
Synthesis of C-5a-chain extended derivatives of 4-epi-isofagomine: Powerful β-galactosidase inhibitors and low concentration activators of GM1-gangliosidosis-related human lysosomal β-galactosidase
Keywords: Iminoalditol; 4-epi-Isofagomine; Galactosidase inhibitor; Pharmacological chaperone; GM1-gangliosidosis