Keywords: دیستروگلیکان; Dystroglycan; Axon; Optic chiasm; Retina; Basement membrane; Extracellular matrix;
مقالات ISI دیستروگلیکان (ترجمه نشده)
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Keywords: دیستروگلیکان; Dystrophin; Dystrophin–glycoprotein complex; Dystroglycan; Metalloproteinase; Gelatinase; Duchenne muscular dystrophy
Keywords: دیستروگلیکان; Duchenne muscular dystrophy; Dystrophin; Sarcoglycan; limb-girdle muscular dystrophy; Dysferlin; Dystroglycan;
Keywords: دیستروگلیکان; Adhesome; Dystroglycan; Extracellular matrices; Development;
Keywords: دیستروگلیکان; ECM; extracellular matrix; Fn; Fibronectin; BM; basement membrane; DGC; Dystrophin-glycoprotein complex; UGC; Utrophin-glycoprotein complex; NMJ; Neuromuscular junction; MTJ; myotendinous junction; HSPG; heparin sulfate proteoglycan; EMT; epithelial to me
Keywords: دیستروگلیکان; Dp; Dystrophin; DMD; Duchenne Muscular Dystrophy; DAPC; Dystrophin Associated Protein Complex; DG; Dystroglycan; MDDGC9; Muscular Dystrophy, Dystroglycanopathy, Type C9; OMIM; Online Mendelian Inheritance in Man; ABD; Actin Binding Domain; SpR; Spectrin R
Keywords: دیستروگلیکان; Laminin; Dystroglycan; Dystrophin; Integrin; Zebrafish;
Keywords: دیستروگلیکان; Astrocyte; Dystroglycan; Water transport; Homeostasis; Edema; Adhesion; Extracellular matrix; Ischemia; Oxygen/glucose deprivation;
Distrofias musculares congénitas
Keywords: دیستروگلیکان; Distrofia muscular; merosina; colágeno VI; SEPN1; LMNA; distroglicano; algoritmo diagnóstico; Muscular dystrophy; merosin; collagen VI; SEPN1; Lamin A/C; Dystroglycan; diagnostic guideline.;
β-dystroglycan is regulated by a balance between WWP1-mediated degradation and protection from WWP1 by dystrophin and utrophin
Keywords: دیستروگلیکان; WWP1; Dystroglycan; E3 ligase; Ubiquitination; Muscular dystrophy; Protein degradation;
Walker-Warburg syndrome and tectocerebellar dysraphia: A novel association caused by a homozygous DAG1 mutation
Keywords: دیستروگلیکان; Cobblestone malformation complex; Dystroglycan; DAG1; Walker-Warburg syndrome; Tectocerebellar dysraphia; WWS; Walker-Warburg Syndrome; DG; dystroglycan; TCD; tectocerebellar dysraphia; COB; cobblestone malformation; SWI; susceptibility weighted imaging;
Limb girdle muscular dystrophy type 2I: No correlation between clinical severity, histopathology and glycosylated α-dystroglycan levels in patients homozygous for common FKRP mutation
Keywords: دیستروگلیکان; Limb girdle muscular dystrophy; FKRP; Dystroglycan; Laminin α2;
Laminin is instructive and calmodulin dependent kinase II is non-permissive for the formation of complex aggregates of acetylcholine receptors on myotubes in culture
Keywords: دیستروگلیکان; Synapse formation; Laminin; MuSK; Electrical activity; Dystroglycan; Integrin; CaMKII;
α-Dystroglycan hypoglycosylation affects cell migration by influencing β-dystroglycan membrane clustering and filopodia length: A multiscale confocal microscopy analysis
Keywords: دیستروگلیکان; FRAP; fluorescence recovery after photobleaching; DG; Dystroglycan; ERK; extracellular-signal-related kinase; MAPK; mitogen-activated protein kinase; LARGE; acetylglucosaminyltransferase-like; ECM; extracellular matrix; GFP; Green Fluorescent protein; ICQ
Gallus gallus orthologous to human alpha-dystroglycanopathies candidate genes: Gene expression and characterization during chicken embryogenesis
Keywords: دیستروگلیکان; POMT1; Dystroglycanopathies; Chicken; Walker-Warburg syndrome; CMD; Congenital muscular dystrophy; DG; dystroglycan; DGC; Dystrophin-binding glycoprotein complex; FCMD; Fukuyama's Disease; Gg; Gallus gallus; Hs; Homo sapiens; LGMD; Limb-Girdle Muscular Dy
β-Dystroglycan cleavage by matrix metalloproteinase-2/-9 disturbs aquaporin-4 polarization and influences brain edema in acute cerebral ischemia
Keywords: دیستروگلیکان; Ang II; Angiotensin II; ANOVA; analysis of variance; AQP4; aquaporin-4; BBB; blood-brain barrier; BM; basement membrane; BP; blood pressure; DG; dystroglycan; DGC; dystrophin glycoprotein complex; HE; hematoxylin-eosin; ICA; internal carotid artery; M
α-dystroglycan is a potential target of matrix metalloproteinase MMP-2
Keywords: دیستروگلیکان; Dystroglycan; MMP-2; Metalloproteinase
Small molecules enhance functional O-mannosylation of Alpha-dystroglycan
Keywords: دیستروگلیکان; Dystroglycan; Dystroglycanopathy; O-Mannosylation; Cell-based high-throughput screening;
A new monoclonal antibody DAG-6F4 against human alpha-dystroglycan reveals reduced core protein in some, but not all, dystroglycanopathy patients
Keywords: دیستروگلیکان; aDG; alpha dystroglycan; DGC; dystrophin-glycoprotein complex; DAG; dystroglycan; LGMD2I; limb-girdle muscular dystrophy type 2I; FKRP; fukutin-related protein; MDC1C; congenital muscular dystrophy type 1C; WGA; wheat germ agglutinin; HRP; horseradish per
Upregulation and lysosomal degradation of AQP4 in rat brains with bacterial meningitis
Keywords: دیستروگلیکان; Aquaporin-4; Dystroglycan; Bacterial meningitis; Lysosome;
Dystroglycan depletion inhibits the functions of differentiated HL-60 cells
Keywords: دیستروگلیکان; Dystroglycan; HL-60 cells; Differentiation; Phagocytosis; Respiratory burst activity; Migration
Hypoglycosylation of dystroglycan due to T192M mutation: A molecular insight behind the fact
Keywords: دیستروگلیکان; MD; muscular dystrophy; DG; dystroglycan; MDDGC9; muscular dystrophy dystroglycanopathy of limb girdle, type C; OMIM; online mendelian inheritance in man; α-DG; alpha dystroglycan; β-DG; beta dystroglycan; DGC; dystrophin dystroglycan complex; ECM; extr
The PDZ-Containing Unconventional Myosin XVIIIA Regulates Embryonic Muscle Integrity in Zebrafish
Keywords: دیستروگلیکان; Myosin XVIIIA; MYO18A; Unconventional myosin; Myofiber; Muscle; Dystrophin; Dystroglycan; ZebrafishCoMO, control MO; DAPC, dystrophin-associated protein complex; DAPI, 4′,6′-diamidino-2-phenylindole dilactate; DG, dystroglycan; ECM, extracellular matrix;
Research ReportGenetic and pharmacological manipulations that alter metabolism suppress seizure-like activity in Drosophila
Keywords: دیستروگلیکان; SLA; Seizure-like activity; BS; Bang-sensitive; CS; Canton-S; EAS; Easily-shocked; BSS; Bang-senseless; TKO; Technical-knockout; Seizure; Epilepsy; Metabolism; Dystroglycan; Tolbutamide; Drosophila;
The bHLH transcription factor hand is required for proper wing heart formation in Drosophila
Keywords: دیستروگلیکان; Adult myogenesis; Muscle attachment; Wing maturation; Spectrin; Armadillo; Dystroglycan;
Mechanism of podocyte detachment: Targeting transmembrane molecules between podocytes and glomerular basement membrane
Keywords: دیستروگلیکان; Podocytes; Integrin α3β1; ILK; CD151; Dystroglycan; Detachment; Adhesion
Detection of the dystroglycanopathy protein, fukutin, using a new panel of site-specific monoclonal antibodies
Keywords: دیستروگلیکان; Fukutin; Fukuyama muscular dystrophy; Monoclonal antibody; Dystroglycan; Dystroglycanopathy; Golgi; Phage-displayed peptide library; Epitope mapping
DAG1, no gene for RNA regulation?
Keywords: دیستروگلیکان; Dystroglycan; Large introns; Transcription; Splicing; Nucleus Escape; Post-translational modifications
The inside and out of dystroglycan post-translational modification
Keywords: دیستروگلیکان; Dystroglycan; Glycosylation; Dystroglycanopathy; Laminin; Signalling; Adhesion;
The dystrophin–glycoprotein complex in brain development and disease
Keywords: دیستروگلیکان; muscular dystrophy; dystrophin; dystroglycan; cognitive impairment; neuronal migration; dystonia.
Dystroglycan is associated to the disulfide isomerase ERp57
Keywords: دیستروگلیکان; DG; dystroglycan; pre-DG; dystroglycan precursor; NEM; N-ethylmaleimide; DTT; dithiothreitol; sWGL; succinylated wheat germ lectin; Dystroglycan; ERp57; Immunoprecipitation; Fluorescence microscopy; Solid-phase binding assay;
The role of cell-extracellular matrix interactions in glomerular injury
Keywords: دیستروگلیکان; Integrins; Collagen; Laminin; Glomerulus; Discoidin domain receptor; Fibrosis; Growth factors; Dystroglycan;
Secretion of N-terminal domain of α-dystroglycan in cerebrospinal fluid
Keywords: دیستروگلیکان; DG; dystroglycan; α-DG-N; N-terminal domain of α-dystroglycan; CSF; cerebrospinal fluid; PC; proprotein convertase; Dystroglycan; Muscular dystrophy; Cerebrospinal fluid; Processing of protein; Proprotein convertase; Glycosylation;
The N-terminal domain of α-dystroglycan, released as a 38 kDa protein, is increased in cerebrospinal fluid in patients with Lyme neuroborreliosis
Keywords: دیستروگلیکان; Dystroglycan; Proteolytic processing; Body fluids; Central nervous system; Neuroborreliosis
Pikachurin interaction with dystroglycan is diminished by defective O-mannosyl glycosylation in congenital muscular dystrophy models and rescued by LARGE overexpression
Keywords: دیستروگلیکان; Retina; Ribbon synapse; Dystroglycan; Pikachurin; Congenital muscular dystrophy; Protein glycosylation;
Defective glycosylation of α-dystroglycan contributes to podocyte flattening
Keywords: دیستروگلیکان; adhesion molecule; dystroglycan; foot process; glycosylation; podocyte
Reduced α-Dystroglycan Expression Correlates with Shortened Patient Survival in Pancreatic Cancer
Keywords: دیستروگلیکان; pancreatic cancer; dystroglycan; DAG1; survival
A second Ig-like domain identified in dystroglycan by molecular modelling and dynamics
Keywords: دیستروگلیکان; Dystroglycan; Ig-like fold; Protein modelling; Molecular dynamics; Dystroglycanopathies
Reactive gliosis of astrocytes and Müller glial cells in retina of POMGnT1-deficient mice
Keywords: دیستروگلیکان; Muscle-eye-brain disease; Dystroglycan; Retinal detachment;
Stress and muscular dystrophy: A genetic screen for Dystroglycan and Dystrophin interactors in Drosophila identifies cellular stress response components
Keywords: دیستروگلیکان; Muscular dystrophy; Stress; Drosophila; Dystrophin; Dystroglycan; Genetic screen;
MMP-mediated cleavage of β-dystroglycan in myelin sheath is involved in autoimmune neuritis
Keywords: دیستروگلیکان; Dystroglycan; Demyelination; Autoimmune neuritis; Matrix metalloproteinases; CaptoprilDG, dystroglycan; EAN, experimental autoimmune neuritis; MMP, matrix metalloproteinase; PNS, peripheral nerve system; PMSF, phenylmethanesulfonyl fluoride; SDS–PAGE, sod
Fukutin mutations in congenital muscular dystrophies with defective glycosylation of dystroglycan in Korea
Keywords: دیستروگلیکان; Muscular dystrophy; Congenital; Mutation; Dystroglycan
Protein O-mannosylation in animal development and physiology: From human disorders to Drosophila phenotypes
Keywords: دیستروگلیکان; Protein O-mannosylation; Dystroglycan; Dystroglycanopathy; Muscular dystrophy; Drosophila glycosylation
From glycosylation disorders back to glycosylation: What have we learned?
Keywords: دیستروگلیکان; Dystroglycan; Mucin O-glycosylation; Oligosaccharyltransferase; Glucosyltransferase; COG complex; CMP-sialic acid
Receptor binding and cell entry of Old World arenaviruses reveal novel aspects of virus–host interaction
Keywords: دیستروگلیکان; LCMV, lymphocytic choriomeningitis virus; LASV, Lassa virus; DG, dystroglycan; ECM, extracellular matrixArenavirus; Receptor; Dystroglycan; Virus entry
Functional diversity of dystroglycan
Keywords: دیستروگلیکان; Dystroglycan; Glycosylation; Muscular dystrophy; Biomarker; Signalling; Nucleus
Aberrant development of neuromuscular junctions in glycosylation-defective Largemyd mice
Keywords: دیستروگلیکان; Glycosylation; Neuromuscular junction; Skeletal muscle; Dystroglycan;
The synaptic CT carbohydrate modulates binding and expression of extracellular matrix proteins in skeletal muscle: Partial dependence on utrophin
Keywords: دیستروگلیکان; Dystroglycan; Laminin; Neuromuscular junction; Synapse; Neuregulin; Utrophin; Glycosylation; Agrin; Integrin; Muscular dystrophy; Muscle
Dynamic Regulation of alpha-Dystroglycan in Mouse Placenta
Keywords: دیستروگلیکان; Placenta; Dystroglycan
Aberrant expression of β-dystroglycan may be due to processing by matrix metalloproteinases-2 and -9 in oral squamous cell carcinoma
Keywords: دیستروگلیکان; Oral squamous cell carcinoma; Dystroglycan; Metastasis; Matrix metalloproteinase