Keywords: بیماری Creutzfeldt-Jakob; Blood transfusions; Creutzfeldt-Jakob disease; endoscopes; prion disease; transmissible spongioform encephalopathies;
مقالات ISI بیماری Creutzfeldt-Jakob (ترجمه نشده)
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Keywords: بیماری Creutzfeldt-Jakob; Diagnostic validity; Incorporation bias; Partial verification bias; Creutzfeldt-Jakob disease; 14-3-3; Autopsy;
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Lipid profiles; Serum; Uric acid; Neurodegenerative disease;
Keywords: بیماری Creutzfeldt-Jakob; EEG; electroencephalogram; sCJD; sporadic Creutzfeldt-Jakob disease; PSWC; periodic sharp-wave complex; Creutzfeldt-Jakob disease; Akinetic mutism state; Total disease duration; Tube feeding; Gastrostomy; Tracheotomy;
Keywords: بیماری Creutzfeldt-Jakob; Rapidly progressive dementia; Young onset dementia; Early onset dementia; Presenile dementia; Neuropsychiatry; Prion disease; Creutzfeldt-Jakob disease; Neuropsychiatric symptoms;
Keywords: بیماری Creutzfeldt-Jakob; AA; ascorbic acid; BSE; Bovine spongiform encephalopathies; B3LYP; Becke 3 parameter Lee Yang Parr; BP86; Becke Perdew86; CD; Circular dichroism; CJD; Creutzfeldt-Jakob disease; CPMD; Car-Parrinello molecular dynamics; DFT; Density functional theory;
Non-cell-autonomous actions of α-synuclein: Implications in glial synucleinopathies
Keywords: بیماری Creutzfeldt-Jakob; Astrocyte; Microglia; Neurodegeneration; Neuroinflammation; Parkinson disease; Protein aggregation; Multiple system atrophy; AD; Alzheimer disease; CJD; Creutzfeldt-Jakob disease; CNP; 3â²-cyclic nucleotide 3â²-phosphodiesterase; CSF; cerebrospinal fl
The Heidenhain variant of Creutzfeldt-Jakob disease and concomitant tau pathology: A case report
Keywords: بیماری Creutzfeldt-Jakob; Prion; Creutzfeldt-Jakob disease; Visuospatial dysfunction; Heidenhain variant;
l-Arginine ethylester enhances in vitro amplification of PrPSc in macaques with atypical L-type bovine spongiform encephalopathy and enables presymptomatic detection of PrPSc in the bodily fluids
Keywords: بیماری Creutzfeldt-Jakob; Atypical bovine spongiform encephalopathy; Protein misfolding cyclic amplification; Arginine ethylester; Bodily fluid; Nonhuman primate; PrPSc; Pathogenic form of prion protein; PrPC; cellular prion protein; CJD; Creutzfeldt-Jakob disease; BSE; Bovine s
Polo-like kinase 3 (PLK3) mediates the clearance of the accumulated PrP mutants transiently expressed in cultured cells and pathogenic PrPSc in prion infected cell line via protein interaction
Keywords: بیماری Creutzfeldt-Jakob; PLKs; polo-like kinases; KD; kinase domain; PBD; polo-box domain; TSE; transmissible spongiform encephalopathies; CJD; Creutzfeldt-Jakob disease; GSS; Gerstmann-Straüssler-Scheinker; FFI; fatal familial insomnia; BSE; bovine spongiform encephalopat
Relation between clinical findings and progression of cerebral cortical pathology in MM1-type sporadic Creutzfeldt-Jakob disease: Proposed staging of cerebral cortical pathology
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Spongiform change; Hypertrophic astrocytosis; Neuropil rarefaction; Neuron loss;
Clinical and familial characteristics of eight Chinese patients with T188K genetic Creutzfeldt-Jakob disease
Keywords: بیماری Creutzfeldt-Jakob; Genetic CJD; T188K; PRNP; Creutzfeldt-Jakob disease; Surveillance;
Molecular cloning and sequence analysis of prion protein gene in Xiji donkey in China
Keywords: بیماری Creutzfeldt-Jakob; TSEs; transmissible spongiform encephalopathies; CJD; Creutzfeldt-Jakob disease; vCJD; variant Creutzfeldt-Jakob diseases; BSE; bovine spongiform encephalopathy; CWD; chronic wasting disease; FME; feline spongiform encephalopathy; TME; mink spongiform
Dysregulation of brain olfactory and taste receptors in AD, PSP and CJD, and AD-related model
Keywords: بیماری Creutzfeldt-Jakob; AD; Alzheimer's disease; ADYLC3; adenylyl cyclase 3; ATP; adenosine triphosphate; cAMP; cyclic adenosine monophosphate; CJD; Creutzfeldt-Jakob disease; CNG; cyclic nucleotide-gated; Gnal; olfactory G protein; GUS-β; β-glucuronidase; HSD; Honestly Si
Antibodies to N-methyl-D-aspartate glutamate receptors in Creutzfeldt-Jakob disease patients
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; N-methyl-D-aspartate glutamate receptors; Autoantibodies;
Molecular cloning and polymorphism analysis of the prion protein gene in Tan sheep of Ningxia, China
Keywords: بیماری Creutzfeldt-Jakob; TSE; transmissible spongiform encephalopathies; CJD; Creutzfeldt-Jakob disease; BSE; bovine spongiform encephalopathy; PrP; prion protein; PrPc; cellular prion protein; PRNP; prion protein gene; SNPs; single nucleotide polymorphisms; ARQ; A136R154Q171;
Synthesis of 9-substituted 2,3,4,9-tetrahydro-1H-carbazole derivatives and evaluation of their anti-prion activity in TSE-infected cells
Keywords: بیماری Creutzfeldt-Jakob; Prion diseases; Transmissible spongiform encephalopathies; Anti-prion compound; 2,3,4,9-Tetrahydro-1H-carbazole; Ring-opening reaction; Structure-activity relationships; TSEs; transmissible spongiform encephalopathies; CJD; Creutzfeldt-Jakob disease;
Main étrangère révélatrice d'une maladie de Creutzfeldt-Jakob
Keywords: بیماری Creutzfeldt-Jakob; Maladie de Creutzfeldt-Jakob; Main étrangère; Apraxie diagnostique; Creutzfeldt-Jakob disease; Alien hand; Diagnostic apraxia;
Elevated Levels of Tau Protein in Cerebrospinal Fluid of Patients With Probable Creutzfeldt-Jakob Disease
Keywords: بیماری Creutzfeldt-Jakob; Cerebrospinal fluid; Creutzfeldt-Jakob disease; ELISA; Tau; 14-3-3;
Clinical diagnosis of Creutzfeldt-Jakob disease: Accuracy based on analysis of autopsy-confirmed cases
Keywords: بیماری Creutzfeldt-Jakob; Cerebrospinal fluid; Clinical diagnosis; Creutzfeldt-Jakob disease; Diagnostic criteria; Magnetic resonance imaging; Myoclonus; Periodic sharp-wave complexes;
Champ 2- diagnostics différentiels des états de mal épileptiques
Keywords: بیماری Creutzfeldt-Jakob; Ãtat de mal épileptique; Pseudocrises; Myoclonies; Encéphalopathie; Coma postanoxique; Maladie de Creutzfeldt-Jakob; Ãlectroencéphalogramme; Status epilepticus; Pseudo-seizures; Myoclonus; Encephalopathy; Postanoxic coma; Creutzfeldt-Jakob disease;
Anti-PrP Mab 6D11 suppresses PrPSc replication in prion infected myeloid precursor line FDC-P1/22L and in the lymphoreticular system in vivo
Keywords: بیماری Creutzfeldt-Jakob; Monoclonal antibodies; Scrapie; Neuroinvasion; Prion; Treatment; Creutzfeldt-Jakob disease;
The ubiquitin-proteasome system in spongiform degenerative disorders
Keywords: بیماری Creutzfeldt-Jakob; AD; Alzheimer's disease; AgRP; Agouti related protein; AIDS; acquired immune deficiency syndrome; APP; amyloid precursor protein; ASPA; aspartoacylase gene; Atrn; attractin; BSE; bovine spongiform encephalopathy; CD; Canavan's spongiform leukodystroph
Developmental expression of PrP in the post-implantation embryo
Keywords: بیماری Creutzfeldt-Jakob; Prnp; gene encoding the prion protein; PrP; prion protein; PrPC; normal, cellular prion protein; SHa; Syrian hamster; Tg; transgenic; Mo; mouse; CJD; Creutzfeldt-Jakob disease; Prion; Prnp; Expression regulation; Transgenic mice; β-galactosidase;
Two-dimensional Protein Electrophoresis: From Molecular Pathway Discovery to Biomarker Discovery in Neurological Disorders
Keywords: بیماری Creutzfeldt-Jakob; Proteomics; two-dimensional electrophoresis; neurological disorders; Alzheimer's disease; Creutzfeldt-Jakob disease; biomarkers;
Periodic motor cortical excitability changes associated with PSDs of EEG in Creutzfeldt-Jakob disease (CJD)
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Periodic synchronous discharges; Transcranial magnetic stimulation; Motor cortex excitability;
Diffusion-weighted MRI in familial Creutzfeldt-Jakob disease with the codon 200 mutation in the prion protein gene
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Diagnostic methods; Diffusion-weighted imaging; Familial; Magnetic resonance imaging; Prion disease; Prion gene mutation;
Safe method for isolation of prion protein and diagnosis of Creutzfeldt-Jakob disease
Keywords: بیماری Creutzfeldt-Jakob; Prion; Creutzfeldt-Jakob disease; Guanidine; Western blot;
Extended period of asymptomatic prion disease after low dose inoculation: Assessment of detection methods and implications for infection control
Keywords: بیماری Creutzfeldt-Jakob; Prions; Creutzfeldt-Jakob disease; Asymptomatic infection; Preclinical infection; Subclinical infection; Transmissible spongiform encephalopathy; Detection methods;
Expression of PrPC in the rat brain and characterization of a subset of cortical neurons
Keywords: بیماری Creutzfeldt-Jakob; Disorders of the nervous system; Degenerative disease (other); A; anterior complex of the thalamus; CB; calbindin; CBP; calcium-binding proteins; CJD; Creutzfeldt-Jakob disease; CR; calretinin; FFI; fatal familial insomnia; MD; mediodorsal thalamic nucl
Quantifying the parameters of Prusiner's heterodimer model for prion replication
Keywords: بیماری Creutzfeldt-Jakob; 87.10.+e; 87.15.Rn; 87.15.Aa; Prion kinetics; 2D lattice model; Heterodimer model; Creutzfeldt-Jakob disease;
Copper, oxidative stress, and human health
Keywords: بیماری Creutzfeldt-Jakob; Aβ; amyloid-β; AD; Alzheimer's disease; AGE; advanced glycosylated end products; ALS; amyotrophic lateral sclerosis; APP; amyloid precursor protein; BH4; tetrahydrobiopterin; CJD; Creutzfeldt-Jakob disease; eNOS; endothelial nitric oxide synthase; I