Keywords: بیماری Polyglutamine; Polyglutamine disease; Model characterization; Disease development; C-Fos neuronal activation; Elevated plus maze;
مقالات ISI بیماری Polyglutamine (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: بیماری Polyglutamine; Environmental modifiers; Tandem repeat disorders; Polyglutamine disease; Neurodegenerative disorder; Alzheimer's disease; Parkinson's disease; Lifestyle; Cognitive stimulation; Environmental enrichment; Exercise; Physical activity; Stress; Diet;
Sex-dependent behavioral impairments in the HdhQ350/+ mouse line
Keywords: بیماری Polyglutamine; Huntington's disease; Mouse model; Sex-dependent; Polyglutamine disease; Protein aggregation; Neurodegeneration;
Multiple system atrophy and CAG repeat length: A genetic screening of polyglutamine disease genes in Italian patients
Keywords: بیماری Polyglutamine; Polyglutamine disease; MSA; Spinocerebellar ataxia; SCA; Huntington disease;
Immunohistochemical localization of exoribonucleases (DIS3L2 and XRN1) in intranuclear inclusion body disease
Keywords: بیماری Polyglutamine; Exoribonuclease; DIS3L2; XRN1; Intranuclear inclusion body disease; Polyglutamine disease;
n-Butylidenephthalide exhibits protection against neurotoxicity through regulation of tryptophan 2, 3 dioxygenase in spinocerebellar ataxia type 3
Keywords: بیماری Polyglutamine; Machado-Joseph disease; Polyglutamine disease; Spinocerebellar ataxia; Tryptophan 2, 3-dioxygenase; Tryptophan metabolism;
Basic NeuroscienceWhat's wrong with my mouse cage? Methodological considerations for modeling lifestyle factors and gene-environment interactions in mice
Keywords: بیماری Polyglutamine; Environmental modifiers; Gene-environment interactions; Housing conditions; Experience-dependent plasticity; Neurological disease; Psychiatric disorders; Tandem repeat disorders; Polyglutamine disease; Neurodegenerative disorders; Alzheimer's disease; H
Quantification of Ataxin-3 and Ataxin-7 aggregates formed in vivo in Drosophila reveals a threshold of aggregated polyglutamine proteins associated with cellular toxicity
Keywords: بیماری Polyglutamine; Polyglutamine disease; Protein aggregates; SCA3; SCA7; Drosophila melanogaster;
Characterization of C-terminal adaptors, UFD-2 and UFD-3, of CDC-48 on the polyglutamine aggregation in C. elegans
Keywords: بیماری Polyglutamine; AAA ATPase; C. elegans; CDC-48/p97/VCP; Polyglutamine disease; UFD-3;
Role of glutathione S-transferases in the spinocerebellar ataxia type 2 clinical phenotype
Keywords: بیماری Polyglutamine; Oxidative stress; Polyglutamine disease; Spinocerebellar ataxia type 2; Glutathione S-transferase; Antioxidant enzymes; Presymptomatic;
Roles of the nucleolus in the CAG RNA-mediated toxicity
Keywords: بیماری Polyglutamine; Nucleolar stress; Nucleolin; p53; Patient fibroblast; Polyglutamine disease; UCE methylation
Mahogunin ring finger 1 suppresses misfolded polyglutamine aggregation and cytotoxicity
Keywords: بیماری Polyglutamine; AIP4; atrophin-interacting protein 4; Baf; bafilomycin; BMP; bis(monoacylglycero)phosphate; CMA; chaperone-mediated autophagy; CQ; chloroquine; HD; Huntington disease; HECT; homologous to E6-AP C-terminus; IB; inclusion bodies; Lamp2a; lysosome associated
Cerebral involvement in spinal and bulbar muscular atrophy (Kennedy's disease): A pilot study of PET
Keywords: بیماری Polyglutamine; Androgen receptor; Kennedy's disease; Polyglutamine disease; Positron emission tomography; Spinal and bulbar muscular atrophy; Motor neuron disease
Overexpression of HGF attenuates the degeneration of Purkinje cells and Bergmann glia in a knockin mouse model of spinocerebellar ataxia type 7
Keywords: بیماری Polyglutamine; Hepatocyte growth factor; c-Met; Polyglutamine disease; Glutamate transporter; GLAST; GLT-1; SCA
Comparative analyses of Purkinje cell gene expression profiles reveal shared molecular abnormalities in models of different polyglutamine diseases
Keywords: بیماری Polyglutamine; Huntington' s Disease; Spinocerebellar ataxia; Laser capture microdissection; Purkinje cell; Polyglutamine disease; Microarray
NIRF/UHRF2 occupies a central position in the cell cycle network and allows coupling with the epigenetic landscape
Keywords: بیماری Polyglutamine; CAN gene; candidate cancer gene; CD; cluster of differentiation; CDK; cyclin-dependent kinase; COPA; cancer outlier profile analysis; DNMT; DNA methyltransferase; GRN; gene regulatory network; HDAC; histone deacetylase; H3K9; Histone H3 lysine 9; ICBP90;
What have we learned from gene expression profiles in Huntington's disease?
Keywords: بیماری Polyglutamine; Polyglutamine disease; huntingtin; Transcriptomic profiling; Striatum; Cortex; Muscle; Blood; Microarray; Biomarker;
Toward understanding Machado-Joseph disease
Keywords: بیماری Polyglutamine; ATXN3; ataxin-3; bZIP; basic leucine zipper motif; CBPC; REB binding protein; cDNA; complementary DNA; CHIP; C-terminus of Hsc70 interacting protein; CK2; casein kinase 2; CMV; cytomegalovirus; CNS; central nervous system; CREB; cAMP-response element bind
Modest proteasomal inhibition by aberrant ubiquitin exacerbates aggregate formation in a Huntington disease mouse model
Keywords: بیماری Polyglutamine; Polyglutamine disease; Ubiquitin proteasome system; Neurodegeneration; Transgenic mice; Inclusions; Huntingtin
Polyglutamine-induced neurodegeneration in SCA3 is not mitigated by non-expanded ataxin-3: Conclusions from double-transgenic mouse models
Keywords: بیماری Polyglutamine; Ataxin-3; Disease modification; Double-transgenic mice; Mouse model; Polyglutamine disease; Spinocerebellar ataxia type 3
Androgens inhibit androgen receptor promoter activation in motor neurons
Keywords: بیماری Polyglutamine; Androgen receptor; Spinal and bulbar muscular atrophy; Kennedy's disease; Polyglutamine disease; Motor neuron; Neurodegeneration; Prostate cancer
Androgen receptor and Kennedy disease/spinal bulbar muscular atrophy
Keywords: بیماری Polyglutamine; Neuromuscular systems; Sexual dimorphism; Testosterone; Axonopathy; Myopathy; Polyglutamine disease
Intranuclear immunolocalization of 14-3-3 protein isoforms in brains with spinocerebellar ataxia type 1
Keywords: بیماری Polyglutamine; 14-3-3 proteins; Spinocerebellar ataxia type 1; Ataxin 1; Neuronal intranuclear inclusion; Polyglutamine disease
Molecular Pathogenesis of Spinocerebellar Ataxia Type 6
Keywords: بیماری Polyglutamine; Spinocerebellar ataxia type 6 (SCA6); channelopathy; polyglutamine disease; P/Q-type calcium channel; Purkinje cell; cerebellum;
Modulation of polyglutamine inclusion formation by the Hsp70 chaperone machine
Keywords: بیماری Polyglutamine; Polyglutamine disease; Misfolding; Aggregation; Molecular chaperones; Protein quality control;
Pharmacological protein targets in polyglutamine diseases: Mutant polypeptides and their interactors
Keywords: بیماری Polyglutamine; Neurodegeneration; Polyglutamine disease; Polypeptide; Protein conformation; Drug target;
The phenylic hydroxyl group is essential for the induction of stress response by sodium salicylate
Keywords: بیماری Polyglutamine; Heat shock protein; Sodium salicylate; Hsp-inducer; Polyglutamine disease
Polyglutamine and polyalanine expansions in ataxin7 result in different types of aggregation and levels of toxicity
Keywords: بیماری Polyglutamine; SCA7; Polyglutamine disease; Polyalanine; Trinucleotide repeat; Aggregation
Compounds blocking mutant huntingtin toxicity identified using a Huntington's disease neuronal cell model
Keywords: بیماری Polyglutamine; Huntingtin; Polyglutamine disease; Compound screen; LDH assay; Cell toxicity; Aggregation;