
Mevalonolactone disrupts mitochondrial functions and induces permeability transition pore opening in rat brain mitochondria: Implications for the pathogenesis of mevalonic aciduria
Keywords: انتقال نفوذپذیری میتوکندری; Mevalonic aciduria; Mevalonate kinase deficiency; Mevalonic acid; Mevalonolactone; Mitochondrial function; Mitochondrial permeability transition; ACO; aconitase; Alm; alamethicin; BSA; bovine serum albumin; CAC; citric acid cycle; CCCP; carbonyl cyanide 3