Diagnosis, Course, and Management of Angioedema in Patients With Acquired C1-Inhibitor Deficiency

The incidence of C1-INH-AAE was 1 for every 8.8 patients with C1-INH-HAE. Thirty percent of the deaths were related to the disease. Treatments approved for C1-INH-HAE are effective in C1-INH-AAE, although with minimal differences.