Keywords: بیماری پریون; Parkinsonism; Lenalidomide; Creutzfeldt-Jakob disease; Prion disease;
مقالات ISI بیماری پریون (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: بیماری پریون; Multiple system atrophy; PRNP; Prion disease; Prion protein; Sporadic Creutzfeld-Jakob disease; α-synuclein; α-syn; confidence intervals; CI; cytoplasmic inclusions; GCIs; multiple system atrophy; MSA; sporadic Creutzfeld-Jakob disease; sCJD; odds ratio
Keywords: بیماری پریون; Fatal familial insomnia; Agrypnia excitata; Prion disease; PRNP gene; D178N mutation; Myoclonus;
Keywords: بیماری پریون; Prion protein; Protein misfolding; Prion disease; Alzheimer's disease; Signaling pathways; Calcium;
Keywords: بیماری پریون; Blood transfusions; Creutzfeldt-Jakob disease; endoscopes; prion disease; transmissible spongioform encephalopathies;
Keywords: بیماری پریون; Iron; Conversion; Prion disease; Microarray; Gene expression; Redox;
Keywords: بیماری پریون; Protein misfolding; Amyloid oligomers; Aβ channels; Protofibrils; Fibrils; Alzheimer's disease; Prion disease; Parkinson's disease
Keywords: بیماری پریون; Prion disease; PrPSc; Autophagy; Proteasome; Lysosomal degradation; Therapeutics;
Keywords: بیماری پریون; Rapidly progressive dementia; Young onset dementia; Early onset dementia; Presenile dementia; Neuropsychiatry; Prion disease; Creutzfeldt-Jakob disease; Neuropsychiatric symptoms;
Keywords: بیماری پریون; Diffusion MRI; Biophysical models; Creutzfeldt–Jakob disease; Prion disease; Spongiform degenerationADC, apparent diffusion coefficient; BIC, Bayesian information criterion; CJD, Creutzfeldt–Jakob disease; CNR, contrast to noise ratio; DWI, diffusion weig
Keywords: بیماری پریون; Genetic counseling; Predictive genetic testing; Presymptomatic testing protocol; Huntington disease; Alzheimer disease; Frontotemporal degeneration; CADASIL; Prion disease;
Keywords: بیماری پریون; Prion disease; Mitochondrial fusion; Fission; Scrapie; Mitochondrial dysfunction;
Keywords: بیماری پریون; Magnetic resonance imaging (MRI); Alzheimer disease (AD); Positron emission tomography (PET); Frontotemporal lobar degeneration (FTLD); Lewy body dementia (LBD); Prion disease; Multiple sclerosis (MS); Vascular cognitive impairment;
Keywords: بیماری پریون; Prion disease; Corticobasal; Alien limb; Dystonia; Myoclonus;
Rapid progressive visual decline and visual field defects in two patients with the Heidenhain variant of Creutzfeld-Jakob disease
Keywords: بیماری پریون; HvCJD; Visual field defects; MRI; Prion disease;
Exosomes and their role in the intercellular trafficking of normal and disease associated prion proteins
Keywords: بیماری پریون; Prion disease; Exosomes; Prion; Neurodegenerative disease;
Experimental sheep BSE prions generate the vCJD phenotype when serially passaged in transgenic mice expressing human prion protein
Keywords: بیماری پریون; Bovine spongiform encephalopathy (BSE); Prions; Prion disease; Variant Creutzfeldt-Jakob disease (vCJD); Sheep-BSE; Transmissible spongiform encephalopathy (TSE);
PD-1 deficiency is not sufficient to induce myeloid mobilization to the brain or alter the inflammatory profile during chronic neurodegeneration
Keywords: بیماری پریون; Programmed cell death-1; Myeloid cells; Neuroinflammation; Prion disease;
Neuroanatomical correlates of prion disease progression - a 3T longitudinal voxel-based morphometry study
Keywords: بیماری پریون; Prion disease; Structural MRI; Longitudinal voxel based morphometry; 3T MRI; CJD;
Development of radioiodinated acridine derivatives for in vivo imaging of prion deposits in the brain
Keywords: بیماری پریون; Prion disease; PrPSc; Quinacrine; Acridine; Single photon emission computed tomography (SPECT);
The retention of prion protein in the endoplasmic reticulum prevents N2A cells from proteasome inhibition-induced cytotoxicity
Keywords: بیماری پریون; PrPC; PrPSc; Endoplasmic reticulum; KDEL ER-retention motif; Prion disease;
Diets with different lipid contents do not modify the neuronal membrane lipid raft profile in a scrapie murine model
Keywords: بیماری پریون; Prion disease; Murine model; Lipid rafts; Phospholipids; Gangliosides; Hyperlipidic diet; Hypolipidic diet
MicroRNA abundance is altered in synaptoneurosomes during prion disease
Keywords: بیماری پریون; Prion disease; MiRNA; Synapse; Dendrite; Synaptoneurosome; Neurodegeneration;
Complement factors alter the amount of PrPSc in primary-cultured mouse cortical neurons associated with increased membrane permeability
Keywords: بیماری پریون; Prion disease; Complement factor; Primary-cultured neuron; Membrane permeability; Neuropathogenesis;
The Autophagy–Lysosomal Pathway in Neurodegeneration: A TFEB Perspective
Keywords: بیماری پریون; TFEB; autophagy–lysosomal pathway; neurodegenerative disease; prion disease
Stabilization of microtubular cytoskeleton protects neurons from toxicity of N-terminal fragment of cytosolic prion protein
Keywords: بیماری پریون; CtmPrP; transmembrane form of prion protein with the C-terminus residing in the lumen of endoplasmic reticulum; cytoPrP; cytosolic prion protein; ER; endoplasmic reticulum; GPI; glycosylphosphatidylinositol; GSK-3; glycogen synthase kinase 3; HBSS; Hank's
Temporary upregulation of anti-inflammatory cytokine IL-13 expression in the brains of CD14 deficient mice in the early stage of prion infection
Keywords: بیماری پریون; Prion disease; CD14; IL-13; Pathogenesis;
Accelerated clinical course of prion disease in mice compromised in repair of oxidative DNA damage
Keywords: بیماری پریون; Neurodegeneration; Prion disease; DNA damage; DNA repair; Reactive oxygen species; Free radicals;
Nrf-2 regulation of prion protein expression is independent of oxidative stress
Keywords: بیماری پریون; Nrf-2; Transcription factor; Promoter; Oxidative stress; Prion disease
Six-year follow-up of a point-source exposure to CWD contaminated venison in an Upstate New York community: risk behaviours and health outcomes 2005-2011
Keywords: بیماری پریون; Wasting disease, chronic; Prion disease; Public health surveillance; Community health;
Interaction between 14-3-3β and PrP influences the dimerization of 14-3-3 and fibrillization of PrP106–126
Keywords: بیماری پریون; Prion disease; 14-3-3; PrP; Fibril; Disaggregation
Application of quantitative DTI metrics in sporadic CJD
Keywords: بیماری پریون; Creutzfeldt–Jakob disease; Prion disease; Atrophy; DWI; sCJD; MD
Role of CD40 in prion disease and the immune response to recombinant PrP
Keywords: بیماری پریون; CD40; Prion disease; PrP knockout mice; CD40 knockout mice; Recombinant PrP; Anti-PrP antibodies;
Lipid profiles in brains from sheep with natural scrapie
Keywords: بیماری پریون; Scrapie; Prion disease; Brain lipid composition; Fatty acid profile
Sporadic fatal insomnia with clinical, laboratory, and genetic findings
Keywords: بیماری پریون; Familial fatal insomnia; Sporadic fatal insomnia; Prion disease
Transcriptional regulation of specific protein 1 (SP1) by hypoxia-inducible factor 1 alpha (HIF-1α) leads to PRNP expression and neuroprotection from toxic prion peptide
Keywords: بیماری پریون; Specific protein 1; Prp(106–126); HIF-1α; Prion disease
Patienten mit Prionenerkrankungen an der Dialyse – eine Risikobewertung
Keywords: بیماری پریون; Risikobewertung; Dialysegeräte; Prionenerkrankungen; nosokomiale Übertragungrisk assessment; dialysis; dialyser; prion disease; nosocomial transmission
Prion-induced toxicity in PrP transgenic Drosophila
Keywords: بیماری پریون; PrP; Prion disease; Conformation; Neurotoxicity; Drosophila; Transgenic
Increased Immunohistochemical Labelling for Prion Protein Occurs in Diverse Neurological Disorders of Sheep: Relevance for Normal Cellular PrP Function
Keywords: بیماری پریون; prion disease; prion protein; scrapie; transmissible spongiform encephalopathy
All major prion types recognised by a multiplex immunofluorometric assay for disease screening and confirmation in sheep
Keywords: بیماری پریون; Multiplex; Immunoassay; Differential diagnosis; Prion disease; Mass spectrometry;
SIRT1, a histone deacetylase, regulates prion protein-induced neuronal cell death
Keywords: بیماری پریون; Resveratrol; SIRT1; Prion disease; PrP (106–126); Neuronal apoptosis; Neuroprotection
Minimal Involvement of the Circumventricular Organs in the Pathogenesis of Spontaneously Arising and Experimentally Induced Classical Bovine Spongiform Encephalopathy
Keywords: بیماری پریون; bovine spongiform encephalopathy; circumventricular organs; pathogenesis; prion disease;
Cellular immune activation markers neopterin and beta 2-microglobulin are not elevated in the cerebrospinal fluid of patients with Creutzfeldt-Jakob disease
Keywords: بیماری پریون; Creutzfeldt-Jakob disease (CJD); Prion disease; Cerebrospinal fluid (CSF); Neuroinflammation; Neopterin; β2-Microglobulin;
Heat shock protein 104 inhibited the fibrillization of prion peptide 106-126 and disassembled prion peptide 106-126 fibrils in vitro
Keywords: بیماری پریون; Hsp104; PrP106-126; Prion disease; Fibril; Cytotoxicity;
Discovery of 6-substituted indole-3-glyoxylamides as lead antiprion agents with enhanced cell line activity, improved microsomal stability and low toxicity
Keywords: بیماری پریون; Drug discovery; Indoles; Prion disease; Structure–activity relationships; ZebrafishBSE, bovine spongiform encephalopathy; CJD, Creutzfeldt–Jakob disease; CWD, chronic wasting disease; FFI, familial fatal insomnia; GSS, Gerstmann–Sträussler–Scheinker syndr
Prion diseases: a primer for general pathologists
Keywords: بیماری پریون; creutzfeldt–Jakob disease; prion; prion disease; transmissible spongiform encephalopathy
Rapid screening and confirmatory methods for biochemical diagnosis of human prion disease
Keywords: بیماری پریون; Transmissible spongiform encephalopathy; Prion disease; Diagnosis; Human; Spleen; Tonsil
Changes in sympathetic activity in prion neuroinvasion
Keywords: بیماری پریون; Prion disease; Mice; Western blotting; Histopathology; Plasma catecholamines; Neuroinvasion; Blood pressure;
Natural polyphenols as inhibitors of amyloid aggregation. Molecular dynamics study of GNNQQNY heptapeptide decamer
Keywords: بیماری پریون; Amyloid fibril; Molecular dynamic simulation; Prion disease; β sheet; Aggregation; Oligomer; Hydrogen bond; Beta sheet inhibitor; Myricetin;
The role of cerebrospinal fluid proteins as early diagnostic markers for sporadic Creutzfeldt–Jakob disease
Keywords: بیماری پریون; Sporadic CJD; 14-3-3; S-100b; Tau protein; Cerebrospinal fluid; Spongiform encephalopathy; Prion disease