Keywords: فیبروز کبدی مادرزادی; RDC; reactive ductular cell; DAMPs; danger associated molecular patterns; PAMPs; pathogen associated molecular patterns; cAMP; cyclic adenosine monophosphate; NOS; nitric oxide synthase; RNOS; reactive nitrogen oxide species; CFTR; cystic fibrosis transme
مقالات ISI فیبروز کبدی مادرزادی (ترجمه نشده)
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در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: فیبروز کبدی مادرزادی; JSRD; Joubert syndrome and related disorders; PH; portal hypertension; RC sing; red color sign; CT; computed tomography; RV; reference value; CHF; congenital hepatic fibrosis; EVL; endoscopic variceal ligation; EIS; endoscopic injection sclerotherapy; PSE
Keywords: فیبروز کبدی مادرزادی; HTx; hepatocyte transplant; OLT; orthotopic liver transplantation; CYP; cytochrome P450; DLT; domino liver transplantation; OD; organ donor; MD; metabolic and diseased livers; MMA; methylmalonic acidemia; PHO; primary hyperoxaluria; MSUD; Maple Syrup Urin
Choroby wÄ
troby i nerek w przebiegu ciliopatii
Keywords: فیبروز کبدی مادرزادی; ciliopatie; rzÄski pierwotne; wrodzone wÅóknienie wÄ
troby; choroba Caroliego; wielotorbielowata choroba wÄ
troby; autosomalnie recesywna wielotorbielowatoÅÄ nerek; autosomalnie dominujÄ
ca wielotorbielowatoÅÄ nerek; nefronoftyza; Ciliopathies; Pri
B-type natriuretic peptide overexpression ameliorates hepatorenal fibrocystic disease in a rat model of polycystic kidney disease
Keywords: فیبروز کبدی مادرزادی; adeno-associated virus; ADPKD; ARPKD; congenital hepatic fibrosis; gene therapy;
Choroba czy zespóÅ Caroliego? Od zaburzeÅ embriogenezy do przeszczepienia wÄ
troby
Keywords: فیبروز کبدی مادرزادی; wewnÄ
trzwÄ
trobowe drogi żóÅciowe; wrodzone wÅóknienie wÄ
troby; zapalenie dróg żóÅciowych; Intrahepatic bile ducts; Congenital hepatic fibrosis; Cholangitis;
Mutations in DCDC2 (doublecortin domain containing protein 2) in neonatal sclerosing cholangitis
Keywords: فیبروز کبدی مادرزادی; ADPKD; autosomal dominant polycystic kidney disease; ARPKD; autosomal recessive polycystic kidney disease; ACALT; acetylated alpha-tubulin; BA; biliary atresia; Ca2+; calcium; CHF; congenital hepatic fibrosis; DCDC2; doublecortin domain containing protein
Consensus Expert Recommendations for the Diagnosis and Management of Autosomal Recessive Polycystic Kidney Disease: Report of an International Conference
Keywords: فیبروز کبدی مادرزادی; ADPKD; Autosomal-dominant polycystic kidney disease; ARPKD; Autosomal-recessive polycystic kidney disease; CHF; Congenital hepatic fibrosis; CKD; Chronic kidney disease; CMV; Cytomegalovirus; GA; Gestational age; HNF1B; Hepatocyte nuclear factor-1beta; HT
ReviewNon-cirrhotic portal hypertension - Diagnosis and management
Keywords: فیبروز کبدی مادرزادی; APASL; Asia Pacific Association for the Study of the Liver; CHF; congenital hepatic fibrosis; CSRS, PSRS, DSRS; central, proximal, and distal splenorenal shunt; EHPVO; extrahepatic portal venous obstruction; ERCP; endoscopic retrograde cholangiopancreatog
Characteristics of Congenital Hepatic Fibrosis in a Large Cohort of Patients With Autosomal Recessive Polycystic Kidney Disease
Keywords: فیبروز کبدی مادرزادی; Ductal Plate Malformation; Noncirrhotic Portal Hypertension; Genetics; Hepatorenal Fibrocystic Disease; APRI; aspartate aminotransferase to platelet ratio index; ARPKD; autosomal recessive polycystic kidney disease; CBD; common bile duct; CHF; congenital
Ciliopathies: The Central Role of Cilia in a Spectrum of Pediatric Disorders
Keywords: فیبروز کبدی مادرزادی; ARPKD; Autosomal recessive polycystic kidney disease; BBS; Bardet-Biedl syndrome; CHD; Congenital heart disease; CHF; Congenital hepatic fibrosis; CNS; Central nervous system; PCD; Primary ciliary dyskinesia; RP; Retinitis pigmentosa; SI; Situs inversus t
Enfermedades fibropoliquísticas congénitas hepáticas
Keywords: فیبروز کبدی مادرزادی; Malformación de la placa ductal; Fibrosis hepática congénita; Quiste de colédoco; Poliquistosis hepatorrenal; Enfermedad de Caroli; Enfermedad fibropoliquística hepáticaDuctal plate malformation; Congenital hepatic fibrosis; Choledoch cysts; Hepatorenal p
Hepatorenal findings in obligate heterozygotes for autosomal recessive polycystic kidney disease
Keywords: فیبروز کبدی مادرزادی; Autosomal recessive polycystic kidney disease; Congenital hepatic fibrosis; PKHD1; Polycytsic liver disease; Nephrocalcinosis; Medullary sponge kidney;
Polycystic Liver Diseases: Congenital Disorders of Cholangiocyte Signaling
Keywords: فیبروز کبدی مادرزادی; AC; adenyl cyclase; AC6; adenylyl-cyclases-6; ADPKD; autosomal-dominant polycystic kidney disease; AKT; v-akt murine thymoma viral oncogene homolog 1; ARPKD; autosomal-recessive polycystic kidney disease; cAMP; cycle adenosine monophosphate; CD; Caroli di
The Spectrum of Polycystic Kidney Disease in Children
Keywords: فیبروز کبدی مادرزادی; Polycystic kidney disease; Pediatric; Genetic; Renal cysts; Congenital hepatic fibrosis;
Poliquistosis renal infantil autosómica recesiva con disgenesia biliar. A propósito de un caso
Keywords: فیبروز کبدی مادرزادی; Poliquistosis renal autosómica recesiva; Quistes renales; Fibrosis hepática congénitaAutosomal recessive polycystic kidney disease; Renal cysts; Congenital hepatic fibrosis
Genotype–phenotype correlations in fetuses and neonates with autosomal recessive polycystic kidney disease
Keywords: فیبروز کبدی مادرزادی; autosomal recessive polycystic kidney disease; congenital hepatic fibrosis; foetopathology; PKHD1; prenatal diagnosis
PKHD1 sequence variations in 78 children and adults with autosomal recessive polycystic kidney disease and congenital hepatic fibrosis
Keywords: فیبروز کبدی مادرزادی; PKHD1; Autosomal recessive polycystic kidney disease; Congenital hepatic fibrosis; DNA sequencing; Missense variant; Pathogenicity prediction
MKS3-Related Ciliopathy with Features of Autosomal Recessive Polycystic Kidney Disease, Nephronophthisis, and Joubert Syndrome
Keywords: فیبروز کبدی مادرزادی; ARPKD; Autosomal recessive polycystic kidney disease; CHF; Congenital hepatic fibrosis; CNS; Central nervous system; JSRD; Joubert syndrome and related disorders; MKS; Meckel syndrome; MTS; Molar tooth sign; OMA; Oculomotor apraxia;
Imaging findings in congenital hepatic fibrosis
Keywords: فیبروز کبدی مادرزادی; Congenital hepatic fibrosis; Imaging findings; Non-invasive diagnosis
Ductal plate malformation and congenital hepatic fibrosis
Keywords: فیبروز کبدی مادرزادی; Congenital hepatic fibrosis; Fibrocystic diseases of the liver; Ductal plate malformation; Distal splenorenal shunting; Endoscopic variceal ligation; Portal hypertension;
Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis: Summary statement of a First National Institutes of Health/Office of Rare Diseases conference
Keywords: فیبروز کبدی مادرزادی; ACE; Angiotensin converting enzyme; ADPKD; Autosomal dominant polycystic kidney disease; ARB; Angiotensin II receptor blocker; ARPKD/CHF; Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis; cAMP; Cyclic adenosine monophosphate;
Autosomal-recessive polycystic kidney disease
Keywords: فیبروز کبدی مادرزادی; end-stage renal disease; congenital hepatic fibrosis; Bardet-Biedel syndrome; nephronophthisis;