Keywords: پیرو فسفات معدنی; ECM; extracellular matrix; OPN; osteopontin; BSP; bone sialoprotein; PDL; periodontal ligament; PPi; inorganic pyrophosphate; TNAP; tissue-nonspecific alkaline phosphatase; ANK; progressive ankylosis protein; ENPP1; ectonucleotide pyrophosphatase phosphod
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Keywords: پیرو فسفات معدنی; ACh+; Acetylcholine; AOCB[6]; (Allyloxy)12 cucurbit[6]uril; AFM; Atomic force microscopy; cAMP; 3',5'-Cyclic monophosphate; ChemFET; Chemical field-effect transistor; CB[6]; Cucurbit[6]uril; DDFTTF; 5,5â²-Bis-(7-dodecyl-9Hfluoren-2-yl)-2,2â²-bithiop
Keywords: پیرو فسفات معدنی; PPi; inorganic pyrophosphate; PPiase; inorganic pyrophosphate hydrolase (E.C. 3.6.1.1; GO; 0004427); PPa; soluble inorganic pyrophosphatases of family I; PPa-ek; soluble inorganic pyrophosphate hydrolase of the family I and eukaryotic type; PPa-pk; solubl
Keywords: پیرو فسفات معدنی; SIBLING; Small Integrin-Binding Ligand N-linked Glycoprotein; BSP; bone sialoprotein; OPN; osteopontin; TNAP; tissue-nonspecific alkaline phosphatase; PPi; inorganic pyrophosphate; ANK; progressive ankylosis protein; ENPP1; ectonucleotide pyrophosphatase
Keywords: پیرو فسفات معدنی; AA; arachidonic acid; aP2 (or FABP4); adipocyte protein 2; BMD; bone mass density; BMP-2; bone morphogenic protein-2; CE; cholesterol esters; CHL; cholesterol; cAMP; cyclic 3,5-adenosine monophosphate; CLA; conjugated isomers of linoleic acid; COX; cycloo
Keywords: پیرو فسفات معدنی; ADPG; ADPglucose; AGP; ADPG pyrophosphorylase; AGPP; ADPG pyrophosphatase; A/N-inv; alkaline/neutral invertase; BT1; Brittle 1; F6P; fructose-6-phosphate; G1P; glucose-1-phosphate; G6P; glucose-6-phosphate; GBSS; granule bound starch synthase; GPT; glucos
Keywords: پیرو فسفات معدنی; ACC; acetyl-CoA carboxylase; ACL; ATP:citrate lyase; ACP; acyl-carrier protein; AGPase; ADP-glucose pyrophosphate; AOX; acyl-CoA oxidase; ARA; arachidonic acid; BE; branching enzymes; CDP-DAG; CDP-diacylglycerol; DAG; diacylglycerol; DGAT; diacylglycerol
Etidronate for Prevention of Ectopic Mineralization in Patients With Pseudoxanthoma Elasticum
Keywords: پیرو فسفات معدنی; arterial calcification; bisphosphonates; etidronate; PXE; 18F-NaF PET; 18fluoride sodium positron emission tomography; ALT; alanine transaminase; AST; aspartate transaminase; BCVA; best corrected visual acuity; CT; computed tomography; eGFR; estimated glo
Repeatedly low plasma alkaline phosphatase in a 56-year-old woman. A case of hypophosphatasia diagnosed in adulthood
Keywords: پیرو فسفات معدنی; HPP; hypophosphatasia; ALP; alkaline phosphatase; P-ALP; plasma alkaline phosphatase; TNSALP; the gene encoding the tissue-nonspecific isoenzyme of alkaline phosphatase; ALPL; synonym to TNSALP; PPi; inorganic pyrophosphate; PLP; pyridoxal 5´-phosphate;
Hypophosphatasia: Biochemical hallmarks validate the expanded pediatric clinical nosology
Keywords: پیرو فسفات معدنی; Alkaline phosphatase; Biomarkers; Bone; Enzymopathy; Inborn-error-of-metabolism; Inorganic pyrophosphate; Mineralization; Pyridoxal phosphate; Rickets; Vitamin B6;
Pharmacophore requirements for HIV-1 reverse transcriptase inhibitors that selectively “Freeze” the pre-translocated complex during the polymerization catalytic cycle
Keywords: پیرو فسفات معدنی; HIV-1; human immunodeficiency virus type 1; RT; reverse transcriptase; PPi; inorganic pyrophosphate; NTP; nucleoside triphosphate; NDP; nucleoside diphosphate; PFA; phosphonoformic acid, foscarnet; RNase H; ribonuclease H; CPHM; [2-(2-(4-chlorophenyl)hydr
Matrix vesicles from chondrocytes and osteoblasts: Their biogenesis, properties, functions and biomimetic models
Keywords: پیرو فسفات معدنی; ABs; apoptotic bodies; ACP; amorphous calcium phosphate; ACVs; articular cartilage vesicles; AFM; atomic force microscopy; ANK; ankyrin; AnxA1, AnxA2, AnxA4, AnxA5, AnxA6, AnxA7; vertebrate annexins 1, 2, 4, 5, 6, 7; BCP; basic calcium phosphate; BMP; bon
Insights into Pathomechanisms and Treatment Development in Heritable Ectopic Mineralization Disorders: Summary of the PXE International Biennial Research Symposium-2016
Keywords: پیرو فسفات معدنی; ACDC; arterial calcification due to CD73 deficiency; AMP; adenosine monophosphate; ATP; adenosine triphosphate; GACI; generalized arterial calcification of infancy; PPi; inorganic pyrophosphate; PTC; premature termination codon; PXE; pseudoxanthoma elasti
Oligomeric state of hypoxanthineâguanine phosphoribosyltransferase from Mycobacterium tuberculosis
Keywords: پیرو فسفات معدنی; Mycobacterium tuberculosis; Hypoxanthineâguanine phosphoribosyltransferase; Enzyme activity; Oligomers; Three-dimensional structure; Structural biology; ANP; acyclic nucleoside monophosphonate; Ec; Escherichia coli; GMP; guanosine 5â²-monophosphate; HG
Spectrophotometric assays for monitoring tRNA aminoacylation and aminoacyl-tRNA hydrolysis reactions
Keywords: پیرو فسفات معدنی; A340; absorbance at 340Â nm; AMP; adenosine 5â²-monophosphate; IMP; inosine 5â²-monophosphate; XMP; xanthine 5â²-monophosphate; PPi; inorganic pyrophosphate; l-Tyr; d-Tyr, l- and d-tyrosine; NAD+; NADH, oxidized and reduced nicotine adenine dinucleotid
Role of leishmanial acidocalcisomal pyrophosphatase in the cAMP homeostasis in phagolysosome conditions required for intra-macrophage survival
Keywords: پیرو فسفات معدنی; cAMP; cyclic adenosine monophosphate; PDE; phosphodiesterase; DAPI; 6-diamidino-2-phenylindole dihydrochloride; PBS; phosphate buffered saline; PC; phagolysosome conditions; LdRAC-A; Leishmania donovani receptor adenylate cyclase A; LdRAC-B; Leishmania do
Abcc6 Knockout Rat Model Highlights the Role of Liver in PPi Homeostasis in Pseudoxanthoma Elasticum
Keywords: پیرو فسفات معدنی; microCT; micro-computed tomography; Pi; inorganic phosphate; PPi; inorganic pyrophosphate; PXE; pseudoxanthoma elasticum; WT; wild type; ZFN; zinc finger nuclease;
Plasma PPi Deficiency Is the Major, but Not the Exclusive, Cause of Ectopic Mineralization in an Abcc6-/- Mouse Model of PXE
Keywords: پیرو فسفات معدنی; asj; ages with stiffened joints; ATP; adenosine triphosphate; GACI; generalized arterial calcification of infancy; PPi; inorganic pyrophosphate; PXE; pseudoxanthoma elasticum; WT; wild-type;
Functional Rescue of ABCC6 Deficiency by 4-Phenylbutyrate Therapy Reduces Dystrophic Calcification in Abcc6-/- Mice
Keywords: پیرو فسفات معدنی; 4-PBA; 4-phenylbutyrate; DCC; dystrophic cardiac calcification; GACI; generalized arterial calcification of infancy; PPi; inorganic pyrophosphate; PXE; pseudoxanthoma elasticum;
TNAP stimulates vascular smooth muscle cell trans-differentiation into chondrocytes through calcium deposition and BMP-2 activation: Possible implication in atherosclerotic plaque stability
Keywords: پیرو فسفات معدنی; Tissue-nonspecific alkaline phosphatase; Microcalcification; Inorganic pyrophosphate; Vascular calcification; VSMCs; Chondrocytes;
Hypophosphatasia: An overview For 2017
Keywords: پیرو فسفات معدنی; Alkaline phosphatase; Hypophosphatasia; Inorganic pyrophosphate; Osteomalacia; Rickets;
Functions of Rho family of small GTPases and Rho-associated coiled-coil kinases in bone cells during differentiation and mineralization
Keywords: پیرو فسفات معدنی; AGC; protein kinase A, G, and C families (PKA, PKC, PKG) of cytoplasmic serine/threonine kinases; AnxA; vertebrate annexin; ALP; alkaline phosphatase; ANK; progressive ankylosis protein; BMP; bone morphogenetic protein; BSP; bone sialoprotein; CHOL; chole
A Diagnostic Algorithm for Children with Low Alkaline Phosphatase Activities: Lessons Learned from Laboratory Screening for Hypophosphatasia
Keywords: پیرو فسفات معدنی; ALP; Alkaline phosphatase; PEA; Phosphoethanolamine; PLP; Pyridoxal-5â²-phosphate; PPi; Inorganic pyrophosphate; TNSALP; Tissue nonspecific ALP;
Research Progress in Pseudoxanthoma Elasticum and Related Ectopic Mineralization Disorders
Keywords: پیرو فسفات معدنی; ACDC; arterial calcification due to CD73 deficiency; GACI; generalized arterial calcification of infancy; Pi; inorganic phosphate; PPi; inorganic pyrophosphate; PXE; pseudoxanthoma elasticum;
Biocatalytic functionalization of hydroxyalkyl acrylates and phenoxyethanol via phosphorylation
Keywords: پیرو فسفات معدنی; PPi; inorganic pyrophosphate; PPPi; inorganic triphosphate; HMP; hexametaphosphate; polyP; polyphosphoric acid; STY; space-time yield; P-yield; phosphorylation yield; consppi; consumption of PPi; Phosphorylation; Phosphatase; Biocatalysis; Reaction engine
Evidence for a non-overlapping subcellular localization of the family I isoforms of soluble inorganic pyrophosphatase in Arabidopsis thaliana
Keywords: پیرو فسفات معدنی; PPi; inorganic pyrophosphate; PPa; plant soluble inorganic pyrophosphatases of the family I; PPa-pk; plant soluble inorganic pyrophosphatases of the family I, closer in amino acid sequence to the Escherichia coli inorganic pyrophosphatase; PPa-ek; plant s
Hypophosphatasia: Natural history study of 101 affected children investigated at one research center
Keywords: پیرو فسفات معدنی; ALP; alkaline phosphatase; BMD; bone mineral density; CDC; Centers for Disease Control and Prevention; DXA; dual-energy X-ray absorptiometry; HPP; hypophosphatasia; NIH; National Institutes of Health; PPi; inorganic pyrophosphate; SAS; Statistical Analysi
Structural and biochemical characterization of bacterial YpgQ protein reveals a metal-dependent nucleotide pyrophosphohydrolase
Keywords: پیرو فسفات معدنی; HD; histidine-aspartate; (d)NTP; (deoxy)ribonucleoside triphosphate; bsYpgQ; Bacillus subtilis YpgQ; dNTP; deoxyribonucleoside triphosphate; NTP; ribonucleoside triphosphate; dNMP; deoxyribonucleoside monophosphate; Pi; inorganic monophosphate; PPi; inorg
FCRL3 gene polymorphisms confer risk for sudden sensorineural hearing loss in a Chinese Han Population
Keywords: پیرو فسفات معدنی; A; adenosine; A; absorbance (1Â cm); aa; amino acid(s); Ab; antibody(ies); Ad; adenovirus; AdoMet (or SAM); S-adenosylmethionine; AMV; avian myeloblastosis virus; Ap; ampicillin; PGal; P-galactosidase; bp; base pair(s); BSA; bovine serum albumin; C; cytid
Leishmania amazonensis: Characterization of an ecto-pyrophosphatase activity
Keywords: پیرو فسفات معدنی; Ecto-PPase; ecto-pyrophosphatase; Pi; inorganic phosphate; PPi; pyrophosphate; PPase; pyrophosphatase; sPPase; soluble pyrophosphatase; Leishmania amazonensis; Ecto-pyrophosphatase; Inorganic pyrophosphate;
Metabolic flux analysis of recombinant Pichia pastoris growing on different glycerol/methanol mixtures by iterative fitting of NMR-derived 13C-labelling data from proteinogenic amino acids
Keywords: پیرو فسفات معدنی; αKG; α-ketoglutarate; GA3P; Glyceraldehyde-3-phosphate; PG2; 2-phosphoglycerate; PG3; 3-phosphoglycerate; GA3Pper; Glyceraldehyde-3-phosphate peroxisome; DHA; Dihydroxyacetone; DHAP; Dihydroxyacetone phosphate; E4P; Eritrose-4-phosphate; Rib5P; Ribose-5
Clinical spectrum of hypophosphatasia diagnosed in adultsâ
Keywords: پیرو فسفات معدنی; AP; alkaline phosphatase; CPPD; calcium pyrophosphate deposition disease; HPP; hypophosphatasia; OS; osteoid covered surface; OV; osteoid volume; OW; osteoid width; PEA; phosphoethanolamine; PLP; pyridoxal 5â²-phosphate; PPi; inorganic pyrophosphate; TNS
Aminoacyl-coenzyme A synthesis catalyzed by a CoA ligase from Penicillium chrysogenum
Keywords: پیرو فسفات معدنی; AMP; adenosine 5â²-monophosphate; ATP; adenosine 5â²-triphosphate; CoA; coenzyme A; HPLC; high-performance liquid chromatography; NRPS; non-ribosomal peptide synthetase; PPi; inorganic pyrophosphate; Coenzyme A ligase; Aminoacyl-coenzyme A; β-Phenylala
Development of a charcoal paper adenosine triphosphate:pyrophosphate exchange assay: Kinetic characterization of NEDD8 activating enzyme
Keywords: پیرو فسفات معدنی; APP-BP-1/UBA3; ATP; Charcoal paper; E1; Inorganic pyrophosphate; NEDD8 activating enzyme; Ubiquitin-like modifier;
Optimized chromatographic and bioluminescent methods for inorganic pyrophosphate based on its conversion to ATP by firefly luciferase
Keywords: پیرو فسفات معدنی; Inorganic pyrophosphate; ATP; Firefly luciferase; Ion-pair-HPLC; Bioluminescence; Experimental factorial design
Bisphosphonates: Mechanism of Action and Role in Clinical Practice
Keywords: پیرو فسفات معدنی; ATP; adenosine triphosphate; BMD; bone mineral density; DXA; dual-energy x-ray absorptiometry; FDA; Food and Drug Administration; GIO; glucocorticoid-induced osteoporosis; HORIZON; Health Outcomes and Reduced Incidence with Zoledronic Acid Once Yearly; IV
A multienzyme bioluminescent time-resolved pyrophosphate assay
Keywords: پیرو فسفات معدنی; Bioluminescent assay; Enzyme kinetics; Inorganic pyrophosphate; Time-resolved kinetics; Gene expression; Nucleic acid detection;
Expression of new human inorganic pyrophosphatase in thyroid diseases: Its intimate association with hyperthyroidism
Keywords: پیرو فسفات معدنی; Inorganic pyrophosphatase; Inorganic pyrophosphate; Thyroid; Hyperthyroidism
Human mitochondrial pyrophosphatase: cDNA cloning and analysis of the gene in patients with mtDNA depletion syndromes
Keywords: پیرو فسفات معدنی; GFP, green fluorescent protein; GST, glutathione S-transferase; PPi, inorganic pyrophosphate; PPase, pyrophosphatase; mtDNA, mitochondrial DNA; MDS, mtDNA depletion syndromeHuman pyrophosphatase; Inorganic pyrophosphate; Mitochondrial DNA; Mitochondrial d
Deletion mutation analysis on C-terminal domain of plant vacuolar H+-pyrophosphatase
Keywords: پیرو فسفات معدنی; Proton translocation; Proton translocase; Tonoplast; Vacuole; Vacuolar H+-pyrophosphatase; Inorganic pyrophosphate; Heterologous expression; C-terminal truncation; Deletion mutagenesis; K+-binding;
Large-scale purification of the proton pumping pyrophosphatase from Thermotoga maritima: A “Hot-Solve” method for isolation of recombinant thermophilic membrane proteins
Keywords: پیرو فسفات معدنی; PPi; inorganic pyrophosphate; H+-PPase; proton-pumping pyrophosphatase; DTT; ditiothreitol; DDM; n-dodecyl-β-d-maltopyranoside; TVP; Thermotoga maritima membrane-bound H+-PPase; PMSF; phenyl-methyl-sulphonyl-fluoride; MES; 2-morpholinoethansulfonic acid;
Oligomerization of H+-pyrophosphatase and its structural and functional consequences
Keywords: پیرو فسفات معدنی; H+-PPase; H+-translocating pyrophosphatase; PPi; inorganic pyrophosphate; ScPP; S. coelicolor H+-PPase; BM; 3-(N-maleimidylpropionyl)biocytin; CuPh; Cu(II)-(1,10-phenanthroline)3; DTT; dithiothreitol; 2-ME; 2-mercaptoethanol; ECL; enhanced chemiluminescen