Keywords: ACTH; adrenocorticotropic hormone; ADH; anti-diuretic hormone; AP; alternative pathway; BD; brain dead/brain death; C1-INH; C1 esterase inhibitor; CD59; membrane attack complex-inhibitory protein; CP; classical pathway; CR1; complement receptor 1; CR2; co
مقالات ISI (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: Hereditary angioedema; Bradykinin; C1 inhibitor deficiency; Bradykinin B2 receptor antagonist; Icatibant; Children; Adolescents; Pediatrics; Treatment; AE; adverse event; C1-INH; C1 inhibitor; C1-INH-HAE; hereditary angioedema with C1-inhibitor deficiency
Keywords: ABMR; Antibody mediated rejection; aHUS; Atypical hemolytic syndrome; AP; Alternative pathway; DBD; Deceased brain dead; DCD; Deceased cardiac death; DSA; Donor specific antibodies; C1-INH; C1-inhibitor; C3; Complement component C3; CDC; Complement-depend
Keywords: AMI; Acute myocardial infarction; C1-inh; C1-inhibitor; C1s-inh; C1s-inhibitor; C4BP; C4b-binding protein; CK(-MB); creatine kinase (-MB); CPN; carboxypeptidase-N; CR1; complement receptor 1; CVF; cobra venom factor; DDA; disodium disuccinate astaxanthin;
Keywords: Pediatric hereditary angioedema; Hereditary angioedema; Age onset; C1-INH; C1 inhibitor; CCHMC; Cincinnati Children's Hospital Medical Center; EMR; Electronic medical records; ER; Emergency room; HAE; Hereditary angioedema; IQR; Interquartile range; pdC1I
Keywords: AChR; acetylcholine receptor; aHUS; atypical hemolytic uremic syndrome; AMD; age-related macular degeneration; AMR; antibody-mediated rejection; ANCA; anti-neutrophil cytoplasmic antibody; AP; alternative pathway; C1-INH; C1 esterase inhibitor; C3GN; C3 g
Keywords: MAC; membrane attack complex; TGF-β; transforming growth factor β; TLR; toll-like receptor; MDSC; myeloid-derived suppressor cells; Tregs; regulatory T cells; AMD; age-related macular degeneration; C1-INH; C1 inhibitor; Complement system; Cancer therapy
Pharmacokinetics of human recombinant C1-esterase inhibitor and development of anti-drug antibodies in healthy dogs
Keywords: AUC; area under the curve; AUClast; area under the plasma concentration-time curve from the time of dosing to the last measurable (positive) concentration; AUC-INFobs; area under the plasma concentration-time curve from the time of dosing extrapolated to
Health-Related Quality of Life with Subcutaneous C1-Inhibitor for Prevention of Attacks of Hereditary Angioedema
Keywords: C1-inhibitor protein; Hereditary angioedema; Patient-reported outcomes; Quality of life; Productivity; Satisfaction; Subcutaneous; HAEGARDA; C1-INH; C1-inhibitor; C1-INH-HAE; Hereditary angioedema with C1-inhibitor deficiency; CI; Confidence interval; EQ-
Hereditary Angioedema with Normal C1 Inhibitor and F12 Mutations in 42 Brazilian Families
Keywords: Hereditary angioedema; Normal C1 inhibitor; F12 mutations; Estrogen; Brazilian population; ACEI; Angiotensin-converting enzyme inhibitor; C1-INH; C1 inhibitor; C1-INH-HAE; Hereditary angioedema with C1 inhibitor deficiency; eOC; Estrogen-containing oral c
Targeted next-generation sequencing for the molecular diagnosis of hereditary angioedema due to C1-inhibitor deficiency
Keywords: C1-INH; C1-inhibitor; C1-INH-HAE; hereditary angioedema due to C1-INH deficiency; CI; confidence interval; MLPA; multiplex ligation-dependent probe amplification; NGS; next-generation sequencing; CNV; copy number variation; SNV; single-nucleotide variant;
Mutation of the angiopoietin-1 gene (ANGPT1) associates with a new type of hereditary angioedema
Keywords: Hereditary angioedema; angiopoietin-1; gene; mutation; multimers; tunica interna endothelial cell kinase 2 receptor; ANGPT1; Angiopoietin-1; ANGPT2; Angiopoietin-2; C1-INH; C1 inhibitor; C1-INH-HAE; Hereditary angioedema caused by C1 inhibitor deficiency;
Size-dependent pharmacological activities of differently degraded fucoidan fractions from Fucus vesiculosus
Keywords: APTT; activated partial thromboplastin time; C1-INH; C1 esterase inhibitor; DC; doubling concentration; dn/dc; refractive index increment; DS; degree of sulfation; F.v.-fuc; fucoidan extracted from Fucus vesiculosus; FXII; factor XII; IC50; half maximal i
A novel prophylaxis with C1-inhibitor concentrate in hereditary angioedema during erythema marginatum
Keywords: C1-inhibitor; C1-INH; C1-INH-HAE; hereditary angioedema with C1-inhibitor deficiency; EM; erythema marginatum; HAE; hereditary angioedema; mg; milligram; pdC1-INH; plasma-derived C1-inhibitor; C1-inhibitor deficiency; Erythema marginatum; Hereditary angio
Complement factor C4 activation in patients with hereditary angioedema
Keywords: C1-INH; C1 esterase inhibitor; C1-INH-HAE; hereditary angioedema with C1-INH deficiency; C4; complement factor C4; mAb; monoclonal antibodies; ELISA; enzyme-linked immunosorbent assay; CP; classical pathway; LP; lectin pathway; fC1-INH; functional C1-INH;
Diminished capacity of opsonization and immune complex solubilization, and detection of anti-C1q antibodies in sera from patients with hereditary angioedema
Keywords: Anti-C1q antibody; Autoimmune disease; Hereditary angioedema; Immune complex; Phagocytosis; C1-INH; C1 esterase inhibitor; CR; Complement receptor; HAE; Hereditary angioedema; IC; Immune complex; NHPS; Normal human pooled sera; PBS; Phosphate buffered sal
Recombinant Human C1-Esterase Inhibitor to Treat Acute Hereditary Angioedema Attacks in Adolescents
Keywords: C1-esterase; Hereditary angioedema; Adolescent; Safety; Efficacy; Ruconest; Pharmacokinetics; AE; Adverse event; C1-INH; C1-esterase inhibitor; Cmax; Maximum concentration; HAE; Hereditary angioedema; IV; Intravenous; OLE; Open-label extension; RCT; Rando
Diagnosis, Course, and Management of Angioedema in Patients With Acquired C1-Inhibitor Deficiency
Keywords: Acquired angioedema; C1-INH deficiency; Prevalence; Treatment; Diagnosis; Plasma-derived C1-inhibitor; Icatibant; ACE-I; Angiotensin-converting enzyme inhibitor; C1-INH; C1-inhibitor; C1-INH-AAE; Acquired angioedema due to C1-inhibitor deficiency; C1-INH-
Effect of C1-INH on ischemia/reperfusion injury in a porcine limb ex vivo perfusion model
Keywords: Skeletal muscle; Ischemia reperfusion injury; C1-INH; Endothelial cell; Plasma cascade systems;
C1-inhibitor efficiently delays clot development in normal human whole blood and inhibits Escherichia coli-induced coagulation measured by thromboelastometry
Keywords: aPTT; activated partial thromboplastin time; C1-INH; C1-inhibitor; E. coli; Escherichia coli; EXTEM; extrinsic thromboelastometry; HAE; hereditary angioedema; HSA; human serum albumin; INTEM; intrinsic thromboelastometry; LI; lysis index; min; minute; NAT
Safety and Usage of C1-Inhibitor in Hereditary Angioedema: Berinert Registry Data
Keywords: Berinert; Plasma-derived C1-INH; Patient registry; Thromboembolic event; Real-world; Prophylaxis; On demand; Self-administration; Safety; Dosing; AE; Adverse event; C1-INH; C1 inhibitor; DVT; Deep vein thrombosis; EU; European Union; HAE; Hereditary angio
Mechanisms of allergy and clinical immunologyDeficiency of plasminogen activator inhibitor 2 in plasma of patients with hereditary angioedema with normal C1 inhibitor levels
Keywords: Hereditary angioedema; C1 inhibitor; bradykinin; plasminogen activator inhibitor; BCIP/NBT; 5-Bromo-4-chloroindolyl phosphate/nitroblue tetrazolium; C1-INH; C1 inhibitor; HAE; Hereditary angioedema; HAE-N; Hereditary angioedema with normal C1 inhibitor le
Effects of Bothrops atrox venom and two isolated toxins on the human complement system: Modulation of pathways and generation of anaphylatoxins
Keywords: MP; metalloprotease/Batroxase; PLA2; phospholipase A2/BatroxPLA2; NHS; normal human serum; CP; classical pathway; LP; lectin pathway; AP; alternative pathway; FB; Factor B; C1-INH; C1-Inhibitor; Snake venoms; Bothrops atrox; Metalloprotease; Phospholipase
Original ContributionsEfficacy of Different Medical Therapies for the Treatment of Acute Laryngeal Attacks of Hereditary Angioedema due to C1-esterase Inhibitor Deficiency
Keywords: C1-INH; efficacy; HAE; laryngeal; re-dosing;
ELISA to measure neutralizing capacity of anti-C1-inhibitor antibodies in plasma of angioedema patients
Keywords: NAbs; neutralizing antibodies; C1-inh; C1-inhibitor; AAE; acquired angioedema; HAE; hereditary angioedema; NC%; percentage neutralizing capacity; Auto-autoantibodies; Acquired angioedema; Hereditary angioedema; C1-inhibitor deficiency;
C1-inhibitor polymers activate the FXII-dependent kallikrein-kinin system: Implication for a role in hereditary angioedema
Keywords: BSA; bovine serum albumin; C1-inh; complement C1 esterase inhibitor; C1PIV; in vivo sized C1-inh polymers; CPDA; citrate phosphate dextrose adenine; CPK; chromozyme PK; FXII; coagulation factor XII; FXIIa; activated FXII; dBSA; heat denatured BSA; HAE; he
Characterization of patients with angioedema without wheals: The importance of F12 gene screening
Keywords: C1-INH; C1 inhibitor; HAE; hereditary angioedema; FXII-HAE; hereditary angioedema with factor XII mutation; U-HAE; hereditary angioedema with unknown genetic mutation; InH-AAE; idiopathic non-histaminergic acquired angioedema; SERPING1; serpin peptidase i
Immune deficiencies, infection, and systemic immune disordersEndothelial cell activation during edematous attacks of hereditary angioedema types I and II
Keywords: Hereditary angioedema; C1-inhibitor deficiency; attack; endothelial cells; activation; von Willebrand factor; endothelin-1; soluble E-selectin; clinical study; BMI; Body mass index; C1-INH; C1-inhibitor; C4; Complement factor 4; CRP; C-reactive protein; E
Activation of the ficolin-lectin pathway during attacks of hereditary angioedema
Keywords: Hereditary angioedema; C1-inhibitor; ficolins; MASPs; lectin pathway; edematous attack; C1-INH; C1-inhibitor; FCN3-TCC; Ficolin-3-mediated terminal complement complex; HAE-C1-INH; Hereditary angioedema due to the deficiency of C1-inhibitor; LMM; Linear
ReviewComplement activation-related pseudoallergy: A stress reaction in blood triggered by nanomedicines and biologicals
Keywords: C; complement; CARPA; complement activation-related pseudoallergy; C1-INH; C1-esterase inhibitor; CrEL; Cremophor EL; HSR; hypersensitivity reaction; MLV; large multilamellar vesicles; PEG; polyethylene glycol; RCM; radiocontrast media; sC5b-9; S protein-
Mutations analysis of C1 inhibitor coding sequence gene among Portuguese patients with hereditary angioedema
Keywords: HAE; C1-INH; Mutations; SERPING1 gene;
Factor XII-independent activation of the bradykinin-forming cascade: Implications for the pathogenesis of hereditary angioedema types I and II
Keywords: Bradykinin; factor XII; prekallikrein; kininogen; C1 inhibitor; APMSF; (p-Amidinophenyl)methanesulfonyl fluoride; C1-INH; C1 inhibitor; CTI; Corn trypsin inhibitor; HAE; Hereditary angioedema; HK; High-molecular-weight kininogen; Hsp90; Heat shock protein
ELISA for determination of total coagulation factor XII concentration in human plasma
Keywords: 4-PL; 4-parameter nonlinear logistic curve fitting; ANCOVA; analysis of covariance; APlC; anti phospholipid syndrome; B; within-laboratory standard deviation; C1-inh; complement C1 esterase inhibitor; CV; coefficient of variation; ELISA; enzyme linked imm
Hereditary Angioedema with Normal C1-INH (HAE Type III)
Keywords: Hereditary angioedema; normal C1-INH; type III; estrogen; diagnosis; treatment; factor XII mutation; ACE; Angiotensin-converting enzyme; C1-INH; C1 inhibitor; HAE; Hereditary angioedema; HAE-C1-INHdef; Hereditary angioedema due to C1 inhibitor deficienc
Multiple domains of MASP-2, an initiating complement protease, are required for interaction with its substrate C4
Keywords: CUB; complement C1r/C1s, Uegf, Bmp1-like domain; EGF; epidermal growth factor-like domain; CCP; complement control protein-like domain; SP; serine protease domain; Abz; 2-aminobenzoyl; Lys(Dnp); lysine dinitrophenyl; DMF; dimethyl formamide; MBL; mannose-
Brief CommunicationA novel mutation in the coagulation factor 12 gene in subjects with hereditary angioedema and normal C1-inhibitor
Keywords: aPTT; Activated partial thromboplastin time; bp; Base pair(s); C1-INH; C1-esterase inhibitor; DNA; Deoxyribonucleic acid; FXII; Coagulation factor XII; FXIIa; Activated coagulation factor XII; F12; Coagulation factor 12 gene; HAE; Hereditary angioedema; H
Ecallantide (DX-88) for acute hereditary angioedema attacks: Integrated analysis of 2 double-blind, phase 3 studies
Keywords: Ecallantide; Evaluation of DX-88's Effects in Mitigating Angioedema 3 and 4; hereditary angioedema; mean symptom complex severity; plasma kallikrein inhibitor; treatment outcome score; AE; Treatment-emergent adverse event; C1-INH; C1 esterase inhibitor;
MAp19, the alternative splice product of the MASP2 gene
Keywords: MBL; mannan-binding lectin; MASP; MBL-associated serine protease; MAp; MBL-associated protein; pAb; polyclonal antibody; MBS; m-maleimidobenzoyl-N-hydroxysuccinimid; DVS; divinylsulfone; PPD; purified protein derivative; HRP; horseradish peroxidase; KLH;
Efficacy of human C1 esterase inhibitor concentrate compared with placebo in acute hereditary angioedema attacks
Keywords: C1 inhibitor; C1-INH; C1 inhibitor deficiency; angioedema; hereditary angioedema; HAEC1-INH, C1 esterase inhibitor; HAE, Hereditary angioedema
Novel pathogenic mechanism and therapeutic approaches to angioedema associated with C1 inhibitor deficiency
Keywords: Angioedema; C1 inhibitor; complement; endothelial cells; vascular leakage; B1R; B2R; gC1QR; bradykinin; leakage assay; AAE; Acquired angioedema; ADMEC; Human adult dermal microvascular endothelial cell; APL; Attack phase plasma; B1R; Type 1 bradykinin rec
Elucidation of the substrate specificity of the MASP-2 protease of the lectin complement pathway and identification of the enzyme as a major physiological target of the serpin, C1-inhibitor
Keywords: NHMec; 7-amino-4-methyl coumarin group; Abz; 2-aminobenzoyl; Lys(Dnp); lysine dinitrophenyl; DMF; dimethyl formamide; PoPS; prediction of protease specificity program; MBL; mannose-binding lectin; MASP; mannose-binding lectin-associated serine protease; C
Critical role of kallikrein in hereditary angioedema pathogenesis: A clinical trial of ecallantide, a novel kallikrein inhibitor
Keywords: Ecallantide; bradykinin; C1 inhibitor; C1-INH; contact; hereditary angioedema; HAE; kallikrein; kininAE, Adverse event; APTT, Activated partial thromboplastin time; C1-INH, C1 esterase inhibitor; CTC, National Cancer Institute Common Toxicity Criteria; HA
Complement Factor 1 Inhibitor Improves Cardiopulmonary Function in Neonatal Cardiopulmonary Bypass
Keywords: A-a O2 gradient; arteriolar-alveolar oxygen gradient; C1-inh; complement factor 1 esterase inhibitor; CPB; cardiopulmonary bypass; dP/dt; time derivative of left ventricular pressure; ELISA; enzyme-linked immunosorbent assay; LV; left ventricle; PBS; phos
Genetic Test Indications and Interpretations in Patients With Hereditary Angioedema
Keywords: AAE; acquired angioedema; AAE-I; AAE type I; AAE-II; AAE type II; ACE; angiotensin-converting enzyme; C1-INH; C1 inhibitor; É-ACA; É-aminocaproic acid; FFP; fresh frozen plasma; HAE; hereditary angioedema; HAE-I; hereditary angioedema type I; HAE-II; he
Functional analysis of the classical, alternative, and MBL pathways of the complement system: standardization and validation of a simple ELISA
Keywords: AAE; acquired angioedema; AGN; acute poststreptococcal glomerulonephritis; AP; alternative pathway; C1-INH; C1 inhibitor; C3NeF; C3 nephritic factor; CP; classical pathway; HAE; hereditary angioedema; HUVS; hypocomplementaemic urticarial vasculitis syndro
Complement activation-related pseudoallergy: A new class of drug-induced acute immune toxicity
Keywords: C; complement; CARPA; complement activation-related pseudoallergy; C1-INH; C1-esterase inhibitor; CrEL; Cremophor EL; HSR; hypersensitivity reaction; MLV; large multilamellar vesicles; PEG; polyethylene glycol; RCM; radiocontrast media; SC5b-9; S protein-