Keywords: C1 بازدارنده; FB; factor B; TCC; terminal complement complex; FH; factor H; Clu; clusterin; C1Inh; C1 inhibitor; CRP; C-reactive protein; ELISA; enzyme linked immunosorbent assay; AED; anti-epileptic drugs; CNS; central nervous system; WNRTB; Wales Neuroscience Researc
مقالات ISI C1 بازدارنده (ترجمه نشده)
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Keywords: C1 بازدارنده; Hereditary angioedema; Bradykinin; C1 inhibitor deficiency; Bradykinin B2 receptor antagonist; Icatibant; Children; Adolescents; Pediatrics; Treatment; AE; adverse event; C1-INH; C1 inhibitor; C1-INH-HAE; hereditary angioedema with C1-inhibitor deficiency
Keywords: C1 بازدارنده; Contact system; Hereditary angioedema; C1 inhibitor; Bradykinin; C4; C1 inhibitor complexes; Vascular permeability;
Keywords: C1 بازدارنده; Prophylaxis; Hereditary angioedema; Androgens; Tranexamic acid; Progestagens; C1 inhibitor;
Keywords: C1 بازدارنده; Pediatric hereditary angioedema; Hereditary angioedema; Age onset; C1-INH; C1 inhibitor; CCHMC; Cincinnati Children's Hospital Medical Center; EMR; Electronic medical records; ER; Emergency room; HAE; Hereditary angioedema; IQR; Interquartile range; pdC1I
Keywords: C1 بازدارنده; MAC; membrane attack complex; TGF-β; transforming growth factor β; TLR; toll-like receptor; MDSC; myeloid-derived suppressor cells; Tregs; regulatory T cells; AMD; age-related macular degeneration; C1-INH; C1 inhibitor; Complement system; Cancer therapy
A missense mutation in the plasminogen gene, within the plasminogen kringle 3 domain, in hereditary angioedema with normal C1 inhibitor
Keywords: C1 بازدارنده; Hereditary angioedema; Plasminogen; Kringle domain; C1 inhibitor; Coagulation factor XII; Missense mutation;
Hereditary Angioedema with Normal C1 Inhibitor and F12 Mutations in 42 Brazilian Families
Keywords: C1 بازدارنده; Hereditary angioedema; Normal C1 inhibitor; F12 mutations; Estrogen; Brazilian population; ACEI; Angiotensin-converting enzyme inhibitor; C1-INH; C1 inhibitor; C1-INH-HAE; Hereditary angioedema with C1 inhibitor deficiency; eOC; Estrogen-containing oral c
Mutation of the angiopoietin-1 gene (ANGPT1) associates with a new type of hereditary angioedema
Keywords: C1 بازدارنده; Hereditary angioedema; angiopoietin-1; gene; mutation; multimers; tunica interna endothelial cell kinase 2 receptor; ANGPT1; Angiopoietin-1; ANGPT2; Angiopoietin-2; C1-INH; C1 inhibitor; C1-INH-HAE; Hereditary angioedema caused by C1 inhibitor deficiency;
Cytokine and estrogen stimulation of endothelial cells augments activation of the prekallikrein-high molecular weight kininogen complex: Implications for hereditary angioedema
Keywords: C1 بازدارنده; Hereditary angioedema; C1 inhibitor; bradykinin; heat shock protein 90; APMSF; (4-Amidinophenyl)-methanesulfonyl fluoride; HAE; Hereditary angioedema; HK; High molecular weight kininogen; PAI-2; Plasminogen activator inhibitor-2; TPA; Tissue plasminogen a
Identification and characterization of C1 inhibitor in Nile tilapia (Oreochromis niloticus) in response to pathogenic bacteria
Keywords: C1 بازدارنده; Oreochromis niloticus; C1 inhibitor; Immune response; Streptococcus agalactiae; Monocytes/macrophages;
C1 Inhibitor as a glycoprotein: The influence of polysaccharides on its function and autoantibody target
Keywords: C1 بازدارنده; AAE, acquired angioedema; C1Inh, C1 Inhibitor; C1Inh-HAE, hereditary angioedema with C1 Inhibitor deficiency; FXII, Factor XII; FXIIa, activated Factor XII; HAE, hereditary angioedema; HK, high-molecular-weight kininogenAcquired angioedema; C1 inhibitor;
Mechanisms of allergy and clinical immunologyDeficiency of plasminogen activator inhibitor 2 in plasma of patients with hereditary angioedema with normal C1 inhibitor levels
Keywords: C1 بازدارنده; Hereditary angioedema; C1 inhibitor; bradykinin; plasminogen activator inhibitor; BCIP/NBT; 5-Bromo-4-chloroindolyl phosphate/nitroblue tetrazolium; C1-INH; C1 inhibitor; HAE; Hereditary angioedema; HAE-N; Hereditary angioedema with normal C1 inhibitor le
Safety and Usage of C1-Inhibitor in Hereditary Angioedema: Berinert Registry Data
Keywords: C1 بازدارنده; Berinert; Plasma-derived C1-INH; Patient registry; Thromboembolic event; Real-world; Prophylaxis; On demand; Self-administration; Safety; Dosing; AE; Adverse event; C1-INH; C1 inhibitor; DVT; Deep vein thrombosis; EU; European Union; HAE; Hereditary angio
Psychometric Field Study of Hereditary Angioedema Quality of Life Questionnaire for Adults: HAE-QoL
Keywords: C1 بازدارنده; Disease-specific; Quality of life; Hereditary angioedema; C1 inhibitor; Questionnaire; Validation studies; Psychometric; Adults; HAE-QoL; SF-36v2; AE-QoL; Angioedema quality of life questionnaire; C1-INH-HAE; Hereditary angioedema due to C1 inhibitor defi
Tolerability and Effectiveness of 17-α-Alkylated Androgen Therapy for Hereditary Angioedema: A Re-examination
Keywords: C1 بازدارنده; 17-α-Alkylated androgen; Hereditary angioedema; Treatment; Effectiveness; Side effects; C1 inhibitor; Severity; Danazol; Prophylaxis; AA; 17-α-Alkylated androgens; C1INH; C1 inhibitor; HAE; Hereditary angioedema; HAE-nl-C1INH; HAE with normal C1 inhibit
The autoimmune side of hereditary angioedema: insights on the pathogenesis
Keywords: C1 بازدارنده; Autoimmunity; C1 inhibitor; Complement system; Hereditary angioedema; Systemic lupus erythematosus
Comparison of Chromogenic and ELISA Functional C1 Inhibitor Tests in Diagnosing Hereditary Angioedema
Keywords: C1 بازدارنده; Hereditary angioedema; C1 inhibitor; Complement testing; C1 INH; C1 inhibitor; HAE; Hereditary angioedema;
Exploration biologique des angiÅdèmes à kinines
Keywords: C1 بازدارنده; AngiÅdème; Bradykinine; C1 inhibiteur; Kininoformation; Kininases; Phase contact; Angioedema; Bradykinin; C1 inhibitor; Kinin formation; Kininases; Contact Phase;
Characterization of patients with angioedema without wheals: The importance of F12 gene screening
Keywords: C1 بازدارنده; C1-INH; C1 inhibitor; HAE; hereditary angioedema; FXII-HAE; hereditary angioedema with factor XII mutation; U-HAE; hereditary angioedema with unknown genetic mutation; InH-AAE; idiopathic non-histaminergic acquired angioedema; SERPING1; serpin peptidase i
Molecular phylogeny of C1 inhibitor depicts two immunoglobulin-like domains fusion in fishes and ray-finned fishes specific intron insertion after separation from zebrafish
Keywords: C1 بازدارنده; C1 inhibitor; Serpin G1; Group V4; Synteny; Phylogenetic analysis; Intron gain;
A C1 inhibitor ortholog from rock bream (Oplegnathus fasciatus): Molecular perspectives of a central regulator in terms of its genomic arrangement, transcriptional profiles and anti-protease activities of recombinant peptide
Keywords: C1 بازدارنده; C1 inhibitor; Oplegnathus fasciatus; Genomic and promoter organization; Spatial and temporal transcriptional analysis; Anti-protease activity;
Factor XII-independent activation of the bradykinin-forming cascade: Implications for the pathogenesis of hereditary angioedema types I and II
Keywords: C1 بازدارنده; Bradykinin; factor XII; prekallikrein; kininogen; C1 inhibitor; APMSF; (p-Amidinophenyl)methanesulfonyl fluoride; C1-INH; C1 inhibitor; CTI; Corn trypsin inhibitor; HAE; Hereditary angioedema; HK; High-molecular-weight kininogen; Hsp90; Heat shock protein
Angiœdème récurrent : démarche diagnostique et place de la biologie
Keywords: C1 بازدارنده; Angiœdème; Urticaire; Histamine; Bradykinine; C1Inh; DiagnosticAngioedema; Histamine; Bradykinin; Urticaria; Diagnosis; C1 inhibitor
Hereditary Angioedema with Normal C1-INH (HAE Type III)
Keywords: C1 بازدارنده; Hereditary angioedema; normal C1-INH; type III; estrogen; diagnosis; treatment; factor XII mutation; ACE; Angiotensin-converting enzyme; C1-INH; C1 inhibitor; HAE; Hereditary angioedema; HAE-C1-INHdef; Hereditary angioedema due to C1 inhibitor deficienc
Update on Preventive Therapy (Prophylaxis) for Hereditary Angioedema
Keywords: C1 بازدارنده; Hereditary angioedema; Prophylaxis; C1 inhibitor; Androgens; Antifibrinolytics;
Treatment of Laryngeal Hereditary Angioedema
Keywords: C1 بازدارنده; angioedema; hereditary angioedema; HAE; laryngeal; C1 inhibitor
Hereditary Angioedema in Japan: Genetic Analysis of 13 Unrelated Cases
Keywords: C1 بازدارنده; Hereditary angioneuroedema; C1 inhibitor; Mutation
Urticaire/angioedème histaminique ou bradykinique ?
Keywords: C1 بازدارنده; Urticaire; Angioedème; Bradykinique; Histaminique; C1 inhibiteurUrticaria; Angioedema; Bradykinin; Histaminergic; C1 inhibitor
Safety and Efficacy of Prophylactic Nanofiltered C1-inhibitor in Hereditary Angioedema
Keywords: C1 بازدارنده; C1 inhibitor; Concentrate; Hereditary angioedema; Prophylaxis; Therapy;
Actualités biologiques sur les angioedèmes à kinines
Keywords: C1 بازدارنده; Exploration angioedème; kinines; kininogénase; kininase; perméabilité endothéliale; C1 inhibiteur; facteur XII; Angioedema exploration; kinins; kininogenase; kininase; endothelial permeability; C1 inhibitor; factor XII; BK; bradykinine; C1Inh; C1 inh
Immunotherapy for Primary Immunodeficiency Diseases
Keywords: C1 بازدارنده; Antibody deficiency; Immunoglobulin therapy; Common variable immunodeficiency; Hereditary angioedema; C1 inhibitor;
Long-term follow up analysis of nadroparin for hereditary angioedema. A preliminary report
Keywords: C1 بازدارنده; C1 inhibitor; Complement; Heparin; Hereditary angioedema; Nadroparin
SERPING1 mutations in 59 families with hereditary angioedema
Keywords: C1 بازدارنده; C1Inh; C1 inhibitor protein; C1NH; C1 inhibitor locus; HAE; hereditary angioedema; RCL; reactive center loop; Hereditary angioedema; C1 Inhibitor; Complement; Rare diseases; Mutational spectrum;
MAp19, the alternative splice product of the MASP2 gene
Keywords: C1 بازدارنده; MBL; mannan-binding lectin; MASP; MBL-associated serine protease; MAp; MBL-associated protein; pAb; polyclonal antibody; MBS; m-maleimidobenzoyl-N-hydroxysuccinimid; DVS; divinylsulfone; PPD; purified protein derivative; HRP; horseradish peroxidase; KLH;
Pancreatitis aguda asociada a angioedema hereditario
Keywords: C1 بازدارنده; Angioedema hereditario; Pancreatitis; Factor C1 inhibidor; Hereditary angioedema; Pancreatitis; C1 inhibitor;
Subcutaneous infusion of human C1 inhibitor in swine
Keywords: C1 بازدارنده; Hereditary angioedema; C1 inhibitor; Pig; Subcutaneous;
The plasma bradykinin-forming pathways and its interrelationships with complement
Keywords: C1 بازدارنده; Bradykinin; Kininogen; Prekallikrein; Complement; Anaphylatoxin; C1 Inhibitor; gC1qR; Factor XII;
Factor XII–independent cleavage of high-molecular-weight kininogen by prekallikrein and inhibition by C1 inhibitor
Keywords: C1 بازدارنده; Factor XII; prekallikrein; kininogen; C1 inhibitor; angioedemaAPMSF, (4-Amidinophenyl)-methanesulfonyl fluoride; C1INH, C1 inhibitor; CTI, Corn trypsin inhibitor; DFP, Diisofluorophosphate; HAE, Hereditary angioedema; HBS, HEPES-buffered saline; HK, High-
Efficacy of human C1 esterase inhibitor concentrate compared with placebo in acute hereditary angioedema attacks
Keywords: C1 بازدارنده; C1 inhibitor; C1-INH; C1 inhibitor deficiency; angioedema; hereditary angioedema; HAEC1-INH, C1 esterase inhibitor; HAE, Hereditary angioedema
Novel pathogenic mechanism and therapeutic approaches to angioedema associated with C1 inhibitor deficiency
Keywords: C1 بازدارنده; Angioedema; C1 inhibitor; complement; endothelial cells; vascular leakage; B1R; B2R; gC1QR; bradykinin; leakage assay; AAE; Acquired angioedema; ADMEC; Human adult dermal microvascular endothelial cell; APL; Attack phase plasma; B1R; Type 1 bradykinin rec
Peut-on proposer un acte de chirurgie esthétique à un(e) patient(e) atteint(e) d'un Ådème angioneurotique ?
Keywords: C1 بازدارنده; Ådème angioneurotique; Androgènes de synthèse; C1 inhibiteur; Prothèses mammaires; Hereditary angio-oedema; Attenuated androgens; C1 inhibitor; Breast implants;
8. Hereditary angioedema
Keywords: C1 بازدارنده; Hereditary angioedema; bradykinin; C1 inhibitor; C1 esterase inhibitor; complement; androgens; antifibrinolytics; danazolACE, Angiotensin-converting enzyme; C1 Inh, C1 inhibitor; EACA, ɛ-Aminocaproic acid; HAE, Hereditary angioedema
Metallopeptidase activities in hereditary angioedema: Effect of androgen prophylaxis on plasma aminopeptidase P
Keywords: C1 بازدارنده; Hereditary angioedema; aminopeptidase P; C1 inhibitor; androgen; danazol; stanozolol; bradykinin; des-Arg9-bradykininACE, Angiotensin I–converting enzyme; APP, Aminopeptidase P; C1-INH, C1 inhibitor; CPN, Carboxypeptidase N; des-Arg9-BK, Des-Arg9-bradykin
Anti-vascular permeability of the cleaved reactive center loop within the carboxyl-terminal domain of C1 inhibitor
Keywords: C1 بازدارنده; C1 inhibitor; Lipopolysaccharide; Endothelial cell; Adhesion molecule
Mutation screening of C1 inhibitor gene in 108 unrelated families with hereditary angioedema: Functional and structural correlates
Keywords: C1 بازدارنده; C1 inhibitor; Complement; Hereditary angioedema; Mutations; Serpins
Critical role of kallikrein in hereditary angioedema pathogenesis: A clinical trial of ecallantide, a novel kallikrein inhibitor
Keywords: C1 بازدارنده; Ecallantide; bradykinin; C1 inhibitor; C1-INH; contact; hereditary angioedema; HAE; kallikrein; kininAE, Adverse event; APTT, Activated partial thromboplastin time; C1-INH, C1 esterase inhibitor; CTC, National Cancer Institute Common Toxicity Criteria; HA
The deficiency of C1 inhibitor and its treatment
Keywords: C1 بازدارنده; C1 inhibitor; Hereditary angioedema; Dx-88; Icatibant; Danazol; Tranexamic acid;
C1 inhibitor: Biologic activities that are independent of protease inhibition
Keywords: C1 بازدارنده; C1 inhibitor; Cecal ligation and puncture model; Endotoxin shock; Gram negative bacterial sepsis; Selectins; Serine proteinase inhibitors; CEA; carcinoembryonic antigen; CLP; cecal ligation and puncture; LBP; LPS-binding protein; LPS; lipopolysaccharide;
Missense mutations in the coagulation factor XII (Hageman factor) gene in hereditary angioedema with normal C1 inhibitor
Keywords: C1 بازدارنده; Factor XII; Hageman factor; F12; Intrinsic coagulation pathway; Angioedema; C1 inhibitor; Kinin system; Bradykinin; Contact activation; Coagulation