
Keywords: کوآنزیم A; VLCFA; very-long-chain fatty acid; ACP; acyl carrier protein; CoA; coenzyme A; KCS; KETOACYL-COA SYNTHASE; KCR; KETOACYL-COA REDUCTASE; HCD; HYDROXYACYL-COA DEHYDRATASE; ECR; ENOYL-COA REDUCTASE; ELO; ELONGATION DEFECTIVE; CER2; ECERIFERUM2; LACS; LONG-CH