Keywords: Glucocerebrosidase deficiency; Lysosomal storage disease; Resting energy expenditure; Insulin resistance; High-density lipoprotein cholesterol; Hepatocellular carcinoma; Gaucher disease; ApoAI; apolipoprotein AI; ApoB; apolipoprotein B; ApoE; apolipoprote
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Keywords: NAFLD; nonalcoholic fatty liver disease; NASH; nonalcoholic steatohepatitis; FC; free cholesterol; VLDL; very low density lipoprotein; LDL; low density lipoprotein; mTOR; mechanistic target of rapamycin signaling; AMPK; AMP-activated protein kinase; TG; t
Keywords: Glutamine; TFEB; mTOR; Autophagy; Lysosomes;
Keywords: (BMM); bone marrow macrophage; (LROs); lysosome-related organelles; (M-CSF); macrophage-colony stimulating factor; (siRNA); small interfering RNA; (V-ATPase); vacuolar-type H+-ATPase.; Lysosomes; Osteoclasts; Osteoblast; RAB27A; TFEB;
Keywords: AraC; cytosine arabinoside; αSyn; α-synuclein; BSA; bovine serum albumin; Con; control; CQ; chloroquine; DIV; days in vitro; DMSO; dimethyl sulfoxide; E. coli; Escherichia coli; FBS; fetal bovine serum; GAPDH; glyceraldehyde 3-phosphate dehydrogenase; G
Keywords: Aβ; beta-amyloid peptide; AAV; adeno-associated virus; ABAD; amyloid-beta-binding alcohol dehydrogenase; AD; Alzheimer's disease; ALP; autophagy-lysosome pathways; Apaf-1; apoptic protease-activating factor 1; APP; amyloid precursor protein; AICD; APP in
Keywords: Stem cells; Heart failure; Lysosome; TFEB; Cell senescence;
Keywords: Lysosome; Endocytosis; Microglia; TFEB; MITF; Amyloid-beta; Alzheimer's disease;
Keywords: AbA; Aureobasidin A; ABC; ATP-binding cassette; AMPK; AMP-activated protein kinase; ATG; Autophagy-related; ATP; Adenosine triphosphate; C1P; Ceramide-1-phosphate; CERS; Ceramide synthase; CK2; Casein kinase II; CLS; Chronological lifespan; CMA; Chaperone
Keywords: ATGL; adipose triglyceride lipase; ATP-ase; adenosine tri-phosphatase; CD; carnitine deficiency; CK; creatine kinase; COX; cytochrome oxidase; CPT; carnitine-palmitoyl-transferase; DAPI; 4â²,6-diamidin-2-phenylindole; EMG; electromyography; ETF; electron
Keywords: Epidemiology; Single Nucleotide Polymorphisms; Colon Cancer; eQTL; CRC; colorectal cancer; CYP17A1; cytochrome P450, family 17, subfamily A, polypeptide 1; EIF3H; eukaryotic translation initiation factor 3, subunit H; eQTL; expression quantitative trait l
Keywords: Renal cell carcinoma; Chromosome translocation; TFE3; TFEB;
Keywords: ERK; extracellular signal regulated protein kinase; FoxO1/3; forkhead family transcription factor; GSK3; glycogen synthase kinase-3; HIF; hypoxia-inducible factor; IGF; insulin-like growth factor; IRE1; inositol-requiring protein 1; JNK; c-Jun N-terminal
Keywords: AD; Alzheimer's disease; ALS; amyotrophic lateral sclerosis; ANOVA; Analysis of variance; Aβ; amyloid β; bHLH; basic Helix-Loop-Helix; C4; complement C4; CLEAR; coordinated lysosomal expression and regulation; Cyba; cytochrome b-245 light chain; DW; d
Carcinoma de células renales asociado a amplificación del gen TFEB. Presentación de un caso y revisión de la literatura
Keywords: TFEB; Carcinoma de células renales; Cromosoma 6p; TFEB; Renal cell carcinoma; 6p cromosome;
A role for Glucagon-Like Peptide-1 in the regulation of β-cell autophagy
Keywords: Akt; protein kinase B; Ambra1; Autophagy And Beclin 1 Regulator 1; AMPK; 5â² AMP-activated protein kinase; Atg; autophagy related proteins; CAMKK; Ca2+/calmodulin-dependent protein kinase kinase; DFCP1; double FYVE-containing protein 1; DPP4; dipeptidyl
Arsenic trioxide induces autophagic cell death in osteosarcoma cells via the ROS-TFEB signaling pathway
Keywords: Arsenic trioxide; Autophagy; TFEB; Reactive oxygen species; Osteosarcoma;
6-Hydroxydopamine induces autophagic flux dysfunction by impairing transcription factor EB activation and lysosomal function in dopaminergic neurons and SH-SY5Y cells
Keywords: PD; Parkinson's disease; iPSC; induced pluripotent stem cells; 6-OHDA; 6-hydroxydopamine; DAT; dopamine transporter; ROS; reactive oxygen species; TUNEL; terminal deoxynucelotidyl transferase-mediated deoxyuridine triphosphate nick end labeling; CCK-8;
Current mechanistic insights into the CCCP-induced cell survival response
Keywords: CCCP, Carbonyl Cyanide m Chlorophenyl Hydrazone (PubChem CID: 2603); FCCP, Carbonyl Cyanide p Trifluoromethoxyphenylhydrazone (PubChem CID: 3330); N-Acetyl-l-cysteine (PubChem CID: 12035); Mitochondria; CCCP; NRF2; TFEB; Mitophagy;
STAT3 contributes to lysosomal-mediated cell death in a novel derivative of riccardin D-treated breast cancer cells in association with TFEB
Keywords: STAT3; signal transducers and activators of transcription 3; RD-N; Riccardin D-N; CTSB; cathepsin B; LMP; lysosomal membrane permeabilization; LAMP1; lysosome associated membrane protein 1; LM-PCD; lysosomal-mediated programme of cell death; AO; acridine
Apolipoprotein E4 inhibits autophagy gene products through direct, specific binding to CLEAR motifs
Keywords: Alzheimer's disease; APOE genotype; ApoE protein; autophagy; DNA binding; TFEB; Transcription; Protein aggregation; Molecular-dynamic simulation; EMSA; PLA;
Impaired TFEB-Mediated Lysosome Biogenesis and Autophagy Promote Chronic Ethanol-Induced Liver Injury and Steatosis in Mice
Keywords: Fatty Liver; Gene Regulation; Hepatic Protection; Mouse Model; Ad; adenovirus; AH; alcoholic hepatitis; ALD; alcoholic liver disease; ALT; alanine aminotransferase; ATP6V0E1; ATPase H+ transporting V0 subunit E1; ATP6V1D; ATPase H+ transporting V1 subunit
Silver nanoparticles induce lysosomal-autophagic defects and decreased expression of transcription factor EB in A549 human lung adenocarcinoma cells
Keywords: Silver nanoparticles; Lysosomal-autophagic defect; p62; LC3B-II; TFEB; A549 cells;
Bafilomycin A1 increases the sensitivity of tongue squamous cell carcinoma cells to cisplatin by inhibiting the lysosomal uptake of platinum ions but not autophagy
Keywords: Head and neck cancer; Chemotherapy resistance; Bafilomycin A1; Autophagy; Lysosome; TFEB;
FLCN: The causative gene for Birt-Hogg-Dubé syndrome
Keywords: AEC; alveolar epithelial type II cell; AKT; protein kinase B; AMPK/Ampk; 5â²-AMP activated protein kinase; AMPKα (also AAK-2); AMPKα subunit; ATP; adenosine triphosphate; Bcl-2; B-cell lymphoma 2; BHD; Birt-Hogg-Dubé; BAT; brown adipose tissue; C. ele
Autophagy in ischemic stroke
Keywords: 3-MA; 3-methyladenine; Aβ; amyloid β; AIF; apoptosis-inducing factor; Akt; protein kinase B; AMPK; AMP-activated protein kinase; ATF6; activating transcription factor 6; Atg; autophagy-related genes; ATP; adenosine 5â²-triphosphate; BBB; blood-brain ba
Transcription Factor EB Expression in Early Breast Cancer Relates to Lysosomal/Autophagosomal Markers and Prognosis
Keywords: Acidity; Breast cancer; Cathepsin D; LAMP2a; TFEB;
Modulation of proteostasis by transcription factor NRF2 and impact in neurodegenerative diseases
Keywords: α-SYN; alpha synuclein; β-TrCP; β-transducin repeat containing E3 ubiquitin protein ligase; Aβ; amyloid beta; AD; Alzheimer's disease; ALS; amyotrophic lateral sclerosis; AMPK; AMP-activated protein kinase; ARE; antioxidant response element; ASK1; apo
TFEB activation protects against cardiac proteotoxicity via increasing autophagic flux
Keywords: TFEB; mTOR; The autophagic-lysosomal pathway; Proteotoxicity; Misfolded proteins; Cardiomyocytes;
The cycloartane triterpenoid ADCX impairs autophagic degradation through Akt overactivation and promotes apoptotic cell death in multidrug-resistant HepG2/ADM cells
Keywords: 3-MA; 3-methyladenine; ADCX; 25-O-acetyl-7,8-didehydrocimigenol 3-O-beta-D-xylopyranoside; TCM; traditional Chinese medicine; HCC; hepatocellular carcinoma; ABC; ATP-binding cassette; ULK1; unc-51-like kinase 1; HCQ; hydroxychloroquine; CTSB; cathepsin B;
Happily (n)ever after: Aging in the context of oxidative stress, proteostasis loss and cellular senescence
Keywords: AD; Alzheimer's Disease;; AGEs; advanced glycation endproducts; ALP; autophagy-lysosome pathway; ARF; alternate reading frame; ATGs; autophagy-related proteins; BAG3; Bcl2-associated athanogene 3; Bcl-2; B-cell lymphoma 2; BrdU; 5-bromodeoxyuridine;; CMA;
Invited perspectivePPARα in lysosomal biogenesis: A perspective
Keywords: Lysosomal biogenesis; TFEB; Lipid metabolism; Fibrate drugs; PPARα;
Inhibition of mTOR improves the impairment of acidification in autophagic vesicles caused by hepatic steatosis
Keywords: Autophagy; Lysosome; Vacuolar-ATPase; Rapamycin; Analysis of variance; ANOVA; mammalian target of rapamycin; mTOR; nonalcoholic fatty liver disease; NAFLD; nonalcoholic steatohepatitis; NASH; endoplasmic reticulum; ER; green fluorescent protein; GFP; micr
HGSNAT has a TATA-less promoter with multiple starts of transcription
Keywords: HGSNAT; heparan-alpha-glucosaminide N-acetyltransferase; N-acetyltransferase; Acetyl-CoA:α-glucosaminide N-acetyltransferase; MPS IIIC; Mucopolysaccharidosis type IIIC; DS-ATG; downstream initiation codon; US-ATG; upstream initiation codon; TF; transcrip
TFEB regulates PER3 expression via glucose-dependent effects on CLOCK/BMAL1
Keywords: TFEB; PER3; CLOCK; BMAL1; Circadian rhythm
Increase of transcription factor EB (TFEB) and lysosomes in rat DRG neurons and their transportation to the central nerve terminal in dorsal horn after nerve injury
Keywords: DH; dorsal horn; DRG; dorsal root ganglion; IB4; Isolectin B4; Iba1; ionized calcium binding adapter molecule 1; IHC; immunohistochemistry; Neu-1; neuramidase-1; PB; phosphate buffer; PBS; phosphate-buffered saline; PFA; paraformaldehyde; RT; room tempera
Intracellular Ca2+ signaling and Ca2+ microdomains in the control of cell survival, apoptosis and autophagy
Keywords: Apoptosis; Autophagy; Endoplasmic reticulum; IP3 receptor; Lysosomes; Mitochondria; AMBRA1; autophagy/Beclin 1 regulator 1; AMPK; AMP-activated kinase; ATF4; activating transcription factor-4; Atg; autophagy-related; BIRD-2; Bcl-2/IP3R disruptor-2; CREB;
The Autophagy–Lysosomal Pathway in Neurodegeneration: A TFEB Perspective
Keywords: TFEB; autophagy–lysosomal pathway; neurodegenerative disease; prion disease
Glucolipotoxicity diminishes cardiomyocyte TFEB and inhibits lysosomal autophagy during obesity and diabetes
Keywords: ATGL; Adipose triglyceride lipase; CHOP; CCAAT-enhancer-binding protein homologous protein; CLEAR; coordinated lysosomal enhancement and regulation; CMA; chaperone mediated autophagy; CQ; chloroquine; eIF2α; eukaryotic translation initiation factor 2α;
Disorders of lysosomal acidification-The emerging role of v-ATPase in aging and neurodegenerative disease
Keywords: Lysosome; Acidification; pH; v-ATPase; Endocytosis; Autophagy; Lysosomal storage disease; Alzheimer's disease; Parkinson's disease; mTORC; Calcium; TFEB; Cathepsin; Caloric restriction;
Increased expression of transcription factor EB (TFEB) is associated with autophagy, migratory phenotype and poor prognosis in non-small cell lung cancer
Keywords: Lung cancer; TFEB; LAMP2a; Cathepsin D; Lysosomes; Autophagy;
Ambroxol-induced rescue of defective glucocerebrosidase is associated with increased LIMP-2 and saposin C levels in GBA1 mutant Parkinson's disease cells
Keywords: PD; Parkinson's disease; GD; Gaucher disease; GCase; glucocerebrosidase; Sap C; saposin C; PSAP; prosaposin; LIMP-2; lysosomal integral membrane 2; ER; endoplasmic reticulum; TFEB; transcription factor EB; GSK3; glycogen synthase kinase 3; UPS; ubiquitin
The MITF family of transcription factors: Role in endolysosomal biogenesis, Wnt signaling, and oncogenesis
Keywords: MITF; TFEB; TFE3; TFEC; Lysosome; Multivesicular bodies; Wnt/STOP; Melanoma; GSK3 inhibitors; Chloroquine;
A role for the autophagy regulator Transcription Factor EB in amiodarone-induced phospholipidosis
Keywords: Phospholipidosis; Amiodarone; Lysosomal enzymes; TFEB; Autophagy; Amiodarone (PubChem CID: 2157); Cimetidine (PubChem CID: 2756);
TNF compromises lysosome acidification and reduces α-synuclein degradation via autophagy in dopaminergic cells
Keywords: TNF; tumor necrosis factor-α; PD; Parkinson's disease; α-SYN; α-synuclein; DA; dopamine; CQ; chloroquine; CM; conditioned medium; LPS; lipopolysaccharide; CHX; cycloheximide; 3-MA; 3-methyladenine; tf-LC3; RFP-GFP-tandem fluorescent LC3; TFEB; transcri
Autophagy in neurodegenerative diseases: From pathogenic dysfunction to therapeutic modulation
Keywords: Aβ; amyloid beta; AD; Alzheimer's disease; ALS; amyotrophic lateral sclerosis; APP; amyloid precursor protein; ATP; adenosine triphosphate; Bci3; Bax cannel inhibitor 3; cAMP; cyclic adenosine monophosphate; CMA; chaperone-mediated autophagy; DLB; dement
MYC and metabolism on the path to cancer
Keywords: 2-DG; 2-deoxyglucose; 4E-BP; eIF4E-binding protein; 5,10-methylene THF; 5,10-methylenetetrahydrofolate; ACC; acetyl-CoA carboxylase; ACLY; ATP-citrate lyase; AMPK; AMP-activated protein kinase; ATP; adenosine triphosphate; ChIP-seq; chromatin immunoprecip
Regulation of autophagy: Modulation of the size and number of autophagosomes
Keywords: Ape1; aminopeptidase I; Atg; autophagy-related; ChIP; chromatin immunoprecipitation; Cvt; cytoplasm-to-vacuole targeting; TFEB; transcription factor EB; UPS; ubiquitin-proteasome system; Autophagy; Lysosome; Phagophore; Stress; Vacuole; Yeast;
mTOR and autophagy: A dynamic relationship governed by nutrients and energy
Keywords: Akt1; v-akt murine thymoma viral oncogene homolog 1; AMBRA; Autophagy/Beclin-1 regulator 1; AMPK; AMP-dependent protein kinase; ATG; autophagy-related; BECN1; beclin 1; DEPTOR; DEP domain containing mTOR-interacting protein; EGFR; epidermal growth factor
miR128 up-regulation correlates with impaired amyloid β(1-42) degradation in monocytes from patients with sporadic Alzheimer's disease
Keywords: Sporadic Alzheimer's disease; Lysosomal enzymes; Cathepsin B; miR-128; TFEB; Monocytes;