Keywords: ابتلا به کمبود های ایمنی; Redundancy; Essentiality; Infections; Immunopathology; Innate immunity; Adaptive immunity; Primary immunodeficiencies;
مقالات ISI ابتلا به کمبود های ایمنی (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: ابتلا به کمبود های ایمنی; Primary immunodeficiencies; Common variable immunodeficiency; Autoimmunity; Granulomatous and lymphocytic interstitial lung disease; IPEX; Immune dysregulation, polyendocrinopathy, enteropathy, X-linked;
Keywords: ابتلا به کمبود های ایمنی; Splicing prediction; Splicing-affecting variants; Cryptic splice sites; Primary immunodeficiencies; ESE; exon splicing enhancer; ESS; exon splicing silencer; NMD; nonsense-mediated decay; SRE; splicing regulatory element; VUS; variants of unknown signific
Keywords: ابتلا به کمبود های ایمنی; Primary immunodeficiencies; autoimmunity; inflammation; CEREDIH; Centre de Référence Déficits Immunitaires Héréditaires (French national PID registry); CVID; Common variable immunodeficiency; HSCT; Hematopoietic stem cell transplantation; PID; Primar
Keywords: ابتلا به کمبود های ایمنی; Inmunodeficiencias primarias; Infecciones; Fenotipo; Poblaciones linfocitarias; Inmunoglobulinas; Primary immunodeficiencies; Infections; Phenotype; Lymphocyte populations; Immunoglobulins;
Keywords: ابتلا به کمبود های ایمنی; Primary immunodeficiencies; Hematopoietic stem cell transplantation; ImmunosuppressionInmunodeficiencias primarias; Trasplante alogénico de progenitores hematopoyéticos; Inmunosupresión
Keywords: ابتلا به کمبود های ایمنی; Primary immunodeficiencies; whole-genome sequencing; whole-exome sequencing; linkage analysis; homozygosity mappingCMC, Chronic mucocutaneous candidiasis; ED-ID, Ectodermal dysplasia and immunodeficiency; HSE, Herpes virus encephalitis; IL-2Rγ, IL-2 recep
Keywords: ابتلا به کمبود های ایمنی; Genotype versus phenotype expressions; immunology; immunoreconstitution; intravenous immunoglobulin; primary immunodeficiencies; newborn screening for severe combined immunodeficiency; whole-genome sequencing; AD; Autosomal dominant; ADA; Adenosine deamin
Modified T-cells (using TCR and CTAs), chimeric antigen receptor (CAR) and other molecular tools in recent gene therapy
Keywords: ابتلا به کمبود های ایمنی; Clinical trials; Disorders; Gene therapy; Molecular biology; Pharmacotherapy; Vector; PID; Primary immunodeficiencies; ADA; Adenosine deaminase; CAR; Chimeric antigen receptors; TCR; T cell receptor; CTAs; Cancer testis antigens; TALEN; Transcription acti
Diagnostic biologique des déficits immunitaires primitifs
Keywords: ابتلا به کمبود های ایمنی; déficit immunitaire primitif; diagnostic immunologique; immunological diagnosis; primary immunodeficiencies;
Mutations in PIK3R1 can lead to APDS2, SHORT syndrome or a combination of the two
Keywords: ابتلا به کمبود های ایمنی; Genetic diagnosis; Primary immunodeficiencies; SHORT syndrome;
DOCK8 deficiency: Insights into pathophysiology, clinical features and management
Keywords: ابتلا به کمبود های ایمنی; Actin; CDC42; Combined immunodeficiency; Dedicator of cytokinesis; DOCK2; DOCK8; Hyper IgE syndrome; Primary immunodeficiency; RAC1; STAT3; AR-HIES; autosomal recessive hyper IgE syndrome; AD-HIES; autosomal dominant hyper IgE syndrome; CDC42; cell divisi
Análisis de la supervivencia de los niños con inmunodeficiencias primarias que han recibido un trasplante de progenitores hematopoyéticos en España
Keywords: ابتلا به کمبود های ایمنی; Inmunodeficiencias primarias; Trasplante alogénico de progenitores hematopoyéticos; Inmunosupresión; Primary immunodeficiencies; Hematopoietic stem cell transplantation; Immunosuppression;
Recent advances in understanding the pathophysiology of primary T cell immunodeficiencies
Keywords: ابتلا به کمبود های ایمنی; primary immunodeficiencies; T lymphocytes; autoimmunity; innate immunity; inflammation
Synergy in activating class I PI3Ks
Keywords: ابتلا به کمبود های ایمنی; phosphoinositide 3 kinases; lipid signaling; cancer; phosphoinositides; primary immunodeficiencies; lipid kinases
Monogenic mutations differentially affect the quantity and quality of T follicular helper cells in patients with human primary immunodeficiencies
Keywords: ابتلا به کمبود های ایمنی; Follicular helper T cells; humoral immunity; primary immunodeficiencies; cytokine signaling; Bcl-6; B-cell lymphoma 6; cTFH; Circulating follicular helper T; DN; Double-negative; DP; Double-positive; GC; Germinal center; GOF; Gain of function; IL-10R; IL-
Sphingosine-1-phosphate receptors control B-cell migration through signaling components associated with primary immunodeficiencies, chronic lymphocytic leukemia, and multiple sclerosis
Keywords: ابتلا به کمبود های ایمنی; Sphingosine-1-phosphate; B cells; migration; autoimmunity; circulation; fingolimod; FTY720; primary immunodeficiencies; ALL; Acute lymphoblastic leukemia; B-CLL; B-cell chronic lymphocytic leukemia; BCR; B-cell receptor; BFP; Blue fluorescent protein; BTK
Gene therapy of primary T cell immunodeficiencies
Keywords: ابتلا به کمبود های ایمنی; ADA; adenosine deaminase; GVHD; graft versus host disease; HSC; hematopoietic stem cell; HSCT; hematopoietic stem cell transplantation; IPS; induced pluripotent cells; LV; Lentivirus; PIDs; primary immunodeficiencies; RV; retrovirus; SAE; serious adverse
Primary immunodeficiencies: A rapidly evolving story
Keywords: ابتلا به کمبود های ایمنی; Primary immunodeficiencies; combined immunodeficiencies; well-defined syndromes with immunodeficiency; predominantly antibody defects; defects of immune dysregulation; congenital defects of phagocytes; defects in innate immunity; autoinflammatory disorder
Fenotipos clínicos asociados a la deficiencia selectiva de IgA: revisión de 330 casos y propuesta de un protocolo de seguimiento
Keywords: ابتلا به کمبود های ایمنی; Deficiencia selectiva de IgA; Inmunodeficiencias primarias; Autoinmunidad; Enfermedades alérgicas; CeliaquíaSelective IgA deficiency; Primary immunodeficiencies; Autoimmunity; Allergic diseases; Coeliac disease
Advances in basic and clinical immunology in 2011
Keywords: ابتلا به کمبود های ایمنی; Immunology; primary immunodeficiencies; intravenous immunoglobulin; transmembrane activator and calcium modulator and cyclophilin ligand interactor; common variable immunodeficiency; cell immunity; severe combined immunodeficiency; newborn screeningADA, A
Excellent survival after sibling or unrelated donor stem cell transplantation for chronic granulomatous disease
Keywords: ابتلا به کمبود های ایمنی; Chronic granulomatous disease; primary immunodeficiencies; bone marrow transplantation; graft-versus-host diseaseCGD, Chronic granulomatous disease; ConA, Concanavalin A; GvHD, Graft-versus-host disease; HSCT, Hematopoietic stem cell transplantation; MRD,
Advances in basic and clinical immunology in 2010
Keywords: ابتلا به کمبود های ایمنی; Immunology; primary immunodeficiencies; B cell; innate immunity; hereditary angioedema; drug allergy; cell immunity; severe combined immunodeficiency; newborn screeningAPECED, Autoimmunity, polyendocrinopathy, candidiasis, and ectodermal dystrophy; C1INH,
γ Chain transducing element: A shared pathway between endocrine and immune system
Keywords: ابتلا به کمبود های ایمنی; Primary immunodeficiencies; Growth hormone receptor; Signal transduction; γ Chain; JAK; STAT
Gene therapy for primary immunodeficiencies: Looking ahead, toward gene correction
Keywords: ابتلا به کمبود های ایمنی; Primary immunodeficiencies; severe combined immunodeficiency; gene therapy; gene correction; locus-specific targeting; homing endonucleases; meganucleases; zinc finger nucleases; safe harbors; transposonsADA, Adenosine deaminase; CGD, Chronic granulomatou
Primary immunodeficiencies: 2009 update
Keywords: ابتلا به کمبود های ایمنی; Primary immunodeficiencies; T cells; B cells; severe combined immunodeficiency; predominantly antibody deficiencies; DNA repair defects; phagocytes; complement; immune dysregulation syndromes; innate immunity; autoinflammatory disordersADA, Adenosine deam
La thérapie cellulaire des maladies héréditaires du système hématopoïétique
Keywords: ابتلا به کمبود های ایمنی; Thérapie cellulaire et génique; Cellules souches hématopoïétiques; Déficits immunitaires primitifsCell and gene therapy; Hematopoietic stem cells; Primary immunodeficiencies
Advances in basic and clinical immunology in 2006
Keywords: ابتلا به کمبود های ایمنی; Immunology; Toll-like receptors; CD1d T cells; immunomodulators; primary immunodeficiencies; drug allergy; angioedema; vaccinesCF, Cystic fibrosis; CVID, Common variable immunodeficiency; HAE, Hereditary angioedema; NK, Natural killer; PGE2, Prostaglandin