Keywords: همسایه; Wilson disease; Hereditary hemochromatosis; Genetic mutation; Biological function; Genotypes and phenotypes; WD; Wilson disease; HH; Hereditary hemochromatosis; TGN; trans-Golgi network; ATP7B; ATPase; Cu + transporting; beta polypeptide; HFE; hemochrom
مقالات ISI همسایه (ترجمه نشده)
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Keywords: همسایه; Stroke; hepcidin; hemojuvelin; heparin;
Keywords: همسایه; β2M; beta 2-microglobulin; aa; amino acid; ACD; anemia of chronic diseases; BMP; bone morphogenetic protein; BMPR; bone morphogenetic protein receptor; CD; cluster of differentiation; Cp; ceruloplasmin; DcytB; duodenal cytochrome b; Dmt1; proton-coupled
Keywords: همسایه; ANOVA; analysis of variance; DHT; dihydrotestosterone; E; estrogen; GAPDH; glyceraldehyde-3-phosphate dehydrogenase; Hamp1; hepcidin antimicrobial peptide 1; HFE; hemochromatosis; HJV; hemojuvelin; KO; knockout; LPI; labile plasma iron; mRNA; messenger RN
Erythropoietin administration increases splenic erythroferrone protein content and liver TMPRSS6 protein content in rats
Keywords: همسایه; Hepcidin; Hemojuvelin; TMPRSS6; Fam132b; Fam132a;
Contiguous gene deletion in HFE2 region (1q21.1) and pathogenic HFE2 mutations in a Chinese hereditary hemochromatosis patient
Keywords: همسایه; HH; Hereditary hemochromatosis; HFE; hemochromatosis; HJV; hemojuvelin; HFE2; hemochromatosis type 2; HAMP; hepcidin; TfR2; transferrin receptor 2; TS; transferrin saturation; SI; serum iron; SF; serum ferritin; TF; transferrin; HGB; hemoglobin; RET; reti
Homocysteine upregulates hepcidin expression through BMP6/SMAD signaling pathway in hepatocytes
Keywords: همسایه; Hyperhomocysteinemia; Homocysteine; Hepcidin; BMP6/SMAD; Hepatocytes; ALK2; activin receptor-like kinase 2; ALK3; activin receptor-like kinase 3; ALK6; activin receptor-like kinase 6; BMP4; bone morphogenetic protein 4; BMP6; bone morphogenetic protein 6;
The dietary flavonoid myricetin regulates iron homeostasis by suppressing hepcidin expression
Keywords: همسایه; AI; anemia of inflammation; BMP; bone morphogenetic protein; ERK; extracellular signal-regulated kinase; ESAs; erythropoiesis-stimulating agents; HAMP; hepcidin antimicrobial peptide; HJV; hemojuvelin; IL-6; interleukin-6; JAK; Janus kinase; LPS; lipopoly
Research ArticleIron overload in hereditary tyrosinemia type 1 induces liver injury through the Sp1/Tfr2/hepcidin axis
Keywords: همسایه; HTI; hereditary tyrosinemia type I; Fah; fumarylacetoacetate hydrolase; Tfr2; transferrin receptor 2; HH; hereditary hemochromatosis; Hjv; hemojuvelin; NTBC; 2-(2-nitro-4-trifluoromethylbe -nzoyl)-1,3-cyclohexanedione; Fpn; ferroportin; Tfr1; transferrin
ReviewIron metabolism and related genetic diseases: A cleared land, keeping mysteries
Keywords: همسایه; Iron; Transferrin; Ferritin; Hepcidin; Ceruloplasmin; Ferroportin; Erythroferrone; Non-transferrin bound iron; Hemojuvelin; Transferrin receptor; Haemochromatosis; Liver;
Decrease in APP and CP mRNA expression supports impairment of iron export in Alzheimer's disease patients
Keywords: همسایه; ACO1; acotinase 1; AD; Alzheimer's disease; ANCOVA; univariate analysis of co-variance; APP; amyloid-beta precursor protein; Aβ; amyloid-beta; CDR; Clinical Dementia Rating; Cp; ceruloplasmin; CPO; Cp oxidase activity; eQTLs; expression quantitative trai
Diagnostic Evaluation of Hereditary Hemochromatosis (HFE and Non-HFE)
Keywords: همسایه; Hemochromatosis; Hepcidin; HFE; TFR2; Hemojuvelin; Ferroportin; Phlebotomy;
Dietary fat level affects tissue iron levels but not the iron regulatory gene HAMP in rats
Keywords: همسایه; DMT1; divalent metal transporter 1; C/EBPα; CCAAT/enhancer binding protein α; FPN; ferroportin; HAMP; human antimicrobial peptide; Hb; hemoglobin; Hct; hematocrit; HF; high fat; HFE; hemochromatosis protein; HJV; hemojuvelin; IRE; iron-responsive elemen
Mammalian iron transporters: Families SLC11 and SLC40
Keywords: همسایه; Nramp1; natural resistance-associated macrophage protein-1; DMT1; divalent metal transporter-1; DCT1; divalent cation transporter-1; Nramp2; natural resistance-associated macrophage protein-2; Ireg1; iron regulated-transporter-1; MTP1; metal transporter p
Les hémochromatoses
Keywords: همسایه; Surcharge en fer; hémochromatose; transferrine; ferritine; fer non lié Ã la transferrine; hepcidine; hémojuvéline; récepteur de la transferrine de type 2; ferroportine; céruloplasmine; Iron overload; hemochromatosis; transferring; ferritin; non-tra
Hereditary hemochromatosis and transferrin receptor 2
Keywords: همسایه; TfR2; HFE; Hepcidin; Hemojuvelin; BMP; Ferroportin;
Research ArticleThe hemochromatosis proteins HFE, TfR2, and HJV form a membrane-associated protein complex for hepcidin regulation
Keywords: همسایه; HH; hereditary hemochromatosis; TfR; transferrin receptor; HJV; hemojuvelin; MHC; major histocompatibility complex; β2M; beta 2 microglobulin; Fe2-Tf; transferrin-bound iron; GPI; glycophosphatidylinositol; BMP; bone morphogenetic protein; SMAD; small mo
Liver hemojuvelin protein levels in mice deficient in matriptase-2 (Tmprss6)
Keywords: همسایه; Iron metabolism; Hepcidin; Hemojuvelin; TMPRSS6
Crystal structure of a hemojuvelin-binding fragment of neogenin at 1.8Â Ã
Keywords: همسایه; DCC; deleted in colorectal cancer; Ig; immunoglobulin; FNIII; fibronectin type III; RGM; repulsive guidance molecule; BMP; bone morphogenetic protein; Ihog; interference hedgehog; Neogenin; Hemojuvelin; Crystal structure; FNIII domain; Iron homeostasis; R
Iron Regulation of Hepcidin Despite Attenuated Smad1,5,8 Signaling in Mice Without Transferrin Receptor 2 or Hfe
Keywords: همسایه; Bone Morphogenetic Protein 6; Id1; ANOVA; analysis of variance; BMP; bone morphogenetic protein; HH; hereditary hemochromatosis; Hjv; hemojuvelin; RT-PCR; reverse-transcription polymerase chain reaction; Tfr2; transferrin receptor 2;
ReviewHepcidin in human iron disorders: Therapeutic implications
Keywords: همسایه; HC; hemochromatosis; TfR2; transferrin receptor 2; HAMP; hepcidin gene; HJV; hemojuvelin; Tf; transferrin; FPN; ferroportin; LEAP-1; liver expressed antimicrobial protein; BMPs; bone morphogenetic proteins; RGMs; repulsive guidance molecules; RGMs; transm
Sex and Acquired Cofactors Determine Phenotypes of Ferroportin Disease
Keywords: همسایه; Hemochromatosis; Iron Overload; Genetic Disease; Family Study; BMI; body mass index; FPN; ferroportin; HIC; hepatic iron concentration; HJV; hemojuvelin; N; normal; TFR2; transferrin receptor 2; WT; wild type;
Effect of erythropoietin on hepcidin expression in hemojuvelin-mutant mice
Keywords: همسایه; Hepcidin; Hemojuvelin; BMP6; Iron; Erythropoietin
Hereditary Hemochromatosis: Pathogenesis, Diagnosis, and Treatment
Keywords: همسایه; Iron Metabolism; Hereditary Disorders; Micronutrients; Hepcidin; HFE; BMP; bone morphogenic protein; FPN; ferroportin; HAMP; hepcidin gene; HJV; hemojuvelin; RGM; repulsive guidance molecule; TfR; transferrin receptor; TS; transferrin saturation;
Current approach to hemochromatosis
Keywords: همسایه; Hemochromatosis; Iron overload; HFE; Hepcidin; Hemojuvelin; Ferroportin; Transferrin receptor 2; Transferrin; Saturation ferritin; Venesection
Effect of phlebotomy on hepcidin expression in hemojuvelin-mutant mice
Keywords: همسایه; Hemojuvelin; Hamp1; Hamp2; Sex difference; Phlebotomy
Hepatic iron metabolism gene expression profiles in HFE associated Hereditary Hemochromatosis
Keywords: همسایه; HFE; Hepcidin; Hemojuvelin; TfR2; Ferroportin
Hepcidin generated by hepatoma cells inhibits iron export from co-cultured THP1 monocytes
Keywords: همسایه; Ferroportin; Hemochromatosis; Anemia of chronic disease; HFE; Hemojuvelin
Hereditary hemochromatosis
Keywords: همسایه; Iron overload; HFE; Hepcidin; Ferroportin; Hemojuvelin; Transferrin receptor 2
Hepcidin: Iron-hormone and anti-microbial peptide
Keywords: همسایه; aa; amino acids; C/EBP; CCAAT/enhancer binding protein; DCYTB; cytochrome b-like ferriductase; DMT1; divalent metal transporter-1; FPN1; ferroportin 1; hepc hepcidin; HFE; hemochromatosis gene; HH; hereditary hemochromatosis; HJV; hemojuvelin; HNF4a; hepa
New insights into iron homeostasis through the study of non-HFE hereditary haemochromatosis
Keywords: همسایه; iron; haemochromatosis; HFE; hepcidin; hemojuvelin; transferrin receptor 2; ferroportin;