Keywords: مکانیوم ایلئوس; Body mass index; Constipation; Cystic fibrosis; Distal intestinal obstruction (DIOS); Growth curves; Meconium ileus;
مقالات ISI مکانیوم ایلئوس (ترجمه نشده)
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Keywords: مکانیوم ایلئوس; Meconium ileus; Meconium peritonitis; Gastrografin; Cystic fibrosis;
Keywords: مکانیوم ایلئوس; Neonatal; Gastrointestinal; Intestinal atresia; Malrotation; Tracheoesophageal fistula; Pyloric stenosis; Hirschsprung disease; Meconium ileus;
Keywords: مکانیوم ایلئوس; AUC; area under curve; CF; cystic fibrosis; CFNBS; cystic fibrosis newborn screening; CFSPID; CF screen-positive inconclusive diagnosis; CI; confidence interval; IRT; immunoreactive trypsinogen; MI; meconium ileus; PAP; pancreatitis-associated protein.; C
Keywords: مکانیوم ایلئوس; Evidence-based medicine; upper gastrointestinal tract; lower gastrointestinal tract; small bowel obstruction; large bowel obstruction; diagnosis; sensitivity and specificity; confidence interval; duodenal atresia; duodenal stenosis; jejunal atresia; ileal
Keywords: مکانیوم ایلئوس; CF; cystic fibrosis; FEV1; forced expiration volume in the first second; FEV1%predicted; percentage predicted of forced expiration volume in the first second; CFTR; cystic fibrosis transmembrane conductance regulator; WIRCT; Wisconsin randomized clinical
Keywords: مکانیوم ایلئوس; Cystic fibrosis; Meconium ileus; PrematurityFibrose cística; Íleo meconial; Prematuridade
Keywords: مکانیوم ایلئوس; Cystic fibrosis; Meconium ileus; Distal intestinal obstruction syndrome; Surgery
Keywords: مکانیوم ایلئوس; BMI; Body mass index; CF; Cystic fibrosis; CFF; CF Foundation; D&A; Delayed and attenuated; HV; Height velocity; MI; Meconium ileus; PHV; Peak height velocity; PI; Pancreatic insufficiency; PS; Pancreatic sufficiency;
Early life growth patterns persist for 12â¯years and impact pulmonary outcomes in cystic fibrosis
Keywords: مکانیوم ایلئوس; BMIz; age- and sex-specific z-scores for body mass index; CF; cystic fibrosis; CXR; chest radiograph; FEV1; forced expiratory volume in 1â¯s; HTz; age- and sex-specific z-scores for length (<2â¯years) or height (â¥2â¯years); I6; non-responders whose g
Manifestações precoces da fibrose cística em paciente prematuro com íleo meconial complexo ao nascimento
Keywords: مکانیوم ایلئوس; Fibrose cística; Íleo meconial; PrematuridadeCystic fibrosis; Meconium ileus; Prematurity
Meconium ileus in cystic fibrosis is not linked to central repetitive region length variation in MUC1, MUC2, and MUC5AC
Keywords: مکانیوم ایلئوس; Meconium ileus; Genetic modifier; MUC1; MUC2; MUC5AC
Comparison of different IRT-PAP protocols to screen newborns for cystic fibrosis in three central European populations
Keywords: مکانیوم ایلئوس; CF; cystic fibrosis; CFNBS; cystic fibrosis newborn screening; DBS; dried blot spot; FS; failsafe strategy; IRT; immunoreactive trypsinogen; NBS; newborn screening; MI; meconium ileus; PAP; pancreatitis associated protein; PS; pancreatic sufficient; PI; p
Phenotypic expression of the 3120+1G>A mutation in non-Caucasian children with cystic fibrosis in South Africa
Keywords: مکانیوم ایلئوس; Growth; Meconium ileus; Lung function; Failure to thrive; Pseudomonas aeruginosa;
“Pulling the plug”—Management of meconium plug syndrome in neonates
Keywords: مکانیوم ایلئوس; Meconium plug syndrome; Meconium ileus; Left colon syndrome; Hirchsprung’s disease
A review of pathophysiology and management of fetuses and neonates with meconium ileus for the pediatric surgeon
Keywords: مکانیوم ایلئوس; Meconium ileus; Cystic fibrosis; Prenatal diagnosis; Neonate; Fetus;
Neonatal Bowel Obstruction
Keywords: مکانیوم ایلئوس; Neonatal bowel obstruction; Intestinal atresia; Malrotation; Hirschsprung disease; Meconium ileus; Anorectal malformations;
Ursodeoxycholic acid treatment in patients with cystic fibrosis at risk for liver disease
Keywords: مکانیوم ایلئوس; Cystic fibrosis; Liver disease; Meconium ileus; Ursodeoxycholic acid
Constipation in pediatric Cystic Fibrosis patients: An underestimated medical condition
Keywords: مکانیوم ایلئوس; Abdominal radiography; Interobserver variability; Intraobserver variability; Fat malabsorption; Meconium ileus; Steatorrhea; Total fat absorption
Clinical outcome of cystic fibrosis presenting with or without meconium ileus: a matched cohort study
Keywords: مکانیوم ایلئوس; Cystic fibrosis; Meconium ileus; Nutritional status; Pulmonary function tests; Pseudomonas aeruginosa colonization; CFTR analysis
Relative Contribution of Genetic and Nongenetic Modifiers to Intestinal Obstruction in Cystic Fibrosis
Keywords: مکانیوم ایلئوس; CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; DIOS; distal intestinal obstruction syndrome; DZ; dizygous; LOD; logarithm of odds of linkage; MI; meconium ileus; MZ; monozygous; PI; pancreatic insufficiency; PS; pancreatic
Genetic and physiologic correlates of longitudinal immunoreactive trypsinogen decline in infants with cystic fibrosis identified through newborn screening
Keywords: مکانیوم ایلئوس; CF; Cystic fibrosis; CFTR; Cystic Fibrosis Transmembrane Conductance Regulator; FN; False-negative; HAZ; Height for age Z score; IRT; Immunoreactive trypsinogen; MI; Meconium ileus; NBS; Newborn screening; PI; Pancreatic insufficient; PS; Pancreatic suffi
Mucoviscidose : organisation du dépistage néonatal français, premiers résultats enregistrés
Keywords: مکانیوم ایلئوس; Dépistage néonatal; Trypsine immunoréactive; Iléus méconial; Mutations; Neonatal screening; Immunoreactive trypsin; Meconium ileus; CFTR analysis;
Complications associated with symptomatic diagnosis in infants with cystic fibrosis
Keywords: مکانیوم ایلئوس; CF; Cystic fibrosis; FEV1; Forced expiratory volume in 1 second; IQR; Interquartile range; MI; Meconium ileus; NBS; Newborn screening; PRE; Prenatal diagnosis; SYMP; Symptomatic diagnosis;
Assessing the cost of cystic fibrosis diagnosis and treatment
Keywords: مکانیوم ایلئوس; CF; Cystic fibrosis; CFF; Cystic Fibrosis Foundation; CFTR; Cystic fibrosis transmembrane conductance regulator gene; DNA; Deoxyribonucleic acid; FEV1; Forced expiratory volume in 1 second; IRT; Immunoreactive trypsinogen; MI; Meconium ileus; NBS; Newborn
Preventing early, prolonged vitamin E deficiency: an opportunity for better cognitive outcomes via early diagnosis through neonatal screening
Keywords: مکانیوم ایلئوس; α-T; Alpha-tocopherol; ANCOVA; Analysis of covariance; ANOVA; Analysis of variance; C; Control; CF; Cystic fibrosis; CSI; Cognitive skills index; GEE; Generalized estimating equations; MI; Meconium ileus; PI; Pancreatic insufficiency; RCT; Randomized cli
Cystic fibrosis in neonates and infants
Keywords: مکانیوم ایلئوس; Cystic fibrosis; Meconium ileus; Screening; Cystic fibrosis transmembrane regulator;