Aquaporin-4; Sertoli cells; Water transport;

دانلود رایگان متن کامل مقاله ISI 26 صفحه سال انتشار : 2014 سفارش ترجمه

CFTR structure and cystic fibrosis

Keywords: Cystic fibrosis; CFTR; Membrane protein; Protein structure; Ion channel;

دانلود رایگان متن کامل مقاله ISI 32 صفحه سال انتشار : 2014 سفارش ترجمه

The protein kinases TPL2 and EGFR contribute to ERK1/ERK2 hyper-activation in CFTRΔF508-expressing airway epithelial cells exposed to Pseudomonas aeruginosa

Keywords: AEC; airway epithelial cells; CF; cystic fibrosis; CFTR; CF transmembrane regulator; EGF; epidermal growth factor; EGFR; EGF receptor; ERK; extracellular signal-regulated kinase; MAPK; mitogen activated protein kinase; PsaDM; P. aeruginosa diffusible mate

دانلود رایگان متن کامل مقاله ISI 4 صفحه سال انتشار : 2013 سفارش ترجمه

Characterization of a recurrent 3.8 kb deletion involving exons 17a and 17b within the CFTR gene

Keywords: CFTR; Rearrangement; MLPA; Carrier screening;

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2013 سفارش ترجمه

Effects of ivacaftor on severely ill patients with cystic fibrosis carrying a G551D mutation

Keywords: CFTR; FEV1; Mucus; Adults; VX-770;

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2013 سفارش ترجمه

Ceramide mediates lung fibrosis in cystic fibrosis

Keywords: Ceramide; Cystic fibrosis; Acid sphingomyelinase; Cftr;

دانلود رایگان متن کامل مقاله ISI 5 صفحه سال انتشار : 2013 سفارش ترجمه

Distribution of CFTR mutations in the Czech population: Positive impact of integrated clinical and laboratory expertise, detection of novel/de novo alleles and relevance for related/derived populations

Keywords: AT; Austrian/Austria; CE; Central Europe; CF; Cystic Fibrosis; CZ; Czech Republic/Czech; CFTR; cystic fibrosis transmembrane conductance regulator gene; DE; German/Germany; HU; Hungarian/Hungary; MLPA; multiplex ligation-dependent probe amplification; NBS

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2013 سفارش ترجمه

CFTR haplotypes in northern Iranian population

Keywords: CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane receptor; Cystic fibrosis; F508del; Haplotype; Iran;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2013 سفارش ترجمه

Cutl1: A potential target for cancer therapy

Keywords: CDP; CCAAT displacement protein; HCC; human hepatocellular carcinoma; LETFs; liver-enriched transcription factors; HNF; hepatocyte nuclear factor; Shh; Sonic hedgehog; C/EBPα; CCAAT/enhancer-binding protein; MMTV; mouse mammary tumor virus; PCAF; p300/CR

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2013 سفارش ترجمه

Nickel inhibits β-1 adrenoceptor mediated activation of cardiac CFTR chloride channels

Keywords: Rabbit cardiomyocytes; PKA-dependent Cl− current; CFTR; CFTR-inhibitor; Nickel; Ni2+;

دانلود رایگان متن کامل مقاله ISI 6 صفحه سال انتشار : 2013 سفارش ترجمه

Tuning NF-κB activity: A touch of COMMD proteins

Keywords: CFTR; cystic fibrosis transmembrane conductance regulator; COMMD; copper metabolism gene MURR1 domain-containing protein; CRL; Cullin RING ligase; CRM1; chromosome region maintenance 1/exportin 1; CYLD; cylindromatosis; DUB; deubiquitinating enzyme; ENaC;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2013 سفارش ترجمه

Abundant sequence divergence in the native Japanese cattle Mishima-Ushi (Bos taurus) detected using whole-genome sequencing

Keywords: mtDNA; mitochondrial DNA; BACs; bacterial artificial chromosomes; SNPs; single-nucleotide polymorphisms; indels; insertions and deletions; UTRs; untranslated regions; PCR; polymerase chain reaction; nsSNPs; non-synonymous SNPs; GO; gene ontology; QTL; qua

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2013 سفارش ترجمه

Influenza A virus (H1N1) increases airway epithelial cell secretion by up-regulation of potassium channel KCNN4

Keywords: Ion channels; Airway epithelium; Influenza; CFTR; KCNN4;

دانلود رایگان متن کامل مقاله ISI 7 صفحه سال انتشار : 2013 سفارش ترجمه

Corrector VX-809 stabilizes the first transmembrane domain of CFTR

Keywords: CFTR; Cystic fibrosis; Corrector; VX-809; P-glycoprotein; Transmembrane domain; Arginine mutagenesis; Processing mutations;

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2013 سفارش ترجمه

Effect of VX-770 (Ivacaftor) and OAG on Ca2 + influx and CFTR activity in G551D and F508del-CFTR expressing cells

Keywords: Cystic fibrosis; Calcium signaling; CFTR; TRPC6; G551D-CFTR; VX-770; OAG;

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2013 سفارش ترجمه

Left ventricular and aortic dysfunction in cystic fibrosis mice

Keywords: CFTR; Cystic fibrosis; Left ventricular function; Aorta;

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2013 سفارش ترجمه

COMMD1 modulates noxious inflammation in cystic fibrosis

Keywords: COMMD1; CFTR; NF-kappaB; IL-8; Inflammation;

دانلود رایگان متن کامل مقاله ISI 8 صفحه سال انتشار : 2013 سفارش ترجمه

CFTR: Effect of ICL2 and ICL4 amino acids in close spatial proximity on the current properties of the channel

Keywords: CFTR; ICL; Structure-function; Channel gating; ABC transporter;

دانلود رایگان متن کامل مقاله ISI 9 صفحه سال انتشار : 2013 سفارش ترجمه