Coenzyme Q10 deficiency in mitochondrial DNA depletion syndromes
Keywords: کروماتوگرافی مایع با فشار بالا; CoQ; Coenzyme Q10; MDS; mitochondrial DNA depletion syndromes; HPLC; high pressure liquid chromatography; mtDNA; mitochondrial DNA; MRC; mitochondrial respiratory chain; CS; citrate synthase; Mitochondrial DNA depletion syndrome; Coenzyme Q10 deficiency;