Perlak wrodzony bez destrukcji piramidy kości skroniowej

Congenital cholesteatoma is a rare disease. On otoscopy it appears as a pearly white mass, medial to an intact tympanic membrane, usually at the anterosuperior quadrant, with no previous history of otorhoea, perforation or ear surgery. Congenital cholesteatoma grows slowly. It may be asymptomatic or present as a conductive hearing loss, ear pain or may facial nerve palsy. Rarely it can lead to intracranial or extracranial complications, some of which may be life threatening. Early diagnosis and treatment can lead to better outcomes.