Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; Plin; perilipin; PPAR; peroxisome proliferator-activated receptor; SREBP1c; sterol regulatory element-binding transcription factor 1c; ChREBP; carbohydrate response element binding protein; SCD1; stearoyl-CoA desaturase 1; ACSL1; long-chain acyl-CoA synth
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Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; ABC; ATP-binding cassette transporter; ACACA; acetyl-CoA carboxylase α; ACACB; acetyl-CoA carboxylase β, ACLY, ATP citrate lyase; ACADM; medium-chain acyl-CoA dehydrogenase; ACOX1; acyl-CoA oxidase 1; AFB1; aflatoxin B1; AMPK; adenosine monophosphate-ac
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; FA; fatty acid; FABP; fatty acid binding protein; WT; wild type; DKO; double knock out; LPS; lipopolysaccharide; TCA; tricarboxylic acid; TNF-α; tumor necrotic factor-α; IL-1β; interleukin-1β; ATP; adenosine triphosphate; TG; triacylglycerol; NEFA; no
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; Lysosome-associated membrane protein-2; Autophagy; Diabetes; Obesity; Lysosome; ATF4; activating transcription factor 4; ACO; acyl-CoA oxidase; BAT; brown adipose tissue; Cidea; cell death-inducing DNA fragmentation factor-α-like effector A; FGF21; fibro
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; A; adenine; ACMG; American College of Medical Genetics; Ala; alanine; Asp; aspartic acid; BCL2L12; B-cell lymphoma-2-like protein 12; BRCA1; breast cancer-1 gene; C; cytosine; CCDS; Consensus Coding Sequence; CD; circular dichroism; CDC; coding sequence;
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; DBSs; dried blood spots; CPT-1; carnitine palmitoyltransferase 1; VLCAD; very-long-chain acyl-CoA dehydrogenase; LCHAD; long-chain 3-hydroxyacyl-CoA dehydrogenase; MCAD; medium-chain acyl-CoA dehydrogenase; PA; propionic acidemia; MMA; methylmalonic acide
Serine prevented high-fat diet-induced oxidative stress by activating AMPK and epigenetically modulating the expression of glutathione synthesis-related genes
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; Acadm; medium-chain acyl-CoA dehydrogenase; AMPKα; AMP-activated protein kinase, α subunit; AST; aspartate aminotransferase; ALT; alanine aminotransferase; BSO; buthionine sulfoximine; CBS; cystathionine-β-synthetase; CPT1a; carnitine palmitoyltransfer
High-fat diet alters PAS kinase regulation by fasting and feeding in liver
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; ACC; acetyl CoA carboxylase; Akt/PKB; protein kinase B; CHREBP; carbohydrate-responsive element-binding protein; CPT1-A; carnitine palmitoyltransferase 1A; DAPI; 4,6-diamidino-2-phenylindole; FAS; fatty acid synthase; FOXO1; forkhead box protein O1; GCK;
Pirin: A novel redox-sensitive modulator of primary and secondary metabolism in Streptomyces
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; 2D-DIGE; 2D-differential gel electrophoresis; ACAD; acyl-CoA dehydrogenase; ACT; actinorhodin; ANOVA; analysis of variance; Att/Int; attachment/integration; CHAPS; 3-[(3-cholamidopropyl)dimethylammonio]-1-propanesulfonate; DTT; dithiothreitol; CID; collis
Muscle-specific knockout of general control of amino acid synthesis 5 (GCN5) does not enhance basal or endurance exercise-induced mitochondrial adaptation
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; Acetylation; GCN5; Mitochondria; SIRT1; Deacetylase; PGC-1α; AMP; adenosine monophosphate; Ca2+; calcium; CBP; CREB-binding protein; Cre-MCK; creatine kinase promoter; CHO; carbohydrate; DAC; deacetylase; ETC; electron transport chain; ExT; endurance exe
Screening of MCAD deficiency in Japan: 16Â years' experience of enzymatic and genetic evaluation
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; MCAD; medium-chain acyl-CoA dehydrogenase; FAOD; fatty acid oxidation disorder; MS/MS; tandem mass spectrometry; NBS; newborn screening; DBS; dried blood specimen; MCAD deficiency; Tandem mass spectrometry; Newborn screening; Japanese; Non-Caucasian; Phen
cis-4-Decenoic and decanoic acids impair mitochondrial energy, redox and Ca2Â + homeostasis and induce mitochondrial permeability transition pore opening in rat brain and liver: Possible implications for the pathogenesis of MCAD deficiency
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; AA; antimycin A; ANT; adenine nucleotide translocator; ATC; atractyloside; BSA; bovine serum albumin; CCCP; carbonyl cyanide 3-chlorophenyl hydrazine; cDA; cis-4-decenoic acid; CsA; cyclosporin A; DA; decanoic acid; DC; decanoylcarnitine; EGTA; ethylene g
Hepatic SIRT1 Attenuates Hepatic Steatosis and Controls Energy Balance in Mice by Inducing Fibroblast Growth Factor 21
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; Liver-Specific Disruption of Sirt1; Hepatocyte-Derived Hormone; Metabolic Homeostasis; Obesity; Ad; adenovirus; BAT; brown adipose tissue; CPT1α; carnitine palmitoyltransferase 1α; FAS; fatty acid synthase; FGF21; fibroblast growth factor 21; MCAD; medi
MDG-1, a polysaccharide from Ophiopogon japonicus, prevents high fat diet-induced obesity and increases energy expenditure in mice
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; Ophiopogon japonicus; Polysaccharide; Anti-obesity; Energy expenditure; Diet induced obesity; Mitochondrial function; T2DM; type 2 diabetes mellitus; HFD; high fat diet; qPCR; quantitative real-time polymerase chain reaction; RER; respiratory exchange rat
Increased dietary fat contributes to dysregulation of the LKB1/AMPK pathway and increased damage in a mouse model of early-stage ethanol-mediated steatosis
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; ACC; acetyl CoA carboxylase; ALD; alcoholic liver disease; ALT; alanine aminotransferase; AMPK; AMP-activated protein kinase; ACLY; ATP citrate lyase; ChREBP; carbohydrate response element binding protein; CYP2E1; cytochrome p450 2E1; ELOVL5; fatty acid e
Enzymatically synthesized glycogen reduces lipid accumulation in diet-induced obese rats
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; ACC; acetyl-CoA carboxylase; ACO; acyl-CoA oxidase; cDNA; complementary DNA; CHL; cholesterol; CPT; carnitine palmitoyltransferase; CT; computed tomography; ESG; enzymatically synthesized glycogen; FAS; fatty acid synthase; HF; high fat; LCAD; long-chain
Mechanism of superoxide and hydrogen peroxide generation by human electron-transfer flavoprotein and pathological variants
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; ETF; electron transfer flavoprotein; QO; ubiquinone oxidoreductase; FAD; flavin adenine dinucleotide; AMP; adenosine monophosphate; SOR; superoxide reductase; SOD; superoxide dismutase; HRP; horseradish peroxidase; MCAD; medium-chain acyl-CoA dehydrogenas
Bio-informatics based analysis of genes implicated in alcohol mediated liver injury
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; (ATF4); Activating transcription factor 4; (ACOX); Acyl-CoA oxidase; (ADIPOR); Adiponectin; (ADH); Alcohol dehydrogenase; (ALDH); Aldehyde dehydrogenase; (ALAS1); 5-Aminolevulinic acid synthase-1; (ANXA2); Annexin A2; (APOB); Apolipoprotein B; (APOE); Apo
Lipid metabolism in mammalian tissues and its control by retinoic acid
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; ACC; acetyl-coA carboxylase; ACOX; acyl-CoA oxidase; AMPK; AMP-activated protein kinase; atRA; all-trans retinoic acid; BAT; brown adipose tissue; BCMO1; β,β-carotene monooxygenase 1; C/EBP; CCAAT-enhancer binding protein; CAC; carnitine/acylcarnitine c
Ammonium metabolism in humans
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; NH3; ammonia; NH4+; ammonium ions; AST; aspartate aminotransferase; ALT; alanine aminotransferase; BCAT; branched-chain amino acids aminotransferase; KGA; kidney-type glutaminase; GAC; glutaminase C; GAM; glutaminase M; GDH1; glutamate dehydrogenase-1; GD
Data mining methods for classification of Medium-Chain Acyl-CoA dehydrogenase deficiency (MCADD) using non-derivatized tandem MS neonatal screening data
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; Data mining; Rare diseases; MCADD; Medium-Chain Acyl-CoA dehydrogenase; Logistic regression;
Oleate-enriched diet improves insulin sensitivity and restores muscle protein synthesis in old rats
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; Aging; Nutrition; High-fat diet; Skeletal muscle; Protein synthesis; CPT-1b; carnitine palmitoyltransferase-1b; IR; insulin resistance; Il-1β; interleukin-1 beta; mTOR; mammalian target of rapamycin; MCAD; medium-chain acyl-CoA dehydrogenase; MPS; muscle
ESI-MS/MS measurement of free carnitine and its precursor γ-butyrobetaine in plasma and dried blood spots from patients with organic acidurias and fatty acid oxidation disorders
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; CPT; carnitine palmitoyltransferase; DBS; dried blood spots; FAOD; fatty acid oxidation disorder; IVA; isovaleric aciduria; GA-I; glutaric aciduria; LCHAD; long-chain 3-hydroxyacyl-CoA dehydrogenase; MA; malonic aciduria; MAD; multiple acyl-CoA dehydrogen
162nd ENMC International Workshop: Disorders of muscle lipid metabolism in adults 28-30 November 2008, Bussum, The Netherlands
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; CPT; carnitine palmitoyl transferase; ETF; electron transfer flavoprotein; ETF-QO; electron transfer flavoprotein ubiquinone-oxidoreductase; LCEH; long-chain-2-enoyl-CoA hydratase; LCHAD; long-chain-3-hydroxyacyl-CoA dehydrogenase; LCKAT; long-chain-3-ket
Chronic hypoxia- and cold-induced changes in cardiac enzyme and gene expression in CD-1 mice
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; Cardiac hypertrophy; Metabolic remodeling; Peroxisome proliferator-activated receptor α; Medium-chain acyl-CoA dehydrogenase; β-Hydroxyacyl-CoA dehydrogenase; Carnitine palmitoyltransferase I
Allelic diversity in MCAD deficiency: The biochemical classification of 54 variants identified during 5 years of ACADM sequencing
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; Medium-chain acyl-coA dehydrogenase; Fatty acid oxidation; Biochemical genetics; Gene sequencing; Variant of unknown significance; Newborn screening; In silico
Eicosapentaenoic acid improves hepatic steatosis independent of PPARα activation through inhibition of SREBP-1 maturation in mice
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; ACC; acetyl-CoA carboxylase; ALT; alanine aminotransferase; apo; apolipoprotein; AOX; acyl-CoA oxidase; AST; aspartate aminotransferase; CoA; coenzyme A; CPT-I; carnitine palmitoyl-CoA transferase-I; EPA; eicosapentaenoic acid; FA; fatty acid; FAS; fatty
Impact of short- and medium-chain organic acids, acylcarnitines, and acyl-CoAs onmitochondrial energy metabolism
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; CoA; coenzyme A; KGDHc; alpha-ketoglutarate dehydrogenase complex; PDHc; pyruvate dehydrogenase complex; DBH; decylubihydroquinone; TCA; tricarboxylic acid; SMOAA; short- and medium-chain organic acids, acylcarnitines, and acyl-CoAs; GCDH; glutaryl-CoA de
Healthcare Use and Costs of Medium-chain Acyl-Coa Dehydrogenase Deficiency in Australia: Screening Versus No Screening
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; ED; Emergency department; LOS; Length of stay; MCAD; Medium-chain acyl-CoA dehydrogenase; MS/MS; Tandem mass spectrometry;
The natural history of medium-chain acyl CoA dehydrogenase deficiency in the Netherlands: Clinical presentation and outcome
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; CPT; Carnitine palmitoyltransferase; CRF; Case record form; ECG; Electrocardiography; MCAD; Medium-chain acyl-CoA dehydrogenase; mFAO; Mitochondrial fatty acid oxidation;
Supplementation with α-linolenic acid-rich diacylglycerol suppresses fatty liver formation accompanied by an up-regulation of β-oxidation in Zucker fatty rats
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; ACAT; acyl-CoA carnitine acyltransferase; ACO; acyl-CoA oxidase; ALA; α-linolenic acid; ALADG; α-linolenic acid-rich diacylglycerol; ALATG; α-linolenic acid-rich triacylglycerol; DG; diacylglycerol; DGAT; diacylglycerol acyltransferase; DHA; docosahexa
Enzymatic diagnosis of medium-chain acyl-CoA dehydrogenase deficiency by detecting 2-octenoyl-CoA production using high-performance liquid chromatography: A practical confirmatory test for tandem mass spectrometry newborn screening in Japan
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; Medium-chain acyl-CoA dehydrogenase; Enzymatic assay; 2-Octenoyl-CoA; High-performance liquid chromatography; Tandem mass spectrometry; Newborn screening; Japanese;
Screening of newborns and high-risk group of children for inborn metabolic disorders using tandem mass spectrometry in South Korea: a three-year report
Keywords: زنجیره آلییل CoA dehydrogenase زنجیره متوسط; PA; propionyl-CoA carboxylase deficiency; MMA; methylmalonyl-CoA mutase deficiency; GA 1; glutaryl-CoA dehydrogenase deficiency; GA 2; multiple-CoA dehydrogenase deficiency; MCC; multiple-CoA carboxylase deficiency; HMG; 3-hydroxy-3-methylglutaryl-CoA lya