Keywords: کم خونی همولیتیک; Red cell disorder; Pyruvate kinase; Mutation; Hemolytic anemia; PKLR gene;
مقالات ISI کم خونی همولیتیک (ترجمه نشده)
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Keywords: کم خونی همولیتیک; Sickle cell disease; Disease severity; Molecular signature; Clustering; Fetal hemoglobin; Hemolytic anemia;
Keywords: کم خونی همولیتیک; Metastasis; Extramammary; Paget disease; Surgery; Hemolytic anemia; Spine;
Keywords: کم خونی همولیتیک; Glutathione; Hemolytic anemia; GCLC; Glutamate-cysteine ligase; Gamma-glutamylcysteine synthetase;
Keywords: کم خونی همولیتیک; Hemolytic anemia; Valvular heart disease; Repair of valves; Rheumatic heart disease;
Keywords: کم خونی همولیتیک; Pyruvate Kinase deficiency; Phenotypic and molecular investigation; Hemolytic anemia; Hydrops fetalis; PKLR mutation
Keywords: کم خونی همولیتیک; G6PD deficiency; Hemolytic anemia; Meta-analysis; Prevalence
Keywords: کم خونی همولیتیک; Anemia; Iron deficiency; Anemia of inflammation; Anemia of chronic disease; Hemolytic anemia;
Keywords: کم خونی همولیتیک; Glucose-6-phosphate dehydrogenase; Hemolytic anemia; Favism; X-linked genetic polymorphism; Malaria selection;
Keywords: کم خونی همولیتیک; Systemic lupus erythematosus; Hemolytic anemia; Leukopenia; Thrombocytopenia
Keywords: کم خونی همولیتیک; Adverse drug reaction; allergy; cephalosporin; Clostridium difficile; death; hemolytic anemia; hospitalized; oral; outpatient; nephropathy; parenteral; serious cutaneous adverse reaction; Stevens-Johnson syndrome; ADR; Adverse drug reaction; EHR; Electron
Keywords: کم خونی همولیتیک; Paroxysmal nocturnal hemoglobinuria; Hemolytic anemia; Alternative pathway of complement; Humanized anti-C5 monoclonal antibody; Eculizumab; C3 blockade; C1 inhibition; Bone marrow failure;
Keywords: کم خونی همولیتیک; Red blood cells; Erythrocytes; Hemolytic anemia; G6PD deficiency; Favism; Methemoglobin; Cytochrome b5 reductase; Sickle cell trait; Thalassemia; Pentose-phosphate pathway; Glutathione; Oxidative stress; Free radicals;
Keywords: کم خونی همولیتیک; Cerebral hemorrhage; Hemolytic anemia; Pregnancy; HELLP syndrome; Case report
Keywords: کم خونی همولیتیک; Glucose-6-phosphate isomerase (GPI); GPI deficiency; Hemolytic anemia; Glycolysis; Portugal
Keywords: کم خونی همولیتیک; anemia; G-6PD deficiency; hemolytic anemia; neonatal hyperbilirubinemia; Red blood cell enzyme deficiency
Acute and sub-chronic toxicological studies of the iridoid glycosides extract of Lamiophlomis rotata (Benth.) Kudo in rats
Keywords: کم خونی همولیتیک; Lamiophlomis rotata(Benth.) Kudo; Iridoid glycosides; Acute toxicity; Sub-chronic toxicity; Hemolytic anemia; LR; Lamiophlomis rotata (Benth.) Kudo; IGLR; iridoid glycosides of Lamiophlomis rotata; EtOH; ethyl alcohol; WBC; white blood cell; RBC; red bloo
Cobalamin deficiency presenting with thrombotic microangiopathy (TMA) features: A systematic review
Keywords: کم خونی همولیتیک; Cobalamin; Hemolytic anemia; Pseudo-thrombotic microangiopathy; Vitamin B12; Thrombotic thrombocytopenic purpura;
CD59 deficiency presenting as polyneuropathy and Moyamoya syndrome with endothelial abnormalities of small brain vessels
Keywords: کم خونی همولیتیک; MMD; MMS; High-resolution vessel wall imaging; HR-VWI; CIPD; GBS; Pediatric stroke; Early-onset stroke; Hemolysis; Hemolytic anemia;
Two novel mutations (p.(Ser160Pro) and p.(Arg472Cys)) causing glucose-6-phosphate isomerase deficiency are associated with erythroid dysplasia and inappropriately suppressed hepcidin
Keywords: کم خونی همولیتیک; Glucose-6-phosphate isomerase deficiency; Hemolytic anemia; Dysplastic erythropoiesis; Hepcidin to ferritin ratio; Soluble transferrin receptor; Iron loading;
It's Complicated: Parvovirus B19 in Thalassemia
Keywords: کم خونی همولیتیک; Hemoglobin H disease; Hemolytic anemia; Parvovirus B19; Thalassemia; Transient aplastic crisis;
Next-generation sequencing unravels homozygous mutation in glucose-6-phosphate isomerase, GPIc.1040GÂ >Â A (p.Arg347His) causing hemolysis in an Indian infant
Keywords: کم خونی همولیتیک; Inherited anemias; Red cell enzymopathies; Hemolytic anemia; Glucose phosphate isomerase deficiency;
Glucose 6 phosphatase dehydrogenase (G6PD) and neurodegenerative disorders: Mapping diagnostic and therapeutic opportunities
Keywords: کم خونی همولیتیک; Glucose 6 phosphate dehydrogenase; Hemolytic anemia; Metabolic disorders; Neurodegenerative disorders; MS; multiples sclerosis; DOPA; L-3, 4-dihydroxyphenylalanine; G6 PD; glucose 6 phosphatase dehydrogenase; PPP; pentose phosphate pathway; EC; enzyme com
Thrombotic Microangiopathies (TTP, HUS, HELLP)
Keywords: کم خونی همولیتیک; Thrombocytopenia; Microangiopathies; Hemolytic anemia; TTP; HUS; ITP; HELLP; DIC;
Molecular characterization of six new cases of red blood cell hexokinase deficiency yields four novel mutations in HK1
Keywords: کم خونی همولیتیک; Red blood cells; Glycolysis; Hexokinase deficiency; Hemolytic anemia;
Genotype-phenotype correlations in hereditary elliptocytosis and hereditary pyropoikilocytosis
Keywords: کم خونی همولیتیک; HE; hereditary elliptocytosis; HPP; hereditary pyropoikilocytosis; RBC; red blood cell; Elmax; the maximum value of elongation index; Hemolytic anemia; Red blood cell membrane; Elliptocytosis; Pyropoikilocytosis; Mutation;
Passenger lymphocyte syndrome in ABO and Rhesus D minor mismatched liver and kidney transplantation: A prospective analysis
Keywords: کم خونی همولیتیک; Blood group; Hemolytic anemia; Microchimerism; Passenger lymphocyte syndrome; Transplantation
Thrombotic Microangiopathies (TTP, HUS, HELLP)
Keywords: کم خونی همولیتیک; Thrombocytopenia; Microangiopathies; Hemolytic anemia; TTP; HUS; ITP; HELLP; DIC;
Molecular and clinical heterogeneity in pyruvate kinase deficiency in India
Keywords: کم خونی همولیتیک; Pyruvate kinase; Hemolytic anemia; Red cell enzymes; Molecular modeling; Glycolytic enzymes
Should a Positive Direct Antiglobulin Test Be Considered a Prognostic Predictor in Chronic Lymphocytic Leukemia?
Keywords: کم خونی همولیتیک; Autoimmune phenomena; Hemolytic anemia; Prognosis; IgHV unmutated status; Lymphoproliferative diseases
Percutaneous Paravalvular Leak Closure
Keywords: کم خونی همولیتیک; Percutaneous closure; Prosthetic valve; Paravalvular regurgitation; Congestive heart failure; Hemolytic anemia;
Epidemiology of Pulmonary Arterial Hypertension
Keywords: کم خونی همولیتیک; Pulmonary arterial hypertension; Idiopathic pulmonary arterial hypertension; HIV infection; Portopulmonary hypertension; Systemic sclerosis; Hemolytic anemia; Pulmonary veno-occlusive disease; Anorectic drugs;
Falsely decreased HbA1c in a type 2 diabetic patient treated with dapsone
Keywords: کم خونی همولیتیک; dapsone; HbA1c; hemolytic anemia
Protocolo diagnóstico de las anemias hemolíticas
Keywords: کم خونی همولیتیک; Test de Coombs; Reticulocitos; Esquistocitos; Lactatodeshidrogenasa (LDH); Anemia hemolíticaCoombs test; Reticulocytes; Schistocytes; Lactate dehydrogenase; Hemolytic anemia
Missense mutation in PFKM associated with muscle-type phosphofructokinase deficiency in the Wachtelhund dog
Keywords: کم خونی همولیتیک; Hemolytic anemia; Red cell defect; Myopathy; Hereditary disease; Dog
The association of psoriasis with autoimmune diseases
Keywords: کم خونی همولیتیک; Addison disease; alopecia areata; autoimmune diseases; celiac disease; chronic glomerulonephritis; chronic urticaria; cohort studies; Crohn’s disease; database; giant cell arteritis; Graves disease; Hashimoto disease; hemolytic anemia; immune thrombocytop
Diagnosis and treatment of cold agglutinin mediated autoimmune hemolytic anemia
Keywords: کم خونی همولیتیک; Hemolytic anemia; Autoimmune; Cold agglutinin; Cold agglutinin disease; Lymphoproliferative; Diagnosis; Therapy; Rituximab; Fludarabine
Principles of Percutaneous Paravalvular Leak Closure
Keywords: کم خونی همولیتیک; aortic regurgitation; congestive heart failure; heart valve prosthesis; hemolytic anemia; mitral regurgitation; percutaneous closure3D, 3-dimensional; AVPII, Amplatzer Vascular Plug II; TEE, transesophageal echocardiography
Hemolytic Anemia in Dogs and Cats Due to Erythrocyte Enzyme Deficiencies
Keywords: کم خونی همولیتیک; Hemolytic anemia; Erythrocyte; Pyruvate kinase deficiency; Phosphofructokinase deficiency; Dogs; Cats;
The ability of clinical and laboratory findings to predict in-hospital death in patients with thrombotic thrombocytopenic purpura in an internal and emergency medicine department
Keywords: کم خونی همولیتیک; Thrombotic thrombocytopenic purpura; hemolytic anemia; lactic acid;
Usefulness of glycated albumin as an indicator of glycemic control status in patients with hemolytic anemia
Keywords: کم خونی همولیتیک; Hemolytic anemia; Glycated albumin; Glycated hemoglobin; Glycemic control
Porpora trombotica trombocitopenica (PTT) o sindrome di Moschowitz: una vera urgenza ematologica
Keywords: کم خونی همولیتیک; Thrombotic thrombocytopenic purpura; Hemolytic anemia; Thrombocytopenia; Thrombotic microangiopathy;
Prevalence of G6PD deficiency in a large cohort of HIV-infected patients
Keywords: کم خونی همولیتیک; G6PD deficiency; HIV; Hemolytic anemia
Hemoglobinuria and Acute Kidney Injury Requiring Hemodialysis Following Intravenous Immunoglobulin Infusion
Keywords: کم خونی همولیتیک; Intravenous immunoglobulin (IVIG); hemoglobinuria; hemolytic anemia; acute kidney injury; hemodialysis;
Red cell pyruvate kinase deficiency in Southern Sardinia
Keywords: کم خونی همولیتیک; Pyruvate kinase deficiency; Hemolytic anemia
Hereditary spherocytosis
Keywords: کم خونی همولیتیک; Hereditary spherocytosis; Red cell membrane; Hemolytic anemia; Diagnosis; TherapySphérocytose héréditaire; Membrane érythrocytaire; Anémie hémolytique; Diagnostic; Thérapie
Hemolytic anemia in a patient with hypertrophic obstructive cardiomyopathy
Keywords: کم خونی همولیتیک; Hypertrophic obstructive cardiomyopathy; Hemolytic anemia; Hemodynamics
Synchrony of G6PD activity and RBC fragility under oxidative stress exerted at normal and G6PD deficiency
Keywords: کم خونی همولیتیک; G6PD activity; Oxidative stress; NO donors; Sulfhydryl blocking agents; Hemolytic anemia
Immune hemolytic anemia associated with drug therapy
Keywords: کم خونی همولیتیک; Hemolytic anemia; Drugs and hemolytic anemia; Cephalosporins and hemolytic anemia; Piperacillin and hemolytic anemia; Fludarabine and hemolytic anemia; Drug antibodies
Quantitative erythrocyte membrane proteome analysis with Blue-Native/SDS PAGE
Keywords: کم خونی همولیتیک; BN, blue native; DDM, dodecyl-β-D-maltoside; GO, gene ontology; ESI, electrospray ionization; LC, liquid chromatography; MS, mass spectrometry; MS/MS, tandem mass spectrometryErythrocyte; Hemolytic anemia; Blue-native PAGE; Membrane proteins; CyDye labeli