Keywords: بیماری Creutzfeldt-Jakob; PrP; prion protein; PrPC; normal cellular isoform of PrP; PrPSc; abnormal misfolded isoform of PrP; CJD; Creutzfeldt Jakob disease; sCJD; sporadic CJD; dCJD; dura mater graft-associated CJD; p-dCJD; plaque-type dCJD; np-dCJD; non-plaque-type dCJD; 129M/M;
مقالات ISI بیماری Creutzfeldt-Jakob (ترجمه نشده)
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Keywords: بیماری Creutzfeldt-Jakob; Parkinsonism; Lenalidomide; Creutzfeldt-Jakob disease; Prion disease;
Keywords: بیماری Creutzfeldt-Jakob; Inherited prion disease; Creutzfeldt-Jakob disease; Prion protein; Rare gene variant; Novel gene variant interpretation;
Keywords: بیماری Creutzfeldt-Jakob; AA; amino acid; Aβo; oligomeric β-amyloid; Aβ; β-amyloid; AD; Alzheimer's disease; α7nAChR; α7 nicotinic acetylcholine receptor; ALS; amyotrophic lateral sclerosis; APLP1; amyloid beta precursor-like protein 1; APP; amyloid precursor protein; β-A
Keywords: بیماری Creutzfeldt-Jakob; α-Syn; α-synuclein; Aβ; beta-amyloid; AD; Alzheimer's disease; AON; anterior olfactory nucleus; ALS; amyotrophic lateral sclerosis; APP; amyloid precursor protein; CBD; corticobasal degeneration; CJD; Creutzfeldt-Jakob disease; DLB; dementia with Lewy
Keywords: بیماری Creutzfeldt-Jakob; Brain biopsy; Cerebellar ataxia; Creutzfeldt-Jakob disease; Brownell-Oppenheimer syndrome;
Keywords: بیماری Creutzfeldt-Jakob; CDC; Centers for Disease Control and Prevention; CJD; Creutzfeldt-Jakob disease; HCV; hepatitis C virus; HIV; human immunodeficiency virus; HSV; herpes simplex virus; PFU; plaque-forming unit; ppm; parts per million; vCJD; variant Creutzfeldt-Jakob diseas
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Overlap Parasomnias; Status Dissociatus; Videopolisomnography; CJD; Creutzfeldt-Jakob Disease; CSF; cerebrospinal fluid; CT; computed tomography; EEG; electroencephalogram; EMG; electromyogram; EOG; electroculogram; MRI; Magneti
Keywords: بیماری Creutzfeldt-Jakob; Neuropsychiatric disturbances; Infectious diseases; Delirium; HIV-AIDS; Pediatric autoimmune neuropsychiatric disorders associated with streptococcal infections; Herpes simplex encephalitis; Neurocysticercosis; Neurosyphilis; Creutzfeldt-Jakob disease; N
Keywords: بیماری Creutzfeldt-Jakob; Prion; Prion-seeding activity; SD50; Non-neural tissue; Creutzfeldt-Jakob disease;
Keywords: بیماری Creutzfeldt-Jakob; α-syn; α-synuclein; Aβ; β-amyloid; AD; Alzheimer's disease; ADAMs; a disintegrin and metalloproteinases; ALS; amyotrophic lateral sclerosis; BSE; bovine spongiform encephalopathy; CJD; Creutzfeldt-Jakob disease; CNS; central nervous system; CSF; cer
Keywords: بیماری Creutzfeldt-Jakob; BSE; bovine spongiform encephalopathy; cAMP; cyclic adenosine monophosphate; CJD; Creutzfeldt-Jakob disease; CSF; cerebrospinal fluid; EM; electron microscopy; ER; endoplasmic reticulum; ERK1/2; extracellular signal-regulated protein kinases 1 and 2; GPI;
Keywords: بیماری Creutzfeldt-Jakob; AMPA; α-amino-3-hydroxy-5-methyl-4-isoxazolepropionic acid; BSE; bovine spongiform encephalopathy; CJD; Creutzfeldt-Jakob disease; vCJD; the variant of CJD; F14; PrP knockout fusion cell line; F21; wild-type fusion cell line; ICP-MS; inductively-coupled
Keywords: بیماری Creutzfeldt-Jakob; bénéfice/risque; déficit; hormone de croissance humaine; maladie de Creutzfeldt-Jakob; somatropinebenefit/risk; Creutzfeldt-Jakob disease; deficiency; human growth hormone; somatropin
Keywords: بیماری Creutzfeldt-Jakob; Prion diseases; Infectious forms; Prion strains; Creutzfeldt-Jakob disease; Kuru;
Keywords: بیماری Creutzfeldt-Jakob; Autoimmune cerebellitis; CLIPPERS; Creutzfeldt-Jakob disease; Epstein-Barr virus; Influenza; JC virus granule cell neuronopathy; Listeria rhombencephalitis; Progressive multifocal leukoencephalopathy;
Apolipoprotein E genotypes and longevity across dementia disorders
Keywords: بیماری Creutzfeldt-Jakob; Apolipoprotein E; Alzheimer's disease; Dementia with Lewy bodies; Vascular dementia; Frontotemporal dementia; Parkinson's disease dementia; Creutzfeldt-Jakob disease;
Atypical presentation of probable Creutzfeldt-Jakob disease associated with anti-Zic4 antibody: Literature review of neuronal antibodies in Creutzfeldt-Jakob disease
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Neuronal antibodies; Anti-Zic4 antibody; Autoimmune encephalitis; Stroke-like symptoms;
Reply to: Amyotrophic lateral sclerosis with frontotemporal dementia (ALS-FTD) syndrome as a phenotype of Creutzfeldt-Jakob disease (CJD)? A case report
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Frontotemporal dementia; Amyotrophic lateral sclerosis; Real-time quaking-induced conversion assay;
Plasma-derived products and Creutzfeldt-Jakob disease: Comparison of legislation around the world
Keywords: بیماری Creutzfeldt-Jakob; Legislations comparison; Patients and prescribers information; Creutzfeldt-Jakob disease; Plasma-derived products; Blood donors selection; Comparaison des législations; Information des patients et des prescripteurs; Maladie de Creutzfeldt-Jakob; Médicam
Mitochondrial DNA differentiates Alzheimer's disease from Creutzfeldt-Jakob disease
Keywords: بیماری Creutzfeldt-Jakob; Mitochondrial DNA; Cerebrospinal fluid; Creutzfeldt-Jakob disease; Alzheimer's disease; Biomarker; Digital PCR;
Consideraciones perioperatorias para la realización de una biopsia cerebral en un paciente con enfermedad de Creutzfeldt-Jakob esporádica subtipo VV2
Keywords: بیماری Creutzfeldt-Jakob; Anestesia; Enfermedad de Creutzfeldt-Jakob; Procedimientos quirúrgicos; EncefalopatÃa espongiforme transmisible; Control de la infección; Biopsia cerebral; Anesthesia; Creutzfeldt-Jakob disease; Surgical procedures; Transmissible spongiform encephalopa
Le diagnostic de maladie de Creutzfeldt-Jakob est-il facile ?
Keywords: بیماری Creutzfeldt-Jakob; Maladie de Creutzfeldt-Jakob; Maladie à prions sporadiques; Examens complémentaires; Diagnostic; Creutzfeldt-Jakob disease; Sporadic prionopathy; Diagnosis procedures;
Comparison of the clinical course of Japanese MM1-type sporadic Creutzfeldt-Jakob disease between subacute spongiform encephalopathy and panencephalopathic-type
Keywords: بیماری Creutzfeldt-Jakob; Akinetic mutism state; Creutzfeldt-Jakob disease; MM1-type; Myoclonus; Periodic sharp-wave complexes; Tube-feeding;
Association of prion protein genotype and scrapie prion protein type with cellular prion protein charge isoform profiles in cerebrospinal fluid of humans with sporadic or familial prion diseases
Keywords: بیماری Creutzfeldt-Jakob; Biomarker; Creutzfeldt-Jakob disease; PrPC charge isoforms; Truncated PrPC forms;
Special Needs Populations: Perioperative Care of the Patient With Creutzfeldt-Jakob Disease
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; CJD; prion; neurosurgery; diagnostic biopsy; infection prevention; disinfection and sterilization;
An overview of the diagnostic tools
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob Disease; PrPTSE; vCJD; Detection; Confirmation; PMCA; QuIC,Maladie de Creutzfeldt-Jakob; PrPEST; vMCJ; Détection; Confirmation; PMCA; QuIC,
Risk of transmission of Creutzfeldt-Jakob disease via blood and blood products. The French risk-analysis over the last 15 years
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Transmissible spongiform encephalopathy; Risk analysis; Transfusion-related risk; Plasma-derived medicinal productsMaladie de Creutzfeldt-Jakob; Encéphalopathie spongiforme transmissible; Analyse de risque; Risque transfusionnel
Once upon a Cataract Surgeon
Keywords: بیماری Creutzfeldt-Jakob; 14-3-3; Creutzfeldt-Jakob disease; diffusion-weighted imaging; diplopia; neurocognitive
Alteration of the endocannabinoid system in mouse brain during prion disease
Keywords: بیماری Creutzfeldt-Jakob; prion; endocannabinoid; cannabinoid receptor; neurodegenerative disease; brain; mouse; AEA; arachidonoylethanolamide or anandamide; CBD; cannabidiol; CBR; cannabinoid receptor; CJD; Creutzfeldt-Jakob disease; GAPDH; glyceraldehyde-3-phosphate dehydrogenas
Usefulness of high b-value diffusion-weighted MRI in the diagnosis of Creutzfeldt-Jakob disease
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; MRI; Magnetic resonance imaging; Diffusion-weighted imaging; DWI; b valueEnfermedad de Creutzfeldt-Jakob; Resonancia magnética cerebral; Secuencias potenciadas en difusión; DWI; Valor b
14-3-3 proteins in neurodegeneration
Keywords: بیماری Creutzfeldt-Jakob; TH; tyrosine hydroxylase; 3â²UTR; three prime untranslated region; CSF; cerebrospinal fluid; 2D-PAGE; two-dimensional polyacrylamide gel electrophoresis; PD; Parkinson disease; AD; Alzheimer disease; CJD; Creutzfeldt-Jakob disease; MSA; multiple system a
Rare E196K mutation in the PRNP gene of a patient exhibiting behavioral abnormalities
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Transmissible spongiform encephalopathies; Genetic; Prion protein gene; PRNP; Point mutation
Featured ArticleCerebrospinal fluid biomarker results in relation to neuropathological dementia diagnoses
Keywords: بیماری Creutzfeldt-Jakob; Alzheimer disease; Amyloid; Autopsy; Biochemical markers; Creutzfeldt-Jakob disease; Frontotemporal dementia; Lewy body disease; Neuropathology; Tau; Vascular dementia;
Prion Diseases
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Prion diseases; Rapidly progressive dementia; Transmissible spongiform encephalopathies;
Hyperparathyroïdie primitive : un diagnostic différentiel de la maladie de Creutzfeldt-Jakob
Keywords: بیماری Creutzfeldt-Jakob; Démence; Maladie de Creutzfeldt-Jakob; Hypercalcémie; Hyperparathyroïdie primitive; Dementia; Creutzfeldt-Jakob disease; Hypercalcemia; Primary hyperparathyroidism;
Apport de l'IRM de diffusion dans le diagnostic de la maladie de Creutzfeldt-Jakob sporadique
Keywords: بیماری Creutzfeldt-Jakob; Maladie de Creutzfeldt-Jakob sporadique; IRM; Séquences de diffusion; Creutzfeldt-Jakob disease; Magnetic resonance imaging; Diffusion-weighted imaging;
Enfermedad de Creutzfeldt-Jakob: hallazgos en resonancia magnética
Keywords: بیماری Creutzfeldt-Jakob; Resonancia magnética; Enfermedad de Creutzfeldt-Jakob; Difusión; Demencia; Encéfalo; Magnetic resonance imaging; Creutzfeldt-Jakob disease; Diffusion; Dementia; Brain;
The diagnostic efficiency of biomarkers in sporadic Creutzfeldt-Jakob disease compared to Alzheimer's disease
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Alzheimer's disease; Tau; Phosphorylated tau; 14-3-3 protein; Neuron-specific enolase; Cerebrospinal fluid; Biomarker
Imagerie de la maladie de Creutzfeldt-Jakob
Keywords: بیماری Creutzfeldt-Jakob; Maladie de Creutzfeldt-Jakob; IRM; Creutzfeldt-Jakob disease; MR;
MRI and FDG PET/CT findings in a case of probable Heidenhain variant Creutzfeldt-Jakob disease
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Heidenhain variant; Magnetic resonance imaging; 18F-FDG positron emission tomography (PET)Maladie de Creutzfeldt-Jakob; Variant Heidenhain; Imagerie par résonance magnétique; Tomographie par émission de positons (TEP)/TDM au FDG
Phenotypic similarities causing clinical misdiagnosis of pathologically-confirmed sporadic Creutzfeldt-Jakob disease as dementia with Lewy bodies
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Dementia with Lewy bodies; Diagnosis;
A Patient With Creutzfeldt-Jakob Disease With an Insertion of 7 Octa-Repeats in the PRNP Gene: Molecular Characteristics and Clinical Features
Keywords: بیماری Creutzfeldt-Jakob; Creutzfeldt-Jakob disease; Octapeptide; Proteinase K-resistant prion protein;
Correlation between periodic sharp wave complexes and diffusion-weighted magnetic resonance images in early stage of Creutzfeldt-Jakob disease: A report of two cases
Keywords: بیماری Creutzfeldt-Jakob; EEG; Periodic sharp wave complexes; LORETA; MRI; Creutzfeldt-Jakob disease
High titers of mucosal and systemic anti-PrP antibodies abrogate oral prion infection in mucosal-vaccinated mice
Keywords: بیماری Creutzfeldt-Jakob; scrapie; immunization; salmonella vaccine strain; Creutzfeldt-Jakob disease; bovine spongiform encephalopathy; chronic wasting diseaseBSE, bovine spongiform encephalopathy; CFA, complete Freund's adjuvant; CWD, chronic wasting disease; ELISA, enzyme-linke
Increased oxidation, glycoxidation, and lipoxidation of brain proteins in prion disease
Keywords: بیماری Creutzfeldt-Jakob; AASA; aminoadipic semialdehyde; BSE; bovine spongiform encephalopathy; CEL; N-É-carboxyethyllysine; CJD; Creutzfeldt-Jakob disease; CML; N-É-carboxymethyllysine; DBI; double bond index; GSA; glutamic semialdehyde, 4-HNE, 4-hydroxynonenal; MCO; metal-cat
A role for His155 in binding of human prion peptide144–167 to immobilised prion protein
Keywords: بیماری Creutzfeldt-Jakob; Prion; Transmissible spongiform encephalopathy; Creutzfeldt-Jakob disease; Surface plasmon resonance; Peptides
Las encefalopatias espongiformes o enfermedades por priones en el pais vasco
Keywords: بیماری Creutzfeldt-Jakob; EncefalopatÃas espongiformes; prion; enfermedad de Creutzfeldt-Jakob; Insomnio Letal Familiar; Spongiform encephalopathies; prion; Creutzfeldt-Jakob disease; Fatal Familial Insomnia; Entzefalopatia espongiformeak; priona; Creutzfeldt-Jakob-en gaixotasuna
The neurochemical nature of PrPc-containing cells in the rat brain
Keywords: بیماری Creutzfeldt-Jakob; CB; calbindin; CBP; calcium-binding proteins; CJD; Creutzfeldt-Jakob disease; CR; calretinin; FFI; Fatal Familial Insomnia; PNN; perineuronal nets; PrPC; cellular prion protein; PrPSc; scrapie prion protein; PV; parvalbumin; TSEs; transmissible spongiform
The prion strain phenomenon: Molecular basis and unprecedented features
Keywords: بیماری Creutzfeldt-Jakob; Prions; Prion strains; Protein misfolding; Scrapie; Creutzfeldt-Jakob disease